X chromosome-linked muscular dystrophy (mdx) in the mouse

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Myogenin Regulates Exercise Capacity but Is Dispensable for Skeletal Muscle Regeneration in Adult mdx Mice

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Cloning of cDNA Encoding a Regeneration-Associated Muscle Protease Whose Expression Is Attenuated in Cell Lines Derived from Duchenne Muscular Dystrophy Patients

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Comparative Genomics of X-linked Muscular Dystrophies: The Golden Retriever Model

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A computerized MRI biomarker quantification scheme for a canine model of Duchenne muscular dystrophy

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Genetic modifiers of D uchenne and facioscapulohumeral muscular dystrophies

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Targeting RAGE as a potential therapeutic approach to Duchenne muscular dystrophy

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Coenzyme Q10 supplementation acts as antioxidant on dystrophic muscle cells

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Glucocorticoids and immunosup pressants do not change the prevalence of necrosis and regeneration in mdx skeletal muscles

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Ectopic Calcification is Caused by Elevated Levels of Serum Inorganic Phosphate in Mdx Mice

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Cardiac Myosin Binding Protein-C Plays No Regulatory Role in Skeletal Muscle Structure and Function

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Muscular nitric oxide synthase (muNOS) and utrophin

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Role of bone marrow cell trafficking in replenishing skeletal muscle SP and MP cell populations

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A 31P-NMR study of muscle exercise metabolism in mdx mice: Evidence for abnormal pH regulation

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A linkage study of Emery-Dreifuss muscular dystrophy

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Nutraceuticals and Their Potential to Treat Duchenne Muscular Dystrophy: Separating the Credible from the Conjecture

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Shortcomings of Animal Models and the Rise of Engineered Human Cardiac Tissue

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Development of muscular dystrophy in a CRISPR-engineered mutant rabbit model with frame-disrupting ANO5 mutations

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ISLR regulates skeletal muscle atrophy via IGF1-PI3K/Akt-Foxo signaling pathway

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Mutation-independent Proteomic Signatures of Pathological Progression in Murine Models of Duchenne Muscular Dystrophy

van Westering, T. L. E., Johansson, H. J., Hanson, B., Coenen-Stass, A. M. L., Lomonosova, Y. N., Tanihata, J., Motohashi, N., Yokota, T., Takeda, S., Lehtiö, J., et al. (2020) · Molecular & Cellular Proteomics · doi:10.1074/mcp.ra120.002345 · Cited by 35

Nanomedicine for Gene Delivery and Drug Repurposing in the Treatment of Muscular Dystrophies

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Blastocyst Injection of Wild Type Embryonic Stem Cells Induces Global Corrections in Mdx Mice

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Loss of nNOS inhibits compensatory muscle hypertrophy and exacerbates inflammation and eccentric contraction-induced damage in mdx mice

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Assessment of housekeeping genes for use in normalization of real time PCR in skeletal muscle with chronic degenerative changes

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Proteome analysis in dystrophic mdx mouse muscle reveals a drastic alteration of key metabolic and contractile proteins after chronic exercise and the potential modulation by anti-oxidant compounds

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Defective Flux of Thrombospondin-4 through the Secretory Pathway Impairs Cardiomyocyte Membrane Stability and Causes Cardiomyopathy

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Connective tissue proliferation and growth factors in animal models of Duchenne muscular dystrophy

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Differential distribution of dystrophin and β-spectrin at the sarcolemma of fast twitch skeletal muscle fibers

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Characterisation of Progressive Skeletal Muscle Fibrosis in the Mdx Mouse Model of Duchenne Muscular Dystrophy: An In Vivo and In Vitro Study

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Tranilast administration reduces fibrosis and improves fatigue resistance in muscles of mdx dystrophic mice

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β1D chain increases α7β1 integrin and laminin and protects against sarcolemmal damage in mdx mice

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Cardiac telomere length in heart development, function, and disease

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Transcriptomic analysis of dystrophin RNAi knockdown reveals a central role for dystrophin in muscle differentiation and contractile apparatus organization

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MALDI reveals membrane lipid profile reversion in MDX mice

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Myogenic Potential of Muscle Side and Main Population Cells after Intravenous Injection into Sub-lethally Irradiated mdx Mice

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Reversal by relaxin of altered ileal spontaneous contractions in dystrophic (mdx) mice through a nitric oxide-mediated mechanism

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In Vivo Viscoelastic Response (VisR) Ultrasound for Characterizing Mechanical Anisotropy in Lower-Limb Skeletal Muscles of Boys with and without Duchenne Muscular Dystrophy

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Acute AT1R blockade prevents isoproterenol-induced injury in mdx hearts

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LONG‐TERM CLENBUTEROL ADMINISTRATION ALTERS THE ISOMETRIC CONTRACTILE PROPERTIES OF SKELETAL MUSCLE FROM NORMAL AND DYSTROPHIN‐DEFICIENT MDX MICE

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The organisation of spinal projecting brainstem neurons in an animal model of muscular dystrophy

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Sarcoglycans in muscular dystrophy

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Genetic correction of dystrophin deficiency and skeletal muscle remodeling in adult MDX mouse via transplantation of retroviral producer cells.

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Actinin-Associated LIM Protein-Deficient Mice Maintain Normal Development and Structure of Skeletal Muscle

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Impaired nitrergic relaxations in the gastric fundus of dystrophic (mdx) mice

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Molecular and genetic mapping of the mouse mdx locus

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Quantitative T2 Combined with Texture Analysis of Nuclear Magnetic Resonance Images Identify Different Degrees of Muscle Involvement in Three Mouse Models of Muscle Dystrophy: mdx, Largemyd and mdx/Largemyd

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Distinct roles of TRAF6 at early and late stages of muscle pathology in the mdx model of Duchenne muscular dystrophy

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Muscular dystrophy modeling in zebrafish

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Gene therapies in canine models for Duchenne muscular dystrophy

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Duchenne muscular dystrophy hiPSC–derived myoblast drug screen identifies compounds that ameliorate disease in mdx mice

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Comparative analysis of Dp427-deficient mdx tissues shows that the milder dystrophic phenotype of extraocular and toe muscle fibres is associated with a persistent expression of β-dystroglycan

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Microarray analysis of mdx mice expressing high levels of utrophin: Therapeutic implications for dystrophin deficiency

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Effect of cyclopiazonic acid, an inhibitor of the sarcoplasmic reticulum Ca‐ATPase, on skeletal muscles from normal and mdx mice

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Phosphodiesterase 4 inhibitor and phosphodiesterase 5 inhibitor combination therapy has antifibrotic and anti‐inflammatory effects in mdx mice with Duchenne muscular dystrophy

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Acidic Fibroblast Growth Factor (aFGF) in Developing Normal and Dystrophic (mdx) Mouse Muscles. Distribution in Degenerating and Regenerating mdx Myofibres

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Dystrophin-like immunoreactivity in monkey and human brain areas involved in learning and motor functions

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Tenascin-C expression in dystrophin-related muscular dystrophy

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Targeted deletion of the zebrafish obscurin A RhoGEF domain affects heart, skeletal muscle and brain development

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Effects of chronic treatment with gold nanoparticles on inflammatory responses and oxidative stress in Mdx mice

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Duchenne muscular dystrophy (DMD) cardiomyocyte-secreted exosomes promote the pathogenesis of DMD-associated cardiomyopathy

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Non-invasive Optical Imaging of Muscle Pathology in mdx Mice Using Cathepsin Caged Near-Infrared Imaging

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IGF-II ameliorates the dystrophic phenotype and coordinately down-regulates programmed cell death

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Xanthine oxidase is hyper-active in Duchenne muscular dystrophy

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Cortical and brainstem neurons containing calcium‐binding proteins in a murine model of Duchenne's muscular dystrophy: Selective changes in the sensorimotor cortex

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A mutation in CHN-1/CHIP suppresses muscle degeneration in Caenorhabditis elegans

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Altered electrical activity in colonic smooth muscle cells from dystrophic (mdx) mice

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Dystrophin Delivery in Dystrophin-Deficient DMD mdx Skeletal Muscle by Isogenic Muscle-Derived Stem Cell Transplantation

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Circulating Biomarkers for Duchenne Muscular Dystrophy

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Muscle Atrophy Reversed by Growth Factor Activation of Satellite Cells in a Mouse Muscle Atrophy Model

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Linking cytoarchitecture to metabolism: sarcolemma-associated plectin affects glucose uptake by destabilizing microtubule networks in mdx myofibers

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Functional improvement of dystrophic muscle by repression of utrophin: let-7c interaction

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Total Absence of Dystrophin Expression Exacerbates Ectopic Myofiber Calcification and Fibrosis and Alters Macrophage Infiltration Patterns

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