Progressive Disruption of Cellular Protein Folding in Models of Polyglutamine Diseases

Cited by (640)

Items 601–640 of 640

  1. Preserving protein homeostasis prevents motor impairment in DNA Damage Response-compromised C. elegans
    Wouter Huiting, Alejandra Duque‐Jaramillo, Renée I. Seinstra, Harm H. Kampinga, Ellen A. A. Nollen, Steven Bergink · 2021 · bioRxiv (Cold Spring Harbor Laboratory)
  2. Faculty Opinions recommendation of The rate of the molecular clock and the cost of gratuitous protein synthesis.
    Joshua B. Plotkin · 2010 · Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature
  3. References
    2009 · Chapman & Hall/CRC eBooks
  4. Analysis of translational fidelity in cellular proteins
    Raffaella Garofalo · 2019 · eDiss (Georg-August-Universität Göttingen)
  5. Polyglutamine Folding Diseases
    Shallee T. Page · 2014 · Springer eBooks
  6. Neuroendocrine control of the proteostatic network by HPK-1 delays aging
    María I. Lázaro‐Peña, Carlos A. Díaz-Balzac, Ritika Das, Andrew V. Samuelson · 2022 · bioRxiv (Cold Spring Harbor Laboratory)
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  9. Huntington’s Chorea
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  10. Faculty Opinions recommendation of Neuronal circuitry regulates the response of Caenorhabditis elegans to misfolded proteins.
    Thorsten Hoppe, Alexandra Segref · 2011 · Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature
  11. Reviewer #2 (Public Review): Impairment of lipid homoeostasis causes accumulation of protein aggregates in the lysosome
    Yong John, Jacqueline E. Villalta, Vu Ngoc · 2023 · eLife
  12. eLife Assessment: Impairment of lipid homoeostasis causes accumulation of protein aggregates in the lysosome
    Martin Sebastian Denzel · 2023 · eLife
  13. Author Response: Impairment of lipid homoeostasis causes accumulation of protein aggregates in the lysosome
    John Yong, Jacqueline E. Villalta, Ngoc Vu, Matthew A. Kukurugya, Bryson D. Bennett, Magdalena Preciado López, Julia R. Lazzari-Dean, Kayley Hake, Calvin H. Jan · 2023 · eLife
  14. Reviewer #1 (Public Review): Impairment of lipid homoeostasis causes accumulation of protein aggregates in the lysosome
    John Yong, Jacqueline E. Villalta, Ngoc Vu · 2023 · eLife
  15. Author response: Homeodomain-interacting protein kinase maintains neuronal homeostasis during normal Caenorhabditis elegans aging and systemically regulates longevity from serotonergic and GABAergic neurons
    María I. Lázaro‐Peña, Adam Cornwell, Carlos A. Díaz-Balzac, Ritika Das, Zachary C. Ward, Nicholas Macoretta, Juilee Thakar, Andrew V. Samuelson · 2023 · eLife
  16. Editor's evaluation: Homeodomain-interacting protein kinase maintains neuronal homeostasis during normal Caenorhabditis elegans aging and systemically regulates longevity from serotonergic and GABAergic neurons
    Paschalis Kratsios · 2023 · eLife
  17. D-Pinitol extends antioxidant activity and longevity of Caenorhabditis elegans via insulin-like signaling pathway
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  18. Recent aspects in the molecular genetics of Huntington's disease
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  19. A fluorescent folding reporter uncovers myosin misfolding as a driver of Hypertrophic Cardiomyopathy
    Renato Arnese, Philipp J. Dexheimer, Beatriz Escobar-Doncel, Lotta Krüger, Govinda Adhikari, Nina Krpan, Daria Sehr, Juliane Kley, Luiza Deszcz, Anton Meinhart et al. · 2025 · bioRxiv (Cold Spring Harbor Laboratory)
  20. Adjusting extracellular pH restores proteostasis and extends lifespan in a yeast model of polyglutamine toxicity
    Khaleda Afrin Bari, Gabriela Nunes Marsiglio-Librais, Martin L. Duennwald, Patrick Lajoie · 2025 · bioRxiv (Cold Spring Harbor Laboratory)
  21. Exogenous Huntingtin-Exon1 Aggregates Exhibit Distinct Levels of Toxicity to Caenorhabditis elegans
    Ephraim Ezeigbo, Kaitlyn M. Keith, Zachary L. Ellis, Korina Pebley, Tyler Girman, Anjola Adewoye, Alyssa R. Stonebraker, Pritom Kumar Biswas, Justin A. Legleiter · 2025 · ACS Chemical Neuroscience
  22. Additional file 1 of Neuronal cell-based high-throughput screen for enhancers of mitochondrial function reveals luteolin as a modulator of mitochondria-endoplasmic reticulum coupling
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    Sudhanshu Sharma, Dineshbabu Takkella, Benoît Y. Michel, Alain Burger, Krishna Gavvala · 2025 · Journal of Photochemistry and Photobiology A Chemistry
  24. PRO-FitS: a novel phenotypic assay to identify enhancers of proteostasis in C. elegans
    Daniela Vilasboas‐Campos, Jorge H. Fernandes, M. C. M. M. Michelle Cristina Magalhàes Melgaço Costa Costa, Joana Pereira‐Sousa, J. P. T. Lopes, Liliana Meireles-Costa, Bruna Ferreira-Lomba, Jorge Diogo Da Silva, Patricia Maciel, Andreia Teixeira‐Castro · 2026 · bioRxiv (Cold Spring Harbor Laboratory)
  25. Differential inclusion formation of an aggregation-prone protein reveals differences in the proteostasis capacity of neuronal cell lines
    Shannon McMahon, Dezerae Cox, Flora Cheng, Albert Lee, Justin J. Yerbury, Heath W. Ecroyd · 2026 · Biochimica et Biophysica Acta (BBA) - Molecular Cell Research
  26. Development of Inhibitors of Amyloid Fibril Propagation
    Maya Bendifallah · 2019 · theses.fr (ABES)
  27. Study of the co-translational assembly mechanism of transcription complexes in mammalian cells
    Pooja Mukherjee · 2019 · theses.fr (ABES)
  28. Investigation of IAPP fibrillation inhibition by co-chaperonin prefoldin
    Ricarda Törner · 2021 · theses.fr (ABES)
  29. Novel Frameshift Variant in SORL1 Gene Identified in a EOAD Family Causes APP Sorting Dysfunction and Endolysosomal Swelling
    Gege Jiang, Guanfeng Xie, Liqin Huang, Shangqi Sun, Zhihao Wang, Zhentao Zhang, Tingting Xiao, Jing Xiong · 2026 · Molecular Neurobiology
  30. Microbial production of D-arabitol from D-xylose by engineered Trichosporonoides oedocephalis: Fermentation performance and salt-stress transcriptional responses
    Yue Tang, Xin Ju, Yuqi Peng, Zhicheng Xie, Wei Liu, Jiaolong Fu, Jiajia Chen, Liangzhi Li · 2026 · Food Bioscience
  31. Caenorhabditis elegans small heat-shock protein HSP-12.6 has a highly specialized protective function towards muscle thick filaments in vivo
    Abigail Fern, Jasmine Alexander-Floyd, Anhelina Volchok, Susan M. Cahill, Srikar Donepudi, Jana Smuts, Tali Gidalevitz · 2026 · Philosophical Transactions of the Royal Society B Biological Sciences
  32. From aggregate structure to disease trajectory: the role of the proteostasis network
    Jessica Tittelmeier, Carmen I. Nussbaum-Krammer · 2026 · Philosophical Transactions of the Royal Society B Biological Sciences
  33. Differential proteostasis imbalance and the molecular basis of distinct synucleinopathies and tauopathies
    Virginie Redeker, Ronald Melki · 2026 · Philosophical Transactions of the Royal Society B Biological Sciences
  34. Loss of the UFM-1 pathway enhances the ER Unfolded Protein Response under stress to improve proteostasis and organismal health in Caenorhabditis elegans
    Samantha Moores, Betty Ortiz, Peter Juo · 2026 · bioRxiv (Cold Spring Harbor Laboratory)
  35. BindingDB Entry 50027252: Toward optimization of the linker substructure common to transthyretin amyloidogenesis inhibitors using biochemical and structural studies.
    BindingDB · 2010 · UC San Diego
  36. BindingDB Entry 50030238: Toward optimization of the second aryl substructure common to transthyretin amyloidogenesis inhibitors using biochemical and structural studies.
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  37. Protein Quality Control Systems in Neurodegeneration—Chaperones, Cytoskeleton, and the Pathogenic Transition of Tau
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  38. Cardiac and vascular involvement in protein misfolding diseases
    Kimon Stamatelopoulos, Georgios A. Georgiopoulos, Alberto Aimo, Evmorfia Aivalioti, Karen Carolyn Bauer, Simon Tual‐Chalot, Simon C Kraler, Dimitrios Bampatsias, Mario Nuvolone, Mahmoud Abdellatif et al. · 2026 · Nature Reviews Cardiology
  39. A regulated response to mitochondrial dysfunction modulates longevity and rates of living
    David Zeferino d’Azevedo Cristina · 2008 · Portuguese National Funding Agency for Science, Research and Technology (RCAAP Project by FCT)
  40. Proteotoxicity of polyglutamine expansion proteins: Cellular mechanisms and their modulation by molecular chaperones
    Christian Behrends · 2007 · Elektronische Hochschulschriften der LMU München (Ludwig-Maximilians-Universität München)