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Cited by 8Blood disorders and treatmentsImmunodeficiency and Autoimmune DisordersOral microbiology and periodontitis research

The DOI matches its Crossref record; 1 of the 1 references it cites were found in a registry or an index.

Kostmann syndrome: oral aspects and 10‐year follow‐up case report

Fernandes, Karin Sá, da Silva Santos, Paulo Sérgio, de Rezende, Nathalie Pepe Medeiros, Gallottini, Marina·2016·Special Care in Dentistry
DOI 10.1111/scd.12192
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Abstract

Kostmann syndrome (KS) is an autosomal recessive disorder characterized by a low neutrophil count and recurrent bacterial infections, including periodontal disease. This report describes the case of a 5-year-old female KS patient treated with regular infusions of granulocyte stimulating factor (granulokine), with primary complaint of gingival bleeding and tooth mobility, and followed up for 10 years. Conventional periodontal treatment and some extractions were performed, after neutrophil function tests using flow cytometry. The invasive procedures were carried out at an outpatient clinic under antibiotic prophylaxis due to a low neutrophil count and an impaired neutrophil function presented. During the 10-year follow-up period, despite episodes of recurrent gingivitis and periodontitis the present report describes the positive outcome of dental treatment of a patient with KS.

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Crossref · 10.1111/scd.12192

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Cited by

Sorted by citations

  • Dental Management of Genetic Dental Disorders: A Critical Review

    Dujic, H., Bücher, K., Schüler, I. M., Schmidt, P., Hertel, S., Timpel, J., Jablonski-Momeni, A., Schilke, R., Kapferer-Seebacher, I., Zschocke, J., et al. (2025) · Journal of Dental Research · doi:10.1177/00220345241305330 · Cited by 9

    “The spectrum ranges from reporting on the achievement of dental treatment without further monitoring to less frequent reports with more than a decade of monitoring (e.g., Bergendal et al. 2015; Fernandes et al. 2016; James and Roudsari 2019).”

See all 8

Metadata

Authors
Fernandes, K. S., da Silva Santos, P. S., de Rezende, N. P. M., & Gallottini, M.
Affiliations
  • Universidade de São Paulo (BR)
  • Assistant Professor Department of Stomatology, Bauru School of Dentistry, University of São Paulo São Paulo, Brazil
  • Centro Universitário Herminio Ometto de Araras (BR)
Corresponding author
Fernandes, Karin Sá
ORCID
Venue
Special Care in Dentistry
Publisher
Wiley
Published
2016-08-03
Volume
36
Issue
6
Pages
339-344
ISSN
  • 0275-1879 (ISSN-L)
  • 1754-4505
DOI
10.1111/scd.12192
OpenAlex
W2513727899
Cited by
8
References
1
Citations by year
2026: 1 · 2025: 3 · 2023: 1 · 2021: 2 · 2020: 1
FWCI
0.00
Type
journal article
Language
en
Open access
closed
Licence
onlinelibrary.wiley.com/termsAndConditions#vor (vor)
Locations
  • Special Care in Dentistry (publishedVersion)
  • PubMed (publishedVersion)
Topics
  • Health Sciences › Medicine › Hematology › Blood disorders and treatments
  • Life Sciences › Immunology and Microbiology › Immunology › Immunodeficiency and Autoimmune Disorders
  • Health Sciences › Dentistry › Periodontics › Oral microbiology and periodontitis research
Keywords
Kostmann syndrome, neutropenia, periodontitis, gingivitis, gingival bleeding, tooth mobility, granulocyte colony-stimulating factor, antibiotic prophylaxis, neutrophil function, dental treatment, pediatric patients, long-term follow-up
MeSH terms
Congenital Bone Marrow Failure Syndromes, Child, Preschool, Female, Humans, Mouth Diseases, Neutropenia, Dental Care for Chronically Ill, Dental Care for Children

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CoChat. (2026). Citation check: Kostmann syndrome: oral aspects and 10‐year follow‐up case report. https://app.cochat.ai/papers/10.1111/scd.12192
The paper
Fernandes, K. S., da Silva Santos, P. S., de Rezende, N. P. M., & Gallottini, M. (2016). Kostmann syndrome: oral aspects and 10‐year follow‐up case report. Special Care in Dentistry. https://doi.org/10.1111/scd.12192