Cystic fibrosis

Cystic Fibrosis

Rowe, S. M., Miller, S., & Sorscher, E. J. (2005) · New England Journal of Medicine · doi:10.1056/nejmra043184 · Cited by 1,398 · see citing works

Early Pulmonary Inflammation in Infants with Cystic Fibrosis

Khan, T. Z., Wagener, J. S., Bost, T., Martínez, J. A. B., Accurso, F. J., & Riches, D. W. H. (1995) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/ajrccm/151.4.1075 · Cited by 1,264 · see citing works

Evidence for Periciliary Liquid Layer Depletion, Not Abnormal Ion Composition, in the Pathogenesis of Cystic Fibrosis Airways Disease

Matsui, H., Grubb, B. R., Tarran, R., Randell, S. H., Gatzy, J. T., Davis, C. W., & Boucher, R. C. (1998) · Cell · doi:10.1016/s0092-8674(00)81724-9 · Cited by 1,168 · see citing works

CYSTIC FIBROSIS OF THE PANCREAS AND ITS RELATION TO CELIAC DISEASE

Andersen, D. H. (1938) · American journal of diseases of children · doi:10.1001/archpedi.1938.01980140114013 · Cited by 1,150 · see citing works

PTC124 targets genetic disorders caused by nonsense mutations

Welch, E. M., Barton, E. R., Zhuo, J., Tomizawa, Y., Friesen, W. J., Trifillis, P., Paushkin, S. V., Patel, M., Trotta, C. R., Hwang, S., et al. (2007) · Nature · doi:10.1038/nature05756 · Cited by 1,138 · see citing works

CFTR as a cAMP-Dependent Regulator of Sodium Channels

Stutts, M. J., Canessa, C. M., Olsen, J. C., Hamrick, M., Cohn, J. A., Rossier, B. C., & Boucher, R. C. (1995) · Science · doi:10.1126/science.7543698 · Cited by 1,088 · see citing works

Guidelines for Diagnosis of Cystic Fibrosis in Newborns through Older Adults: Cystic Fibrosis Foundation Consensus Report

Farrell, P. M., Rosenstein, B. J., White, T. B., Accurso, F. J., Castellani, C., Cutting, G. R., Durie, P. R., LeGrys, V. A., Massie, J., Parad, R. B., et al. (2008) · The Journal of Pediatrics · doi:10.1016/j.jpeds.2008.05.005 · Cited by 1,077 · see citing works

Human β-Defensin-1 Is a Salt-Sensitive Antibiotic in Lung That Is Inactivated in Cystic Fibrosis

Goldman, M. J., Anderson, G. M., Stolzenberg, E. D., Kari, U. P., ZASLOFF, M. A., & Wilson, J. M. (1997) · Cell · doi:10.1016/s0092-8674(00)81895-4 · Cited by 1,077 · see citing works

Cystic Fibrosis Airway Epithelia Fail to Kill Bacteria Because of Abnormal Airway Surface Fluid

Smith, J. J., Travis, S. M., Greenberg, E. P., & Welsh, M. J. (1996) · Cell · doi:10.1016/s0092-8674(00)81099-5 · Cited by 1,039 · see citing works

Cystic fibrosis: A worldwide analysis ofCFTR mutations?correlation with incidence data and application to screening

Bobadilla, J. L., Macek, M., Fine, J. P., & Farrell, P. M. (2002) · Human Mutation · doi:10.1002/humu.10041 · Cited by 1,032 · see citing works

Cystic Fibrosis Pulmonary Guidelines

Flume, P. A., O'Sullivan, B. P., Robinson, K. A., Goss, C. H., Mogayzel, P. J., Willey‐Courand, D. B., Bujan, J., Finder, J. D., Lester, M., Quittell, L. M., et al. (2007) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.200705-664oc · Cited by 1,024 · see citing works

Azithromycin in Patients With Cystic Fibrosis Chronically Infected With Pseudomonas aeruginosa: A Randomized Controlled Trial

Saiman, L., Marshall, B. C., Mayer-Hamblett, N., Burns, J. L., Quittner, A. L., Cibene, D. A., Coquillette, S., Fieberg, A. Y., Accurso, F. J., Campbell III, P. W., et al. (2003) · JAMA · doi:10.1001/jama.290.13.1749 · Cited by 958 · see citing works

Effects of reduced mucus oxygen concentration in airway Pseudomonas infections of cystic fibrosis patients

Worlitzsch, D., Tarran, R., Ulrich, M., Schwab, U., Cekici, A., Meyer, K. C., Birrer, P., Bellon, G., Berger, J., Weiss, T., et al. (2002) · Journal of Clinical Investigation · doi:10.1172/jci0213870 · Cited by 932 · see citing works

A Controlled Trial of Long-Term Inhaled Hypertonic Saline in Patients with Cystic Fibrosis

Elkins, M. R., Robinson, M., Rose, B. R., Harbour, C., Moriarty, C. P., Marks, G. B., Belousova, E. G., Xuan, W., & Bye, P. T. P. (2006) · New England Journal of Medicine · doi:10.1056/nejmoa043900 · Cited by 855 · see citing works

Early Diagnosis of Cystic Fibrosis Through Neonatal Screening Prevents Severe Malnutrition and Improves Long-Term Growth

Farrell, P. M., Kosorok, M. R., Rock, M. J., Laxova, A., Zeng, L., Lai, H.-C., Hoffman, G. L., Laessig, R. H., Splaingard, M., & the Wisconsin Cystic Fibrosis Neonatal Screening Study Group (2001) · PEDIATRICS · doi:10.1542/peds.107.1.1 · Cited by 836 · see citing works

Administration of an adenovirus containing the human CFTR cDNA to the respiratory tract of individuals with cystic fibrosis

Crystal, R. G., McElvaney, N. G., Rosenfeld, M. A., Chu, C.-S., Mastrangeli, A., Hay, J. G., Brody, S. L., Jaffe, H. A., Eissa, N. T., & Danel, C. J. (1994) · Nature Genetics · doi:10.1038/ng0994-42 · Cited by 824 · see citing works

A comparison of survival, growth, and pulmonary function in patients with cystic fibrosis in Boston and Toronto

Corey, M. L., McLaughlin, F. J., Williams, M., & Levison, H. (1988) · Journal of Clinical Epidemiology · doi:10.1016/0895-4356(88)90063-7 · Cited by 812 · see citing works

Allergic Bronchopulmonary Aspergillosis in Cystic Fibrosis—State of the Art: Cystic Fibrosis Foundation Consensus Conference

Stevens, D. A., Moss, R. B., Kurup, V. P., Knutsen, A. P., Greenberger, P., Judson, M. A., Denning, D. W., Crameri, R., Brody, A. S., Light, M., et al. (2003) · Clinical Infectious Diseases · doi:10.1086/376525 · Cited by 790 · see citing works

Disruption of the CFTR Gene Produces a Model of Cystic Fibrosis in Newborn Pigs

Rogers, C. S., Stoltz, D. A., Meyerholz, D. K., Ostedgaard, L. S., Rokhlina, T., Taft, P. J., Rogan, M. P., Pezzulo, A. A., Karp, P. H., Itani, O. A., et al. (2008) · Science · doi:10.1126/science.1163600 · Cited by 752 · see citing works

Effect of High-Dose Ibuprofen in Patients with Cystic Fibrosis

Konstan, M. W., Byard, P. J., Hoppel, C. L., & Davis, P. B. (1995) · New England Journal of Medicine · doi:10.1056/nejm199503303321303 · Cited by 724 · see citing works

Mucus Clearance and Lung Function in Cystic Fibrosis with Hypertonic Saline

Donaldson, S. H., Bennett, W. D., Zeman, K. L., Knowles, M. R., Tarran, R., & Boucher, R. C. (2006) · New England Journal of Medicine · doi:10.1056/nejmoa043891 · Cited by 689 · see citing works

CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP

Schwiebert, E. M., Egan, M. E., Hwang, T.-H., Fulmer, S. B., Allen, S. S., Cutting, G. R., & Guggino, W. B. (1995) · Cell · doi:10.1016/s0092-8674(05)80011-x · Cited by 641 · see citing works

Nontuberculous Mycobacteria: I: Multicenter Prevalence Study in Cystic Fibrosis

Olivier, K. N., Weber, D. J., Wallace, R. J., Faiz, A. R., Lee, J., Zhang, Y., Brown‐Elliott, B. A., Handler, A., Wilson, R. W., Schechter, M. S., et al. (2003) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.200207-678oc · Cited by 629 · see citing works

Cystic fibrosis mortality and survival in the UK: 1947–2003

DODGE, J. A., Lewis, P. A., Stanton, M., & Wilsher, J. (2006) · European Respiratory Journal · doi:10.1183/09031936.00099506 · Cited by 627 · see citing works

Antibiotic therapy against Pseudomonas aeruginosa in cystic fibrosis: a European consensus

Döring, G., Conway, S. P., Heijerman, H. G. M., Hodson, M. E., Høiby, N., Smyth, A. R., & Touw, D. J. (2000) · European Respiratory Journal · doi:10.1034/j.1399-3003.2000.16d30.x · Cited by 618 · see citing works

Consensus on the use and interpretation of cystic fibrosis mutation analysis in clinical practice

Castellani, C., Cuppens, H., Maçek, M., Cassiman, J. J., Kerem, E., Durie, P. R., Tullis, E. D., Assael, B. M., Bombieri, C., Brown, A., et al. (2008) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2008.03.009 · Cited by 602 · see citing works

Hsp90 Cochaperone Aha1 Downregulation Rescues Misfolding of CFTR in Cystic Fibrosis

Wang, X., Venable, J. D., LaPointe, P., Hutt, D. M., Koulov, A. V., Coppinger, J. A., Gürkan, C., Kellner, W. A., Matteson, J., Plutner, H., et al. (2006) · Cell · doi:10.1016/j.cell.2006.09.043 · Cited by 597 · see citing works

Consensus Report on Nutrition for Pediatric Patients With Cystic Fibrosis

Borowitz, D., Baker, R. D., & Stallings, V. A. (2002) · Journal of Pediatric Gastroenterology and Nutrition · doi:10.1097/00005176-200209000-00004 · Cited by 579 · see citing works

Cystic Fibrosis Adult Care

Yankaskas, J. R., Marshall, B. C., Sufian, B. S., Simon, R. H., & Rodman, D. M. (2004) · CHEST Journal · doi:10.1378/chest.125.1_suppl.1s · Cited by 571 · see citing works

Curcumin, a Major Constituent of Turmeric, Corrects Cystic Fibrosis Defects

Egan, M. E., Pearson, M., Weiner, S. A., Rajendran, V., Rubin, D., Glöckner-Pagel, J., Canny, S., Du, K., Lukács, G. L., & Caplan, M. J. (2004) · Science · doi:10.1126/science.1093941 · Cited by 562 · see citing works

Longitudinal Assessment ofPseudomonas aeruginosain Young Children with Cystic Fibrosis

Burns, J. L., Gibson, R. L., McNamara, S., Yim, D. L., Emerson, J., Rosenfeld, M., Hiatt, P., McCoy, K., Castile, R. G., Smith, A. L., et al. (2001) · The Journal of Infectious Diseases · doi:10.1086/318075 · Cited by 555 · see citing works

Long term azithromycin in children with cystic fibrosis: a randomised, placebo-controlled crossover trial

Equi, A., Balfour-Lynn, I. M., Bush, A., & Rosenthal, M. (2002) · The Lancet · doi:10.1016/s0140-6736(02)11081-6 · Cited by 542 · see citing works

Effect of long term treatment with azithromycin on disease parameters in cystic fibrosis: a randomised trial

Wolter, J. M. (2002) · Thorax · doi:10.1136/thorax.57.3.212 · Cited by 516 · see citing works

Airway Surface Dehydration in Cystic Fibrosis: Pathogenesis and Therapy

Boucher, R. C. (2007) · Annual Review of Medicine · doi:10.1146/annurev.med.58.071905.105316 · Cited by 509 · see citing works

Genetic Modifiers of Lung Disease in Cystic Fibrosis

Drumm, M. L., Konstan, M. W., SCHLUCHTER, M. D., Handler, A., Pace, R. G., Zou, F., Zariwala, M. A., Fargo, D. C., Xu, A., Dunn, J. M., et al. (2005) · New England Journal of Medicine · doi:10.1056/nejmoa051469 · Cited by 498 · see citing works

Registry of the International Society for Heart and Lung Transplantation: Twenty-fourth Official Adult Lung and Heart–Lung Transplantation Report—2007

Trulock, E. P., Christie, J. D., Edwards, L. B., Boucek, M. M., Aurora, P., Taylor, D. O., Dobbels, F., Rahmel, A. O., Keck, B. M., & Hertz, M. I. (2007) · The Journal of Heart and Lung Transplantation · doi:10.1016/j.healun.2007.06.003 · Cited by 484 · see citing works

Guide to Bone Health and Disease in Cystic Fibrosis

Aris, R. M., Merkel, P. A., Bachrach, L. K., et al. (2005) · The Journal of Clinical Endocrinology & Metabolism · doi:10.1210/jc.2004-1629 · Cited by 452 · see citing works

Exacerbations in cystic fibrosis {middle dot} 1: Epidemiology and pathogenesis

Goss, C. H., & Burns, J. L. (2007) · Thorax · doi:10.1136/thx.2006.060889 · Cited by 445 · see citing works

Risk Factors For Rate of Decline in Forced Expiratory Volume in One Second in Children and Adolescents with Cystic Fibrosis

Konstan, M. W., Morgan, W. J., Butler, S. M., Pasta, D. J., Craib, M. L., Silva, S. J., Stokes, D. C., Wohl, M. E. B., Wagener, J. S., Regelmann, W. E., et al. (2007) · The Journal of Pediatrics · doi:10.1016/j.jpeds.2007.03.006 · Cited by 436 · see citing works

Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: a prospective phase II trial

Kerem, E., Hirawat, S., Armoni, S., Yaakov, Y., Shoseyov, D., Cohen, M., Nissim‐Rafinia, M., Blau, H., Rivlin, J., Aviram, M., et al. (2008) · The Lancet · doi:10.1016/s0140-6736(08)61168-x · Cited by 401 · see citing works

Acceleration of lung disease in children with cystic fibrosis after Pseudomonas aeruginosa acquisition

Kosorok, M. R., Zeng, L., West, S. E. H., Rock, M. J., Splaingard, M., Laxova, A., Green, C. G., Collins, J., & Farrell, P. M. (2001) · Pediatric Pulmonology · doi:10.1002/ppul.2009.abs · Cited by 401 · see citing works

The prevalence of cystic fibrosis in the European Union

Farrell, P. M. (2008) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2008.03.007 · Cited by 395 · see citing works

Association of Cystic Fibrosis with Abnormalities in Fatty Acid Metabolism

Freedman, S. D., Blanco, P. G., Zaman, M. M., Shea, J. C., Ollero, M., Hopper, I. K., Weed, D., Gelrud, A., Regan, M. M., Laposata, M., et al. (2004) · New England Journal of Medicine · doi:10.1056/nejmoa021218 · Cited by 395 · see citing works

Growth and nutritional indexes in early life predict pulmonary function in cystic fibrosis

Konstan, M. W., Butler, S. M., Wohl, M. E. B., Stoddard, M., Matousek, R., Wagener, J. S., Johnson, C. A., & Morgan, W. J. (2003) · The Journal of Pediatrics · doi:10.1067/mpd.2003.152 · Cited by 393 · see citing works

Cystic fibrosis: terminology and diagnostic algorithms

Boeck, K. D. (2005) · Thorax · doi:10.1136/thx.2005.043539 · Cited by 387 · see citing works

Nutritional Benefits of Neonatal Screening for Cystic Fibrosis

Farrell, P. M., Kosorok, M. R., Laxova, A., Shen, G., Koscik, R. E., Bruns, W. T., Splaingard, M., & Mischler, E. H. (1997) · New England Journal of Medicine · doi:10.1056/nejm199710023371403 · Cited by 386 · see citing works

Cystic fibrosis: impaired bicarbonate secretion and mucoviscidosis

Quinton, P. (2008) · The Lancet · doi:10.1016/s0140-6736(08)61162-9 · Cited by 376 · see citing works

Sick Chaperones, Cellular Stress, and Disease

Macario, A. J. L., & de Macario, E. C. (2005) · New England Journal of Medicine · doi:10.1056/nejmra050111 · Cited by 372 · see citing works

The cystic fibrosis transmembrane conductance regulator is a dual ATP and chloride channel.

Reisin, I. L., Prat, A. G., Abraham, E. H., Amara, J. F., Gregory, R. J., Ausiello, D. A., & Cantiello, H. F. (1994) · Journal of Biological Chemistry · doi:10.1016/s0021-9258(17)32033-1 · Cited by 355 · see citing works

A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis

Eigen, H., Rosenstein, B. J., FitzSimmons, S., et al. (1995) · The Journal of Pediatrics · doi:10.1016/s0022-3476(95)70343-8 · Cited by 345 · see citing works

Defective lipoxin-mediated anti-inflammatory activity in the cystic fibrosis airway

Karp, C. L., Flick, L. M., Park, K. W., Softic, S., Greer, T. M., Keledjian, R., Yang, R., Uddin, J., Guggino, W. B., Atabani, S. F., et al. (2004) · Nature Immunology · doi:10.1038/ni1056 · Cited by 344 · see citing works

Epidemiology of cystic fibrosis-related diabetes

Marshall, B. C., Butler, S. M., STODDARD, M. L., Moran, A., Liou, T. G., & Morgan, W. J. (2005) · The Journal of Pediatrics · doi:10.1016/j.jpeds.2004.12.039 · Cited by 329 · see citing works

Cleavage of CXCR1 on neutrophils disables bacterial killing in cystic fibrosis lung disease

Hartl, D., Latzin, P., Hordijk, P. L., Marcos, V., Rudolph, C., Woischnik, M., Krauss‐Etschmann, S., Koller, B., Reinhardt, D., Roscher, A. A., et al. (2007) · Nature Medicine · doi:10.1038/nm1690 · Cited by 322 · see citing works

Persistent Methicillin-resistant Staphylococcus aureus and Rate of FEV1 Decline in Cystic Fibrosis

Dasenbrook, E. C., Merlo, C. A., Diener‐West, M., Lechtzin, N., & Boyle, M. (2008) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.200802-327oc · Cited by 319 · see citing works

Production of CFTR-null and CFTR-ΔF508 heterozygous pigs by adeno-associated virus–mediated gene targeting and somatic cell nuclear transfer

Rogers, C. S., Hao, Y., Rokhlina, T., Samuel, M., Stoltz, D. A., Li, Y., Petroff, E., Vermeer, D. W., Kabel, A. C., Yan, Z., et al. (2008) · Journal of Clinical Investigation · doi:10.1172/jci34773 · Cited by 318 · see citing works

Colistin inhalation therapy in cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection

Jensen, T., Pedersen, S. S., Garne, S., et al. (1987) · Journal of Antimicrobial Chemotherapy · doi:10.1093/jac/19.6.831 · Cited by 315 · see citing works

Diagnostic Sweat Testing: The Cystic Fibrosis Foundation Guidelines

LeGrys, V. A., Yankaskas, J. R., Quittell, L. M., Marshall, B. C., & Mogayzel, P. J. (2007) · The Journal of Pediatrics · doi:10.1016/j.jpeds.2007.03.002 · Cited by 306 · see citing works

Newborn Screening for Cystic Fibrosis: Evaluation of Benefits and Risks and Recommendations for State Newborn Screening Programs—

Grosse, S. D., Boyle, C. A., Botkin, J. R., et al. (2005) · The Journal of Pediatrics · doi:10.1016/j.jpeds.2005.09.004 · Cited by 304 · see citing works

Repeated Aerosolized AAV-CFTR for Treatment of Cystic Fibrosis: A Randomized Placebo-Controlled Phase 2B Trial

Moss, R. B., Milla, C. E., Colombo, J. L., Accurso, F. J., Zeitlin, P. L., Clancy, J. P., Spencer, L. T., Pilewski, J. M., Waltz, D. A., Dorkin, H. L., et al. (2007) · Human Gene Therapy · doi:10.1089/hum.2007.022 · Cited by 276 · see citing works

Sodium 4-phenylbutyrate downregulates Hsc70: implications for intracellular trafficking of ΔF508-CFTR

Rubenstein, R. C., & Zeitlin, P. L. (2000) · American Journal of Physiology-Cell Physiology · doi:10.1152/ajpcell.2000.278.2.c259 · Cited by 269 · see citing works

A randomised clinical trial of nebulised tobramycin or colistin in cystic fibrosis

Hodson, M. E., Gallagher, C. G., & Govan, J. R. W. (2002) · European Respiratory Journal · doi:10.1183/09031936.02.00248102 · Cited by 269 · see citing works

Reduction of Sputum Pseudomonas aeruginosa Density by Antibiotics Improves Lung Function in Cystic Fibrosis More than Do Bronchodilators and Chest Physiotherapy Alone

Regelmann, W. E., Elliott, G. R., Warwick, W. J., & Clawson, C. C. (1990) · American Review of Respiratory Disease · doi:10.1164/ajrccm/141.4_pt_1.914 · Cited by 261 · see citing works

PTC124 is an orally bioavailable compound that promotes suppression of the human CFTR -G542X nonsense allele in a CF mouse model

Du, M., Liu, X., Welch, E. M., Hirawat, S., Peltz, S. W., & Bedwell, D. M. (2008) · Proceedings of the National Academy of Sciences · doi:10.1073/pnas.0711795105 · Cited by 257 · see citing works

Eradication of early Pseudomonas aeruginosa infection

Høiby, N., Frederiksen, B., & Pressler, T. (2005) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2005.05.018 · Cited by 255 · see citing works

Altered respiratory epithelial cell cytokine production in cystic fibrosis

Bonfield, T. L., Konstan, M. W., & Berger, M. (1999) · Journal of Allergy and Clinical Immunology · doi:10.1016/s0091-6749(99)70116-8 · Cited by 255 · see citing works

Loss of CFTR Chloride Channels Alters Salt Absorption by Cystic Fibrosis Airway Epithelia In Vitro

Zabner, J., Smith, J. J., Karp, P. H., Widdicombe, J. H., & Welsh, M. J. (1998) · Molecular Cell · doi:10.1016/s1097-2765(00)80284-1 · Cited by 251 · see citing works

Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface.

Imundo, L. F., Barasch, J. M., Prince, A. S., & Al‐Awqati, Q. (1995) · Proceedings of the National Academy of Sciences · doi:10.1073/pnas.92.7.3019 · Cited by 251 · see citing works

Burkholderia cenocepacia and Burkholderia multivorans: influence on survival in cystic fibrosis

Jones, A. M. (2004) · Thorax · doi:10.1136/thx.2003.017210 · Cited by 251 · see citing works

A physical linkage between cystic fibrosis airway surface dehydration and Pseudomonas aeruginosa biofilms

Matsui, H., Wagner, V., Hill, D. B., Schwab, U. E., Rogers, T. D., Button, B. M., Taylor, R. M., Superfine, R., Rubinstein, M., Iglewski, B. H., et al. (2006) · Proceedings of the National Academy of Sciences · doi:10.1073/pnas.0606428103 · Cited by 245 · see citing works

Allergic bronchopulmonary aspergillosis in cystic fibrosis. A European epidemiological study

Mastella, G., Rainisio, M., Harms, H. K., et al. (2000) · European Respiratory Journal · doi:10.1034/j.1399-3003.2000.016003464.x · Cited by 244 · see citing works

Inflammation and Infection in Naive Human Cystic Fibrosis Airway Grafts

Tirouvanziam, R. M., de Bentzmann, S., Hubeau, C., Hinnrasky, J., Jacquot, J. P., Péault, B., & Puchelle, É. (2000) · American Journal of Respiratory Cell and Molecular Biology · doi:10.1165/ajrcmb.23.2.4214 · Cited by 234 · see citing works

FREQUENT ANTIBIOTIC THERAPY IMPROVES SURVIVAL OF CYSTIC FIBROSIS PATIENTS WITH CHRONIC PSEUDOMONAS AERUGINOSA INFECTION

Szaff, M., Høiby, N., & Flensborg, E. W. (1983) · Acta Paediatrica · doi:10.1111/j.1651-2227.1983.tb09789.x · Cited by 233 · see citing works

Nonpharmacologic Airway Clearance Therapies

McCool, F. D., & Rosen, M. J. (2006) · CHEST Journal · doi:10.1378/chest.129.1_suppl.250s · Cited by 232 · see citing works

Factors Influencing Outcomes in Cystic Fibrosis

Johnson, C. A., Butler, S. M., Konstan, M. W., Morgan, W. J., & Wohl, M. E. B. (2003) · CHEST Journal · doi:10.1378/chest.123.1.20 · Cited by 226 · see citing works

Diabetes Is Associated With Dramatically Decreased Survival in Female but Not Male Subjects With Cystic Fibrosis

Milla, C. E., Billings, J. L., & Moran, A. (2005) · Diabetes Care · doi:10.2337/diacare.28.9.2141 · Cited by 210 · see citing works

Multicenter Cross-Sectional Study of Nontuberculous Mycobacterial Infections among Cystic Fibrosis Patients, Israel

Levy, I. E., Grisaru‐Soen, G., Lerner‐Geva, L., et al. (2008) · Emerging infectious diseases · doi:10.3201/eid1403.061405 · Cited by 202 · see citing works

Lung Transplantation and Survival in Children with Cystic Fibrosis

Liou, T. G., Adler, F. R., Cox, D. R., & Cahill, B. C. (2007) · New England Journal of Medicine · doi:10.1056/nejmoa066359 · Cited by 196 · see citing works

COMPOSITION OF TRACHEOBRONCHIAL SECRETIONS IN CYSTIC FIBROSIS OF THE PANCREAS AND BRONCHIECTASIS

Chernick, W. S., & Barbero, G. J. (1959) · PEDIATRICS · doi:10.1542/peds.24.5.739 · Cited by 195 · see citing works

The cystic fibrosis transmembrane conductance regulator: an intriguing protein with pleiotropic functions

Vankeerberghen, A., Cuppens, H., & Cassiman, J. J. (2002) · Journal of Cystic Fibrosis · doi:10.1016/s1569-1993(01)00003-0 · Cited by 188 · see citing works

Macrolide activities beyond their antimicrobial effects: macrolides in diffuse panbronchiolitis and cystic fibrosis

Schultz, M. (2004) · Journal of Antimicrobial Chemotherapy · doi:10.1093/jac/dkh309 · Cited by 187 · see citing works

Innate immune response in CF airway epithelia: hyperinflammatory?

Machen, T. E. (2006) · American Journal of Physiology-Cell Physiology · doi:10.1152/ajpcell.00605.2005 · Cited by 182 · see citing works

Early eradication therapy againstPseudomonas aeruginosain cystic fibrosis patients

Taccetti, G., Campana, S., Festini, F., et al. (2005) · European Respiratory Journal · doi:10.1183/09031936.05.00009605 · Cited by 181 · see citing works

Impact of <i>Burkholderia</i> Infection on Lung Transplantation in Cystic Fibrosis

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Impact of Pregnancy on Women With Cystic Fibrosis

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