Tumours and hemihypertrophy associated with Wiedemann-Beckwith syndrome

Wiedemann, H. -R.

doi:10.1007/bf00496807

Cited by 281Genetic Syndromes and ImprintingBirth, Development, and HealthVascular Malformations and Hemangiomas

Tumours and hemihypertrophy associated with Wiedemann-Beckwith syndrome

Wiedemann, H. -R.·1983·European Journal of Pediatrics

DOI 10.1007/bf00496807

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Less than 1% of children with BWS will develop an ACC.
“Due to the low overall incidence (<1% of children with BWS will develop an ACC), no specific screening recommendations for ACC exist.”
From Adrenocortical carcinoma (2014) · cites this paper as [44]
ACC comprises 5% to 15% of malignancies in BWS.
“Although data vary significantly, ACC comprises 5% to 15% of malignancies in BWS (43, 44).”
From Adrenocortical carcinoma (2014) · cites this paper as [44]

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Background
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Authors: Wiedemann, H. R.
Affiliations: University Hospital Schleswig-Holstein (DE)
Corresponding author: Wiedemann, H. -R.
Venue: European Journal of Pediatrics
Publisher: Springer Science and Business Media LLC
Published: 1983-12
Volume: 141
Issue: 2
Pages: 129-129
ISSN: 0340-6199 (ISSN-L)
1432-1076
DOI: 10.1007/bf00496807
OpenAlex: W2011313235
Cited by: 281
References: 0
Citations by year: 2023: 1 · 2021: 2 · 2020: 4 · 2019: 1 · 2018: 1 · 2017: 2 · 2016: 4 · 2015: 4 · 2014: 2 · 2013: 6 · 2012: 6
FWCI: 0.76
Type: journal article
Language: en
Open access: closed
Licence: www.springer.com/tdm (tdm)
Locations: European Journal of Pediatrics (publishedVersion)
Topics: Life Sciences › Biochemistry, Genetics and Molecular Biology › Genetics › Genetic Syndromes and Imprinting
Health Sciences › Medicine › Pediatrics, Perinatology and Child Health › Birth, Development, and Health
Health Sciences › Medicine › Surgery › Vascular Malformations and Hemangiomas
Keywords: Beckwith-Wiedemann syndrome, hemihypertrophy, tumors, neoplasms

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Tumours and hemihypertrophy associated with Wiedemann-Beckwith syndrome

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