The DOI matches its Crossref record; 11 of the 11 references it cites were found in a registry or an index.
Epidemiology of systemic sclerosis: incidence, prevalence, survival, risk factors, malignancy, and environmental triggers
Abstract
PURPOSE OF REVIEW: To identify the recent data regarding prevalence, incidence, survival, and risk factors for systemic sclerosis (SSc) and to compare these data to previously published findings. RECENT FINDINGS: SSc disease occurrence data are now available for Argentina, Taiwan, and India and continue to show wide variation across geographic regions. The survival rate is negatively impacted by older age of onset, male sex, scleroderma renal crisis, pulmonary fibrosis, pulmonary arterial hypertension, cancer, and antitopoisomerase and anti-U1 antibodies. It appears that silica exposure confers an increased risk for developing scleroderma, but this exposure accounts for a very small proportion of male patients. Smoking is not associated with increased SSc susceptibility. Malignancies are reported in scleroderma at an increased rate, but the magnitude of this risk and the type of cancer vary among reports. SUMMARY: Prevalence and incidence of SSc appears to be greater in populations of European ancestry and lower in Asian groups. Exposure to silica dust appears to be an environmental trigger, but this only accounts for a small proportion of male cases. Evidence for increased risk of neoplasia is suggestive, but the magnitude of the risk and the types of malignancies vary among reports.
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Cites
Changes in causes of death in systemic sclerosis, 1972–2002
Steen, V. D., & Medsger, T. A. (2007) · Annals of the Rheumatic Diseases · doi:10.1136/ard.2006.066068 · Cited by 1,528
Tyndall, A. J., Bannert, B., Vonk, M., Airò, P., Cozzi, F., Carreira, P. E., Bancel, D. F., Allanore, Y., Müller-Ladner, U., Distler, O., et al. (2010) · Annals of the Rheumatic Diseases · doi:10.1136/ard.2009.114264 · Cited by 1,443
Mayes, M. D., Lacey, J. V., Beebe‐Dimmer, J., Gillespie, B. W., Cooper, B., Laing, T. J., & Schottenfeld, D. (2003) · Arthritis & Rheumatism · doi:10.1002/art.11073 · Cited by 935
Self-citationGorlova, O., Martin, J.-E., Rueda, B., Koeleman, B. P. C., Ying, J., Teruel, M., Diaz-Gallo, L.-M., Broen, J. C., Vonk, M. C., Simeon, C. P., et al. (2011) · PLoS Genetics · doi:10.1371/journal.pgen.1002178 · Cited by 231
Self-citationArnett, F. C., Howard, R. F., Tan, F., Moulds, J. M., Bias, W. B., Durban, E., Cameron, H. D., Paxton, G., Hodge, T. J., Weathers, P. E., et al. (1996) · Arthritis & Rheumatism · doi:10.1002/art.1780390814 · Cited by 229
Prevalence of scleroderma spectrum disorders in the general population of south carolina
Maricq, H. R., Weinrich, M. C., Keil, J. E., Smith, E. A., Harper, F. E., Nussbaum, A. I., Carwile Leroy, E., McGregor, A. R., Diat, F., & Rosal, E. J. (1989) · Arthritis & Rheumatism · doi:10.1002/anr.1780320809 · Cited by 172
Systemic sclerosis and the risk of cancer: a nationwide population-based cohort study
Olesen, A. B., Sværke, C., Farkas, D. K., & Sørensen, H. T. (2010) · British Journal of Dermatology · doi:10.1111/j.1365-2133.2010.09861.x · Cited by 149
Epidemiological study of patients with systemic sclerosis in Tokyo
Tamaki, T., Mori, S., & Takehara, K. (1991) · Archives of Dermatological Research · doi:10.1007/bf00371817 · Cited by 134
Makol, A., Reilly, M. J., & Rosenman, K. D. (2010) · American Journal of Industrial Medicine · doi:10.1002/ajim.20917 · Cited by 103
Late-age Onset Systemic Sclerosis
Manno, R., Wigley, F. M., Gelber, A. C., & Hummers, L. K. (2011) · The Journal of Rheumatology · doi:10.3899/jrheum.100956 · Cited by 69
Cited by
Unraveling SSc Pathophysiology; The Myofibroblast
van Caam, A., Vonk, M., van den Hoogen, F., van Lent, P., & van der Kraan, P. (2018) · Frontiers in Immunology · doi:10.3389/fimmu.2018.02452 · Cited by 153
Metadata
- Authors
- Barnes, J., & Mayes, M. D.
- Venue
- Current Opinion in Rheumatology
- Published
- 2012-03
- Volume
- 24
- Issue
- 2
- Pages
- 165-170
- ISSN
- 1040-8711 (ISSN-L)
- OpenAlex
- W2020316660
- Cited by
- 329
- References
- 11
- FWCI
- 13.09
- Type
- journal article
- Language
- en
- Open access
- closed
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- Barnes, J., & Mayes, M. D. (2012). Epidemiology of systemic sclerosis: incidence, prevalence, survival, risk factors, malignancy, and environmental triggers. Current Opinion in Rheumatology. https://doi.org/10.1097/bor.0b013e32834ff2e8
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Bibliographic data: Semantic Scholar, OpenAlex, Crossref.
Contains information from the Semantic Scholar Academic Graph Datasets, made available under the ODC Attribution License (ODC-BY 1.0).
Semantic Scholar’s data is described in: Kinney, R., et al. (2023). The Semantic Scholar Open Data Platform. arXiv:2301.10140.
