Flecked Retina Syndrome

Abstract

Fundi characterized by a limited or widespread distribution of deep yellowish or white lesions of various size and configuration without vascular and optic nerve abnormalities or pigment migration have been described under several diagnoses. These have included Hutchinson-Tay choroiditis,1macular degeneration of Holthouse-Batten,2,3Doyne's honeycombed degeneration,4malattia Levantinese,5fundus flavimaculatus,6fundus albipunctatus (stationary form of retinitis punctata albescens),7the speckled multicolored fundus,8the fleck retina9and a general category in which the deposits are called colloid bodies or drusen and are either widespread or limited to the posterior polar region.6Such ophthalmoscopic findings have also been described in some cases classified as hereditary macular degenerations. There are, however, only three characteristic fundi among all of these conditions, despite the multiple appellations. One type is seen only in fundus albipunctatus. In this condition there are white or yellow-white uniform dot-like lesions over