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Amyotrophic lateral sclerosis - frontotemporal spectrum disorder (ALS-FTSD): Revised diagnostic criteria
Open accessAbstract
This article presents the revised consensus criteria for the diagnosis of frontotemporal dysfunction in amyotrophic lateral sclerosis (ALS) based on an international research workshop on frontotemporal dementia (FTD) and ALS held in London, Canada in June 2015. Since the publication of the Strong criteria, there have been considerable advances in the understanding of the neuropsychological profile of patients with ALS. Not only is the breadth and depth of neuropsychological findings broader than previously recognised - - including deficits in social cognition and language - but mixed deficits may also occur. Evidence now shows that the neuropsychological deficits in ALS are extremely heterogeneous, affecting over 50% of persons with ALS. When present, these deficits significantly and adversely impact patient survival. It is the recognition of this clinical heterogeneity in association with neuroimaging, genetic and neuropathological advances that has led to the current re-conceptualisation that neuropsychological deficits in ALS fall along a spectrum. These revised consensus criteria expand upon those of 2009 and embrace the concept of the frontotemporal spectrum disorder of ALS (ALS-FTSD).
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“Cognition is also affected in a majority of cases at some point in the disease course (10).”
From Chronic Traumatic Encephalopathy Within an Amyotrophic Lateral Sclerosis Brain Bank Cohort (2018) · cites this paper as [10]
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“Notably, TGF-ß is upregulated in ALS (55), and aberrant Wnt signaling is associated with TDP43 mislocalization in cellular and animal models (56).”
From Nemo-like kinase disrupts nuclear import and drives TDP43 mislocalization in ALS (2025) · cites this paper as [55]
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Rosen, D. R., Siddique, T., Patterson, D., Figlewicz, D. A., Sapp, P., Hentati, A., Donaldson, D., Goto, J., O'Regan, J. P., Deng, H.-X., et al. (1993) · Nature · doi:10.1038/362059a0 · Cited by 7,062
El Escorial revisited: revised criteria for the diagnosis of amyotrophic lateral sclerosis
Brooks, B. R., Miller, R. G., Swash, M., & Munsat, T. L. (2000) · Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders · doi:10.1080/146608200300079536 · Cited by 5,433
Sensitivity of revised diagnostic criteria for the behavioural variant of frontotemporal dementia
Rascovsky, K., Hodges, J. R., Knopman, D., Mendez, M. F., Kramer, J. H., Neuhaus, J., van Swieten, J. C., Seelaar, H., Dopper, E. G. P., Onyike, C. U., et al. (2011) · Brain · doi:10.1093/brain/awr179 · Cited by 5,221
Classification of primary progressive aphasia and its variants
Gorno-Tempini, M. L., Hillis, A. E., Weintraub, S., Kertesz, A., Mendez, M., Cappa, S. F., Ogar, J. M., Rohrer, J. D., Black, S., Boeve, B. F., et al. (2011) · Neurology · doi:10.1212/wnl.0b013e31821103e6 · Cited by 5,141
Frontotemporal lobar degeneration: A consensus on clinical diagnostic criteria
Neary, D., Snowden, J. S., Gustafson, L., Passant, U., Stuss, D., Black, S., Freedman, M., Kertesz, A., Robert, P. H., Albert, M., et al. (1998) · Neurology · doi:10.1212/wnl.51.6.1546 · Cited by 5,047
Self-citationDeJesus-Hernandez, M., Mackenzie, I. R., Boeve, B. F., Boxer, A. L., Baker, M., Rutherford, N. J., Nicholson, A. M., Finch, N. A., Flynn, H., Adamson, J., et al. (2011) · Neuron · doi:10.1016/j.neuron.2011.09.011 · Cited by 4,936
A Hexanucleotide Repeat Expansion in C9ORF72 Is the Cause of Chromosome 9p21-Linked ALS-FTD
Renton, A. E., Majounie, E., Waite, A., Simón-Sánchez, J., Rollinson, S., Gibbs, J. R., Schymick, J. C., Laaksovirta, H., van Swieten, J. C., Myllykangas, L., et al. (2011) · Neuron · doi:10.1016/j.neuron.2011.09.010 · Cited by 4,409
Self-citationWeıntraub, S. (1990) · Archives of Neurology · doi:10.1001/archneur.1990.00530120075013 · Cited by 3,018
Appelhof, B., Bakker, C., den IJssel, J. C. L. V. D., Zwijsen, S. A., Smalbrugge, M., Verhey, F. R. J., de Vugt, M. E., Zuidema, S. U., & Koopmans, R. T. C. M. (2017) · Dementia and Geriatric Cognitive Disorders · doi:10.1159/000477087 · Cited by 2,774
TDP-43 Mutations in Familial and Sporadic Amyotrophic Lateral Sclerosis
Sreedharan, J., Blair, I. P., Tripathi, V. B., Hu, X., Vance, C., Rogelj, B., Ackerley, S., Durnall, J. C., Williams, K. L., Buratti, E., et al. (2008) · Science · doi:10.1126/science.1154584 · Cited by 2,630
Research works printed but not linked: 3
- 10.1136/jnnp.61.5.450 · DOI
- Ince PG, 2015, Greenfield's Neuropathology, 817
- Le B,I, 2015, Neurobiol Aging, 36, 3116
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Items 101–200 of 908
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Poletti, B., Solca, F., Carelli, L., Faini, A., Madotto, F., Lafronza, A., Monti, A., Zago, S., Ciammola, A., Ratti, A., et al. (2018) · Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration · doi:10.1080/21678421.2018.1473443 · Cited by 53
Self-citationSimon, N., & Goldstein, L. H. (2018) · Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration · doi:10.1080/21678421.2018.1530264 · Cited by 55
Self-citationLiu, Y., Andreucci, A., Iwamoto, N., Yin, Y., Yang, H., Liu, F., Bulychev, A., Hu, X. S., Lin, X., Lamore, S. D., et al. (2022) · Molecular Therapy — Nucleic Acids · doi:10.1016/j.omtn.2022.04.007 · Cited by 56
Connolly, O., Gall, L. L., McCluskey, G., Donaghy, C. G., Duddy, W. J., & Duguez, S. (2020) · Journal of Personalized Medicine · doi:10.3390/jpm10030058 · Cited by 54
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Quinn, C. C., & Elman, L. B. (2020) · CONTINUUM Lifelong Learning in Neurology · doi:10.1212/con.0000000000000911 · Cited by 60
Grassano, M., Moglia, C., Palumbo, F., Koumantakis, E., Cugnasco, P., Callegaro, S., Canosa, A., Manera, U., Vasta, R., Mattei, F. D., et al. (2024) · Annals of Neurology · doi:10.1002/ana.26933 · Cited by 51
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Strikwerda‐Brown, C., Ramanan, S., & Irish, M. (2019) · Neuropsychiatric Disease and Treatment · doi:10.2147/ndt.s158996 · Cited by 48
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Ahmed, R. M., Phan, K., Highton‐Williamson, E., Strikwerda‐Brown, C., Caga, J., Ramsey, E., Zoing, M. C., Devenney, E. M., Kim, W. S., Hodges, J. R., et al. (2019) · Annals of Clinical and Translational Neurology · doi:10.1002/acn3.721 · Cited by 46
Ren, Y., Li, S., Chen, S., Sun, X.-S., Yang, F., Wang, H., Li, M., Cui, F., & Huang, X. (2021) · Frontiers in Neurology · doi:10.3389/fneur.2021.663637 · Cited by 47
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Walt, G. S., Burris, H. M., Brady, C. B., Spencer, K. R., Alvarez, V. E., Huber, B. R., Guilderson, L., Abdul Rauf, N., Collins, D., Singh, T., et al. (2018) · Journal of Neuropathology & Experimental Neurology · doi:10.1093/jnen/nly092 · Cited by 45
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Vacchiano, V., Mastrangelo, A., Zenesini, C., Baiardi, S., Avoni, P., Polischi, B., Capellari, S., Salvi, F., Liguori, R., & Parchi, P. (2023) · Journal of Neurology Neurosurgery & Psychiatry · doi:10.1136/jnnp-2022-330709 · Cited by 49
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Urso, D., Giannoni‐Luza, S., Brayne, C., Ray, N., & Logroscino, G. (2025) · JAMA Neurology · doi:10.1001/jamaneurol.2025.3307 · Cited by 51
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Behavioural and Cognitive Changes in Neurodegenerative Diseases and Brain Injury
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Baek, S., Park, J., Kim, Y. H., Seok, H. Y., Oh, K., Kim, H.-J., Kwon, Y.-J., Sim, Y., Tae, W., Kim, S. H., et al. (2020) · Scientific Reports · doi:10.1038/s41598-020-62049-0 · Cited by 44
Beswick, E., Park, E. Y., Wong, C., Mehta, A. R., Dakin, R. S., Chandran, S., Newton, J. L., Carson, A. J., Abrahams, S., & Pal, S. (2020) · Journal of Neurology · doi:10.1007/s00415-020-10203-z · Cited by 46
Self-citationConsonni, M., Telesca, A., Bella, E. D., Bersano, E., & Lauria, G. (2020) · Journal of Neurology · doi:10.1007/s00415-020-10080-6 · Cited by 44
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SIgN, O. B. O., Marchi, F. D., Carrarini, C., Martino, A., Diamanti, L., Fasano, A., Lupica, A., Russo, M., Salemme, S., Spinelli, E. G., et al. (2021) · Neurological Sciences · doi:10.1007/s10072-021-05188-0 · Cited by 42
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van Eijk, R. P. A., Beelen, A., Kruitwagen, E. T., Murray, D., Radaković, R., Hobson, E., Knox, L., Helleman, J., Burke, T., Rubio, M. Á., et al. (2021) · Journal of Medical Internet Research · doi:10.2196/28766 · Cited by 41
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Acosta‐Uribe, J., Aguillon, D. F., Cochran, J. N., Giraldo, M., Madrigal, L., Killingsworth, B. W., Singhal, R., Labib, S., Alzate, D., Velilla, L. M., et al. (2022) · Genome Medicine · doi:10.1186/s13073-022-01035-9 · Cited by 43
Cousins, K. A. Q., Ash, S., & Grossman, M. (2017) · Cortex · doi:10.1016/j.cortex.2017.08.030 · Cited by 45
Cortical correlates of behavioural change in amyotrophic lateral sclerosis
Consonni, M., Cappa, S. F., Bella, E. D., Contarino, V. E., & Lauria, G. (2018) · Journal of Neurology Neurosurgery & Psychiatry · doi:10.1136/jnnp-2018-318619 · Cited by 40
Trojsi, F., Nardo, F. D., Siciliano, M., Caiazzo, G., Femiano, C., Passaniti, C., Ricciardi, D., Russo, A., Bisecco, A., Esposito, S., et al. (2020) · CNS Spectrums · doi:10.1017/s109285292000005x · Cited by 41
Phenotypic variability in ALS-FTD and effect on survival
Ahmed, R. M., Devenney, E. M., Strikwerda‐Brown, C., Hodges, J. R., Piguet, O., & Kiernan, M. C. (2020) · Neurology · doi:10.1212/wnl.0000000000009398 · Cited by 42
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Tan, H. H. G., Westeneng, H., van der Burgh, H. K., van Es, M. A., Bakker, L. A., van Veenhuijzen, K., van Eijk, K. R., van Eijk, R. P. A., Veldink, J. H., & van den Berg, L. H. (2020) · Annals of Neurology · doi:10.1002/ana.25841 · Cited by 41
Franciotti, R., Pignatelli, P., Carrarini, C., Romei, F. M., Mastrippolito, M., Gentile, A., Mancinelli, R., Fulle, S., Piattelli, A., ONOFRJ, M. C., et al. (2021) · Biomolecules · doi:10.3390/biom11060845 · Cited by 40
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McMillan, C. T., Wuu, J., Rascovsky, K., Cosentino, S., Grossman, M., Elman, L. B., Quinn, C. C., Rosario, L., Stark, J. H., Granit, V., et al. (2022) · Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration · doi:10.1080/21678421.2022.2039713 · Cited by 40
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László, Z. I., Hindley, N., Avila, A. S., Kline, R., Eaton, S. L., Lamont, D. J., Smith, C., Spires‐Jones, T. L., Wishart, T. M., & Henstridge, C. M. (2022) · Acta Neuropathologica Communications · doi:10.1186/s40478-022-01455-z · Cited by 39
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Maranzano, A., Verde, F., Colombo, E., Poletti, B., Doretti, A., Bonetti, R., Gagliardi, D., Meneri, M., Maderna, L., Messina, S., et al. (2023) · Brain · doi:10.1093/brain/awad129 · Cited by 38
Self-citationThe burden of apathy for caregivers of patients with amyotrophic lateral sclerosis
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Tan, R. H., Guennewig, B., Dobson‐Stone, C., Kwok, J. B., Kril, J. J., Kiernan, M. C., Hodges, J. R., Piguet, O., & Halliday, G. M. (2019) · Neurology · doi:10.1212/wnl.0000000000007146 · Cited by 41
Depression and risk of cognitive dysfunctions in amyotrophic lateral sclerosis
Marchi, F. D., Sarnelli, M. F., Solara, V., Bersano, E., Cantello, R. M., & Mazzini, L. (2019) · Acta Neurologica Scandinavica · doi:10.1111/ane.13073 · Cited by 37
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Self-citationKourtesis, P., Margioti, E. S., Demenega, C., Christidi, F., & Abrahams, S. (2020) · Journal of the International Neuropsychological Society · doi:10.1017/s1355617720000314 · Cited by 38
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Strong, M. J. (2017) · Current Opinion in Neurology · doi:10.1097/wco.0000000000000488 · Cited by 37
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Self-citationFalzone, Y., Domi, T., Agosta, F., Pozzi, L., Schito, P., Fazio, R., Carro, U. D., Barbieri, A., Comola, M., Leocani, L., et al. (2020) · Journal of Neurology · doi:10.1007/s00415-020-09838-9 · Cited by 35
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Consonni, M., Contarino, V. E., Catricalà, E., Bella, E. D., Pensato, V., Gellera, C., Lauria, G., & Cappa, S. F. (2018) · NeuroImage Clinical · doi:10.1016/j.nicl.2018.05.020 · Cited by 33
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Vinceti, G., Olney, N. T., Mandelli, M. L., Spina, S., Hubbard, H. I., Santos‐Santos, M., Watson, C., Miller, Z., Lomen, C. E., Nichelli, P., et al. (2019) · Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration · doi:10.1080/21678421.2018.1556695 · Cited by 33
D’Alvano, G., Buonanno, D., Passaniti, C., De Stefano, M., Lavorgna, L., Tedeschi, G., Siciliano, M., & Trojsi, F. (2021) · Brain Sciences · doi:10.3390/brainsci12010049 · Cited by 32
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López‐Carbonero, J. I., García-Toledo, I., Fernández-Hernández, L., Bascuñana, P., Moreno, M., Matías‐Guiu, J. A., & Corrochano, S. (2024) · Translational Neurodegeneration · doi:10.1186/s40035-024-00419-8 · Cited by 35
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Castelnovo, V., Canu, E., Calderaro, D., Riva, N., Poletti, B., Basaia, S., Solca, F., Silani, V., Filippi, M., & Agosta, F. (2020) · NeuroImage Clinical · doi:10.1016/j.nicl.2020.102509 · Cited by 35
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Pasetto, L., Grassano, M., Pozzi, S., Luotti, S., Sammali, E., Migazzi, A., Basso, M., Spagnolli, G., Biasini, E., Micotti, E., et al. (2021) · Brain · doi:10.1093/brain/awab333 · Cited by 34
Ngo, S. T., Mi, J. D., Henderson, R. D., McCombe, P., & Steyn, F. J. (2017) · Degenerative Neurological and Neuromuscular Disease · doi:10.2147/dnnd.s120607 · Cited by 31
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Caga, J., Hsieh, S., Highton‐Williamson, E., Zoing, M. C., Ramsey, E., Devenney, E. M., Ahmed, R. M., & Kiernan, M. C. (2017) · Journal of Neurology · doi:10.1007/s00415-017-8688-4 · Cited by 31
Consonni, M., Bella, E. D., Contarino, V. E., Bersano, E., & Lauria, G. (2020) · Cortex · doi:10.1016/j.cortex.2020.07.007 · Cited by 31
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Verde, F., Milone, I., Colombo, E., Maranzano, A., Solca, F., Torre, S., Doretti, A., Gentile, F., Manini, A., Bonetti, R., et al. (2023) · Frontiers in Aging Neuroscience · doi:10.3389/fnagi.2023.1132808 · Cited by 30
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Perini, G., Rodriguez‐Vieitez, E., Kadir, A., Sala, A., Savitcheva, I., & Nordberg, A. K. (2020) · European Journal of Nuclear Medicine and Molecular Imaging · doi:10.1007/s00259-020-04969-7 · Cited by 30
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Trojsi, F., Nardo, F. D., Caiazzo, G., Siciliano, M., D’Alvano, G., Ferrantino, T., Passaniti, C., Ricciardi, D., Esposito, S., Lavorgna, L., et al. (2020) · Brain Imaging and Behavior · doi:10.1007/s11682-020-00408-1 · Cited by 30
Spinelli, E. G., Ghirelli, A., Basaia, S., Cividini, C., Riva, N., Canu, E., Castelnovo, V., Domi, T., Magnani, G., Caso, F., et al. (2021) · Neurology · doi:10.1212/wnl.0000000000012702 · Cited by 30
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Ovsepian, S. V., O’Leary, V. B., & Martı́nez, S. (2023) · Brain Structure and Function · doi:10.1007/s00429-023-02728-6 · Cited by 30
Jang, H., Shin, D., Kim, Y., Kim, K. W., Lee, J., Kim, J. P., Kim, H. J., Cho, S. H., Kim, S. E., Na, D. L., et al. (2024) · Dementia and Neurocognitive Disorders · doi:10.12779/dnd.2024.23.4.212 · Cited by 29
Iazzolino, B., Peotta, L., Zucchetti, J. P., Canosa, A., Manera, U., Vasta, R., Grassano, M., Palumbo, F., Brunetti, M., Barberis, M., et al. (2020) · Neurology · doi:10.1212/wnl.0000000000011093 · Cited by 28
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Canosa, A., Moglia, C., Manera, U., Vasta, R., Torrieri, M. C., Arena, V., D’Ovidio, F., Palumbo, F., Zucchetti, J. P., Iazzolino, B., et al. (2020) · Journal of Neurology Neurosurgery & Psychiatry · doi:10.1136/jnnp-2020-323876 · Cited by 28
Borrego‐Écija, S., Turón‐Sans, J., Ximelis, T., Aldecoa, I., Molina‐Porcel, L., Povedano, M., Rubio, M. Á., Gámez, J., Cano, A., Paré, M., et al. (2021) · Brain Pathology · doi:10.1111/bpa.12942 · Cited by 29
Poletti, B., Solca, F., Carelli, L., Diena, A., Colombo, E., Torre, S., Maranzano, A., Greco, L., Cozza, F., Lizio, A., et al. (2021) · Neurology · doi:10.1212/wnl.0000000000012774 · Cited by 28
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Zizzi, C. E., Seabury, J., Rosero, S. J., Alexandrou, D., Wagner, E., Weinstein, J. S., Varma, A., Dilek, N., Heatwole, J. M., Wuu, J., et al. (2022) · EClinicalMedicine · doi:10.1016/j.eclinm.2022.101768 · Cited by 28
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Agosta, F., Spinelli, E. G., Riva, N., Fontana, A., Basaia, S., Canu, E., Castelnovo, V., Falzone, Y., Carrera, P., Comı, G., et al. (2019) · European Journal of Neurology · doi:10.1111/ene.13957 · Cited by 27
Gregory, J. M., Elliott, E., McDade, K., Bak, T. H., Pal, S., Chandran, S., Abrahams, S., & Smith, C. (2019) · Neuropathology and Applied Neurobiology · doi:10.1111/nan.12575 · Cited by 27
Self-citation
Metadata
- Authors
- Strong, M. J., Abrahams, S., Goldstein, L. H., Woolley, S., Mclaughlin, P., Snowden, J., Mioshi, E., Roberts-South, A., Benatar, M., HortobáGyi, T., Rosenfeld, J., Silani, V., Ince, P. G., & Turner, M. R.
- Affiliations
- Western University (CA)
- Euan MacDonald Centre for Motor Neuron Disease Research (GB)
- King's College London (GB)
- California Pacific Medical Center (US)
- Salford Royal NHS Foundation Trust (GB)
- University of East Anglia (GB)
- Northwestern University, Roxelyn and Richard Pepper Department of Communication Sciences and Disorders, Evanston, IL, USA,
- University of Miami (US)
- University of Debrecen (HU)
- Loma Linda University Medical Center (US)
- University of Milan (IT)
- University of Sheffield (GB)
- University of Oxford (GB)
- Corresponding author
- Strong, Michael J.
- ORCID
- Venue
- Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration
- Publisher
- Informa UK Limited
- Published
- 2017-01-05
- Volume
- 18
- Issue
- 3-4
- Pages
- 153-174
- ISSN
- 2167-8421 (ISSN-L)
- 2167-9223
- PMC
- PMC7409990
- OpenAlex
- W2562172900
- Cited by
- 909
- References
- 194
- Citations by year
- 2026: 90 · 2025: 117 · 2024: 102 · 2023: 119 · 2022: 108 · 2021: 118 · 2020: 101 · 2019: 61 · 2018: 68 · 2017: 25
- FWCI
- 48.58
- Type
- journal article
- Language
- en
- Open access
- green
- ueaeprints.uea.ac.uk
- Locations
- Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration (publishedVersion)
- PubMed (publishedVersion)
- White Rose Research Online (University of Leeds, The University of Sheffield, University of York) (acceptedVersion)
- UEA Digital Repository (University of East Anglia) (acceptedVersion)
- PubMed Central (acceptedVersion)
- University of Debrecen Electronic Archive (University of Debrecen) (submittedVersion)
- Research Portal (King's College London) (submittedVersion, other-oa)
- Research Explorer (The University of Manchester) (submittedVersion)
- Edinburgh Research Explorer (University of Edinburgh) (submittedVersion, other-oa)
- Funders
- South London and Maudsley NHS Foundation Trust
- National Institute for Health and Care Research
- Motor Neurone Disease Association (TURNER/JAN13/944-795)
- King's College London
- Medical Research Council (MR/K026992/1, MR/K01014X/1)
- National Institute of Neurological Disorders and Stroke (U54NS092091)
- Topics
- Health Sciences › Medicine › Clinical Neurology › Amyotrophic Lateral Sclerosis Research
- Health Sciences › Medicine › Psychiatry and Mental health › Dementia and Cognitive Impairment Research
- Life Sciences › Neuroscience › Cellular and Molecular Neuroscience › Alzheimer's disease research and treatments
- Keywords
- amyotrophic lateral sclerosis, frontotemporal dementia, diagnostic criteria, neuropsychological deficits, social cognition, language deficits, cognitive heterogeneity, survival, consensus criteria
- MeSH terms
- Amyotrophic Lateral Sclerosis, Canada, Diagnosis, Differential, Humans, Language, Neuropsychological Tests, Social Perception, Survival Analysis, Frontotemporal Dementia, Neuroimaging
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