The DOI matches its Crossref record; 115 of the 115 references it cites were found in a registry or an index.
Progress in therapies for cystic fibrosis
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Citations
Cites
Adapting Proteostasis for Disease Intervention
Balch, W. E., Morimoto, R. I., Dillin, A., & Kelly, J. W. (2008) · Science · doi:10.1126/science.1141448 · Cited by 2,495
A CFTR Potentiator in Patients with Cystic Fibrosis and the G551D Mutation
Ramsey, B. W., Davies, J., McElvaney, N. G., Tullis, E., Bell, S. C., Dřevínek, P., Griese, M., McKone, E. F., Wainwright, C. E., Konstan, M. W., et al. (2011) · New England Journal of Medicine · doi:10.1056/nejmoa1105185 · Cited by 2,195
Microbial pathogenesis in cystic fibrosis: mucoid Pseudomonas aeruginosa and Burkholderia cepacia
Govan, J. R. W., & Deretic, V. P. (1996) · Microbiological Reviews · doi:10.1128/mmbr.60.3.539-574.1996 · Cited by 1,812
Cheng, S. H., Gregory, R. J., Marshall, J., Paul, S., Souza, D. W., White, G. A., O'Riordan, C. R., & Smith, A. E. (1990) · Cell · doi:10.1016/0092-8674(90)90148-8 · Cited by 1,792
Lumacaftor–Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR
Wainwright, C. E., Elborn, J. S., Ramsey, B. W., Marigowda, G., Huang, X., Cipolli, M., Colombo, C., Davies, J. C., De Boeck, K., Flume, P. A., et al. (2015) · New England Journal of Medicine · doi:10.1056/nejmoa1409547 · Cited by 1,622
Self-citationMolecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis
Welsh, M. J., & Smith, A. E. (1993) · Cell · doi:10.1016/0092-8674(93)90353-r · Cited by 1,485
Schwank, G., Koo, B.-K., Sasselli, V., Dekkers, J. F., Heo, I., Demircan, T., Sasaki, N., Boymans, S., Cuppen, E., van der Ent, C. K., et al. (2013) · Cell Stem Cell · doi:10.1016/j.stem.2013.11.002 · Cited by 1,424
TMEM16A confers receptor-activated calcium-dependent chloride conductance
Yang, Y. D., Cho, H., Koo, J. Y., Tak, M. H., Cho, Y., Shim, W.-S., Park, S. P., Lee, J., Lee, B., Kim, B.-M., et al. (2008) · Nature · doi:10.1038/nature07313 · Cited by 1,283
TMEM16A, A Membrane Protein Associated with Calcium-Dependent Chloride Channel Activity
Caputo, A., Caci, E., Ferrera, L., Pedemonte, N., Barsanti, C., Sondo, E., Pfeffer, U., Ravazzolo, R., Zegarra-Moran, O., & Galietta, L. J. V. (2008) · Science · doi:10.1126/science.1163518 · Cited by 1,263
Expression Cloning of TMEM16A as a Calcium-Activated Chloride Channel Subunit
Schroeder, B. C., Cheng, T., Jan, Y. N., & Jan, L. Y. (2008) · Cell · doi:10.1016/j.cell.2008.09.003 · Cited by 1,148
Cited by
VX-659–Tezacaftor–Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles
Davies, J. C., Moskowitz, S. M., Brown, C., Horsley, A., Mall, M. A., McKone, E. F., Plant, B. J., Prais, D., Ramsey, B. W., Taylor-Cousar, J. L., et al. (2018) · New England Journal of Medicine · doi:10.1056/nejmoa1807119 · Cited by 331
Triple Therapy for Cystic Fibrosis Phe508del –Gating and –Residual Function Genotypes
Barry, P. J., Mall, M. A., Álvarez, A., Colombo, C., de Winter-de Groot, K. M., Fajac, I., McBennett, K. A., McKone, E. F., Ramsey, B. W., Sutharsan, S., et al. (2021) · New England Journal of Medicine · doi:10.1056/nejmoa2100665 · Cited by 283
Structure, Gating, and Regulation of the CFTR Anion Channel
Csanády, L., Vergani, P., & Gadsby, D. C. (2019) · Physiological Reviews · doi:10.1152/physrev.00007.2018 · Cited by 262
Flume, P. A., Biner, R. F., Downey, D. G., Brown, C., Jain, M., Fischer, R., De Boeck, K., Sawicki, G. S., Chang, P., Paz-Diaz, H., et al. (2021) · The Lancet Respiratory Medicine · doi:10.1016/s2213-2600(20)30510-5 · Cited by 52
Tezacaftor/ivacaftor in people with cystic fibrosis heterozygous for minimal function CFTR mutations
Munck, A., Kerem, E., Ellemunter, H., Campbell, D., Wang, L. T., Ahluwalia, N., Owen, C. A., & Wainwright, C. (2020) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2020.04.015 · Cited by 33
Metadata
- Authors
- De Boeck, K., & Amaral, M. D.
- Venue
- The Lancet Respiratory Medicine
- Publisher
- Elsevier BV
- Published
- 2016-08
- Volume
- 4
- Issue
- 8
- Pages
- 662-674
- ISSN
- 2213-2600 (ISSN-L)
- OpenAlex
- W2316431812
- Cited by
- 451
- References
- 115
- FWCI
- 29.40
- Type
- journal article
- Language
- en
- Open access
- closed
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Registry, retraction, Cites and statistics results are computed, not judged, with one exception: a printed reference that no index lists is read once by a model before it counts as a citation error. Claims are extracted by a model and kept only when their quote appears verbatim in the text; each cited source is then checked, with a model’s help, for whether it says what the claim relies on. Those verdicts can be wrong — read the claim’s quote and the cited source before relying on one.
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How to cite
Cite CoChat for the checks on this page, and the paper for its own findings.
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- CoChat. (2026). Citation check: Progress in therapies for cystic fibrosis. https://app.cochat.ai/papers/10.1016/s2213-2600(16)00023-0
- The paper
- De Boeck, K., & Amaral, M. D. (2016). Progress in therapies for cystic fibrosis. The Lancet Respiratory Medicine. https://doi.org/10.1016/s2213-2600(16)00023-0
Data sources
Bibliographic data: Semantic Scholar, OpenAlex, Crossref.
Contains information from the Semantic Scholar Academic Graph Datasets, made available under the ODC Attribution License (ODC-BY 1.0).
Semantic Scholar’s data is described in: Kinney, R., et al. (2023). The Semantic Scholar Open Data Platform. arXiv:2301.10140.
