A Novel Protective Prion Protein Variant that Colocalizes with Kuru Exposure
Mead, Simon, Whitfield, Jerome, Poulter, Mark, Shah, Paresh, Uphill, James, Campbell, Tracy, Al-Dujaily, Huda, Hummerich, Holger +6 more·2009·New England Journal of Medicine
Cited by (205)
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- Leveraging the dominant-negative effect of the kuru-protective G127V prion protein variant as a novel therapeutic strategyJean R.P. Gatdula, Isabel C. Orbe, Samantha G Tolton et al. · 2026 · bioRxiv (Cold Spring Harbor Laboratory)
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- A self-complementary recombinant adeno-associated virus vector coding for an anchorless prion protein carrying the G127V mutation extends survival in a rodent prion disease modelThomas Zerbes, Claire E. Verkuyl, Cunjie Zhang, Sophie Grunnesjoe, Shehab Eid, Hamza Arshad, Wenda Zhao, Zahra Nasser, Teaghan O’Shea, Ari Bel et al. · 2026 · PLoS Pathogens
- Cofactor Involvement in Prion PropagationSurachai Supattapone, Michael B. Miller · 2012 · Springer eBooks
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- Kuru, the first prion disease: a travel back in time from Papua New Guinea to Neanderthals extinctionPawel Piotr Liberski · 2013 · DOAJ (DOAJ: Directory of Open Access Journals)
- Biophysical characterization of oligomerization and fibrillization of the G131V pathogenic mutant of human prion proteinMeilan Zhang, Haoran Zhang, Hongwei Yao · 2019 · Acta Biochimica et Biophysica Sinica
- The first step towards the development of an electrophoretic prion detectorClaudia Avis Madampage · 2011 · University Library - University of Saskatchewan (University of Saskatchewan)
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- Zur Grenze von Leben gegenüber dem Unbelebten: PrionenManfred Spitzer · 2011
- A Novel Protective Prion Protein Variant that Colocalizes with Kuru ExposureDiederik van de Beek · 2010 · Yearbook of Neurology and Neurosurgery
- Kuru Susceptibility GeneticsMichael D. Geschwind · 2010 · Journal watch
- Anthropological Methods Used in Kuru ResearchShirley Lindenbaum · 2017 · Neuromethods
- Kuru: Introduction to Prion DiseasesPawel Piotr Liberski, Agata Gajos · 2017 · Neuromethods
- The Prion DiseasesPatrick Alfryn Lewis, Jennifer E. Spillane · 2018 · Elsevier eBooks
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- Genetic mutation blocks prion diseaseBoer Deng · 2015 · Nature
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- Transgenic Mouse Models of Prion DiseasesJulie A. Moreno, Glenn C. Telling · 2017 · Neuromethods
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- KuruM.A. Ferguson-Smith · 2013 · Elsevier eBooks
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- Doenças priônicas neurodegenerativas humanas: o que sabemos e sua epidemiologia no BrasilMitzy Stephanny Machado, André Valério da Silva, Juliano Yasuo Oda, Aline Rafaela da Silva Rodrigues Machado, Alex Martins Machado · 2022 · Research Society and Development
- Cofactor Involvement in Prion PropagationSurachai Supattapone, Michael B. Miller · 2023 · Springer eBooks
- The Evolutionary Puzzle of Human TwinshipAugusto Dalla Ragione, Cody T. Ross, Daniel Redhead · 2023
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- Additional file 1 of Four types of scrapie in goats differentiated from each other and bovine spongiform encephalopathy by biochemical methodsJan Langeveld, Laura Pirisinu, Jorg G Jacobs et al. · 2020 · Figshare
- Additional file 3 of Stability of BSE infectivity towards heat treatment even after proteolytic removal of prion proteinJan Langeveld, Anne Balkema‐Buschmann, Becher, Dieter et al. · 2021 · Figshare
- Additional file 5 of Four types of scrapie in goats differentiated from each other and bovine spongiform encephalopathy by biochemical methodsJan Langeveld, Laura Pirisinu, Jorg G Jacobs et al. · 2020 · Figshare
- Additional file 6 of Four types of scrapie in goats differentiated from each other and bovine spongiform encephalopathy by biochemical methodsJan Langeveld, Laura Pirisinu, Jorg G Jacobs et al. · 2020 · Figshare
- Additional file 2 of Four types of scrapie in goats differentiated from each other and bovine spongiform encephalopathy by biochemical methodsJan Langeveld, Laura Pirisinu, Jorg G Jacobs et al. · 2020 · Figshare
- Additional file 1 of Stability of BSE infectivity towards heat treatment even after proteolytic removal of prion proteinJan Langeveld, Anne Balkema‐Buschmann, Becher, Dieter et al. · 2021 · Figshare
- Additional file 3 of Four types of scrapie in goats differentiated from each other and bovine spongiform encephalopathy by biochemical methodsJan Langeveld, Laura Pirisinu, Jorg G Jacobs et al. · 2020 · Figshare
- Additional file 4 of Four types of scrapie in goats differentiated from each other and bovine spongiform encephalopathy by biochemical methodsJan Langeveld, Laura Pirisinu, Jorg G Jacobs et al. · 2020 · Figshare
- Additional file 2 of Stability of BSE infectivity towards heat treatment even after proteolytic removal of prion proteinJan Langeveld, Anne Balkema‐Buschmann, Becher, Dieter et al. · 2021 · Figshare
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