The DOI matches its Crossref record; 101 of the 104 references it cites were found in a registry or an index.
Overview of Castleman disease
Open accessAbstract
Castleman disease (CD) describes a group of at least 4 disorders that share a spectrum of characteristic histopathological features but have a wide range of etiologies, presentations, treatments, and outcomes. CD includes unicentric CD (UCD) and multicentric CD (MCD), the latter of which is divided into idiopathic MCD (iMCD), human herpes virus-8 (HHV8)-associated MCD (HHV8-MCD), and polyneuropathy, organomegaly, endocrinopathy, monoclonal plasma cell disorder, skin changes (POEMS)-associated MCD (POEMS-MCD). iMCD can be further subclassified into iMCD–thrombocytopenia, ascites, reticulin fibrosis, renal dysfunction, organomegaly (iMCD-TAFRO) or iMCD–not otherwise specified (iMCD-NOS). Advances in diagnosis, classification, pathogenesis, and therapy are substantial since the original description of UCD by Benjamin Castleman in 1954. The advent of effective retroviral therapy and use of rituximab in HHV8-MCD have improved outcomes in HHV8-MCD. Anti–interleukin-6–directed therapies are highly effective in many iMCD patients, but additional therapies are required for refractory cases. Much of the recent progress has been coordinated by the Castleman Disease Collaborative Network (CDCN), and further progress will be made by continued engagement of physicians, scientists, and patients. Progress can also be facilitated by encouraging patients to self-enroll in the CDCN’s ACCELERATE natural history registry (#NCT02817997; www.CDCN.org/ACCELERATE).
Overview
The claims and statistics of this paper haven’t been checked yet.
Run the check — free, no account needed. It reads the open-access text and checks the sources it cites.
Integrity signals
Registry
Cites
Statistics
Verification
Claims the paper makes
The claims and statistics of this paper haven’t been checked yet.
Run the check — free, no account needed. It reads the open-access text and checks the sources it cites.
Claims other papers make about this one
Each is checked against this paper’s own text: does it say what the citing paper says it does?
In the citing paper
“Patients with HHV-8–associated multicentric Castleman’s disease are immunocompromised as a result of human immunodeficiency virus infection or a genetic susceptibility, making it difficult to control the HHV-8 infection, which is a common, typically asymptomatic infection in the general population.69”
From Cytokine storm (2020) · cites this paper as [69]
Self-check
Percentages, sums and reported differences re-computed from the paper’s own numbers.
The self-check needs the paper’s full text.
Citations
Cites
Kaposi's sarcoma-associated herpesvirus-like DNA sequences in multicentric Castleman's disease.
Soulier, J., Grollet, L., Oksenhendler, E., Cacoub, P., Cazals-Hatem, D., Babinet, P., d'Agay, M., Clauvel, J., Raphael, M., Degos, L., et al. (1995) · Blood · doi:10.1182/blood.v86.4.1276.bloodjournal8641276 · Cited by 2,296
POEMS syndrome: definitions and long-term outcome
Dispenzieri, A. A., Kyle, R. A., Lacy, M. Q., Rajkumar, S. V., Therneau, T. M., Larson, D. R., Greipp, P. R., Witzig, T. E., Basu, R., Suárez, G. A., et al. (2003) · Blood · doi:10.1182/blood-2002-07-2299 · Cited by 817
Self-citationNishimoto, N., Terao, K., Mima, T., Nakahara, H., Takagi, N., & Kakehi, T. (2008) · Blood · doi:10.1182/blood-2008-05-155846 · Cited by 781
Humanized anti–interleukin-6 receptor antibody treatment of multicentric Castleman disease
Nishimoto, N., Kanakura, Y., Aozasa, K., Johkoh, T., Nakamura, M., Nakano, S., Nakano, N., Ikeda, Y., Sasaki, T., Nishioka, K., et al. (2005) · Blood · doi:10.1182/blood-2004-12-4602 · Cited by 754
Plasma Cell Dyscrasia with Polyneuropathy, Organomegaly, Endocrinopathy, M Protein, and Skin Changes
Bardwick, P. A., Zvaifler, N. J., Gill, G. N., NEWMAN, D., Greenway, G. D., & RESNICK, D. L. (1980) · Medicine · doi:10.1097/00005792-198007000-00006 · Cited by 698
Dupin, N., Diss, T. C., Kellam, P., Tulliez, M., Du, M., Sicard, D., Weiss, R. A., Isaacson, P. G., & Boshoff, C. (2000) · Blood · doi:10.1182/blood.v95.4.1406.004k26_1406_1412 · Cited by 648
Fajgenbaum, D., Uldrick, T., Bagg, A., Frank, D. M., Wu, D., Srkalović, G., Simpson, D., Liu, A. Y., Menke, D., Chandrakasan, S., et al. (2017) · Blood · doi:10.1182/blood-2016-10-746933 · Cited by 601
Self-citationNakanishi, T., SOBUE, I., TOYOKURA, Y., Nishitani, H., Kuroiwa, Y., Satoyoshi, E., Tsubaki, T., Igata, A., & Ozaki, Y. (1984) · Neurology · doi:10.1212/wnl.34.6.712 · Cited by 552
van Rhee, F., Wong, R. S., Munshi, N., Rossi, J.-F., Ke, X.-Y., Fosså, A., Simpson, D., Capra, M., Liu, T., Hsieh, R. K., et al. (2014) · The Lancet Oncology · doi:10.1016/s1470-2045(14)70319-5 · Cited by 454
Demographic variations in the rising incidence of esophageal adenocarcinoma in white males
Bollschweiler, E., Wolfgarten, E., Gutschow, C. A., & H�lscher, A. H. (2001) · Cancer · doi:10.1002/1097-0142(20010801)92:3 · Cited by 452
Research works printed but not linked: 2
- Flendrig, 1969, Benign giant lymphoma: the clinical signs and symptoms and the morphological aspects.y, Folia Med Neerl, 12, 119
- Takai, 2010, Thrombocytopenia with mild bone marrow fibrosis accompanied by fever, pleural effusion, ascites and hepatosplenomegaly [in Japanese], Rinsho Ketsueki, 51, 320
Cited by
Sorted by citations
Fajgenbaum, D. C., & June, C. H. (2020) · New England Journal of Medicine · doi:10.1056/nejmra2026131 · Cited by 3,196
Self-citationCytokine Storm—Definition, Causes, and Implications
Jarczak, D., & Nierhaus, A. (2022) · International Journal of Molecular Sciences · doi:10.3390/ijms231911740 · Cited by 336
Carbone, A., Borok, M. Z., Damania, B., Gloghini, A., Polizzotto, M. N., Jayanthan, R., Fajgenbaum, D. C., & Bower, M. (2021) · Nature Reviews Disease Primers · doi:10.1038/s41572-021-00317-7 · Cited by 214
Self-citationWeathering the COVID-19 storm: Lessons from hematologic cytokine syndromes
England, J. T., Abdulla, A., Biggs, C. M., Lee, A. Y. Y., Hay, K. A., Hoiland, R. L., Wellington, C. L., Sekhon, M. S., Jamal, S., Shojania, K., et al. (2020) · Blood Reviews · doi:10.1016/j.blre.2020.100707 · Cited by 179
Nishimura, Y., Fajgenbaum, D. C., Pierson, S. K., Iwaki, N., Nishikori, A., Kawano, M., Nakamura, N., Izutsu, K., Takeuchi, K., Nishimura, M. F., et al. (2021) · American Journal of Hematology · doi:10.1002/ajh.26292 · Cited by 138
Self-citationKSHV/HHV8-mediated hematologic diseases
Cesarman, E., Chadburn, A., & Rubinstein, P. G. (2021) · Blood · doi:10.1182/blood.2020005470 · Cited by 124
Systemic effects of IL-6 blockade in rheumatoid arthritis beyond the joints
Jarlborg, M., & Gabay, C. (2021) · Cytokine · doi:10.1016/j.cyto.2021.155742 · Cited by 90
Castleman disease and TAFRO syndrome
Masaki, Y., Arita, K., Sakai, T., Takai, K., Aoki, S., & Kawabata, H. (2022) · Annals of Hematology · doi:10.1007/s00277-022-04762-6 · Cited by 70
Mukherjee, S., Martin, R., Sande, B., Paige, J. S., & Fajgenbaum, D. C. (2021) · Blood Advances · doi:10.1182/bloodadvances.2021004441 · Cited by 66
Self-citationGarcía, A. G., Fernández-Martín, J., & Marhuenda, Á. R. (2022) · Rheumatology · doi:10.1093/rheumatology/keac481 · Cited by 63
The clinical picture of Castleman disease: a systematic review and meta-analysis
Hoffmann, C., Oksenhendler, É., Littler, S., Grant, L., Kanhai, K. J. K., & Fajgenbaum, D. C. (2024) · Blood Advances · doi:10.1182/bloodadvances.2024013548 · Cited by 48
Self-citationImmune-Mediated Dermatoses in Patients with Haematological Malignancies: A Comprehensive Review
Maglie, R., Genovese, G., Solimani, F., Guglielmo, A., Pileri, A., Portelli, F., Hertl, M., Marzano, A. V., & Antiga, E. (2020) · American Journal of Clinical Dermatology · doi:10.1007/s40257-020-00553-9 · Cited by 45
Zhang, L., Dong, Y.-J., Peng, H., Li, H., Zhang, M., Wang, H., Liu, Q., Su, L.-P., Zhong, L.-Y., Wu, W., et al. (2023) · The Lancet Regional Health - Western Pacific · doi:10.1016/j.lanwpc.2023.100720 · Cited by 43
Self-citationGao, Y., Liu, Y., Zhang, M., Li, S., Fajgenbaum, D. C., Zhang, L., & Li, J. (2024) · British Journal of Haematology · doi:10.1111/bjh.19334 · Cited by 42
Self-citationLosay, V. A., & Damania, B. (2025) · Viruses · doi:10.3390/v17020177 · Cited by 41
Expert Perspective: Diagnosis and Treatment of Castleman Disease
Chen, L. Y. C., Zhang, L., & Fajgenbaum, D. C. (2025) · Arthritis & Rheumatology · doi:10.1002/art.43269 · Cited by 41
Self-citationPitot, M. A., Amawi, A. D. T., Alexander, L. F., LeGout, J. D., Walkoff, L. A., Navin, P. J., Kawashima, A., Wood, A. J., Dispenzieri, A. A., & Venkatesh, S. K. (2023) · Radiographics · doi:10.1148/rg.220210 · Cited by 36
Self-citationApproach to Imaging of Mediastinal Masses
Ahuja, J., Strange, C. D., Agrawal, R., Erasmus, L. T., & Truong, M. T. (2023) · Diagnostics · doi:10.3390/diagnostics13203171 · Cited by 36
Transcriptome and unique cytokine microenvironment of Castleman disease
Wing, A., Xu, J. Z., Meng, W., Rosenfeld, A. M., Li, E. Y., Wertheim, G. B. W., Paessler, M. E., Bagg, A., Frank, D. M., Tan, K., et al. (2021) · Modern Pathology · doi:10.1038/s41379-021-00950-3 · Cited by 35
Self-citationLymphadenopathy in the rheumatology practice: a pragmatic approach
Rodolfi, S., Della‐Torre, E., Bongiovanni, L., Mehta, P., Fajgenbaum, D. C., & Selmi, C. F. (2023) · Rheumatology · doi:10.1093/rheumatology/kead644 · Cited by 34
Self-citationMalignancy and viral infections in Sub-Saharan Africa: A review
Diakité, M., Shaw‐Saliba, K., & Lau, C. (2023) · Frontiers in Virology · doi:10.3389/fviro.2023.1103737 · Cited by 38
Sun, D.-P., Chen, W.-M., Wang, L., Wang, Z., Liang, J., Zhu, H., Fan, L., Wu, Y., Xu, W., & Li, J. (2021) · Journal of Cancer Research and Clinical Oncology · doi:10.1007/s00432-020-03494-2 · Cited by 33
The critical impacts of cytokine storms in respiratory disorders
Tramboo, S. R., Elkhalifa, A. M. E., Khursheed, S. Q., Ali, S. I., Shah, N. N., Taifa, S., Rakhshan, R., Shah, I. H., Mir, M. A., Malik, M., et al. (2024) · Heliyon · doi:10.1016/j.heliyon.2024.e29769 · Cited by 32
Lust, H., Gong, S., Remiker, A. S., & Rossoff, J. E. (2021) · Pediatric Blood & Cancer · doi:10.1002/pbc.29261 · Cited by 31
Idiopathic multicentric Castleman disease: An update in diagnosis and treatment advances
Lang, E., & van Rhee, F. (2023) · Blood Reviews · doi:10.1016/j.blre.2023.101161 · Cited by 29
UCD with MCD-like inflammatory state: surgical excision is highly effective
Zhang, M., Jia, M.-N., Chen, J., Feng, J., Cao, X., Zhou, D., Fajgenbaum, D. C., Zhang, L., & Li, J. (2021) · Blood Advances · doi:10.1182/bloodadvances.2020003607 · Cited by 29
Self-citationRecent Advances in the Treatment and Supportive Care of POEMS Syndrome
Zerdan, M. B., George, T. I., Bunting, S. T., & Chaulagain, C. P. (2022) · Journal of Clinical Medicine · doi:10.3390/jcm11237011 · Cited by 26
H syndrome treated with Tocilizumab: two case reports and literature review
Jacquot, R., Jouret, M., Valentin, M. G., Richard, M., Jamilloux, Y., Rousset, F., Emile, J., Haroche, J., Steinmüller, L., Zekre, F., et al. (2023) · Frontiers in Immunology · doi:10.3389/fimmu.2023.1061182 · Cited by 23
Pierson, S. K., Brandstadter, J. D., Torigian, D. A., Bagg, A., Lechowicz, M. J., Alapat, D. V., Casper, C., Chadburn, A., Chandrakasan, S., Dispenzieri, A. A., et al. (2025) · Blood Advances · doi:10.1182/bloodadvances.2024014391 · Cited by 23
Self-citationThe role and impact of viruses on cancer development
Rengifo, A. C., Amaya, S., Rodríguez‐Medina, C., & Botero, J. E. (2024) · Periodontology 2000 · doi:10.1111/prd.12566 · Cited by 22
Implications of SARS-CoV-2 Infection in Systemic Juvenile Idiopathic Arthritis
Ailioaie, L. M., Ailioaie, C., & Litscher, G. (2022) · International Journal of Molecular Sciences · doi:10.3390/ijms23084268 · Cited by 21
The lymph node transcriptome of unicentric and idiopathic multicentric Castleman disease
Horna, P., King, R. L., Jevremović, D., Fajgenbaum, D. C., & Dispenzieri, A. A. (2022) · Haematologica · doi:10.3324/haematol.2021.280370 · Cited by 21
Self-citationIs Nuclear Factor Erythroid 2-Related Factor 2 a Target for the Intervention of Cytokine Storms?
Liu, Z., Deng, P., Liu, S., Bian, Y., Xu, Y., Zhang, Q., Wang, H., & Pi, J. (2023) · Antioxidants · doi:10.3390/antiox12010172 · Cited by 21
IgG4-related kidney disease: Clinicopathologic features, differential diagnosis, and mimics
Gilani, S. I., Buglioni, A., & Cornell, L. D. (2023) · Seminars in Diagnostic Pathology · doi:10.1053/j.semdp.2023.12.001 · Cited by 21
Patient’s age and d-dimer levels predict the prognosis in patients with TAFRO syndrome
Kawabata, H., Fujimoto, S., Sakai, T., Yanagisawa, H., Kitawaki, T., Nara, K., Hagihara, M., Yamamoto, H., Tanimizu, M., Kato, C., et al. (2021) · International Journal of Hematology · doi:10.1007/s12185-021-03159-x · Cited by 20
International definition of iMCD-TAFRO: future perspectives
Nishimura, Y., Nishimura, M. F., & Sato, Y. (2022) · Journal of the Japan Society of the Reticuloendothelial System · doi:10.3960/jslrt.21037 · Cited by 20
Maisonobe, L., Bertinchamp, R., Damian, L., Gérard, L., Berisha, M., Guillet, S., Fieschi, C., Malphettes, M., Fadlallah, J., Hié, M., et al. (2021) · British Journal of Haematology · doi:10.1111/bjh.17868 · Cited by 19
Harada, T., Kikushige, Y., Miyamoto, T., Uno, K., Niiro, H., Kawakami, A., Koga, T., Akashi, K., & Yoshizaki, K. (2023) · Nature Communications · doi:10.1038/s41467-023-42718-0 · Cited by 19
A Rare Lymphoproliferative Disease: Castleman Disease
Gündüz, E., Özdemir, N., Bakanay, Ş. M., & Karakuş, S. (2021) · Turkish Journal of Hematology · doi:10.4274/tjh.galenos.2021.2021.0440 · Cited by 19
Morel, A., Meuleman, M.-S., Moktefi, A., & Audard, V. (2021) · Diagnostics · doi:10.3390/diagnostics11040710 · Cited by 18
Cutaneous reactive B‐cell lymphoid proliferations
Khalil, S., Donthi, D., & Gru, A. A. (2022) · Journal of Cutaneous Pathology · doi:10.1111/cup.14264 · Cited by 18
Tu, K., Fan, P.-Y., Chen, T., Chuang, W., Wu, C., Ku, C., Tian, Y.-C., Yang, C.-W., Fang, J., & Yang, H. (2021) · International Journal of Molecular Sciences · doi:10.3390/ijms22126286 · Cited by 17
TAFRO syndrome: A disease that known is half cured
Chen, T., Feng, C., Zhang, X., & Zhou, J. (2022) · Hematological Oncology · doi:10.1002/hon.3075 · Cited by 17
Unicentric form of Castleman´s disease, pitfalls of diagnosis and surgical treatment
Moláček, J., Třeška, V., Skalický, T., VODIČKA, J., Ferda, J., Ferdová, E., Baxa, J., Mach, C., Jungová, A., & Michal, M. (2023) · Frontiers in Oncology · doi:10.3389/fonc.2023.1057683 · Cited by 17
JAK1/2 Inhibition in Severe TAFRO Syndrome: A Case Report
Killian, M., Viel, S., Chalayer, É., Forest, F., Grange, S., Bonnefoy, P. B., Oksenhendler, É., Cathébras, P. J., & Paul, S. (2021) · Annals of Internal Medicine · doi:10.7326/l20-1051 · Cited by 17
Inflammatory diseases in hematology: a review
Henrie, R., Cherniawsky, H. M., Marcon, K. M., Zhao, E. J., Marinkovic, A., Pourshahnazari, P., Parkin, S., & Chen, L. Y. C. (2022) · American Journal of Physiology-Cell Physiology · doi:10.1152/ajpcell.00356.2021 · Cited by 17
Smith, D. G., Eichinger, A., Fennell, É., Xu-Monette, Z. Y., Rech, A. J., Wang, J., Esteva, E., Seyedian, A., Yang, X., Zhang, M., et al. (2025) · Nature Communications · doi:10.1038/s41467-025-61214-1 · Cited by 16
18F-FDG PET/CT imaging features of patients with multicentric Castleman disease
Jiang, Y., Hou, G., Zhu, Z., Huo, L., Li, F., & Cheng, W. (2021) · Nuclear Medicine Communications · doi:10.1097/mnm.0000000000001404 · Cited by 16
Kakutani, T., Nunokawa, T., Chinen, N., & Tamai, Y. (2022) · Medicine · doi:10.1097/md.0000000000032200 · Cited by 15
Increase in Vascular Endothelial Growth Factor (VEGF) Expression and the Pathogenesis of iMCD-TAFRO
Srkalović, G., Nijim, S., Srkalovic, M. B., & Fajgenbaum, D. C. (2024) · Biomedicines · doi:10.3390/biomedicines12061328 · Cited by 14
Self-citationPelliccia, S., Rogges, E., Cardoni, A., Lopez, G., Conte, E., Faccini, A. L., Vito, R. D., Girardi, K., Bianchi, A., Annibali, O., et al. (2023) · British Journal of Haematology · doi:10.1111/bjh.19171 · Cited by 14
Mukherjee, S., Kanhai, K. J. K., Kauffman, D., Martin, R., Paige, J. S., Ghosh, A., Kannan, H., Shupo, F., & Fajgenbaum, D. C. (2022) · Leukemia · doi:10.1038/s41375-022-01690-2 · Cited by 13
Self-citationZhou, J., Zhang, L., Liu, X., Zhang, M., Li, J., & Zhang, W. (2023) · CHEST Journal · doi:10.1016/j.chest.2023.03.022 · Cited by 13
Comprehensive analysis of 65 patients with Castleman disease in a single center in China
Wang, X.-Q., Zhong, N., Sun, Q., Yan, S., Xu, G.-C., Wang, Y., Peng, L., Liu, B., & Bu, L. (2022) · Scientific Reports · doi:10.1038/s41598-022-12797-y · Cited by 13
Liu, Y., Gao, Y., Zhao, H., Zhang, M., Duan, M., Li, J., & Zhang, L. (2024) · Annals of Hematology · doi:10.1007/s00277-024-05783-z · Cited by 12
Caballero, J. C., Conejero, N., Solán, L., de la Pinta, F. J. D., Córdoba, R., & López‐García, A. (2024) · Biomedicines · doi:10.3390/biomedicines12051076 · Cited by 12
Ostrowska, B., Szymczyk, A., Olszewska‐Szopa, M., Romejko‐Jarosińska, J., Domańska‐Czyż, K., Dabrowska-Iwanicka, A. P., Tomczak, W., Rybski, S., Hus, M., Wróbel, T., et al. (2021) · Leukemia & lymphoma/Leukemia and lymphoma · doi:10.1080/10428194.2021.1941926 · Cited by 12
Jiménez-Heffernan, J. A., del Arco, C. D., & Adrados, M. (2022) · Diagnostics · doi:10.3390/diagnostics12020406 · Cited by 12
Liu, W., Cai, Q., Yu, T., Strati, P., Hagemeister, F. B., Zhai, Q.-L., Zhang, M., Li, L., Fang, X., Li, J., et al. (2022) · PubMed Central · Cited by 11
Rasmussen, C., Gérard, L., Fadlallah, J., Corvilain, E., Galicier, L., Meignin, V., Oksenhendler, É., & Boutboul, D. (2023) · Blood Advances · doi:10.1182/bloodadvances.2023010316 · Cited by 11
Ebisawa, K., Shimura, A. N., Honda, A., Masamoto, Y., Nakahara, F., & Kurokawa, M. (2020) · Leukemia & lymphoma/Leukemia and lymphoma · doi:10.1080/10428194.2020.1834094 · Cited by 11
Increased mTORC2 pathway activation in lymph nodes of iMCD‐TAFRO
Phillips, A., Kakkis, J. J., Tsao, P., Pierson, S. K., & Fajgenbaum, D. C. (2022) · Journal of Cellular and Molecular Medicine · doi:10.1111/jcmm.17251 · Cited by 11
Self-citationRubenstein, A. I., Pierson, S. K., Shyamsundar, S., Bustamante, M. S., Gonzalez, M. V., Milller, I. D., Brandstadter, J. D., Mumau, M. D., & Fajgenbaum, D. C. (2024) · British Journal of Haematology · doi:10.1111/bjh.19279 · Cited by 10
Self-citationCostagliola, G., Marco, E. D., Massei, F., Roberti, G., Catena, F., Casazza, G., & Consolini, R. (2024) · Therapeutics and Clinical Risk Management · doi:10.2147/tcrm.s462996 · Cited by 10
Miura, K., Nishimaki‐Watanabe, H., Takahashi, H., Nakagawa, M., Otake, S., Hamada, T., Koike, T., Iizuka, K., Takeuchi, Y., Kurihara, K., et al. (2024) · Biomedicines · doi:10.3390/biomedicines12061277 · Cited by 10
Nishimura, Y., Nishikori, A., Sawada, H., Czech, T. Y., Otsuka, Y., Nishimura, M. F., Mizuno, H., Sawa, N., Momose, S., Ohsawa, K., et al. (2022) · Journal of the Japan Society of the Reticuloendothelial System · doi:10.3960/jslrt.21038 · Cited by 10
18F-FDG PET/CT and contrast-enhanced CT in the diagnosis of Castleman disease
He, L., Chen, Y., Tan, X., Sun, X., Zhang, Q. H., Luo, H., & Jiang, L. (2022) · Japanese Journal of Radiology · doi:10.1007/s11604-022-01318-6 · Cited by 10
Case report: IgG4-related intracranial lesions mimicking multiple sclerosis in a 14-year-old girl
Qing, P., Lu, C., Yan, B., Liu, C., Fox, D. A., Zhao, Y., Liu, Y., & Tan, C. (2022) · Frontiers in Neurology · doi:10.3389/fneur.2022.1007153 · Cited by 10
Cutaneous manifestations of Castleman disease
Chávez‐Álvarez, S., Villarreal‐Martínez, A., Ocampo‐Candiani, J., Gómez‐Flores, M., Vázquez‐Martínez, O., Gonzalez‐Saldivar, G., & Herz‐Ruelas, M. E. (2020) · International Journal of Dermatology · doi:10.1111/ijd.15043 · Cited by 10
Merino, L. R., Pomares, A. A., Revert, J. B., & Montes‐Moreno, S. (2023) · Journal of Clinical Pathology · doi:10.1136/jcp-2022-208696 · Cited by 9
Gao, Y., Li, S., Dang, Y., Duan, M., Zhang, L., & Li, J. (2024) · British Journal of Haematology · doi:10.1111/bjh.19827 · Cited by 9
Laurenti, L., Innocenti, I., Benintende, G., Tomasso, A., Autore, F., Fresa, A., Vuono, F., Baroni, S., Giannotta, C., Chiusolo, P., et al. (2022) · Mediterranean Journal of Hematology and Infectious Diseases · doi:10.4084/mjhid.2022.007 · Cited by 9
Refractory idiopathic multicentric Castleman disease responsive to sirolimus therapy
Bayram, E., Pehlivan, U. A., Fajgenbaum, D. C., & Paydaş, S. (2022) · American Journal of Hematology · doi:10.1002/ajh.26783 · Cited by 9
Self-citationFraticelli, S., Lucioni, M., Neri, G., Marchiori, D., Cristinelli, C., Merli, M., Monaco, R., Borra, T., Lazzaro, A., Uccella, S., et al. (2023) · International Journal of Molecular Sciences · doi:10.3390/ijms24097813 · Cited by 9
Unicentric Castleman disease: A case report of an atypical presentation and successful management
Muhammad, T., Alkheder, A., Mazloum, A., Almooay, A., Naziha, L., & Shaheen, M. (2024) · International Journal of Surgery Case Reports · doi:10.1016/j.ijscr.2024.109688 · Cited by 9
Diagnostic challenges in patients with Castleman disease, a single center experience from Hungary
Brúgós, B. C., Simon, Z., Méhes, G., Illés, Á., & Pfliegler, G. (2024) · Pathology & Oncology Research · doi:10.3389/pore.2024.1611785 · Cited by 9
Chen, L., & Fajgenbaum, D. C. (2023) · Springer eBooks · doi:10.1007/978-3-031-23488-0_51 · Cited by 9
Self-citationSevere systemic inflammation mimicking TAFRO syndrome following COVID-19
Tane, M., Kosako, H., Hosoi, H., Tabata, K., Hiroi, T., Osawa, K., Iwamoto, R., Murata, S., Mushino, T., Murata, S., et al. (2023) · International Journal of Hematology · doi:10.1007/s12185-023-03589-9 · Cited by 8
The experience of diagnosis and treatment for TAFRO syndrome
Wu, X., Zhang, X., Qian, S., Shi, C., Li, X., Feng, X., Zhu, L., Ge, J., Li, Z., & Zhang, M. (2023) · Annals of Hematology · doi:10.1007/s00277-023-05435-8 · Cited by 8
Radiological Imaging Findings of Adrenal Abnormalities in TAFRO Syndrome: A Systematic Review
Kurokawa, R., Baba, A., Kano, R., Kaneko, Y., Kurokawa, M., Gonoi, W., & Abe, O. (2024) · Biomedicines · doi:10.3390/biomedicines12040837 · Cited by 8
Long-term clinicopathological characteristics of TAFRO syndrome and its relapse: a case series study
Yoshimura, Y., Mizuno, H., Ikuma, D., Yamanouchi, M., Sekine, A., Suwabe, T., Oba, Y., Kurihara, S., Sugimoto, H., Inoue, N., et al. (2024) · Clinical Kidney Journal · doi:10.1093/ckj/sfae110 · Cited by 8
Alnoor, F., Rangel, A. E., Luo, M., Silva, O., Chisholm, K. M., O’Malley, D. P., Warnke, R. A., Kumar, J., & Ohgami, R. S. (2024) · International Journal of Laboratory Hematology · doi:10.1111/ijlh.14395 · Cited by 8
Mimickers of pulmonary lymphoma
Nguyen, H., & Song, J. Y. (2020) · Seminars in Diagnostic Pathology · doi:10.1053/j.semdp.2020.05.002 · Cited by 8
IFN-γ promotes the progression of iMCD by activating inflammatory monocytes
Yin, X., Liu, Y., Ding, S., Ge, J., Yang, M., Wang, Z., Lv, Z., Luo, X., Ma, L., Yu, W., et al. (2025) · Blood · doi:10.1182/blood.2024027689 · Cited by 7
Guayboon, T., Chinthammitr, Y., Sukpanichnant, S., Horthongkham, N., & Angkasekwinai, N. (2021) · Medicine · doi:10.1097/md.0000000000028077 · Cited by 7
Hu, S., Li, Z., Wang, H., Chen, L., Ma, Y., Zhu, X., Li, J., Dong, R., Yao, W., Dong, C., et al. (2023) · European Journal of Pediatrics · doi:10.1007/s00431-023-05235-2 · Cited by 7
Liu, Y., Zhen, J., Gao, Y., Li, S., Dang, Y., Xu, H., Zhang, L., & Li, J. (2024) · British Journal of Haematology · doi:10.1111/bjh.19966 · Cited by 7
Feng, A., Gonzalez, M. V., Kalaycıoğlu, M., Yin, X., Mumau, M. D., Shyamsundar, S., Bustamante, M. S., Chang, S. E., Dhingra, S., Dodig‐Crnković, T., et al. (2025) · Frontiers in Immunology · doi:10.3389/fimmu.2025.1528465 · Cited by 7
Self-citationFrom pathogenesis to personalized treatments of neuropathies in hematological malignancies
Briani, C., Visentin, A., Cerri, F., & Quattrini, A. (2020) · Journal of the Peripheral Nervous System · doi:10.1111/jns.12405 · Cited by 7
Yan, A. P., Carcao, M. D., Nagy, A., & Punnett, A. (2022) · Pediatric Blood & Cancer · doi:10.1002/pbc.29638 · Cited by 7
Guo, M., Nong, L., Wang, M., Zhang, Y., Wang, L., Sun, Y., Wang, Q., Liu, H., Ou, J.-P., Cen, X., et al. (2023) · Annals of Hematology · doi:10.1007/s00277-023-05472-3 · Cited by 7
POEMS syndrome: a neuromuscular perspective
Gonçalves, T. A. P., Donadel, C. D., Frezatti, R. S. S., Schiavoni, M. C. L., Gonçalves, M. V. M., Garibaldi, P. M. M., Santis, G. C. D., Marques, W., & Tomaselli, P. J. (2026) · Journal of Neurology Neurosurgery & Psychiatry · doi:10.1136/jnnp-2025-336633 · Cited by 6
Overview of Research Status in Castleman Disease
Wang, W., Liu, Z., & Zhao, X. (2024) · Clinical Lymphoma Myeloma & Leukemia · doi:10.1016/j.clml.2024.05.024 · Cited by 6
Tane, M., Kosako, H., Sonoki, T., & Hosoi, H. (2024) · Biomedicines · doi:10.3390/biomedicines12061287 · Cited by 6
Abdallah, N. H., Habermann, T. M., Buadi, F. K., Gertz, M. A., Lacy, M. Q., Rajkumar, S. V., Dingli, D., Go, R. S., Hayman, S. R., Kumar, S. K., et al. (2022) · American Journal of Hematology · doi:10.1002/ajh.26466 · Cited by 6
Self-citationThe disease course of Castleman disease patients with fatal outcomes in the ACCELERATE registry
Fajgenbaum, D. C., Pierson, S. K., Kanhai, K. J. K., Bagg, A., Alapat, D. V., Lim, M. S., Lechowicz, M. J., Srkalović, G., Uldrick, T. S., van Rhee, F., et al. (2022) · British Journal of Haematology · doi:10.1111/bjh.18214 · Cited by 6
Self-citationCase Report: A rare case of primary hepatic Castleman’s disease mimicking a liver tumor
Chen, H., Pang, X., Li, J., Xu, B., & Liu, Y. (2022) · Frontiers in Oncology · doi:10.3389/fonc.2022.974263 · Cited by 6
Castleman's disease in the pelvic retroperitoneum: A case report
Zhao, Q., Zhang, X., Yang, X., & Huang, S. (2022) · Experimental and Therapeutic Medicine · doi:10.3892/etm.2022.11596 · Cited by 6
Meli, M., Arrabito, M., Salvatorelli, L., Soma, R., Presti, S., Licciardello, M., Miraglia, V. L., Scuderi, M. G., Belfiore, G., Magro, G. G., et al. (2022) · Children · doi:10.3390/children9101472 · Cited by 6
Oportus, J., Hojman, L. P., Gonzalez, V., & Karsulovic, C. (2025) · Lymphatics · doi:10.3390/lymphatics3010001 · Cited by 5
Metadata
- Authors
- Dispenzieri, A., & Fajgenbaum, D. C.
- Affiliations
- Mayo Clinic (US)
- University of Pennsylvania (US)
- Venue
- Blood
- Publisher
- American Society of Hematology
- Published
- 2020-04-16
- Volume
- 135
- Issue
- 16
- Pages
- 1353-1364
- ISSN
- 0006-4971 (ISSN-L)
- 1528-0020
- OpenAlex
- W3006713791
- Cited by
- 487
- References
- 104
- Citations by year
- 2026: 69 · 2025: 90 · 2024: 90 · 2023: 81 · 2022: 91 · 2021: 52 · 2020: 13
- FWCI
- 6.36
- Type
- journal article
- Language
- en
- Open access
- Locations
- Blood (publishedVersion)
- PubMed (publishedVersion)
- PubMed Central (submittedVersion)
- Funders
- National Institutes of Health (2r01hl141408-06)
- National Heart, Lung, and Blood Institute (R01-HL141408)
- Topics
- Health Sciences › Medicine › Oncology › Viral-associated cancers and disorders
- Health Sciences › Medicine › Pathology and Forensic Medicine › Lymphadenopathy Diagnosis and Analysis
- Health Sciences › Medicine › Rheumatology › IgG4-Related and Inflammatory Diseases
- Keywords
- Castleman disease, unicentric Castleman disease, multicentric Castleman disease, idiopathic multicentric Castleman disease, POEMS syndrome, rituximab, disease classification, pathogenesis
- MeSH terms
- Rituximab, Interleukin-6 Inhibitors, Animals, Castleman Disease, Herpesviridae Infections, Humans, Immunologic Factors, Herpesvirus 8, Human
About these checks
Registry, retraction, Cites and statistics results are computed, not judged, with one exception: a printed reference that no index lists is read once by a model before it counts as a citation error. Claims are extracted by a model and kept only when their quote appears verbatim in the text; each cited source is then checked, with a model’s help, for whether it says what the claim relies on. Those verdicts can be wrong — read the claim’s quote and the cited source before relying on one.
Statistics and arithmetic are recomputed, not judged.
Confidence bands are shown only for fields calibrated on our annotated test set. None is calibrated yet, so no band is shown.
What counts as a claim ›How we measure confidence ›How we check this ›
Are you an author, or do you see a problem with this page? Request a review
