The prion hypothesis: from biological anomaly to basic regulatory mechanism

Prions

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Novel Proteinaceous Infectious Particles Cause Scrapie

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Curli Biogenesis and Function

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[URE3] as an Altered URE2 Protein: Evidence for a Prion Analog in Saccharomyces cerevisiae

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A Systematic Survey Identifies Prions and Illuminates Sequence Features of Prionogenic Proteins

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Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication

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Functional Amyloid Formation within Mammalian Tissue

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Normal host prion protein necessary for scrapie-induced neurotoxicity

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Depleting Neuronal PrP in Prion Infection Prevents Disease and Reverses Spongiosis

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Prion-like transmission of protein aggregates in neurodegenerative diseases

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A yeast prion provides a mechanism for genetic variation and phenotypic diversity

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Anchorless Prion Protein Results in Infectious Amyloid Disease Without Clinical Scrapie

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Support for the Prion Hypothesis for Inheritance of a Phenotypic Trait in Yeast

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The physical basis of how prion conformations determine strain phenotypes

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Common mechanisms of amyloid oligomer pathogenesis in degenerative disease

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A Neuronal Isoform of the Aplysia CPEB Has Prion-Like Properties

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Prions Affect the Appearance of Other Prions

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Expression of Amino-Terminally Truncated PrP in the Mouse Leading to Ataxia and Specific Cerebellar Lesions

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Evidence for protein X binding to a discontinuous epitope on the cellular prion protein during scrapie prion propagation

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Ψ, A cytoplasmic suppressor of super-suppressor in yeast

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Slow transmissible diseases of the nervous system

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Propagation of the yeast prion‐like [psi+] determinant is mediated by oligomerization of the SUP35‐encoded polypeptide chain release factor.

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Rnq1

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Distinct prion proteins in short and long scrapie incubation period mice

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The protein product of the het-s heterokaryon incompatibility gene of the fungus Podospora anserina behaves as a prion analog

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A census of glutamine/asparagine-rich regions: Implications for their conserved function and the prediction of novel prions

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Darwinian Evolution of Prions in Cell Culture

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The Prion's Elusive Reason for Being

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PrP Genotype and Agent Effects in Scrapie: Change In Allelic Interaction With Different Isolates of Agent in Sheep, a Natural Host of Scrapie

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Pathway Complexity of Prion Protein Assembly into Amyloid

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The cellular prion protein (PrPC): Its physiological function and role in disease

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Growth control and ribosome biogenesis

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Axonal prion protein is required for peripheral myelin maintenance

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Aplysia CPEB Can Form Prion-like Multimers in Sensory Neurons that Contribute to Long-Term Facilitation

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A Critical Role for Amino-Terminal Glutamine/Asparagine Repeats in the Formation and Propagation of a Yeast Prion

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Molecular recycling within amyloid fibrils

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Epigenetic regulation of translation reveals hidden genetic variation to produce complex traits

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Emerging Principles of Conformation-Based Prion Inheritance

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Influence of Amino Acid Substitutions Related to Inherited Human Prion Diseases on the Thermodynamic Stability of the Cellular Prion Protein

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Multiple Gln/Asn-Rich Prion Domains Confer Susceptibility to Induction of the Yeast [PSI] Prion

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Newly identified prion linked to the chromatin-remodeling factor Swi1 in Saccharomyces cerevisiae

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Targeting Cellular Prion Protein Reverses Early Cognitive Deficits and Neurophysiological Dysfunction in Prion-Infected Mice

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The yeast global transcriptional co-repressor protein Cyc8 can propagate as a prion

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Lethal recessive myelin toxicity of prion protein lacking its central domain

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Regulation of Embryonic Cell Adhesion by the Prion Protein

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Continuum of prion protein structures enciphers a multitude of prion isolate-specified phenotypes

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Translation termination efficiency can be regulated in Saccharomyces cerevisiae by environmental stress through a prion‐mediated mechanism

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Primary sequence independence for prion formation

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Dependence and independence of [PSI+] and [PIN+]: a two‐prion system in yeast?

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Dissection and Design of Yeast Prions

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The Prion Protein Knockout Mouse

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Continuous Quinacrine Treatment Results in the Formation of Drug-Resistant Prions

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Adaptation and Selection of Prion Protein Strain Conformations following Interspecies Transmission of Transmissible Mink Encephalopathy

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A molecular switch controls interspecies prion disease transmission in mice

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