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Echocardiographic characteristics of PRKAG2 syndrome: a research using three-dimensional speckle tracking echocardiography compared with sarcomeric hypertrophic cardiomyopathy

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Human γ2-AMPK Mutations

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Familial Atrial Enlargement, Conduction Disorder and Symmetric Cardiac Hypertrophy Are Early Signs of PRKAG2 R302Q

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Electrocardiographic Characteristics and Their Correlation with Echocardiographic Alterations in Fabry Disease

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Genetic Determinants of Hereditary Bradyarrhythmias: A Contemporary Review of a Diverse Group of Disorders

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Animal Models to Study AMPK

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The PRKAG2 gene and hypertrophic cardiomyopathy: an energetically imbalanced relationship

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Modulating Phenotypic Expression of the PRKAG2 Cardiac Syndrome

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The Genetic Challenges and Opportunities in Advanced Heart Failure

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PRKAG3 polymorphisms associated with sporadic Wolff–Parkinson–White syndrome among a Taiwanese population

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A New Perspective on the Quality of Life of Children with Glycogen Storage Diseases

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Value of Electrocardiography to Distinguish Fabry Disease from Sarcomeric Hypertrophic Cardiomyopathy

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Contribution of hypoxia-inducible factor 1alpha to pathogenesis of sarcomeric hypertrophic cardiomyopathy

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Identification of the pathogenic effects of missense variants causing PRKAG2 cardiomyopathy

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Supraventricular Tachycardias

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Rare Variant in MRC2 Associated With Familial Supraventricular Tachycardia and Wolff-Parkinson-White Syndrome

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The Year in Clinical Cardiac Electrophysiology

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Reversible Transition from a Hypertrophic to a Dilated Cardiomyopathy

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Hypertrophic Cardiomyopathy

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Hypertrophic cardiomyopathy in the structure of infiltrative diseases in children

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When Paying Attention Pays Back: Missense Mutation c.1006G>A p. (Val336Ile) in PRKAG2 Gene Causing Left Ventricular Hypertrophy and Conduction Abnormalities in a Caucasian Patient: Case Report and Literature Review

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AMPKγ2 Regulates Cardiac Hypertrophy and Arrhythmias via Interacting With Myosin

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About split P waves

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PRKAG2-associated hypertrophic cardiomyopathy

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Genetic Cardiomyopathies

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A New Mechanism of Supraventricular Tachycardia: Gene Mutation

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Progressive Conduction System Disease

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Inherited Wolff–Parkinson–White Syndrome

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Progressive Conduction System Disease

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Hypertrophic cardiomyopathy

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Principles and Practice of Genetic Counselling for Inherited Cardiac Conditions

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Cardiac Function in GHR–/– Mice

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Mapping and Ablation of Typical and Atypical Accessory Pathways

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History of Supraventricular Tachycardia

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Inherited Metabolic Diseases: Emphasis on Myocardial Disease and Arrhythmogenesis

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Molecular Genetics of Cardiac Arrhythmias

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Fabry or not Fabry: From genetics to diagnosis

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Cardiac Mapping in Variants of the Ventricular Preexcitation Syndrome

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Inherited Cardiomyopathies

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The Year in Clinical Cardiac Electrophysiology

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Case 141

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Atrioventricular (AV) Reentry Tachycardia

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Accessory pathways in monozygotic twins with different clinical phenotypes: a case report

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Cardiomyopathies – genetic and molecular issues

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A rare genetic variant in PRDM16 is associated with Wolff–Parkinson–White syndrome with complex accessory pathway characteristics and left ventricular non-compaction cardiomyopathy

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The discrepancy between wall thickness, myocardial mass, and ECG appearances in young patients with cardiomyopathies

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Additional file 1 of Echocardiographic characteristics of PRKAG2 syndrome: a research using three-dimensional speckle tracking echocardiography compared with sarcomeric hypertrophic cardiomyopathy

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Beyond Glycogen Storage: AMPKγ2 Regulates Cardiac Hypertrophy and Electrophysiology via Myosin InteractionPreprint

Ge, Q., Saha, K., Burch, M. L., Battista, W. H., Kc, A., Homilius, M., Victorio, R. A., Quan, D., Huang, H.-L., Hazel, J. M., et al. (2026) · bioRxiv (Cold Spring Harbor Laboratory) · doi:10.64898/2026.04.20.719766

AMPKγ2 Meets Myosin: A New Link Between Metabolism and Sarcomere Function

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Transgenic Mice Overexpressing Mutant PRKAG2 Define the Cause of Wolff-Parkinson-White Syndrome in Glycogen Storage Cardiomyopathy

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Abstract 16614: Reduced Glucose Uptake and Increased Glycogen Synthase is Observed Early in a Mouse Model of the Human Arg302Gln-PRKAG2 Cardiac Syndrome

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178 Abnormal Neonate Cardiomyocyte Metabolism is Associated with Alterations in Adult Cardiac Metabolism in a Mouse Model of the Arg302gln-prkag2 Cardiac Syndrome

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Beyond Glycogen Storage: AMPKγ2 Regulates Cardiac Hypertrophy and Electrophysiology via Myosin InteractionPreprint

Ge, Q., Saha, K., Burch, M. L., Battista, W. H., Kc, A., Homilius, M., Victorio, R. A., Quan, D., Huang, H.-L., Hazel, J. M., et al. (2026) · bioRxiv (Cold Spring Harbor Laboratory) · doi:10.64898/2026.04.20.719766

A85. Electrophysiological characteristics and connexin 43 in transgenic mice overexpressing the human PRKAG2 gene

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