Lower limb lengthening in Turner dwarfism
Open accessAbstract
The aim of this study was to review our cases of lower limb lengthening to treat Turner dwarfism, and to speculate whether or not effective limb lengthening can be achieved in this rare condition. Twelve tibiae and 2 femora were lengthened in 6 patients using the Ilizarov method for the tibia and a gradual elongation nail for the femur. The mean age at the time of surgery was 19 years, and the patients were followed up for a minimum of 2 years. The average gain in the tibial and femoral length was 6.2 cm and 6.0 cm, respectively. The average healing index of tibia and femur was 1.9 and 1.7 months. The average tibia-to-femur ratio improved from 0.68 preoperatively to 0.81 postoperatively, and leg-trunk ratios improved from 0.88 to 0.99. Seven segments (50.0 percent) had completed the lengthening protocol without complications. Two segments (14.3 percent) had an intractable pin site infection requiring a pin exchange, and four segments (35.7 percent) had twelve complications (a nonunion at the distraction site, premature consolidation, Achilles tendon contractures and planovalgus). The overall rate of complications was 100 percent for each bone lengthened. All the patients showing a nonunion at the distraction site had a reduced bone mass, which was less than 65 percent of those of the age-matched normal population. Despite the complications, all patients were satisfied with the results, and lower limb lengthening in Turner Dwarfism believed to be a valid option. However, it may require careful management in a specialist unit in order to prevent complications during the lengthening procedure. In addition, the osteopenia associated with an estrogen deficiency leading to problems in consolidation is a difficult issue to address.
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Limited studies have shown limb-lengthening procedures can result in substantial height increase in women with TS.
“Limited studies258,259 have shown that limb-lengthening procedures (distraction osteogenesis) can result in substantial height increase in women with TS.”
From Clinical practice guidelines for the care of girls and women with Turner syndrome. (2024) · cites this paper as [259]
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2 of the 23 references couldn’t be matched to a known paper.
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Clinical practice guidelines for the care of girls and women with Turner syndrome.
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BackgroundLimb Lengthening in Russell-Silver Syndrome: An Update Confirming Safe and Speedy Healing
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“Это связано, в основном, с различной способностью к растяжению мышц-антагонистов и их сухожилий [19, 20].”
Evolution of tactical approaches to eliminating limb length discrepancy
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Tibial Lengthening with Circular External Fixation
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- Authors
- Hahn, S. B., Park, H. W., Park, H. J., Seo, Y. J., & Kim, H. W.
- Affiliations
- Yonsei University (KR)
- Hallym University (KR)
- Venue
- Yonsei Medical Journal
- Published
- 2003
- Volume
- 44
- Issue
- 3
- Pages
- 502
- ISSN
- 0513-5796 (ISSN-L)
- OpenAlex
- W1988027569
- Cited by
- 7
- References
- 23
- Citations by year
- 2024: 2 · 2021: 1 · 2018: 1 · 2014: 1 · 2013: 1
- FWCI
- 0.00
- Type
- journal article
- Language
- en
- Open access
- gold
- doi.org
- Locations
- Yonsei Medical Journal (publishedVersion)
- PubMed (publishedVersion)
- YUHSpace (Yonsei University Medical Library) (submittedVersion, cc-by-nc-nd)
- Topics
- Health Sciences › Medicine › Epidemiology › Bone fractures and treatments
- Life Sciences › Biochemistry, Genetics and Molecular Biology › Genetics › Craniofacial Disorders and Treatments
- Life Sciences › Biochemistry, Genetics and Molecular Biology › Genetics › Connective tissue disorders research
- Keywords
- Turner syndrome, limb length discrepancy, lower limb lengthening, Ilizarov technique, tibia, femur, distraction osteogenesis, nonunion, osteopenia, estrogen deficiency, pin tract infection, Achilles tendon contracture
- MeSH terms
- Adolescent, Adult, Child, Dwarfism, Humans, Leg, Radiography, Retrospective Studies, Turner Syndrome, Treatment Outcome, Ilizarov Technique
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