Congenital Auricular Anomalies: Topographic Anatomy, Embryology, Classification, and Treatment Strategies
Abstract
Congenital auricular anomalies are heterogeneous, with various descriptive and eponymous terms being used. Current classification systems are useful in guiding surgical treatment of severe anomalies. However, they do not generally account for the less severe anomalies, which form the majority of congenital auricular anomalies, nor their contemporary treatment. In this article, the authors review the anatomy and embryology of the external ear and propose a simple classification of congenital auricular anomalies that encompasses all forms of congenital auricular anomalies, facilitates proper diagnosis, and guides treatment. Congenital auricular anomalies should be classified as malformational or deformational anomalies. Malformational auricular anomalies are caused by embryologic maldevelopment that occurs between the fifth and ninth week of gestation resulting in deficient and/or supernumerary auricular components. Deformational auricular anomalies result from in utero or ex utero deformational forces, including those caused by an aberrant insertion of the intrinsic or extrinsic auricular muscles. Malformational auricular anomalies generally require surgical correction during childhood or adolescence. For practical purposes, deformational auricular anomalies have a full complement of chondrocutaneous components that can be digitally manipulated to a normal shape. These anomalies are best treated by auricular molding, which is effective if it is initiated within the first 3 months of life. Deformational auricular anomalies are best regarded as a pediatric public health issue and are best managed nonsurgically. Education of neonatal pediatricians, obstetricians, family doctors, and midwives will allow proper early diagnosis of all congenital auricular anomalies, which is vital to appropriate treatment. These practitioners should be encouraged to manage deformational auricular anomalies early in life so that surgery can be largely avoided in these patients.
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Porter et al described a method to differentiate malformation from deformation using digital pressure to create a normal ear shape; if this is not possible, this indicates a chondro-cutaneous defect, thus malformation.
“A method to differentiate was described by Porter et al,3 who uses digital pressure to create a normal ear shape. If this is not possible, this indicates a chondro-cutaneous defect, thus malformation.”
From Non-surgical Correction of Congenital Ear Anomalies: A Review of the Literature (2020) · cites this paper as [3]
Cites
A new method of total reconstruction of the auricle for microtia
Nagata, S. (1993) · Plastic and Reconstructive Surgery · doi:10.1097/00006534-199308000-00001 · Cited by 640 · see citing works
Nonsurgical correction of congenital auricular deformities
Matsuoy, K., Hayashi, R., Kiyono, M., Hirose, T., & Netsu, Y. (1990) · Clinics in Plastic Surgery · doi:10.1016/s0094-1298(20)31252-9 · Cited by 143 · see citing works
Molding therapy for infants with deformational auricular anomalies
Tan, S. T., Abramson, D. L., MacDonald, D. M., & Mulliken, J. B. (1997) · Annals of Plastic Surgery · doi:10.1097/00000637-199703000-00013 · Cited by 116 · see citing works
Self-citationNon-surgical correction of a congenital lop ear deformity by splinting with Reston foam
Kurozumi, N., Ono, S., & Ishida, H. (1982) · British Journal of Plastic Surgery · doi:10.1016/0007-1226(82)90160-6 · Cited by 92 · see citing works
A splint for correction of congenital ear deformities
Tan, S. T., Shibu, M., & Gault, D. T. (1994) · British Journal of Plastic Surgery · doi:10.1016/0007-1226(94)90144-9 · Cited by 92 · see citing works
Early nonsurgical correction of congenital auricular deformities.
Ullmann, Y., Blazer, S., Ramon, Y., Blumenfeld, I., & Peled, I. J. (2002) · Plastic and Reconstructive Surgery · doi:10.1097/00006534-200203000-00013 · Cited by 77 · see citing works
Ear Projection and the Posterior Auricular Muscle Insertion
Guyuron, B., & DeLuca, L. (1997) · Plastic &amp Reconstructive Surgery · doi:10.1097/00006534-199708000-00030 · Cited by 66 · see citing works
Surgical and conservative repair of Stahl's ear
Nakajima, T., Yoshimura, Y., & Kami, T. (1984) · Aesthetic Plastic Surgery · doi:10.1007/bf01575252 · Cited by 40 · see citing works
Flagged first, then by citations
Cited by
Sorted by citations
Mouse <i>Hoxa2</i> mutations provide a model for microtia and auricle duplication
Minoux, M., Kratochwil, C. F., Ducret, S., Amin, S., Kitazawa, T., Kurihara, H., Bobola, N., Vilain, N., & Rijli, F. M. (2013) · Development · doi:10.1242/dev.098046 · Cited by 97 · see citing works
van Wijk, M. P., Breugem, C. C., & Kon, M. (2009) · Journal of Plastic, Reconstructive & Aesthetic Surgery · doi:10.1016/j.bjps.2009.01.020 · Cited by 88 · see citing works
Daniali, L. N., Rezzadeh, K., Shell, C., Trovato, M., Ha, R., & Byrd, H. S. (2017) · Plastic & Reconstructive Surgery · doi:10.1097/prs.0000000000003150 · Cited by 82 · see citing works
Non-surgical correction of deformational auricular anomalies
Schonauer, F., La Rusca, I., & Molea, G. (2009) · Journal of Plastic, Reconstructive & Aesthetic Surgery · doi:10.1016/j.bjps.2007.11.072 · Cited by 46 · see citing works
van Wijk, M. P., Breugem, C. C., & Kon, M. (2012) · Journal of Plastic, Reconstructive & Aesthetic Surgery · doi:10.1016/j.bjps.2011.08.021 · Cited by 45 · see citing works
Neonatal ear molding: timing and technique.
Anstadt, E. E., Johns, D. N., Kwok, A. C.-M., Siddiqi, F., & Gociman, B. (2016) · PEDIATRICS · doi:10.1542/peds.2015-2831 · Cited by 44 · see citing works
Newborn ear deformities: early recognition and novel nonoperative techniques
Schultz, K., Guillen, D., & Maricevich, R. (2017) · Seminars in Plastic Surgery · doi:10.1055/s-0037-1603958 · Cited by 34 · see citing works
Petersson, R. S., Recker, C. A., Martin, J. R. K., Driscoll, C. L. W., & Friedman, O. (2012) · International Journal of Pediatric Otorhinolaryngology · doi:10.1016/j.ijporl.2012.06.011 · Cited by 33 · see citing works
Management of Congenital Auricular Anomalies.
Joukhadar, N., McKee, D., Caouette-Laberge, L., & Bezuhly, M. (2020) · Plastic & Reconstructive Surgery · doi:10.1097/prs.0000000000006997 · Cited by 32 · see citing works
Deformations of the Ear and Their Nonsurgical Correction
Chang, C. S., & Bartlett, S. P. (2019) · Clinical Pediatrics · doi:10.1177/0009922819844296 · Cited by 30 · see citing works
Nonsurgical Management of Congenital Auricular Anomalies
Lennon, C., & Chinnadurai, S. (2018) · Facial Plastic Surgery Clinics of North America · doi:10.1016/j.fsc.2017.09.001 · Cited by 28 · see citing works
Anthropometric research of congenital auricular deformities for newborns
Zhao, H., Lin, G., Seong, Y. H., Shi, J., Xu, J., & Huang, W. (2019) · The Journal of Maternal-Fetal & Neonatal Medicine · doi:10.1080/14767058.2017.1402877 · Cited by 26 · see citing works
Non-surgical Correction of Congenital Ear Anomalies: A Review of the Literature
Feijen, M. M. W., van Cruchten, C., Payne, P. E., & van der Hulst, R. R. W. J. (2020) · Plastic and Reconstructive Surgery - Global Open · doi:10.1097/gox.0000000000003250 · Cited by 22 · see citing works
Bhatti, S. L., Daly, L. T., Mejia, M., & Perlyn, C. (2021) · Pediatrics In Review · doi:10.1542/pir.2019-0167 · Cited by 16 · see citing works
Using Ear Molding to Treat Congenital Auricular Deformities
Chen, Y., Wang, W., Wang, Y., & Mao, X. (2021) · Frontiers in Pediatrics · doi:10.3389/fped.2021.752981 · Cited by 15 · see citing works
Autologous ear reconstruction for microtia does not result in loss of cutaneous sensitivity.
Denadai, R., Raposo-Amaral, C. E., Zanco, G. L., & Raposo- Amaral, C. A. (2019) · Plastic & Reconstructive Surgery · doi:10.1097/prs.0000000000005485 · Cited by 12 · see citing works
Otoplasty for Congenital Auricular Malformations
Lin, J., & Sclafani, A. P. (2018) · Facial Plastic Surgery Clinics of North America · doi:10.1016/j.fsc.2017.09.003 · Cited by 10 · see citing works
A 10-Year Retrospective Review of the Nonsurgical Treatment of Infant Ear Anomalies
Charipova, K., Rogers, A., Barra, C., & Baker, S. B. (2022) · Plastic & Reconstructive Surgery · doi:10.1097/prs.0000000000009638 · Cited by 10 · see citing works
Charipova (2022) · doi:10.1097/prs.0000000000009335 · Cited by 9 · see citing works
Vincent (2019) · doi:10.1016/j.anplas.2018.06.011 · Cited by 9 · see citing works
Ear Molding in Children—Timing, Technique, and Follow-up: A Systematic Review
Sulibhavi, A., Reddy, S. P., Butts, S. C., & Schmalbach, C. E. (2024) · Facial Plastic Surgery & Aesthetic Medicine · doi:10.1089/fpsam.2023.0321 · Cited by 4 · see citing works
Should Constricted Ear Be Treated as Auricular Malformation or Deformity?
Wang, D., Lin, L., Pan, B., Yang, Q., & Jiang, H. (2018) · Annals of Plastic Surgery · doi:10.1097/sap.0000000000001553 · Cited by 1 · see citing works
- Authors
- Porter, C. J. W., & Tan, S. T.
- Affiliations
- Hutt Hospital (NZ)
- ORCID
- Tan, Swee T.
- Venue
- Plastic and Reconstructive Surgery
- Published
- 2005-05
- Volume
- 115
- Issue
- 6
- Pages
- 1701-1712
- ISSN
- 0032-1052 (ISSN-L)
- OpenAlex
- W2082826551
- Cited by
- 152
- References
- 8
- Citations by year
- 2026: 7 · 2025: 11 · 2024: 13 · 2023: 12 · 2022: 11 · 2021: 19 · 2020: 12 · 2019: 7 · 2018: 7 · 2017: 11 · 2016: 5 · 2015: 3 · 2014: 4 · 2013: 4 · 2012: 7
- FWCI
- 3.13
- Type
- journal article
- Language
- en
- Open access
- closed
- Locations
- Plastic & Reconstructive Surgery (publishedVersion)
- PubMed (publishedVersion)
- Topics
- Health Sciences › Medicine › Surgery › Reconstructive Facial Surgery Techniques
- Health Sciences › Medicine › Genetics › Congenital Ear and Nasal Anomalies
- Life Sciences › Biochemistry, Genetics and Molecular Biology › Genetics › Craniofacial Disorders and Treatments
- Keywords
- auricular muscles, early diagnosis
- MeSH terms
- Congenital Abnormalities, Ear Cartilage, Ear, External, Humans
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