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Cited by 334

The DOI matches its Crossref record; 88 of the 88 references it cites were found in a registry or an index.

Evidence-Based Guideline for the diagnosis and management of eosinophilic granulomatosis with polyangiitis

Open access
Emmi, Giacomo, Bettiol, Alessandra, Gelain, Elena, Bajema, Ingeborg M., Berti, Alvise, Burns, Stella, Cid, Maria C., Cohen Tervaert, Jan W., Cottin, Vincent, Durante, Eugenia, Holle, Julia U., Mahr, Alfred D., Del Pero, Marcos Martinez, Marvisi, Chiara, Mills, John, Moiseev, Sergey, Moosig, Frank, Mukhtyar, Chetan, Neumann, Thomas, Olivotto, Iacopo, Salvarani, Carlo, Seeliger, Benjamin, Sinico, Renato A., Taillé, Camille, Terrier, Benjamin, Venhoff, Nils, Bertsias, George, Guillevin, Loïc, Jayne, David R. W., Vaglio, Augusto·2023·Nature Reviews Rheumatology

Abstract

Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis, characterized by asthma, eosinophilia and granulomatous or vasculitic involvement of several organs. The diagnosis and management of EGPA are often challenging and require an integrated, multidisciplinary approach. Current practice relies on recommendations and guidelines addressing the management of ANCA-associated vasculitis and not specifically developed for EGPA. Here, we present evidence-based, cross-discipline guidelines for the diagnosis and management of EGPA that reflect the substantial advances that have been made in the past few years in understanding the pathogenesis, clinical subphenotypes and differential diagnosis of the disease, as well as the availability of new treatment options. Developed by a panel of European experts on the basis of literature reviews and, where appropriate, expert opinion, the 16 statements and five overarching principles cover the diagnosis and staging, treatment, outcome and follow-up of EGPA. These recommendations are primarily intended to be used by healthcare professionals, pharmaceutical industries and drug regulatory authorities, to guide clinical practice and decision-making in EGPA. These guidelines are not intended to limit access to medications by healthcare agencies, nor to impose a fixed order on medication use. This article presents the first Evidence-Based Guideline dedicated specifically to the diagnosis and management of eosinophilic granulomatosis with polyangiitis. The 16 statements and five overarching principles cover the diagnosis and staging, treatment, outcome and follow-up of eosinophilic granulomatosis with polyangiitis.

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Metadata

Authors
Emmi, G., Bettiol, A., Gelain, E., Bajema, I. M., Berti, A., Burns, S., Cid, M. C., Cohen Tervaert, J. W., Cottin, V., Durante, E., Holle, J. U., Mahr, A. D., Del Pero, M. M., Marvisi, C., Mills, J., Moiseev, S., Moosig, F., Mukhtyar, C., Neumann, T., Olivotto, I., Salvarani, C., Seeliger, B., Sinico, R. A., Taillé, C., Terrier, B., Venhoff, N., Bertsias, G., Guillevin, L., Jayne, D. R. W., & Vaglio, A.
Venue
Nature Reviews Rheumatology
Published
2023-05-09
Volume
19
Issue
6
Pages
378-393
ISSN
  • 1759-4790 (ISSN-L)
  • 1759-4804
OpenAlex
W4376114466
Cited by
334
References
88
FWCI
25.25
Type
journal article
Language
en
Open access
hybrid

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CoChat. (2026). Citation check: Evidence-Based Guideline for the diagnosis and management of eosinophilic granulomatosis with polyangiitis. https://app.cochat.ai/papers/10.1038/s41584-023-00958-w
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Emmi, G., Bettiol, A., Gelain, E., Bajema, I. M., Berti, A., Burns, S., Cid, M. C., Cohen Tervaert, J. W., Cottin, V., Durante, E., Holle, J. U., Mahr, A. D., Del Pero, M. M., Marvisi, C., Mills, J., Moiseev, S., Moosig, F., Mukhtyar, C., Neumann, T., . . . Vaglio, A. (2023). Evidence-Based Guideline for the diagnosis and management of eosinophilic granulomatosis with polyangiitis. Nature Reviews Rheumatology. https://doi.org/10.1038/s41584-023-00958-w

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Contains information from the Semantic Scholar Academic Graph Datasets, made available under the ODC Attribution License (ODC-BY 1.0).

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