Iron-Dependent Self-Assembly of Recombinant Yeast Frataxin: Implications for Friedreich Ataxia

Adamec, Jiri, Rusnak, Frank, Owen, Whyte G., Naylor, Stephen, Benson, Linda M., Gacy, A. Marquis, Isaya, Grazia·2000·The American Journal of Human Genetics

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  11. 2003 International Friedreich's Ataxia Research Conference, 14–16 February 2003, Bethesda, MD, USA
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  23. Efficacy and Safety of Idebenone in the Treatment of Friedreich Ataxia: A Review of Early Results and Future Prospects
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  24. Iron Citrate Toxicity Causes aco1Δ-induced mtDNA Loss in Saccharomyces cerevisiae
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  25. Investigation into the rate-determining step of mammalian heme biosynthesis: Molecular recognition and catalysis in 5-aminolevulinate synthase
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  26. Using Comparative Genome Analysis to Find Interaction Partners for Frataxin
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  32. Alterations of mitochondrial biogenesis and alterations of mitochondrial antioxidant defense in Friedreich's ataxia
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  36. Estudio de la desnaturalización en frío de proteínas mediante simulaciones computacionales
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  40. Function of IscA in biogenesis of Iron-sulfur clusters and repair of NO-modified iron-sulfur proteins
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  41. Friedreich's ataxia and other autosomal recessive ataxias
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  42. Genetic and Physiological Studies in Friedreich's Ataxia
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  43. Functional characterization of Frataxin isoforms and mechanisms of regulation of frataxin expression
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  46. Chapter Frataxin: An Unusual Metal-Binding Protein in Search of a Function
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