Requirement of argininosuccinate lyase for systemic nitric oxide production

Erez, Ayelet, Nagamani, Sandesh C S, Shchelochkov, Oleg A, Premkumar, Muralidhar H, Campeau, Philippe M, Chen, Yuqing, Garg, Harsha K, Li, Li +14 more·2011·Nature Medicine

DOI 10.1038/nm.2544

Cited by (233)

Items 101–200 of 233

Gas6/Axl is the sensor of arginine-auxotrophic response in targeted chemotherapy with arginine-depleting agents
W-B Tsai, Y Long, J-R Park, Jeffrey T. Chang, Hui Liu, Jaime Rodriguez‐Canales, Niramol Savaraj, Lynn G. Feun, Michael A. Davies, Ignacio Ivan Wistuba et al. · 2015 · Oncogene
l -Citrulline, But Not l -Arginine, Prevents Diabetes Mellitus–Induced Glomerular Hyperfiltration and Proteinuria in Rat
Patrik Persson, Angelica Fasching, Tom Teerlink, Peter Hansell, Fredrik Palm · 2014 · Hypertension
Free Radical Scavengers Prevent Argininosuccinic Acid-Induced Oxidative Stress in the Brain of Developing Rats: a New Adjuvant Therapy for Argininosuccinate Lyase Deficiency?
Bianca Seminotti, Janaína Camacho da Silva, Rafael Teixeira Ribeiro, Guilhian Leipnitz, Moaçir Wajner · 2019 · Molecular Neurobiology
Hepatic Suppression of Mitochondrial Complex II Assembly Drives Systemic Metabolic Benefits
Xueqiang Wang, Weiqiang Lv, Jie Xu, Adi Zheng, Mengqi Zeng, Ke Jiang Cao, Xun Wang, Yuting Cui, Hao Li, Meng Yang et al. · 2022 · Advanced Science
Argininosuccinate neurotoxicity and prevention by creatine in argininosuccinate lyase deficiency: An in vitro study in rat three‐dimensional organotypic brain cell cultures
Carmen Díez‐Fernández, Damian Hertig, Marc Loup, Gaëlle Diserens, Hugues Henry, Peter Vermathen, Jean‐Marc Nuoffer, Johannes Häberle, Olivier Braissant · 2019 · Journal of Inherited Metabolic Disease
ASL expression in ALDH1A1+ neurons in the substantia nigra metabolically contributes to neurodegenerative phenotype
Shaul Lerner, Raya Eilam, Lital N. Adler, Julien Baruteau, Topaz Kreiser, Michael Tsoory, Alexander S. Brandis, Tevie Mehlman, Mina Ryten, Juan Antonio Botía et al. · 2021 · Human Genetics
Sodium-Coupled Neutral Amino Acid Transporter 1 (SNAT1) Modulates L-Citrulline Transport and Nitric Oxide (NO) Signaling in Piglet Pulmonary Arterial Endothelial Cells
Anna Dikalova, Angela M. Fagiana, Judy Lynn Aschner, Michael Aschner, Marshall L Summar, Candice Denise Fike · 2014 · PLoS ONE
Biomarkers for liver disease in urea cycle disorders
Sandesh C.S. Nagamani, Saima Ali, Rima Izem, Deborah A. Schady, Prakash M. Masand, Benjamin L. Shneider, Daniel H. Leung, Lindsay Catherine Burrage · 2021 · Molecular Genetics and Metabolism
Insulin transcriptionally regulates argininosuccinate synthase to maintain vascular endothelial function
Ricci J. Haines, Karen D. Corbin, Laura C. Pendleton, Cynthia J. Meininger, Duane C. Eichler · 2012 · Biochemical and Biophysical Research Communications
Challenges, priorities and novel therapies for hypoxemic respiratory failure and pulmonary hypertension in the neonate
Judy Lynn Aschner, Jason Gien, Namasivayam Ambalavanan, John P. Kinsella, Girija Ganesh Konduri, Satyan Lakshminrusimha, Ola Didrik Saugstad, Robin Heise Steinhorn · 2016 · Journal of Perinatology
Pulmonary hypertension in the premature infant population: Analysis of echocardiographic findings and biomarkers
Michael Glenn O’Connor, Divya Suthar, Kimberly Vera, James C. Slaughter, Nathalie L. Maitre, Steven D. Steele, Amy B. Beller, Candice Denise Fike, Judy Lynn Aschner, Paul E. Moore et al. · 2017 · Pediatric Pulmonology
Probiotic strategies for mitigating heat stress effects on broiler chicken performance
Sadık Serkan AYDIN, Durmuş Hatipoğlu · 2024 · International Journal of Biometeorology
Disorders of the Urea Cycle and Related Enzymes
Johannes Häberle, Vicente Rubio · 2016 · Springer eBooks
The Association Between Concentrations of Arginine, Ornithine, Citrulline and Major Depressive Disorder: A Meta-Analysis
Mingyue Fan, Xiao Gao, Li Li, Zhongyu Ren, Leanna M.W. Lui, Roger S. McIntyre, Kayla M. Teopiz, Peng Deng, Bing Cao · 2021 · Frontiers in Psychiatry
NAGS, CPS1, and SLC25A13 (Citrin) at the Crossroads of Arginine and Pyrimidines Metabolism in Tumor Cells
Melissa Owusu-Ansah, Nikita Guptan, Dylon Alindogan, Michio Morizono, Ljubica Caldovic · 2023 · International Journal of Molecular Sciences
Genetic and functional correction of argininosuccinate lyase deficiency using CRISPR adenine base editors
Sami Jalil, Timo Keskinen, Juhana Juutila, Rocio Sartori-Maldonado, Liliya Euro, Anu Suomalainen, Risto Lapatto, Emilia Kuuluvainen, Ville Hietakangas, Timo Otonkoski et al. · 2024 · The American Journal of Human Genetics
Molecular characterization of argininosuccinate synthase and argininosuccinate lyase from the liver of the African lungfish Protopterus annectens, and their mRNA expression levels in the liver, kidney, brain and skeletal muscle during aestivation
You R. Chng, Jasmine L. Y. Ong, Biyun Ching, Xiu L. Chen, Wai Peng Wong, Shit F. Chew, Yuen K. Ip · 2014 · Journal of Comparative Physiology B
A global Slc7a7 knockout mouse model demonstrates characteristic phenotypes of human lysinuric protein intolerance
Bridget M. Stroup, Ronit Marom, Xiaohui Li, Chih‐Wei Hsu, Cheng-Yen Chang, Luan D. Truong, Brian Dawson, Ingo Grafe, Yuqing Chen, Ming‐Ming Jiang et al. · 2020 · Human Molecular Genetics
Unstable argininosuccinate lyase in variant forms of the urea cycle disorder argininosuccinic aciduria
Liyan Hu, Amit V. Pandey, Cécile Balmer, Sandra Eggimann, Véronique Rüfenacht, Jean‐Marc Nuoffer, Johannes Häberle · 2015 · Journal of Inherited Metabolic Disease
Progress toward improved therapies for inborn errors of metabolism
Virginia Maria Ginocchio, Nicola Brunetti‐Pierri · 2015 · Human Molecular Genetics
Prolonged hypoxia augments l-citrulline transport by System A in the newborn piglet pulmonary circulation
Candice Denise Fike, Marta Sidoryk‐Wȩgrzynowicz, Michael Aschner, Marshall L Summar, Lawrence S. Prince, Gary R. Cunningham, Mark R. Kaplowitz, Yongmei Zhang, Judy Lynn Aschner · 2012 · Cardiovascular Research
Chronic liver disease and impaired hepatic glycogen metabolism in argininosuccinate lyase deficiency
Lindsay Catherine Burrage, Simran Madan, Xiaohui Li, Saima Ali, Mahmoud Ali Mohammad, Bridget M. Stroup, Ming‐Ming Jiang, Racel Cela, Terry Bertin, Zixue Jin et al. · 2020 · JCI Insight
Optimizing therapy for argininosuccinic aciduria
Sandesh C.S. Nagamani, Brendan Lee, Ayelet Erez · 2012 · Molecular Genetics and Metabolism
Nitric Oxide and Lutein: Function, Performance, and Protection of Neural Tissue
James M. Stringham, Nicole Tressa Stringham · 2015 · Foods
Transcriptomic Analysis of Thalidomide Challenged Chick Embryo Suggests Possible Link between Impaired Vasculogenesis and Defective Organogenesis
Vimal Veeriah, Pavitra Kumar, Lakshmikirupa Sundaresan, Zeenath Mafitha, Ravi Kr Gupta, Uttara Saran, Jeganathan Manivannan, Suvro Chatterjee · 2017 · Chemical Research in Toxicology
Evidence for an arginine‐dependent route for the synthesis of NO in the model filamentous fungus Aspergillus nidulans
Antonio Franco‐Cano, Ana Teresa Marcos, Joseph Strauss, David Cánovas · 2021 · Environmental Microbiology
Assessment of Nitric Oxide Production in Mitochondrial Encephalomyopathy, Lactic Acidosis, and Stroke-Like Episodes Syndrome with the Use of a Stable Isotope Tracer Infusion Technique
Ayman W. El‐Hattab, Farook Jahoor · 2017 · Journal of Nutrition
Argininosuccinate lyase deficiency causes blood-brain barrier disruption via nitric oxide–mediated dysregulation of claudin expression
Jordan Kho, Urszula Polak, Ming‐Ming Jiang, John D. Odom, Jill V. Hunter, Saima Ali, Lindsay Catherine Burrage, Sandesh C.S. Nagamani, Robia G. Pautler, Hannah P. Thompson et al. · 2023 · JCI Insight
Severity-adjusted evaluation of liver transplantation on health outcomes in urea cycle disorders
Roland Posset, Sven F. Garbade, Florian Gleich, Svenja Scharré, Jürgen G. Okun, Andrea Lynne Gropman, Sandesh C.S. Nagamani, Ann‐Catrin Druck, Friederike Epp, Georg Friedrich Hoffmann et al. · 2023 · Genetics in Medicine
Urea Cycle Disorders
Nicholas Ah Mew, Maria Belen Pappa, Andrea Lynne Gropman · 2014 · Elsevier eBooks
Disorders of the Urea Cycle and Related Enzymes
Johannes Häberle, Vicente Rubio · 2022 · Springer eBooks
Cyclic adenosine monophosphate-induced argininosuccinate synthase 1 expression is essential during mouse decidualization
Zhu Huang, Tong-Song Wang, Yuechao Zhao, Ru-Juan Zuo, Wenbo Deng, Yu-Jing Chi, Zeng‐Ming Yang · 2014 · Molecular and Cellular Endocrinology
The Citrulline Recycling Pathway Sustains Cardiovascular Function in Arginine-Depleted Healthy Mice, but Cannot Sustain Nitric Oxide Production during Endotoxin Challenge
Yang Yuan, Mahmoud Ali Mohammad, Ancizar Betancourt, Inka C. Didelija, Chandrasekar Yallampalli, Juan C. Marini · 2018 · Journal of Nutrition
Understanding the Role of Argininosuccinate Lyase Transcript Variants in the Clinical and Biochemical Variability of the Urea Cycle Disorder Argininosuccinic Aciduria
Liyan Hu, Amit V. Pandey, Sandra Eggimann, Véronique Rüfenacht, Dorothea Möslinger, Jean‐Marc Nuoffer, Johannes Häberle · 2013 · Journal of Biological Chemistry
Arginine recycling in endothelial cells is regulated BY HSP90 and the ubiquitin proteasome system
Xiaomin Wu, Xutong Sun, Shruti Sharma, Qing Lü, Manivannan Yegambaram, Yali Hou, Ting Wang, Jeffrey R. Fineman, Stephen M. Black · 2020 · Nitric Oxide
Tetrahydrobiopterin Supplementation Improves Phenylalanine Metabolism in a Murine Model of Severe Malaria
Matthew S. Alkaitis, Hans Christian Ackerman · 2016 · ACS Infectious Diseases
A retrospective biochemical, molecular, and neurocognitive review of Saudi patients with argininosuccinic aciduria
Ruqaiah Altassan, Dalal Bubshait, Faiqa Imtiaz, Zuhair Abdalla Rahbeeni · 2018 · European Journal of Medical Genetics
Underlying antihypertensive mechanism of egg white-derived peptide QIGLF using renal metabolomics analysis
Zhipeng Yu, Mingjie Zhou, Jingbo Liu, Wenzhu Zhao · 2022 · Food Research International
ASL mRNA-LNP Therapeutic for the Treatment of Argininosuccinic Aciduria Enables Survival Benefit in a Mouse Model
Owen M. Daly, Azita J. Mahiny, Sara Majeski, Kevin McClintock, Julia Reichert, Gábor Boros, Gábor Tamás Szabó, Jonas Reinholz, Petra Schreiner, Steve Reid et al. · 2023 · Biomedicines
ASS1 deficiency is associated with impaired neuronal differentiation in zebrafish larvae
Marie J. Seidl, Svenja Scharré, Roland Posset, Ann‐Catrin Druck, Friederike Epp, Jürgen G. Okun, Bianca Dimitrov, Georg Friedrich Hoffmann, Stefan Kölker, Matthias Zielonka · 2023 · Molecular Genetics and Metabolism
Effects of almonds on ameliorating salt‐induced hypertension in dahl salt‐sensitive rats
Li Zeng, Zerong Liu, Luxin Zhou, Meng Chen, Xuewei Zheng, Pengfei Yang, Xinrui Zhao, Zhongmin Tian · 2021 · Journal of the Science of Food and Agriculture
30-year follow-up of a patient with classic citrullinemia
Nicola Brunetti‐Pierri, Kerri Lamance, Richard Alan Lewis, William James Craigen · 2012 · Molecular Genetics and Metabolism
mRNA therapy restores ureagenesis and corrects glutathione metabolism in argininosuccinic aciduria
Sonam Gurung, Oskar Vilhelmsson Timmermand, Dany P.B. Perocheau, Ana Luisa Gil-Martínez, Magdalena Minnion, Loukia Touramanidou, Sherry Fang, Martina Messina, Youssef Khalil, Abigail R. Barber et al. · 2022 · bioRxiv (Cold Spring Harbor Laboratory)
From the Inside Out: Exposing the Roles of Urea Cycle Enzymes in Tumors and Their Micro and Macro Environments
Emma Hajaj, Sabina Pozzi, Ayelet Erez · 2023 · Cold Spring Harbor Perspectives in Medicine
Vascular Metabolic Mechanisms of Pulmonary Hypertension
Xiao-fan Shi, Yun-chao Su · 2020 · Current Medical Science
Positive Clinical, Neuropsychological, and Metabolic Impact of Liver Transplantation in Patients With Argininosuccinate Lyase Deficiency
Barbara Siri, Benedetta Greco, Diego Martinelli, Sara Cairoli, Alessia Guarnera, Daniela Longo, Antonio Napolitano, Chiara Parrillo, Lucilla Ravà, Raffaele Simeoli et al. · 2025 · Journal of Inherited Metabolic Disease
Natural Product Chemistry for Nitric Oxide Based Therapeutics
Nathan S. Bryan · 2019 · Israel Journal of Chemistry
Inherited Metabolic Diseases
A. A. M. Morris · 2016
Challenges of experimental gene therapy for urea cycle disorders
Hiu Man Viecelli, Beat Thöny · 2014 · Zurich Open Repository and Archive (University of Zurich)
The incidence of movement disorder increases with age and contrasts with subtle and limited neuroimaging abnormalities in argininosuccinic aciduria
Sonam Gurung, Saketh R. Karamched, Dany P.B. Perocheau, Kiran K. Seunarine, Tomas Baldwin, Haya Alrashidi, Loukia Touramanidou, Claire E. Duff, Nour M. Elkhateeb, Karolina M. Stępień et al. · 2023 · Journal of Inherited Metabolic Disease
Nitrite-NO bailout for a NOS complex too big to fail
Mark T. Gladwin, Jesús Tejero · 2011 · Nature Medicine
Amino Acids as Biomarker Candidates for Suicidality in Male OEF/OIF Veterans: Relevance to NMDA Receptor Modulation and Nitric Oxide Signaling
Steven T. Szabo, Jason D. Kilts, Jennifer C. Naylor, Nagy A. Youssef, Jennifer L. Strauss, Rajendra A. Morey, Mira Brancu, Robert M. Hamer, Daniel W. Bradford, VA Mid-Atlantic MIRECC Work Group et al. · 2014 · Military Medicine
Mass Spectrometry Analysis of Shark Skin Proteins
Etty Bachar-Wikström, Braham Deep Singh Dhillon, Navi Gill Dhillon, Lisa A. Abbo, Sara K. Lindén, Jakob D. Wikström · 2023 · International Journal of Molecular Sciences
Impact of supplementation with L-citrulline/arginine after liver transplantation in individuals with Urea Cycle Disorders
Roland Posset, Sven F. Garbade, Florian Gleich, Sandesh C.S. Nagamani, Andrea Lynne Gropman, Friederike Epp, Nesrine Ramdhouni, Ann‐Catrin Druck, Georg Friedrich Hoffmann, Stefan Kölker et al. · 2023 · Molecular Genetics and Metabolism
Ex vivo precision-cut liver slices model disease phenotype and monitor therapeutic response for liver monogenic diseases
Dany P.B. Perocheau, Sonam Gurung, Loukia Touramanidou, Claire E. Duff, Garima Sharma, Neil James Sebire, Patrick F. Finn, Alex Cavedon, Summar Siddiqui, Lisa M. Rice et al. · 2024 · F1000Research
Arginine metabolism of Arabidopsis thaliana is modulated by Heterodera schachtii infection
Shahbaz Anwar, Erich Inselsbacher, Florian M. W. Grundler, Julia P. Hofmann · 2015 · Nematology
Autophagy-urea cycle pathway is essential for the statin-mediated nitric oxide bioavailability in endothelial cells
Wen‐Hua Chen, Bei‐Chia Guo, Chia‐Hui Chen, Man‐Chen Hsu, Chih‐Hsien Wang, Tzong‐Shyuan Lee · 2023 · Journal of Food and Drug Analysis
Intérêts potentiels de la citrulline en réanimation
Luc Cynober · 2013 · Réanimation
Nitric Oxide Signaling in Health and Disease
Nathan S. Bryan, Jack R. Lancaster · 2011 · Humana Press eBooks
Of Mice, Whales, Jellyfish and Men: In Pursuit of Increased Longevity
Paul C. Guest · 2019 · Advances in experimental medicine and biology
Clinical and structural insights into potential dominant negative triggers of proximal urea cycle disorders
Georgios Makris, Matthias Lauber, Véronique Rüfenacht, Corinne Gemperle-Britschgi, Carmen Díez‐Fernández, Ljubica Caldovic, D. Sean Froese, Johannes Häberle · 2020 · Biochimie
High blood pressure, a red flag for the neonatal manifestation of urea cycle disorders
Ulrike Teufel, Peter Burgard, Jochen Meyburg, Martin S. Lindner, Johannes Poeschl, Peter Ruef, Georg Friedrich Hoffmann, Stefan Kölker · 2019 · Orphanet Journal of Rare Diseases
Hair Disorders
Elise A. Olsen, Matilde Iorizzo · 2019 · Harper's Textbook of Pediatric Dermatology
Arabidopsis Argininosuccinate Lyase and Argininosuccinate Synthase are important for resistance against Pseudomonas syringae
Shahbaz Anwar, Muhammad Amjad Ali, Amjad Abbas, Krzysztof Wieczorek · 2019 · Advancements in Life Sciences (University of the Punjab)
Nitric Oxide Signaling in Health and Disease
Nathan S. Bryan, Jack R. Lancaster · 2017 · Springer eBooks
Ex vivo precision-cut liver slices model disease phenotype and monitor therapeutic response for liver monogenic diseases
Dany P.B. Perocheau, Sonam Gurung, Loukia Touramanidou, Claire E. Duff, Garima Sharma, Neil James Sebire, Patrick F. Finn, Alex Cavedon, Summar Siddiqui, Lisa M. Rice et al. · 2023 · F1000Research
Male hypercalciuric stone formers with low renal calcium reabsorption
Valerie Walker, Paul R. Cook, Damian Gerard Griffin · 2013 · Journal of Clinical Pathology
Cellular transport of l -arginine determines renal medullary blood flow in control rats, but not in diabetic rats despite enhanced cellular uptake capacity
Patrik Persson, Angelica Fasching, Tom Teerlink, Peter Hansell, Fredrik Palm · 2016 · American Journal of Physiology-Renal Physiology
Pathway Analysis of a Transcriptome and Metabolite Profile to Elucidate a Compensatory Mechanism for Taurine Deficiency in the Heart of Taurine Transporter Knockout Mice
Takashi Ito, Shigeru Murakami, Stephen W. Schaffer · 2018 · J — Multidisciplinary Scientific Journal
Arginase II: Atherogenesis Beyond Enzyme Activity
Deepesh Pandey, Lewis H. Romer, Dan E. Berkowitz · 2013 · Journal of the American Heart Association
Adaptive Responses of Large Yellow Croaker Larimichthys crocea to Ocean Acidification: Integrative Analysis of Gill and Kidney Transcriptomics and Antioxidant Enzyme Activities
Ting Ye, Xiaoyan Zhang, Feng Liu, Xiao Liang, Dandan Guo, Bao Lou, Zhigang Xie · 2025 · Antioxidants
Predicting epistasis across proteins by structural logic
Michelle Tang, Gareth A. Cromie, Anowarul Kabir, Martin S. Timour, Julee Ashmead, Russell S. Lo, Nathaniel Corley, Frank DiMaio, Hiroki Morizono, Ljubica Caldovic et al. · 2026 · Proceedings of the National Academy of Sciences
Normothermic Machine Perfusion of Explanted Human Metabolic Livers: A Proof of Concept for Studying Inborn Errors of Metabolism
Samira Safarikia, Riccardo Cirelli, Gionata Spagnoletti, Diego Martinelli, Giulia Bravetti, Paola Francalanci, Annamaria D’Alessandro, Giovina Di Felice, Marta Maistri, Elena Baldissone et al. · 2025 · Journal of Inherited Metabolic Disease
Pegylated arginine deiminase depletes plasma arginine but maintains tissue arginine availability in young pigs
Mahmoud Ali Mohammad, Inka C. Didelija, Barbara Stoll, Trung C. Nguyen, Juan C. Marini · 2021 · American Journal of Physiology-Endocrinology and Metabolism
Current Treatment Modalities for Urea Cycle Disorders
Nicholas Ah Mew, Uta Lichter‐Konecki · 2025 · Pediatric Drugs
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Arginine amino acid, nano particles of zinc oxide, and stock density: Effect on growth performance, intestinal morphology, blood indices, and meat quality in broiler chickens
K. Bahrampour, Nazar Afzali, Seyyed Javad Hosseini-Vashan · 2025 · Poultry Science
Severity-adjusted evaluation of initial dialysis on short-term health outcomes in urea cycle disorders
Matthias Zielonka, Stefan Kölker, Sven F. Garbade, Florian Gleich, Sandesh C. Sreenath Nagamani, Andrea Lynne Gropman, Ann‐Catrin Druck, Nesrine Ramdhouni, Laura Göde, Georg Friedrich Hoffmann et al. · 2024 · Molecular Genetics and Metabolism
The Influence of Kidney Disease on Protein and Amino Acid Metabolism
Biruh Workeneh, William E. Mitch · 2012 · Elsevier eBooks
Orphan drugs in development for urea cycle disorders: current perspectives
Johannes Häberle, Shawn E. McCandless · 2014 · Orphan Drugs Research and Reviews
Auxotrophy-Based Detection of Hyperornithinemia in Mouse Blood and Urine
Kenneth M. Palanza, Alex V. Nesta, Renukanandan Tumu, Cherie M. Walton, Michael A. Davis, Thomas R. King · 2016 · Journal of Inborn Errors of Metabolism and Screening
Inherited hyperammonemias: a Contemporary view on pathogenesis and diagnosis
Evelina Maines, Giovanni Piccoli, Antonia Pascarella, Francesca Colucci, Alberto Burlina · 2017 · Expert Opinion on Orphan Drugs
Evolutionary conserved multifunctional nitric oxide synthesis proteins responding to bacterial MAMPs are located at the endoplasmic reticulum
Wenhui Zheng, Hongchen Li, Wenqin Fang, SIMON V. S. IPCHO, Rosanna C. Hennessy, Bjoern Oest Hansen, Guodong Lu, Zonghua Wang, Mari‐Anne Newman, Stefan Olsson · 2020 · bioRxiv (Cold Spring Harbor Laboratory)
Construction of Artificial Cells with Urea Cycle Pathway for Ammonia Detoxification
Tongtong Ren, Dongliang Liu, Jingjing Zhao, Wenxia Xu, Shubin Li, Weichen Wang, Xiangxiang Zhang, Changxin Shi, Xiaojun Han · 2025 · Angewandte Chemie International Edition
Arginine Supplementation in Cardiovascular Disorders
Robert Fried · 2014 · Elsevier eBooks
Production of NO – The l-arginine/NOS/NO System
Bindu Diana Paul, Solomon H. Snyder · 2018 · Royal Society of Chemistry eBooks
Characterisation of risk factors for stones in hyperuricosuric men attending a stone clinic
Valerie Walker, Paul R. Cook, Damian Gerard Griffin · 2014 · Urolithiasis
Atrioventricular block in siblings with argininosuccinic aciduria
Özgür Ulaş Özcan, Sibel Turhan, Veysel Kutay Vurgun, Çetin Erol · 2015 · International Journal of Cardiology
Late‐onset argininosuccinic aciduria in a 72‐year‐old man presenting with fatal hyperammonemia
Laurent Leuger, Xavier Dieu, Juan Manuel Chao de la Barca, Mikael Moriconi, Guillaume Halley, Xavier Donin de Rosière, Pascal Reynier, Delphine Mirebeau‐Prunier, Chadi Homedan · 2021 · JIMD Reports
Causal Links Between Cerebrospinal Fluid Metabolites and Postpartum Depression: A Bidirectional Mendelian Randomization Study
Yanxi Long, Hui Liu, Rumeng Ban, Zifeng Xu, Tao Xu · 2025 · International Journal of Women s Health
Impact of long-term nitrogen scavenger therapy on clinical outcome in individuals with urea cycle disorders
Roland Posset, Friederike Epp, Sven F. Garbade, Florian Gleich, Andrea L. Gropman, Sandesh C.S. Nagamani, Georg Friedrich Hoffmann, Stefan Kölker, Matthias Zielonka · 2026 · Scientific Reports
Regulation of Inducible Nitric Oxide Synthase (NOS2) Expression in Healthy and Inflamed Bowel: A Narrative Review
Małgorzata Krzystek‐Korpacka, Andrzej Korpacki, Adam Wąsowicz, Katarzyna Neubauer · 2026 · International Journal of Molecular Sciences
Effects of laminar shear stress versus resveratrol on the citrulline-NO cycle in endothelial cells
Sue Im Jang, Yong Chool Boo · 2013 · Advances in Biological Chemistry
Hydrogen sulfide: in the aftermath of argininosuccinate lyase and nitric oxide deficiency
Balasubramanian Srilatha, Jun Meng, P. Ganesan Adaikan · 2012 · Genetics in Medicine
Potential interests of citrulline in critically ill patients
Luc Cynober · 2013
Mechanisms of l-Arginine-Auxotrophic Response and Their Cancer Therapeutic Implications
Wen-Bin Tsai, Yan Long, Niramol Savaraj, Lynn G. Feun, Macus Tien Kuo · 2016 · Springer eBooks
Coronary Vasospasm in a Patient With Argininosuccinic Aciduria
Yasuhiro Nagayoshi, Masafumi Nakayama, Haruka Nagano, Kei Morikawa, Masato Nishi, Taiki Nishihara, Naritsugu Sakaino, Hiroaki Kawano, Kenichi Tsujita, Hiroshi Mitsubuchi · 2023 · The American Journal of Cardiology
Nitric oxide is required for lung alveolarization revealed by deficiency of argininosuccinate lyase
Zixue Jin, Ming‐Ming Jiang, Brendan Lee · 2023 · Human Molecular Genetics
The bottlenose dolphin (Tursiops truncatus): a novel model for studying healthy arterial aging
Yara Bernaldo de Quirós, Sophia A. Mahoney, Nicholas S. VanDongen, Nathan Greenberg, Ravinandan Venkatasubramanian, Pedro Saavedra, Gregory D. Bossart, Vienna Elizabeth Brunt, Zachary Stephen Clayton, Antonio Fernández et al. · 2024 · American Journal of Physiology-Heart and Circulatory Physiology
Response to Srilatha et al.
Sandesh C.S. Nagamani, Ayelet Erez, Brendan Lee · 2012 · Genetics in Medicine