Rehabilitation Considerations for Very Young Children with Severe Oligodontia due to Ectodermal Dysplasia: Report of Three Clinical Cases with a 2‐Year Follow‐Up
Open accessAbstract
Introduction . Management of oligodontia can be complicated and requires multidiscipline care, involving a wide spectrum of interventions. The aim of this report is to describe the challenges of oral rehabilitation of three very young children with oligodontia. Report . Three preschool aged Caucasian males, diagnosed with ectodermal dysplasia, were treated with interim removable dentures in order to replace missing teeth, reclaim vertical dimension, and improve function and aesthetics. The main challenges faced were patient cooperation, dental and skeletal characteristics, and parental expectations. Two years post‐treatment, both patients and parents reported excellent adaptation to prosthesis and satisfaction with aesthetics. Conclusion . Rehabilitation of oligodontia may be challenging due to accompanying oral findings, dentofacial growth considerations, and behavioral issues. Establishment of good rapport between patients, parents, and clinician is the key for the success of the treatment even with the use of nonpharmacological behavioral management techniques.
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Ectodermal dysplasias are a group of genetic disorders that impair the development and/or function of at least two ectodermal structures such as hair, teeth, nails, and certain glands.
“The Ectodermal Dysplasias (ED) Classification Working Group defines ectodermal dysplasias as a group of genetic disorders that impair the development and/or function of at least two ectodermal structures such as hair, teeth, nails, and certain glands.”
From Application of a Conservative Prosthodontic Approach in the Rehabilitation of a 10-Year-Old Child with Hypohidrotic Ectodermal Dysplasia (2025) · cites this paper as [1]
The Introduction defines ectodermal dysplasia as a group of genetic disorders involving abnormalities in at least two ectodermal structures, including hair, teeth, nails, and glands. It does not identify the Ectodermal Dysplasias Classification Working Group as the source of that definition. (LLM, conf=0.82)
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- Authors
- Seremidi, K., Markouli, A., Agouropoulos, A., Polychronakis, N., & Gizani, S.
- Affiliations
- National and Kapodistrian University of Athens (GR)
- Corresponding author
- Seremidi, Kyriaki
- Venue
- Case Reports in Dentistry
- Publisher
- Wiley
- Published
- 2022-01
- Volume
- 2022
- Issue
- 1
- Pages
- 9925475-9925475
- ISSN
- 2090-6447 (ISSN-L)
- 2090-6455
- PMC
- PMC8964192
- OpenAlex
- W4220838765
- Cited by
- 6
- References
- 32
- Citations by year
- 2026: 1 · 2025: 3 · 2024: 1 · 2023: 1
- FWCI
- 0.41
- Type
- journal article
- Language
- en
- Open access
- gold
- doi.org
- Licence
- Locations
- Case Reports in Dentistry (publishedVersion, cc-by)
- PubMed Central (publishedVersion, cc-by)
- PubMed (publishedVersion)
- DOAJ (DOAJ: Directory of Open Access Journals) (submittedVersion)
- Topics
- Life Sciences › Biochemistry, Genetics and Molecular Biology › Molecular Biology › dental development and anomalies
- Health Sciences › Dentistry › Periodontics › Dental Health and Care Utilization
- Health Sciences › Health Professions › Emergency Medical Services › Dental Trauma and Treatments
- Keywords
- oligodontia, ectodermal dysplasia, oral rehabilitation, removable dentures, interim prosthesis, preschool children, vertical dimension of occlusion, patient cooperation, behavior management, parental expectations, dentofacial growth
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