Polyglutamine expansion down-regulates specific neuronal genes before pathologic changes in SCA1

Cited by (374)

Items 101–200 of 374

1. From mice to men: lessons from mutant ataxic mice
   Jan Cendelín · 2014 · Cerebellum & Ataxias
2. Post-translational modifications of expanded polyglutamine proteins: impact on neurotoxicity
   Pennuto, M., Palazzolo, I., Poletti, A. · 2009 · Human Molecular Genetics
3. Enhanced SUMOylation in polyglutamine diseases
   Hiroko Ueda, Jun Goto, Hideji Hashida, Xia Lin, Kiyomitsu Oyanagi, Hitoshi Kawano, Huda Yahya Zoghbi, Ichiro Kanazawa, Hitoshi Okazawa · 2002 · Biochemical and Biophysical Research Communications
4. TATA-binding protein in neurodegenerative disease
   Willeke van Roon‐Mom, Suzanne J. Reid, Richard L. M. Faull, Russell G. Snell · 2005 · Neuroscience
5. Gene Expression Profiling in Ataxin-3 Expressing Cell Lines Reveals Distinct Effects of Normal and Mutant Ataxin-3
   Bernd O. Evert, Ina R. Vogt, Ana Maria Menezes Vieira-Saecker, Lucia Ozimek, Rob A. I. de Vos, Ewout R. P. Brunt, Thomas Klockgether, Ullrich Wüllner · 2003 · Journal of Neuropathology & Experimental Neurology
6. Cellular and circuit mechanisms underlying spinocerebellar ataxias
   Pratap Meera, Stefan M. Pulst, Thomas S. Otis · 2016 · The Journal of Physiology
7. Spinocerebellar ataxias
   Bing‐Wen Soong, Patrick J. Morrison · 2018 · Handbook of clinical neurology
8. Progressive impairment of cerebellar mGluR signalling and its therapeutic potential for cerebellar ataxia in spinocerebellar ataxia type 1 model mice
   Аnton N. Shuvaev, Nobutake Hosoi, Yamato Sato, Dai Yanagihara, Hirokazu Hirai · 2016 · The Journal of Physiology
9. Therapeutic opportunities in polyglutamine disease
   Robert E. Hughes, James M. Olson · 2001 · Nature Medicine
10. Computational neurobiology is a useful tool in translational neurology: the example of ataxia
    Sherry-Ann Brown, L. McCullough, L. Loew · 2014 · Frontiers in Neuroscience
11. SCA1 molecular genetics: a history of a 13 year collaboration against glutamines.
    H. Orr, H. Zoghbi · 2001 · Human Molecular Genetics
12. SCA15 Due to Large ITPR1 Deletions in a Cohort of 333 White Families With Dominant Ataxia
    Cécilia Marelli, Joyce van de Leemput, Janel O. Johnson, François Tison, Christel Thauvin‐Robinet, Fabienne Picard, Christine Tranchant, Dena G. Hernandez, Bernard Huttin, J Boulliat et al. · 2011 · Archives of Neurology
13. Role of Heat Shock Proteins During Polyglutamine Neurodegeneration: Mechanisms and Hypothesis
    Andreas Wyttenbach · 2004 · Journal of Molecular Neuroscience
14. Inducible PC12 cell model of Huntington’s disease shows toxicity and decreased histone acetylation
    Shuichi Igarashi, Hokuto Morita, Kyla M. Bennett, Yuji Tanaka, Simone Engelender, Matthew F. Peters, Jillian K. Cooper, Jonathan D. Wood, Akira Sawa, Christopher A. Ross · 2003 · Neuroreport
15. Down-regulation of the dopamine receptor D2 in mice lacking ataxin 1.
    R. Goold, M. Hubank, A. Hunt, J. Holton, R. Menon, T. Révész, M. Pandolfo, A. Matilla-Dueñas · 2007 · Human Molecular Genetics
16. Mutant ataxin1 disrupts cerebellar development in spinocerebellar ataxia type 1
    Chandrakanth Reddy Edamakanti, Jeehaeh Do, Alessandro Didonna, Marco Martina, Puneet Opal · 2018 · Journal of Clinical Investigation
17. Atxn2 Knockout and CAG42-Knock-in Cerebellum Shows Similarly Dysregulated Expression in Calcium Homeostasis Pathway
    Melanie Vanessa Halbach, Suzana Gispert, Tanja Stehning, Ewa Damrath, Michael J. Walter, Georg W. J. Auburger · 2016 · The Cerebellum
18. Polyglutamine Expansions
    Paul Ko Ferrigno, Pamela A. Silver · 2000 · Neuron
19. What is the Pathogenic CAG Expansion Length in Huntington’s Disease?
    Jasmine Donaldson, Sophie Powell, Nadia Rickards, Peter Holmans, Lesley Jones · 2021 · Journal of Huntington s Disease
20. A new humanized ataxin-3 knock-in mouse model combines the genetic features, pathogenesis of neurons and glia and late disease onset of SCA3/MJD
    Pawel Michal Switonski, Wojciech J. Szlachcic, Włodzimierz J. Krzyżosiak, Maciej Figiel · 2014 · Neurobiology of Disease
21. Pharmacological enhancement of mGlu1 metabotropic glutamate receptors causes a prolonged symptomatic benefit in a mouse model of spinocerebellar ataxia type 1
    S. Notartomaso, C. Zappulla, F. Biagioni, M. Cannella, D. Bucci, G. Mascio, P. Scarselli, F. Fazio, F. Weisz, L. Lionetto et al. · 2013 · Molecular Brain
22. Cross linking of polyglutamine domains catalyzed by tissue transglutaminase is greatly favored with pathological-length repeats: does transglutaminase activity play a role in (CAG)n/Qn-expansion diseases?
    Arthur J.L. Cooper, Thomas M. Jeitner, Vittorio Gentile, John P. Blass · 2002 · Neurochemistry International
23. The Structure of the AXH Domain of Spinocerebellar Ataxin-1
    Yu Wai Chen, Mark D. Allen, Dmitry B. Veprintsev, Jan Löwe, Mark Bycroft · 2004 · Journal of Biological Chemistry
24. Transcriptional alterations and chromatin remodeling in polyglutamine diseases
    Dominique Helmlinger, Làszlò Tora, Didier Devys · 2006 · Trends in Genetics
25. Defective calcium homeostasis in the cerebellum in a mouse model of Niemann–Pick A disease
    Luba Ginzburg, Anthony H. Futerman · 2005 · Journal of Neurochemistry
26. Aberrant Cerebellar Circuitry in the Spinocerebellar Ataxias
    Katherine J. Robinson, Maxinne Watchon, Angela S. Laird · 2020 · Frontiers in Neuroscience
27. Glutamate transporters GLAST and EAAT4 regulate postischemic Purkinje cell death: An in vivo study using a cardiac arrest model in mice lacking GLAST or EAAT4
    Akihide Yamashita, Koshi Makita, Toshihiko Kuroiwa, Kohichi Tanaka · 2006 · Neuroscience Research
28. Neuronal intranuclear inclusions and neuropil aggregates in HdhCAG(150) knockin mice
    Sara J. Tallaksen‐Greene, Andrew B. Crouse, Jesse M. Hunter, Peter J. Detloff, Roger L. Albin · 2005 · Neuroscience
29. Mouse Models of Polyglutamine Diseases: Review and Data Table. Part I
    Maciej Figiel, Wojciech J. Szlachcic, Pawel Michal Switonski, Agnieszka Gabka, Włodzimierz J. Krzyżosiak · 2012 · Molecular Neurobiology
30. Insoluble TATA-binding protein accumulation in Huntington’s disease cortex
    Willeke van Roon‐Mom, Suzanne J. Reid, A. Lesley Jones, Marcy E. MacDonald, Richard L. M. Faull, Russell G. Snell · 2002 · Molecular Brain Research
31. Molecular Pathogenesis of Spinocerebellar Ataxia Type 6
    Holly B. Kordasiewicz, Christopher Manuel Gomez · 2007 · Neurotherapeutics
32. Recent advances in understanding the pathogenesis of polyglutamine diseases: involvement of molecular chaperones and ubiquitin-proteasome pathway
    Nihar Ranjan Jana, Nobuyuki Nukina · 2003 · Journal of Chemical Neuroanatomy
33. Impaired mTORC1-Dependent Expression of Homer-3 Influences SCA1 Pathophysiology.
    Céline Ruegsegger, David M. Stucki, Silvio Steiner, Nico Angliker, Julika Radecke, É. Keller, Benoît Zuber, M. Rüegg, Smita Saxena · 2016 · Neuron
34. Calcium Dynamics and Electrophysiological Properties of Cerebellar Purkinje Cells in SCA1 Transgenic Mice
    Takafumi Inoue, Xi Lin, Kristi A. Kohlmeier, Harry T. Orr, Huda Yahya Zoghbi, William N. Ross · 2001 · Journal of Neurophysiology
35. Glial and neuronal expression of polyglutamine proteins induce behavioral changes and aggregate formation in Drosophila
    Doris Kretzschmar, Jakob A. Tschäpe, Alexandre Bettencourt da Cruz, Esther Asan, Burkhard Poeck, Roland Strauß, Gert O. Pflugfelder · 2004 · Glia
36. Identification of a presymptomatic molecular phenotype in Hdh CAG knock-in mice
    Elisa Fossale · 2002 · Human Molecular Genetics
37. The role of LANP and ataxin 1 in E4F‐mediated transcriptional repression
    Cvetanovic, Marija, Rooney, Robert J, Garcia, Jesus J, Toporovskaya, Nataliya, Zoghbi, Huda Y, Opal, Puneet · 2007 · The EMBO Reports
38. Spinocerebellar Ataxia Type 1—Modeling the Pathogenesis of a Polyglutamine Neurodegenerative Disorder in Transgenic Mice
    H. B. Clark, H. Orr · 2000 · Journal of Neuropathology and Experimental Neurology
39. Distinct Behavioral and Neuropathological Abnormalities in Transgenic Mouse Models of HD and DRPLA
    Gabriele Schilling, Hyder Azad Jinnah, Vicky Gonzales, Michael L. Coonfield, Yujin Kim, Jonathan Wood, Donald L. Price, Xiao‐Jiang Li, Nancy A. Jenkins, Neal G. Copeland et al. · 2001 · Neurobiology of Disease
40. Dynamics of CAG repeat loci revealed by the analysis of their variability
    Aida M. Andrés, Óscar Lao, Marta Soldevila, Francesc Calafell, Jaume Bertranpetit · 2002 · Human Mutation
41. Disruption of metabotropic glutamate receptor signalling is a major defect at cerebellar parallel fibre–Purkinje cell synapses in staggerer mutant mice
    Kazuhiro Mitsumura, Nobutake Hosoi, Nobuhiko Furuya, Hirokazu Hirai · 2011 · The Journal of Physiology
42. Increased transcript diversity: novel splicing variants of Machado–Joseph Disease gene (ATXN3)
    Conceição Bettencourt, Cristina Maria Pereira dos Santos, Rafaél Montiel, Maria do Carmo Costa, Pablo Cruz‐Morales, Liliana Ribeiro Santos, Nélson Simões, Teresa Taylor Kay, João Vasconcelos, Patrı́cia Maciel et al. · 2009 · Neurogenetics
43. A positive feedback loop linking enhanced mGluR function and basal calcium in spinocerebellar ataxia type 2
    Pratap Meera, Stefan M. Pulst, Thomas S. Otis · 2017 · eLife
44. The Moonwalker Mouse: New Insights into TRPC3 Function, Cerebellar Development, and Ataxia
    Esther B. E. Becker · 2014 · The Cerebellum
45. Spinocerebellar ataxia type 5
    Katherine A. Dick, Yoshio Ikeda, John Day, Laura P.W. Ranum · 2011 · Handbook of clinical neurology
46. Spinocerebellar ataxias caused by polyglutamine expansions: A review of therapeutic strategies
    Underwood, Benjamin R., Rubinsztein, David C. · 2008 · The Cerebellum
47. Triplet repeats, RNA secondary structure and toxic gain-of-function models for pathogenesis
    Rui P. Galvão, Luı́s Mendes-Soares, Joana Câmara, Isabel Jaco, Maria Carmo‐Fonseca · 2001 · Brain Research Bulletin
48. Interaction of expanded polyglutamine stretches with nuclear transcription factors leads to aberrant transcriptional regulation in polyglutamine diseases
    Takayoshi Shimohata, Osamu Onodera, Shoji Tsuji · 2000 · Neuropathology
49. The histone deacetylase HDAC3 is essential for Purkinje cell function, potentially complicating the use of HDAC inhibitors in SCA1
    Anand Venkatraman, Yuan-Shih Hu, Alessandro Didonna, Marija Cvetanović, Aleksandar Krbanjevic, Patrice Bilesimo, Puneet Opal · 2014 · Human Molecular Genetics
50. Type-1 metabotropic glutamate receptor signaling in cerebellar Purkinje cells in health and disease
    Masanobu Kano, Takaki Watanabe · 2017 · F1000Research
51. Analysis of cerebellar Purkinje cells using EAAT4 glutamate transporter promoter reporter in mice generated via bacterial artificial chromosome-mediated transgenesis
    Dan Gincel, Melissa R. Regan, Lin Jin, Andrew M. Watkins, Dwight E. Bergles, Jeffrey D. Rothstein · 2006 · Experimental Neurology
52. Altered Purkinje cell miRNA expression and SCA1 pathogenesis
    Edgardo Rodríguez-Lebrón, Gumei Liu, Megan S. Keiser, Mark A. Behlke, Beverly L. Davidson · 2013 · Neurobiology of Disease
53. CSF SERPINA3 Levels Are Elevated in Patients With Progressive MS
    Nicolás Fissolo, Clara Matute‐Blanch, Mohamoud Osman, Carme Costa, Rucsanda Pinteac, Berta Miró, Álex Sánchez‐Pla, Verónica Brito, Irena Dujmović, Margarete M. Voortman et al. · 2021 · Neurology Neuroimmunology & Neuroinflammation
54. Epigenetics in Nucleotide Repeat Expansion Disorders
    Fang He, Peter K. Todd · 2011 · Seminars in Neurology
55. Gene Deregulation and Underlying Mechanisms in Spinocerebellar Ataxias With Polyglutamine Expansion
    Anna Niewiadomska-Cimicka, Antoine Hache, Yvon Trottier · 2020 · Frontiers in Neuroscience
56. Identification of candidate Purkinje cell-specific markers by gene expression profiling in wild-type and pcd3J mice
    Yongqi Rong, Taiyu Wang, James I. Morgan · 2004 · Molecular Brain Research
57. Loss of cerebellar glutamate transporters EAAT4 and GLAST differentially affects the spontaneous firing pattern and survival of Purkinje cells
    Emma Perkins, Yvonne L. Clarkson, Daumante Šuminaite, Alastair Robert Lyndon, Kohichi Tanaka, Jeffrey D. Rothstein, Paul Skehel, David J. A. Wyllie, M. T. Jackson · 2018 · Human Molecular Genetics
58. Disrupted Calcium Signaling in Animal Models of Human Spinocerebellar Ataxia (SCA)
    Francesca Prestori, Francesco Domenico Moccia, Egidio Ugo D'Angelo · 2019 · International Journal of Molecular Sciences
59. Keeping Our Calcium in Balance to Maintain Our Balance.
    M. Mark, J. Schwitalla, Michelle Groemmke, S. Herlitze · 2017 · Biochemical and Biophysical Research Communications - BBRC
60. Reduction of Purkinje Cell Pathology in SCA1 Transgenic Mice by p53 Deletion
    Mona D. Shahbazian, Harry T. Orr, Huda Yahya Zoghbi · 2001 · Neurobiology of Disease
61. Mouse Models of Polyglutamine Diseases in Therapeutic Approaches: Review and Data Table. Part II
    Pawel Michal Switonski, Wojciech J. Szlachcic, Agnieszka Gabka, Włodzimierz J. Krzyżosiak, Maciej Figiel · 2012 · Molecular Neurobiology
62. Molecular pathway analysis towards understanding tissue vulnerability in spinocerebellar ataxia type 1
    Terri M. Driessen, Jong Seo Lee, Janghoo Lim · 2018 · eLife
63. SCA1 – Phosphorylation, a Regulator of Atxain-1 Function and Pathogenesis
    H. Orr · 2012 · Progress in neurobiology
64. Compensation of Inositol 1,4,5-Trisphosphate Receptor Function by Altering Sarco-Endoplasmic Reticulum Calcium ATPase Activity in theDrosophilaFlight Circuit
    Santanu Banerjee, Rohit Joshi, Gayatri Venkiteswaran, Neha Agrawal, Sonal Srikanth, Farhan Alam, Gaiti Hasan · 2006 · Journal of Neuroscience
65. Recent advances in degenerative ataxias
    Thomas Klockgether · 2000 · Current Opinion in Neurology
66. Longitudinal single-cell transcriptional dynamics throughout neurodegeneration in SCA1
    Leon Tejwani, Neal G. Ravindra, Chang‐Woo Lee, Yubao Cheng, Billy Nguyen, Kimberly P. Luttik, Luhan Ni, Shupei Zhang, Logan M Morrison, John T. Gionco et al. · 2023 · Neuron
67. A pathogenetic classification of hereditary ataxias: Is the time ripe?
    Giuseppe De Michele, Giovanni Coppola, Sergio Cocozza, Alessandro Filla · 2004 · Journal of Neurology
68. TRPC Channels: Prominent Candidates of Underlying Mechanism in Neuropsychiatric Diseases
    Chang Zeng, Fafa Tian, Bo Xiao · 2014 · Molecular Neurobiology
69. Ca2+ signaling and spinocerebellar ataxia
    Chihiro Hisatsune, Kozo Hamada, Katsuhiko Mikoshiba · 2018 · Biochimica et Biophysica Acta (BBA) - Molecular Cell Research
70. Creatine-supplemented diet extends Purkinje cell survival in spinocerebellar ataxia type 1 transgenic mice but does not prevent the ataxic phenotype
    William F. Kaemmerer, Cecília M. P. Rodrigues, Clifford J. Steer, Walter C. Low · 2001 · Neuroscience
71. Precision medicine in spinocerebellar ataxias: treatment based on common mechanisms of disease.
    David D. Bushart, Geoffrey G. Murphy, Vikram G. Shakkottai · 2016 · PubMed Central
72. The InsP3 receptor: its role in neuronal physiology and neurodegeneration
    Santanu Banerjee, Gaiti Hasan · 2005 · BioEssays
73. Case of Infantile Onset Spinocerebellar Ataxia Type 5
    Francois-Dominique Jacob, Eugenia Ho, Mayra Martinez Ojeda, Basil T. Darras, Omar Khwaja · 2012 · Journal of Child Neurology
74. Spinal cord molecular profiling provides a better understanding of Amyotrophic Lateral Sclerosis pathogenesis
    Andrea Malaspina, Jacqueline de Belleroche · 2004 · Brain Research Reviews
75. Clinical Features and Molecular Mechanisms of Spinal and Bulbar Muscular Atrophy (SBMA)
    Masahisa Katsuno, Haruhiko Banno, Keisuke Suzuki, Hiroaki Adachi, Fumiaki Tanaka, Gen Sobue · 2010 · Advances in experimental medicine and biology
76. Altered Expression of the NoncodinghsrωGene Enhances poly-Q Induced Neurotoxicity inDrosophila
    Sonali Sengupta, S. C. Lakhotia · 2006 · RNA Biology
77. Polyglutamine Disease: Acetyltransferases Awry
    Robert E. Hughes · 2002 · Current Biology
78. Identification of Novel Pathways Associated with Patterned Cerebellar Purkinje Neuron Degeneration in Niemann-Pick Disease, Type C1
    Kyle B. Martin, Ian Martin Williams, Celine V. M. Cluzeau, Antony Cougnoux, Ryan Dale, James Iben, Niamh X. Cawley, Christopher A. Wassif, Forbes D. Porter · 2019 · International Journal of Molecular Sciences
79. Neurological and Motor Disorders: Neuronal Store-Operated Ca2+ Signaling: An Overview and Its Function
    Sunitha Bollimuntha, Biswaranjan Pani, Brij Bhan Singh · 2017 · Advances in experimental medicine and biology
80. Novel therapies in the search for a cure for Huntington's disease
    M. Flint Beal, Philippe Hantraye · 2001 · Proceedings of the National Academy of Sciences
81. Loss of Intrinsic Organization of Cerebellar Networks in Spinocerebellar Ataxia Type 1: Correlates with Disease Severity and Duration
    A. Solodkin, Eitan Peri, E. Chen, E. Ben-Jacob, C. M. Gomez · 2011 · Cerebellum
82. Mouse models for autism: report from a meeting
    Thomas R. Insel · 2001 · Mammalian Genome
83. Candidate Screening of the TRPC3 Gene in Cerebellar Ataxia
    Esther B. E. Becker, Brent L. Fogel, Sanjeev Rajakulendran, Anna Dulneva, Michael G. Hanna, Susan Perlman, Daniel H. Geschwind, Kay E. Davies · 2011 · The Cerebellum
84. Step out of the Groove: Epigenetic Gene Control Systems and Engineered Transcription Factors
    Pernette J. Verschure, Astrid E. Visser, Marianne G. Rots · 2006 · Advances in genetics
85. Calcium homeostasis and spinocerebellar ataxia-1 (SCA-1).
    P. J. Vig, S. Subramony, D. McDaniel · 2001 · Brain Research Bulletin
86. Trinucleotide repeat disease
    Jessica L. Walcott, Diane E. Merry · 2002 · Vitamins and hormones
87. Polyglutamine Disease Toxicity Is Regulated by Nemo-like Kinase in Spinocerebellar Ataxia Type 1
    Ju, Hyoungseok, Kokubu, Hiroshi, Todd, Tiffany W., Kahle, Juliette J., Kim, Soeun, Richman, Ronald, Chirala, Karthik, Orr, Harry T., Zoghbi, Huda Y., Lim, Janghoo · 2013 · The Journal of Neuroscience
88. Pharmacological protein targets in polyglutamine diseases: Mutant polypeptides and their interactors
    Boris A. Margulis, V. Vigont, V. Lazarev, E. Kaznacheyeva, Irina V. Guzhova · 2013 · FEBS Letters
89. Degradation of the Type I Inositol 1,4,5‐Trisphosphate Receptor by Caspase‐3 in SH‐SY5Y Neuroblastoma Cells Undergoing Apoptosis
    Lise Sofie Haug, Sven Ivar Walaas, Anne Carine Østvold · 2000 · Journal of Neurochemistry
90. Glial S100B Protein Modulates Mutant Ataxin-1 Aggregation and Toxicity: TRTK12 Peptide, a Potential Candidate for SCA1 Therapy
    Parminder J. S. Vig, Scoty M. Hearst, Qingmei Shao, Mariper E. Lopez, Henry A. Murphy, Eshan Safaya · 2011 · The Cerebellum
91. Dendritic Kv3.3 Potassium Channels in Cerebellar Purkinje Cells Regulate Generation and Spatial Dynamics of Dendritic Ca2+Spikes
    Edward Zagha, Satoshi Manita, William N. Ross, Bernardo Rudy · 2010 · Journal of Neurophysiology
92. A cell-based screen for modulators of ataxin-1 phosphorylation.
    M. Kaytor, Courtney E. Byam, Susan K. Tousey, Sam Stevens, H. Zoghbi, H. Orr · 2005 · Human Molecular Genetics
93. Modifiers and mechanisms of multi-system polyglutamine neurodegenerative disorders: lessons from fly models
    Moushami Mallik, S. C. Lakhotia · 2010 · Journal of Genetics
94. Spinocerebellar Ataxia Type 6: Molecular Mechanisms and Calcium Channel Genetics
    Xiaofei Du, Christopher Manuel Gomez · 2018 · Advances in experimental medicine and biology
95. Beyond the Glutamine Expansion: Influence of Posttranslational Modifications of Ataxin-1 in the Pathogenesis of Spinocerebellar Ataxia Type 1
    Hyoungseok Ju, Hiroshi Kokubu, Janghoo Lim · 2014 · Molecular Neurobiology
96. DRPLA transgenic mouse substrains carrying single copy of full-length mutant human DRPLA gene with variable sizes of expanded CAG repeats exhibit CAG repeat length- and age-dependent changes in behavioral abnormalities and gene expression profiles
    Kazushi Suzuki, Jiayi Zhou, Toshiya Sato, Keizo Takao, Tsuyoshi Miyagawa, Mutsuo Oyake, Mitunori Yamada, Hitoshi Takahashi, Yuji Takahashi, Jun Goto et al. · 2012 · Neurobiology of Disease
97. Cerebellar ataxias: β‐III spectrin's interactions suggest common pathogenic pathways
    Emma Perkins, Daumante Šuminaite, M. T. Jackson · 2016 · The Journal of Physiology
98. Ataxin-1 occupies the promoter region of E-cadherin in vivo and activates CtBP2-repressed promoter
    Soyeon Lee, Sunghoi Hong, Sung‐Su Kim, Seongman Kang · 2011 · Biochimica et Biophysica Acta (BBA) - Molecular Cell Research
99. Drosophila Myc, a novel modifier suppresses the poly(Q) toxicity by modulating the level of CREB binding protein and histone acetylation
    Mayanglambam Dhruba Singh, Kritika Raj, Surajit Sarkar · 2013 · Neurobiology of Disease
100. PQBP-1 (Np/PQ): a polyglutamine tract-binding and nuclear inclusion-forming protein
     Hitoshi Okazawa, Marius Sudol, Tina Rich · 2001 · Brain Research Bulletin