Tetrahydrobiopterin: biochemistry and pathophysiology
Werner, Ernst R., Blau, Nenad, Thöny, Beat·2011·Biochemical Journal
Cites (228)
Items 201–226 of 226
- Glyceryl ether monooxygenase resembles aromatic amino acid hydroxylases in metal ion and tetrahydrobiopterin dependenceKatrin Watschinger, Markus Andreas Keller, Albin Hermetter, Georg Golderer, Gabriele Werner‐Felmayer, Ernst R. Werner · 2008 · Biological Chemistry
- Cellular accumulation of tetrahydrobiopterin following its administration is mediated by two different processes; direct uptake and indirect uptake mediated by a methotrexate-sensitive processKeiko Sawabe, Yasuko Suetake, Nobuo Nakanishi, Kazunori Osuke Wakasugi, Hiroyuki Hasegawa · 2005 · Molecular Genetics and Metabolism
- Cerebrospinal fluid biopterin and biogenic amine metabolites during oral R-THBP therapy for infantile autismKomori, Hironori, Matsuishi, Toyojiro, Yamada, Shigeto, Yamashita, Yushiro, Ohtaki, Etsuo, Kato, Hirohisa · 1995 · Journal of Autism and Developmental Disorders
- Tetrahydrobiopterin Binding to Aromatic Amino Acid Hydroxylases. Ligand Recognition and SpecificityKnut Teigen, Khanh Kim Dao, Jeffrey A. McKinney, Antonius C.F. Gorren, Bernd Mayer, Nils Åge Frøystein, Jan Haavik, Aurora Martı́nez · 2004 · Journal of Medicinal Chemistry
- Phenylketonuria and BH4 DeficienciesNenad Blau, Alberto Burlina, Barbara K. Burton, Harvey L. Levy, Nicola Longo, Anita MacDonald, Aurora Martı́nez, Francjan J. van Spronsen, Beat Thöny · 2010
- The Mechanism of Cofactor Regeneration During Phenylalanine HydroxylationSteven Bailey, Scott R. Boerth, Shirley B. Dillard, June E. Ayling · 1993 · Advances in experimental medicine and biology
- Over-expression of GTP-cyclohydrolase 1 feedback regulatory protein attenuates LPS and cytokine-stimulated nitric oxide productionManasi Nandi, Peter D. Kelly, Patrick J. Vallance, JAMES M. LEIPER · 2008 · Vascular Medicine
- Transcellular relocation of tetrahydrobiopterin across Caco‐2 cells: A model study of tetrahydrobiopterin absorption through epithelial cells of intestinal mucosaAkiko Ohashi, M. Fukumuro, Keiko Sawabe, Kaori Mamada, Y. Sugawara, Hiroshi Matsuoka, Hiroyuki Hasegawa · 2008 · Journal of Inherited Metabolic Disease
- Tetrahydrobiopterin in intestinal lumen: Its absorption and secretion in the small intestine and the elimination in the large intestineKeiko Sawabe, Yusuke Saeki, Akiko Ohashi, Kaori Mamada, K. O. Wakasugi, Hiroshi Matsuoka, Hiroyuki Hasegawa · 2008 · Journal of Inherited Metabolic Disease
- Tetrahydrobiopterin Attenuates Microvascular Reperfusion Injury Following Murine Pancreas TransplantationManuel Maglione, Martin Hermann, Paul Hengster, Stefan Schneeberger, Walter Mark, Peter Obrist, Gabriele Werner‐Felmayer, Ernst R. Werner, R. Margreiter, Gerald Brandacher · 2006 · American Journal of Transplantation
- Role of tetrahydrobiopterin in resistance to myocardial ischemia in Brown Norway and Dahl S ratsJianzhong An, Jianhai Du, Na Wei, Hao Xu, Kirkwood A. Pritchard, Yang Shi · 2009 · American Journal of Physiology-Heart and Circulatory Physiology
- Stereospecificity and Catalytic Function of Histidine Residues in 4a-Hydroxy-tetrahydropterin Dehydratase/DCoHIgor Rebrin, Beat Thöny, Steven Bailey, June E. Ayling · 1998 · Biochemistry
- The Aromatic Amino Acid Hydroxylase Mechanism: A Perspective From Computational ChemistryElaine Olsson, Knut Teigen, Aurora Martı́nez, Vidar Remi Jensen · 2010 · Advances in inorganic chemistry
- Examination of tetrahydrobiopterin pathway genes in autismNathalie C. Schnetz‐Boutaud, Bernard M. Anderson, K. D. Brown, H. H. Wright, Ruth K. Abramson, Michael L. Cuccaro, John R. Gilbert, Margaret Ann Pericak‐Vance, Jonathan L. Haines · 2009 · Genes Brain & Behavior
- Accumulated BH4 in mouse liver caused by administration of either 6R- or 6SBH4 consisted solely of the 6R-diastereomer: Evidence of oxidation to BH2 and enzymic reductionKeiko Sawabe, Yasuko Suetake, Kazunori Osuke Wakasugi, Hiroyuki Hasegawa · 2005 · Molecular Genetics and Metabolism
- Beneficial effect of tetrahydrobiopterin on the survival of rats exposed to hepatic ischemia-reperfusion injuryYuzuru Hara, Kennichi Teramoto, Yuji Kumashiro, E. Sato, N. Nakamura, S. Takatsu, T. Kawamura, Shigeki Arii · 2005 · Transplantation Proceedings
- The effect of insufficiency of tetrahydrobiopterin on endothelial function and vasoactivitySatoshi Yamashiro, Yukio Kuniyoshi, Katsuya Arakaki, Kazufumi Miyagi, Kageharu Koja · 2002 · The Japanese Journal of Thoracic and Cardiovascular Surgery
- Effects of tetrahydrobiopterin on nitric oxide bioavailability and renal hemodynamics in healthy volunteersFerruh Artunç, Michael Essig, Nilguen Artunc, Claudia Plachtzik, Michael Reich, Gabriele Boehmer, Hans-Ulrich Haering, Christiane Martina Myrtle Erley, Teut Risler · 2008 · Journal of Nephrology
- Cardiac myocyte-specific overexpression of human GTP cyclohydrolase I protects against acute cardiac allograft rejectionIrina A. Ionova, Jeannette M. Vasquez-Vivar, Brian C. Cooley, Ashwani K. Khanna, Jennifer Whitsett, Anja M. Herrnreiter, Raymond Q. Migrino, Zhi‐Dong Ge, Kevin R. Regner, Keith M. Channon et al. · 2010 · American Journal of Physiology-Heart and Circulatory Physiology
- An important role of increase in tetrahydrobiopterin via H2O2–JAK2 signalling pathway in late phase of ischaemic preconditioningToshihito Hiroi, Teruaki Wajima, Yuji Kaneko, Yuji Kiuchi, Shunichi Shimizu · 2010 · Experimental Physiology
- Possible involvement of tetrahydrobiopterin in the trophic effect of insulin-like growth factor-1 on rat pheochromocytoma-12 (PC12) cellsJunko Tanaka, Kunio Koshimura, Yoshio Murakami, Yuzuru Kato · 2002 · Neuroscience Letters
- TETRAHYDROBIOPTERIN METABOLISM IN DOWN'S SYNDROME AND IN NON‐DOWN'S SYNDROME MENTAL RETARDATIONA. A. Aziz, J.A. Blair, R.J. Leeming, Peter E. Sylvester · 1982 · Journal of Intellectual Disability Research
- Effects of tetrahydrobiopterin on venous bubble grade and acute diving‐induced changes in cardiovascular functionDuška Glavaš, Darija Baković, Ante Obad, Ivan Palada, Toni Brešković, Zoran Valić, Alf O. Brubakk, Željko Dujić · 2008 · Clinical Physiology and Functional Imaging
- 8-Azaguanosine-5′-monophosphate synthesis via nucleoside kinase in cultured chinese hamster lung fibroblastsMaria Grazia Tozzi, Marcella Camici, Valeria Falcone, Maura Turriani, Gino Turchi, Pier Luigi Ipata · 1989 · Biochemical and Biophysical Research Communications
- Murine models of inherited monoaminergic and GABAergic neurotransmitter disordersBeat Thöny, K. Michael Gibson · 2006 · Future Neurology
- DIHYDROFOLATE REDUCTASE CATALYZES THE REDUCTION OF 7,8-DIHYDROBIOPTERIN IN LIVER AND BRAINSheldon Milstien, Seymour Kaufman · 1983 · De Gruyter eBooks