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SUBACUTE SPONGIFORM ENCEPHALOPATHY (CREUTZFELDT-JAKOB DISEASE): THE NATURE AND PROGRESSION OF SPONGIFORM CHANGE
Abstract
c.L. MASTERS, E.P. RICHARDSON, JR.; SUBACUTE SPONGIFORM ENCEPHALOPATHY (CREUTZFELDT-JAKOB DISEASE): THE NATURE AND PROGRESSION OF SPONGIFORM CHANGE, Brain,
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“Prion diseases are a group of chronic transmissible neurodegenerative diseases, characterized by both progressive neuronal loss and neuroinflammation [29, 30].”
From Pharmacological modulation of TSPO in microglia/macrophages and neurons in a chronic neurodegenerative model of prion disease (2023) · cites this paper as [29]
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Metadata
- Authors
- MASTERS, C. L., & RICHARDSON, E. P.
- Affiliations
- Harvard University (US)
- Venue
- Brain
- Publisher
- Oxford University Press (OUP)
- Published
- 1978
- Volume
- 101
- Issue
- 2
- Pages
- 333-344
- ISSN
- 0006-8950 (ISSN-L)
- 1460-2156
- OpenAlex
- W2185932558
- Cited by
- 310
- References
- 0
- Citations by year
- 2025: 1 · 2024: 3 · 2023: 3 · 2022: 1 · 2020: 1 · 2019: 3 · 2017: 2 · 2016: 2 · 2015: 3 · 2014: 7 · 2013: 4 · 2012: 5
- FWCI
- 2.63
- Type
- journal article
- Language
- en
- Open access
- closed
- Locations
- Brain (publishedVersion)
- PubMed (publishedVersion)
- Funders
- National Institutes of Health
- Topics
- Life Sciences › Biochemistry, Genetics and Molecular Biology › Molecular Biology › Prion Diseases and Protein Misfolding
- Life Sciences › Neuroscience › Cellular and Molecular Neuroscience › Alzheimer's disease research and treatments
- Health Sciences › Medicine › Genetics (clinical) › Lysosomal Storage Disorders Research
- Keywords
- Creutzfeldt-Jakob disease, subacute spongiform encephalopathy, spongiform change, disease progression, prion disease, neuropathology
- MeSH terms
- Adult, Aged, Brain, Cerebellum, Cerebral Cortex, Corpus Striatum, Female, Gliosis, Hippocampus, Humans, Creutzfeldt-Jakob Syndrome, Male, Medulla Oblongata, Middle Aged, Nerve Degeneration, Pons, Spinal Cord, Telencephalon, Thalamic Nuclei
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