Diagnostik und Therapie der nichtsyndromalen und syndromalen Kraniosynostosen
Abstract
Premature craniosynostosis is caused by a premature closure of single or multiple sutures of the cranial vault. It may result not only in aesthetic but also in functional disorders with an occasional ICP increase leading to a dramatic loss of vision. In the 1970s,Paul Tessier published his craniofacial principles for the primary treatment of craniosynostosis. His approach has gained wide acceptance over the previously described craniectomies and bone flaps, especially because of the significant benefits with an acceptably low level of morbidity. The following paper reviews the different kinds of craniosynostoses, their specific clinical manifestations, the necessary diagnostic examinations and the specific surgical procedures and operative results.
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In 2003, Cedzich and Farmand recommended confirming suspected craniosynostosis with posterior-anterior and lateral skull X-ray and CT, with SPECT scintigraphy to assess suture occlusion and sonography only for follow-up.
“In 2003, Cedzich and Farmand published the status of the necessary diagnosis of craniosynostosis. Accordingly, an existing suspected diagnosis should be confirmed at that time by a posterior-anterior and a lateral conventional X-Ray of the skull and a more detailed image should also be obtained by computed tomography (CT).”
From Developments in diagnostic and surgical techniques in children with sagittal suture craniosynostosis: a systematic review spanning the last 30 years (2025) · cites this paper as [26]
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Evaluation and management of nonsyndromic craniosynostosis
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“4,5 11-15 There is no prospective investigation of ICP at the time of primary surgical intervention in the literature.”
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“For example, Cedzich and Farmand 2003 recommended a combination of conventional radiographs and CT imaging for diagnosis [26], while Fearon et al. 2007 advised against unnecessary CT images due to radiation risks and the good clinical accessibility especially of CI [29].”
1Manualmedizinische Auffälligkeiten und Störungen im Säuglingsalter
Schnellbacher, T., Seifert, I., & Buchmann, J. A. (2020) · Springer eBooks · doi:10.1007/978-3-662-60781-7_3
- Authors
- Cedzich, C., & Farmand, M.
- Affiliations
- Nuremberg Hospital (DE)
- Venue
- HNO
- Published
- 2003-03-01
- Volume
- 51
- Issue
- 3
- Pages
- 198-208
- ISSN
- 0017-6192 (ISSN-L)
- 1433-0458
- OpenAlex
- W2031670666
- Cited by
- 6
- References
- 42
- Citations by year
- 2025: 1 · 2023: 1 · 2020: 1 · 2014: 1 · 2012: 1
- FWCI
- 0.00
- Type
- journal article
- Language
- de
- Open access
- closed
- Licence
- www.springer.com/tdm (tdm)
- Locations
- HNO (publishedVersion)
- PubMed (publishedVersion)
- Topics
- Life Sciences › Biochemistry, Genetics and Molecular Biology › Genetics › Craniofacial Disorders and Treatments
- Health Sciences › Medicine › Surgery › Reconstructive Facial Surgery Techniques
- Health Sciences › Medicine › Surgery › Pectus Deformity Diagnosis and Treatment
- Keywords
- craniosynostosis, nonsyndromic craniosynostosis, syndromic craniosynostosis, premature suture closure, cranial vault, craniosynostosis surgery, craniectomy, bone flap, intracranial pressure, vision loss, diagnostic workup, clinical features
- MeSH terms
- Child, Preschool, Craniosynostoses, Craniotomy, Diagnostic Imaging, Female, Follow-Up Studies, Genetic Counseling, Humans, Image Processing, Computer-Assisted, Infant, Intracranial Pressure, Male, Syndrome, Imaging, Three-Dimensional
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