Biology and Genetics of Prions Causing Neurodegeneration

Prusiner, Stanley B.·2013·Annual Review of Genetics

Cited by (455)

Items 201–300 of 455

  1. Loss of prion protein is associated with the development of insulin resistance and obesity
    Giovanna de Brito, Fernanda C. S. Lupinacci, Flávio H. Beraldo, Tiago G. Santos, Martín Roffé, Marilene Hohmuth Lopes, Vladmir Cláudio Cordeiro de Lima, Vilma Regina Martins, Glaucia N. M. Hajj · 2017 · Biochemical Journal
  2. Inactivation Methods for Prions
    Akikazu Sakudo · 2019 · Current Issues in Molecular Biology
  3. [PSI+] turns 50
    Mick F. Tuite, Gemma L. Staniforth, Brian S. Cox · 2015 · Prion
  4. Future Directions in Imaging Neurodegeneration
    Joseph C. Masdeu · 2017 · Current Neurology and Neuroscience Reports
  5. A standard model of Alzheimer’s disease?
    Lary C. Walker, David G. Lynn, Yury O. Chernoff · 2018 · Prion
  6. Hunting for the cause: Evidence for prion-like mechanisms in Huntington’s disease
    Kirby M. Donnelly, Cevannah M. Coleman, Madison L. Fuller, Victoria L. Reed, Dayna Smerina, David S. Tomlinson, Margaret M.P. Pearce · 2022 · Frontiers in Neuroscience
  7. Proteinopathies: Deciphering Physiology and Mechanisms to Develop Effective Therapies for Neurodegenerative Diseases
    Gouri Chopra, Shabnam Shabir, Sumaira Yousuf, Simran Kauts, Shahnawaz Ali Bhat, Ashiq Hussain Mir, Mahendra P. Singh · 2022 · Molecular Neurobiology
  8. The Effects of Andrographis paniculata (Burm.F.) Wall. Ex Nees and Andrographolide on Neuroinflammation in the Treatment of Neurodegenerative Diseases
    Francesca Bosco, Stefano Ruga, Rita Citraro, Antonio Leo, Lorenza Guarnieri, Jessica Maiuolo, Francesca Oppedisano, Roberta Macrì, Federica Scarano, Saverio Nucera et al. · 2023 · Nutrients
  9. Calling α-synuclein a prion is scientifically justifiable
    Joel C. Watts · 2019 · Acta Neuropathologica
  10. Cellular prion protein: A co-receptor mediating neuronal cofilin-actin rod formation induced by β-amyloid and proinflammatory cytokines
    Keifer P. Walsh, Thomas B. Kuhn, James R. Bamburg · 2014 · Prion
  11. The Role of the Gut Microbiota and Microbial Metabolites in the Pathogenesis of Alzheimer’s Disease
    Yi Wang · 2022 · CNS & Neurological Disorders - Drug Targets
  12. Yeast prions: Paramutation at the protein level?
    Mick F. Tuite · 2015 · Seminars in Cell and Developmental Biology
  13. Prion-like transmission of pathogenic protein aggregates in genetic models of neurodegenerative disease
    Margaret M.P. Pearce · 2017 · Current Opinion in Genetics & Development
  14. Prion Peptides Are Extremely Sensitive to Copper Induced Oxidative Stress
    Simone Dell’Acqua, Chiara Bacchella, Enrico Monzani, Stefania Nicolis, Giuseppe Di Natale, Enrico Rizzarelli, Luigi Casella · 2017 · Inorganic Chemistry
  15. Continues administration of Nano-PSO significantly increased survival of genetic CJD mice
    Orli Binyamin, Guy Keller, Kati Frid, Liraz Larush, Shlomo Magdassi, Ruth Gabizon · 2017 · Neurobiology of Disease
  16. Preparation and Characterization of Tau Oligomer Strains
    Urmi Sengupta, Mariana Carretero Murillo, Rakez Kayed · 2018 · Methods in molecular biology
  17. Replication of multiple system atrophy prions in primary astrocyte cultures from transgenic mice expressing human α-synuclein
    Zuzana Krejciova, George A. Carlson, Kurt Giles, Stanley B. Prusiner · 2019 · Acta Neuropathologica Communications
  18. Membrane interaction to intercellular spread of pathology in Alzheimer’s disease
    Valappil, Deepak Kunhi, Mini, Neeraj Jayakumar, Dilna, Aysha, Nath, Sangeeta · 2022 · Frontiers in Neuroscience
  19. Capturing the conversion of the pathogenic alpha-1-antitrypsin fold by ATF6 enhanced proteostasis
    Shuhong Sun, Chao Wang, Pei Zhao, Gabriel M. Kline, Julia M. D. Grandjean, Xin Jian Jiang, Richard F. Labaudinière, R. Luke Wiseman, Jeffery W. Kelly, William E. Balch · 2023 · Cell chemical biology
  20. Extracellular environment modulates the formation and propagation of particular amyloid structures
    Laura Westergard, Heather L. True · 2014 · Molecular Microbiology
  21. What amyloid ligands can tell us about molecular polymorphism and disease
    Harry LeVine, Lary C. Walker · 2016 · Neurobiology of Aging
  22. Targeting Prion-like Cis Phosphorylated Tau Pathology in Neurodegenerative Diseases
    Önder Albayram, Peter A. Angeli, Elizabeth R. Bernstein, Sean Baxley, Ziang Jeff Gao, Kun Ping Lu, Xiao Zhen Zhou · 2018 · Journal of Alzheimer’s Disease & Parkinsonism
  23. Acute induction of anomalous blood clotting by molecular amplification of highly substoichiometric levels of bacterial lipopolysaccharide (LPS)
    Etheresia Pretorius, Sthembile Mbotwa, Janette Bester, Christopher Robinson, Douglas Bruce Kell · 2016 · bioRxiv (Cold Spring Harbor Laboratory)
  24. Could astrocytes be the primary target of an offending agent causing the primary degenerative diseases of the human central nervous system? A hypothesis
    Roberto E.P. Sica · 2015 · Medical Hypotheses
  25. The frequency of yeast [PSI+] prion formation is increased during chronological ageing
    Shaun H. Speldewinde, Chris M. Grant · 2017 · Microbial Cell
  26. Intercellular Transmission of a Synthetic Bacterial Cytotoxic Prion-Like Protein in Mammalian Cells
    Aida Revilla-García, Cristina Fernández, María Moreno‐del Álamo, Vivian de los Rı́os, Ina Maja Vorberg, Rafael Giraldo · 2020 · mBio
  27. Overexpression of quality control proteins reduces prion conversion in prion-infected cells
    Simrika Thapa, Basant Abdulrahman, Dalia H. Abdelaziz, Lu Li, Manel Ben Aissa, Hermann M. Schätzl · 2018 · Journal of Biological Chemistry
  28. The Prion 2018 round tables (II): Aβ, tau, α-synuclein… are they prions, prion-like proteins, or what?
    Hasier Eraña · 2019 · Prion
  29. α-Synuclein aggregates inhibit ESCRT-III through sequestration and collateral degradation
    Cole S. Sitron, Victoria A. Trinkaus, Ana Galesic, Maximilian Garhammer, Patricia Yuste‐Checa, Ulrich Dransfeld, Dennis Feigenbutz, Jiuchun Zhang, Larysa Ivashko, Irina Dudanova et al. · 2025 · Molecular Cell
  30. Is Multiple System Atrophy a Prion-like Disorder?
    K. A. Jellinger, Gregor Karl Wenning, Nadia Stefanova · 2021 · International Journal of Molecular Sciences
  31. Methionine 109 plays a key role in Cu(II) binding to His111 in the 92–115 fragment of the human prion protein
    Carolina Sánchez‐López, Lina A. Rivillas-Acevedo, Octavio Cruz-Vásquez, Liliana Quintanar · 2017 · Inorganica Chimica Acta
  32. A brief overview of the Swi1 prion—[SWI+]
    Dustin Kenneth Goncharoff, Zhiqiang Du, Liming Li · 2018 · FEMS Yeast Research
  33. Enteric Nervous System and Its Relationship with Neurological Diseases
    María José Luesma Bartolomé, Liberto López-Marco, Marta Monzón, Sonia Santander · 2024 · Journal of Clinical Medicine
  34. Elucidating the structure of an infectious protein
    Markus Zweckstetter, Jesús R. Requena, Holger Wille · 2017 · PLoS Pathogens
  35. Evidence for iatrogenic transmission of Alzheimer’s disease
    Mathias Jucker, Lary C. Walker · 2024 · Nature Medicine
  36. Chronic Progressive Neurodegeneration in a Transgenic Mouse Model of Prion Disease
    Nina Fainstein, Dvir Dori, Kati Frid, Alexa T. Fritz, Ilona Shapiro, Ruth Gabizon, Tamir Ben‐Hur · 2016 · Frontiers in Neuroscience
  37. Nervous System
    Andrew David Miller, James F. Zachary · 2017 · Elsevier eBooks
  38. Amyloid Fragmentation and Disaggregation in Yeast and Animals
    Vitaly V. Kushnirov, Alexander A. Dergalev, Alexander I. Alexandrov · 2021 · Biomolecules
  39. What happened to K och's postulates in diarrhoea?
    Shamima Sultana, Shafiqul Alam Sarker, Harald Brüssow · 2017 · Environmental Microbiology
  40. Linking Antimicrobial Potential of Natural Products Derived from Aquatic Organisms and Microbes Involved in Alzheimer’s Disease - A Review
    Dejan S. Stojković, Marina Kostić, Marija S. Smiljkovic, Milena Aleksić, Perica J. Vasiljevic, Miloš Nikolić, Marina Sokóvić · 2018 · Current Medicinal Chemistry
  41. Three J-proteins impact Hsp104-mediated variant-specific prion elimination: a new critical role for a low-complexity domain
    Scott E. Berger, Anna M. Nolte, Erina Kamiya, Justin Keith Hines · 2019 · Current Genetics
  42. Sephin1 Reduces Prion Infection in Prion-Infected Cells and Animal Model
    Simrika Thapa, Dalia H. Abdelaziz, Basant Abdulrahman, Hermann M. Schätzl · 2020 · Molecular Neurobiology
  43. Novel regulators of PrP C expression as potential therapeutic targets in prion diseases
    Arianna Colini Baldeschi, Silvia Vanni, Marco Zattoni, Giuseppe Legname · 2020 · Expert Opinion on Therapeutic Targets
  44. Endosomal sorting drives the formation of axonal prion protein endoggresomes
    Romain Chassefeyre, Tai Chaiamarit, Adriaan Verhelle, Sammy Weiser Novak, Leonardo Rodrigues de Andrade, Andre Direito Goulart Leitao, Uri Manor, Sandra E. Encalada · 2021 · Science Advances
  45. Assessment of Glial Activation Response in the Progress of Natural Scrapie after Chronic Dexamethasone Treatment
    Isabel M. Guijarro, Moisès Garcés, Pol Andrés‐Benito, Belén Marín, Alicia Otero, Tomás Barrio, Margarita Carmona, Isidró Ferrer, Juan José Badiola, Marta Monzón · 2020 · International Journal of Molecular Sciences
  46. Viral capsid assembly as a model for protein aggregation diseases: Active processes catalyzed by cellular assembly machines comprising novel drug targets
    Rita Marreiros, Andreas Müller‐Schiffmann, Verian Bader, Suganya Selvarajah, Debendranath Dey, Vishwanath R. Lingappa, Carsten Korth · 2014 · Virus Research
  47. The role of the proteosurfaceome and exoproteome in bacterial coaggregation
    Ana Cristina Afonso, María José Saavedra, Manuel V. Simões, Lúcia Chaves Simões · 2024 · Biotechnology Advances
  48. Impact of Amyloid Polymorphism on Prion-Chaperone Interactions in Yeast
    Andrea K. Wegrzynowicz, Sarah C. Miller, Justin Keith Hines · 2019 · Viruses
  49. Prion-like mechanisms in neurodegenerative disease: Implications for Huntington’s disease therapy
    Bhairavi Srinageshwar, Robert B. Petersen, Gary Leo Dunbar, Julien Rossignol · 2020 · Stem Cells Translational Medicine
  50. Genotype-dependent Molecular Evolution of Sheep Bovine Spongiform Encephalopathy (BSE) Prions in Vitro Affects Their Zoonotic Potential
    Zuzana Krejciova, Marcelo A. Barria, Michael Jones, James W. Ironside, Martin Jeffrey, Lorenzo González, Mark W. Head · 2014 · Journal of Biological Chemistry
  51. Autologous neural progenitor cell transplantation into newborn mice modeling for E200K genetic prion disease delays disease progression
    Kati Frid, Orli Binyamin, Nina Fainstein, Guy Keller, Tamir Ben‐Hur, Ruth Gabizon · 2018 · Neurobiology of Aging
  52. Biology and Genetics of PrP Prion Strains
    Sina Ghaemmaghami · 2016 · Cold Spring Harbor Perspectives in Medicine
  53. Regional Differences in Neuroinflammation-Associated Gene Expression in the Brain of Sporadic Creutzfeldt–Jakob Disease Patients
    Areškevičiūtė, Aušrinė, Litman, Thomas, Broholm, Helle, Melchior, Linea C., Nielsen, Pia R., Green, Alison, Eriksen, Jens O., Smith, Colin, Lund, Eva L. · 2020 · International Journal of Molecular Sciences
  54. Osmotic stress induces formation of both liquid condensates and amyloids by a yeast prion domain
    Anastasia V. Grizel, Natalia A. Gorsheneva, Jonathan B Stevenson, Jeremy Pflaum, Florian Wilfling, Aleksandr A. Rubel, Yury O. Chernoff · 2024 · Journal of Biological Chemistry
  55. Engineered β-hairpin scaffolds from human prion protein regions: Structural and functional investigations of aggregates
    Concetta Di Natale, Sara La Manna, Concetta Avitabile, Daniele Florio, Giancarlo Morelli, Paolo A. Netti, Daniela Marasco · 2020 · Bioorganic Chemistry
  56. Neuroprotective Potential of Seed Extracts: Review of In Vitro and In Vivo Studies
    Gabriella Mendes Duarte, Francisco Emanoel Alves de Araújo, João Matheus Caé da Rocha, Francisca Idalina Neta, Amália Cínthia Meneses do Rêgo, Irami Araújo-Filho, Francisco Irochima Pinheiro, Eduardo Pereira de Azevedo, Ricardo Ney Cobucci, Fausto Pierdoná Gúzen · 2023 · Nutrients
  57. Preparation of Amyloid Fibrils Seeded from Brain and Meninges
    K. Scherpelz, Jun-xia Lu, R. Tycko, S. Meredith · 2016 · Methods in molecular biology
  58. Role of the Cell Asymmetry Apparatus and Ribosome-Associated Chaperones in the Destabilization of aSaccharomyces cerevisiaePrion by Heat Shock
    Rebecca L. Howie, Lina Manuela Jay-Garcia, Denis A. Kiktev, Quincy Faber, Margaret Murphy, Katherine A. Rees, Numera Sachwani, Yury O. Chernoff · 2019 · Genetics
  59. Design of a New [PSI+]-No-More Mutation in SUP35 With Strong Inhibitory Effect on the [PSI+] Prion Propagation
    Lavrentii G. Danilov, Andrew G. Matveenko, Varvara E. Ryzhkova, Mikhail V. Belousov, Olga I. Poleshchuk, Daria Likholetova, Petr A. Sokolov, Nina A. Kasyanenko, Andrey V. Kajava, Galina A. Zhouravleva et al. · 2019 · Frontiers in Molecular Neuroscience
  60. Structural Bases of Prion Variation in Yeast
    Vitaly V. Kushnirov, Alexander A. Dergalev, Maya K. Alieva, Alexander I. Alexandrov · 2022 · International Journal of Molecular Sciences
  61. Unknown roles of tau pathology in neurological disorders. Challenges and new perspectives
    Margrethe A. Olesen, Francisca Villavicencio-Tejo, Victor Cuevas-Espinoza, Rodrigo A. Quintanilla · 2024 · Ageing Research Reviews
  62. The [PSI +] yeast prion does not wildly affect proteome composition whereas selective pressure exerted on [PSI +] cells can promote aneuploidy
    Patrick H. W. Chan, Lisa Lee, Erin J. Kim, Tony Hui, Nikolay Stoynov, Roy Nassar, Michelle Moksa, Dale M. Cameron, Martin Hirst, Joerg Gsponer et al. · 2017 · Scientific Reports
  63. Role of viruses, prions and miRNA in neurodegenerative disorders and dementia
    Sayed Sartaj Sohrab, Mohd Suhail, Ashraf Ali, Mohammad Amjad Kamal, Azamal Husen, Fahim Ahmad, Esam I. Azhar, Nigel H. Greig · 2018 · VirusDisease
  64. The role of the cellular prion protein in the uptake and toxic signaling of pathological neurodegenerative aggregates
    Carlo Scialò, Giuseppe Legname · 2020 · Progress in molecular biology and translational science
  65. Copper coordination modulates prion conversion and infectivity in mammalian prion proteins
    Giuseppe Legname · 2023 · Prion
  66. Generating Bona Fide Mammalian Prions with Internal Deletions
    Carola Muñoz-Montesino, Christina Sizun, Mohammed Moudjou, Laëtitia Herzog, Fabienne Reine, Jérôme Chapuis, Danica Ćirić, Angélique Igel‐Egalon, Hubert Laude, Vincent Béringue et al. · 2016 · Journal of Virology
  67. Interaction between Hemin and Prion Peptides: Binding, Oxidative Reactivity and Aggregation
    Simone Dell’Acqua, Elisa Massardi, Enrico Monzani, Giuseppe Di Natale, Enrico Rizzarelli, Luigi Casella · 2020 · International Journal of Molecular Sciences
  68. Decoding the function of the N-terminal tail of the cellular prion protein to inspire novel therapeutic avenues for neurodegenerative diseases
    Nunzio Iraci, Claudia Stincardini, Maria Letizia Barreca, Emiliano Biasini · 2014 · Virus Research
  69. Hexameric Aggregation Nucleation Core Sequences and Diversity of Pathogenic Tau Strains
    Ling Wu, Sidharth S. Madhavan, Christopher Tan, Bin Xu · 2022 · Pathogens
  70. Therapeutic Potential of Capsaicin in Various Neurodegenerative Diseases with Special Focus on Nrf2 Signaling
    Vibhav Varshney, Abhishek Kumar, Vikas Parashar, Ankit Kumar, Ahsas Goyal, Debapriya Garabadu · 2024 · Current Pharmaceutical Biotechnology
  71. From Neurodegeneration to Brain Health: An Integrated Approach
    Robert B. Petersen, Frances M. Lissemore, Brian Stephen Appleby, Neelum T. Aggarwal, Richard Eleftherios Boyatzis, Gemma Casadesús, Jeff Cummings, Anthony Ian Jack, George L. Perry, Jiri Safar et al. · 2015 · Journal of Alzheimer s Disease
  72. Inducers and modulators of protein aggregation in Alzheimer's disease - Critical tools for understanding the foundations of aggregate structures
    Kerry T. Sun, Sue‐Ann Mok · 2025 · Neurotherapeutics
  73. What makes functional amyloids work?
    Ansgar B. Siemer · 2022 · Critical Reviews in Biochemistry and Molecular Biology
  74. Peculiarities of Prion Diseases
    Walker S. Jackson, Clemens Krost · 2014 · PLoS Pathogens
  75. Protein Misfolding Cyclic Amplification of Infectious Prions
    Fabio Moda · 2017 · Progress in molecular biology and translational science
  76. Ubiquitination and SUMOylation of Amyloid and Amyloid-like Proteins in Health and Disease
    Lenzie K. Ford, Luana Fioriti, Eric R. Kandel · 2019 · Current Issues in Molecular Biology
  77. Multimodal 18F-AV-1451 and MRI Findings in Nonfluent Variant of Primary Progressive Aphasia: Possible Insights on Nodal Propagation of Tau Protein Across the Syntactic Network
    Belén Pascual, Quentin Funk, Paolo Zanotti‐Fregonara, Neha Pal, Elijah Rockers, Meixiang Yu, Bryan Spann, Gustavo C. Román, Paul Ernest Schulz, Christof Karmonik et al. · 2019 · Journal of Nuclear Medicine
  78. A seven-residue deletion in PrP leads to generation of a spontaneous prion formed from C-terminal C1 fragment of PrP
    Carola Muñoz-Montesino, Djabir Larkem, Clément Barbereau, Angélique Igel‐Egalon, Sandrine Truchet, Eric Jacquet, Naïma Nhiri, Mohammed Moudjou, Christina Sizun, Human Rezaei et al. · 2020 · Journal of Biological Chemistry
  79. A possible mechanism for the progression of chronic renal disease and congestive heart failure
    Richard N. Ré · 2014 · Journal of the American Society of Hypertension
  80. Drivers: A Biologically Contextualized, Cross-Inferential View of the Epidemiology of Neurodegenerative Disorders
    Jesús de Pedro‐Cuesta, Pablo Martínez‐Martín, Alberto Rábano, Enrique Alcalde-Cabero, Fernando José García López, Javier Almazán‐Isla, María Ruiz-Tovar, Maria-José Medrano, Fuencisla Avellanal, Olga Calero et al. · 2016 · Journal of Alzheimer s Disease
  81. Retinale Bildgebung von Makula und Papille bei neurodegenerativen Erkrankungen
    Gabrielle N. Turski, Steffen Schmitz-Valckenberg, Frank Gerhard Holz, Robert Patrick Finger · 2016 · Der Ophthalmologe
  82. Presymptomatic change in microRNAs modulates Tau pathology
    Salil Sharma, Inès Khadimallah, Adam Williamson Corya, Yousuf Ali, Xi Rao, Yunlong Liu, Hui‐Chen Lu · 2018 · Scientific Reports
  83. Ok Google, how could I design therapeutics against prion diseases?
    Marta Rigoli, Giovanni Spagnolli, Pietro Faccioli, Jesús R. Requena, Emiliano Biasini · 2019 · Current Opinion in Pharmacology
  84. Neuroglial patterns are shared by cerebella from prion and prion-like disorder affected patients
    Moisès Garcés, M. Isabel Guijarro, Antonia Vargas, Juan José Badiola, Marta Monzón · 2019 · Mechanisms of Ageing and Development
  85. Sup35 methionine oxidation is a trigger forde novo[PSI+] prion formation
    Chris M. Grant · 2015 · Prion
  86. Prenatal transmission of scrapie in sheep and goats: A case study for veterinary public health
    D.B. Adams · 2016 · Open Veterinary Journal
  87. Chaperone functional specificity promotes yeast prion diversity
    Andrea K. Wegrzynowicz, Justin Keith Hines · 2018 · PLoS Pathogens
  88. The impact of self-replicating proteins on inflammation, autoimmunity and neurodegeneration—An untraveled path
    Dana Butnaru, Joab Chapman · 2019 · Autoimmunity Reviews
  89. Physics of Protein Aggregation in Normal and Accelerated Brain Aging
    Alberto Javier Espay, Andrea Sturchio, Alberto Imarisio, Emily J. Hill, Brady J. Williamson, Kora T Montemagno, Christian Hoffmann, Hugo Le Roy, Dragomir Milovanović, Fredric P. Manfredsson · 2025 · BioEssays
  90. Stochasticity, Entropy and Neurodegeneration
    Peter K. Panegyres · 2022 · Brain Sciences
  91. A fractional-order yeast prion mathematical model and its solution
    Mitali Maji, Subhas Khajanchi · 2024 · Journal of Applied Mathematics and Computing
  92. Transcriptional response to the [ISP+] prion ofSaccharomyces cerevisiaediffers from that induced by the deletion of its structural gene,SFP1
    Polina B. Drozdova, Tatyana M. Rogoza, Elina A. Radchenko, Polina Lipaeva, Ludmila N Mironova · 2014 · FEMS Yeast Research
  93. Current Plasma Sterilization and Disinfection Studies
    Nobuya Hayashi, Masaaki Goto, Tomomasa Itarashiki, Akira Yonesu, Akikazu Sakudo · 2018 · Journal of Photopolymer Science and Technology
  94. Prions and Non-infectious Amyloids of Mammals – Similarities and Differences
    Alexey P. Galkin, Maria E. Velizhanina, Julia V. Sopova, Aleksandr A. Shenfeld, Sergey P. Zadorsky · 2018 · Biochemistry (Moscow)
  95. Axonal changes in experimental prion diseases recapitulate those following constriction of postganglionic branches of the superior cervical ganglion: a comparison 40 years later
    Pawel Piotr Liberski · 2019 · Prion
  96. Sporadic Creutzfeldt-Jakob Disease in a Woman Married Into a Gerstmann-Sträussler-Scheinker Family: An Investigation of Prions Transmission via Microchimerism
    Aušrinė Areškevičiūtė, Linea Cecilie Melchior, Helle Broholm, Lars-Henrik Krarup, Suzanne Granhøj Lindquist, Peter Johansen, Neil McKenzie, A.J.E Green, Jørgen Erik Nielsen, Henning Bækgaard Laursen et al. · 2018 · Journal of Neuropathology & Experimental Neurology
  97. Enhanced secretion of the amyotrophic lateral sclerosis ALS-associated misfolded TDP-43 mediated by the ER-ubiquitin specific peptidase USP19
    Flavien Picard, Takashi Nonaka, Edwige Belotti, Alexis Osseni, Elisabeth Errazuriz-Cerda, Coline Jost-Mousseau, E Bernard, Agnès Conjard‐Duplany, Delphine Bohl, Masato Hasegawa et al. · 2025 · Cellular and Molecular Life Sciences
  98. Protein Aggregation and Self Assembly in Health and Disease
    Ajoy Basak, Sarmistha Basak · 2021 · Current Proteomics
  99. Transmission-selective muscle pathology induced by the active propagation of mutant huntingtin across the human neuromuscular synapse
    Margarita C. Dinamarca, Laura Colombo, Urszula Brykczynska, Amandine Grimm, Isabelle Fruh, Imtiaz Hossain, Daniela Gabriel, Anne Eckert, Mathias M. Müller, Eline Pecho‐Vrieseling · 2024 · Frontiers in Molecular Neuroscience
  100. What Are the Roles of Cellular Prion Protein in Normal and Pathologic Conditions?
    Eduardo Elias Benarroch · 2024 · Neurology