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ASCs-Exosomes Recover Coupling Efficiency and Mitochondrial Membrane Potential in an in vitro Model of ALS

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Redox Regulation in Amyotrophic Lateral Sclerosis

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Mitochondria and the pathogenesis of ALS

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What is “Hyper” in the ALS Hypermetabolism?

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Coenzyme Q treatment of neurodegenerative diseases of aging

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Oxidative stress and antioxidant enzyme upregulation in SOD1‐G93A mouse skeletal muscle

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Effect of coenzyme Q10 on the mitochondrial function of skin fibroblasts from Parkinson patients

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Calcium: the Darth Vader of ALS

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PGC‐1α protects neurons and alters disease progression in an amyotrophic lateral sclerosis mouse model

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Mitochondrial Dysfunction in Neuromuscular Disorders

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Cytochrome c Oxidase and Its Role in Neurodegeneration and Neuroprotection

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Mitochondrial respiratory chain function in skeletal muscle of ALS patients

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Manganese‐containing superoxide dismutase signal sequence polymorphism associated with sporadic motor neuron disease

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Deciphering the role of PGC-1α in neurological disorders: from mitochondrial dysfunction to synaptic failure

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Mitochondrial dysfunction in neurodegenerative disorders

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Progress in Clinical Neurosciences: The Evidence for ALS as a Multisystems Disorder of Limited Phenotypic Expression

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l-Carnitine suppresses the onset of neuromuscular degeneration and increases the life span of mice with familial amyotrophic lateral sclerosis

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Age‐related decreases in NAD(P)H and glutathione cause redox declines before ATP loss during glutamate treatment of hippocampal neurons

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Nutritional and metabolic support in patients with amyotrophic lateral sclerosis

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Role of platelets in neurodegenerative diseases: a universal pathophysiology

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Could mitochondrial haplogroups play a role in sporadic amyotrophic lateral sclerosis?

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More than a bystander: the contributions of intrinsic skeletal muscle defects in motor neuron diseases

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Mitochondrial abnormalities in muscle and other aging cells: Classification, causes, and effects

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Mitochondrial complex I deficiency and ATP/ADP ratio in lymphocytes of amyotrophic lateral sclerosis patients

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Mitochondrial Involvement in Amyotrophic Lateral Sclerosis: Trigger or Target?

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Therapeutic progress in amyotrophic lateral sclerosis-beginning to learning

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Re-evaluation of the dysfunction of mitochondrial respiratory chain in skeletal muscle of patients with Parkinson?s disease

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Metabolic and Stress Response Changes Precede Disease Onset in the Spinal Cord of Mutant SOD1 ALS Mice

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Effects of mitochondrial dysfunction on glutamate receptor-mediated neurotoxicity in cultured rat spinal motor neurons

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Dysregulated mitochondrial Ca2+ and ROS signaling in skeletal muscle of ALS mouse model

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Triheptanoin Protects Motor Neurons and Delays the Onset of Motor Symptoms in a Mouse Model of Amyotrophic Lateral Sclerosis

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G37R SOD1 mutant alters mitochondrial complex I activity, Ca2+ uptake and ATP production

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Skeletal Muscle Satellite Cells, Mitochondria, and MicroRNAs: Their Involvement in the Pathogenesis of ALS

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Mitochondrial DNA abnormalities in skeletal muscle of patients with sporadic amyotrophic lateral sclerosis

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Visualization of defective mitochondrial function in skeletal muscle fibers of patients with sporadic amyotrophic lateral sclerosis

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Mitochondrial Respiratory Chain Dysfunction in Muscle From Patients With Amyotrophic Lateral Sclerosis

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Mitochondrial dysfunction in amyotrophic lateral sclerosis also affects skeletal muscle

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Mitochondrial changes in skeletal muscle in amyotrophic lateral sclerosis and other neurogenic atrophies

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