Cystic fibrosis

Standardisation of spirometry

Miller, M. R., Hankinson, J., Brusasco, V., Burgos, F., Casaburi, R., Coates, A., Crapo, R., Enright, P., van der Grinten, C. P. M., Gustafsson, P., et al. (2005) · European Respiratory Journal · doi:10.1183/09031936.05.00034805 · Cited by 15,627

Identification of the Cystic Fibrosis Gene: Genetic Analysis

Kerem, B.-S., Rommens, J. M., Buchanan, J. A., Markiewicz, D., Cox, T. K., Chakravarti, A., Buchwald, M., & Tsui, L.-C. (1989) · Science · doi:10.1126/science.2570460 · Cited by 4,142

Antibiotic resistance in Pseudomonas aeruginosa: mechanisms and alternative therapeutic strategies

Pang, Z., Raudonis, R., Glick, B. R., Lin, T., & Cheng, Z. (2018) · Biotechnology Advances · doi:10.1016/j.biotechadv.2018.11.013 · Cited by 2,520

Elexacaftor–Tezacaftor–Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele

Middleton, P. G., Mall, M. A., Dřevínek, P., Lands, L. C., McKone, E. F., Polineni, D., Ramsey, B. W., Taylor-Cousar, J. L., Tullis, E., Vermeulen, F., et al. (2019) · New England Journal of Medicine · doi:10.1056/nejmoa1908639 · Cited by 2,198

A CFTR Potentiator in Patients with Cystic Fibrosis and the G551D Mutation

Ramsey, B. W., Davies, J., McElvaney, N. G., Tullis, E., Bell, S. C., Dřevínek, P., Griese, M., McKone, E. F., Wainwright, C. E., Konstan, M. W., et al. (2011) · New England Journal of Medicine · doi:10.1056/nejmoa1105185 · Cited by 2,195

Lumacaftor–Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR

Wainwright, C. E., Elborn, J. S., Ramsey, B. W., Marigowda, G., Huang, X., Cipolli, M., Colombo, C., Davies, J. C., De Boeck, K., Flume, P. A., et al. (2015) · New England Journal of Medicine · doi:10.1056/nejmoa1409547 · Cited by 1,622

Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial

Heijerman, H. G. M., McKone, E. F., Downey, D. G., Van Braeckel, E., Rowe, S. M., Tullis, E., Mall, M. A., Welter, J. J., Ramsey, B. W., McKee, C. M., et al. (2019) · The Lancet · doi:10.1016/s0140-6736(19)32597-8 · Cited by 1,414

Intermittent Administration of Inhaled Tobramycin in Patients with Cystic Fibrosis

Ramsey, B. W., PEPE, M. S., Quan, J. M., Otto, K., Montgomery, A. B., Williams‐Warren, J., Vasiljev-K, M., Borowitz, D., Bowman, C. M., Marshall, B. C., et al. (1999) · New England Journal of Medicine · doi:10.1056/nejm199901073400104 · Cited by 1,296

The International Thoracic Organ Transplant Registry of the International Society for Heart and Lung Transplantation: Thirty-sixth adult lung and heart–lung transplantation Report—2019; Focus theme: donor and recipient size match

Chambers, D. C., Cherikh, W. S., Harhay, M. O., Hayes, D., Hsich, E., Khush, K. K., Meiser, B., Potena, L., Rossano, J. W., Toll, A. E., et al. (2019) · The Journal of Heart and Lung Transplantation · doi:10.1016/j.healun.2019.08.001 · Cited by 1,269

The future of cystic fibrosis care: a global perspective

Bell, S. C., Mall, M. A., Gutierrez, H., Macek, M., Madge, S. L., Davies, J. C., Burgel, P., Tullis, E., Castaños, C., Castellani, C., et al. (2019) · The Lancet Respiratory Medicine · doi:10.1016/s2213-2600(19)30337-6 · Cited by 1,081

THE FIRST RESULTS OF TARGETED THERAPY IN CHILDREN WITH CYSTIC FIBROSIS IN KAZAKHSTAN

Marshalkina, T., Zhanuzakova, N., Mukatova, I. Y., Kim, S. S., & Amelina, E. (2024) · Ġylym men densaulyķ saķtau. · doi:10.34689/sh.2024.26.4.001 · Cited by 5

Ezrin drives adaptation of monocytes to the inflamed lung microenvironment

Gudneppanavar, R., Pietro, C. D., Öz, H. H., Zhang, P.-X., Cheng, E.-C., Huang, P. H., Tebaldi, T., Biancon, G., Halene, S., Hoppe, A. D., et al. (2024) · Cell Death and Disease · doi:10.1038/s41419-024-07255-8 · Cited by 6

Identification of an Au(I) N-Heterocyclic Carbene Compound as a Bactericidal Agent Against Pseudomonas aeruginosa

Wang, J., Sun, X., Xie, Y., Long, Y., Chen, H. W., He, X., Zou, T., Mao, Z., & Xia, W. T. (2022) · Frontiers in Chemistry · doi:10.3389/fchem.2022.895159 · Cited by 5

Diagnosis and Therapeutic Strategies Based on Nucleic Acid Aptamers Selected against Pseudomonas aeruginosa: The Challenge of Cystic Fibrosis

Gutiérrez‐Santana, J. C., & Coria‐Jiménez, R. (2023) · ChemMedChem · doi:10.1002/cmdc.202300544 · Cited by 5

Longitudinal Evaluation of Physical Fitness in Adults with Cystic Fibrosis in the Era of CFTR-Modulating-Therapies

Welsner, M., Gruber, W., Blosch, C., Koerner‐Rettberg, C., Brinkmann, F., Dillenhoefer, S., Sutharsan, S., Taube, C., Mellies, U., Olivier, M., et al. (2024) · Research Quarterly for Exercise and Sport · doi:10.1080/02701367.2024.2320234 · Cited by 5

Clearing up the smoke: Physical and mental health considerations regarding cannabis use in adolescents with cystic fibrosis

Ince, H. Y., Phan, H., Nasr, S. Z., Pierce, J., & Malas, N. (2022) · Pediatric Pulmonology · doi:10.1002/ppul.26241 · Cited by 5

Differential effects of ELX/TEZ/IVA on organ-specific CFTR function in two patients with the rare CFTR splice mutations c.273+1G>A and c.165-2A>G

Pallenberg, S. T., Held, I., Dopfer, C., Minso, R., Nietert, M. M., Hansen, G., Tümmler, B., & Dittrich, A. (2023) · Frontiers in Pharmacology · doi:10.3389/fphar.2023.1153656 · Cited by 5

Primary nasal epithelial cells from patients with cystic fibrosis hold promise for guiding precision medicine and expanding treatment

Reeves, S. R. (2021) · European Respiratory Journal · doi:10.1183/13993003.02735-2021 · Cited by 5

Organoids in Cancer Research and Regenerative Medicine: Current Status, Challenges, and Future Prospects

Li, R., Wu, Y., Zheng, Z., Zhou, F., Xu, K., & Su, J. (2026) · MedComm · doi:10.1002/mco2.70575 · Cited by 4

Impact of habitual physical activity and exercise capacity on quality of life in adolescents and adults with cystic fibrosis

Welsner, M., Gruber, W., Blosch, C., Olivier, M., Mellies, U., Dillenhoefer, S., Brinkmann, F., Koerner‐Rettberg, C., Sutharsan, S., Taube, C., et al. (2024) · Pediatric Pulmonology · doi:10.1002/ppul.26855 · Cited by 4

Cystic fibrosis–related metabolic defects: crosstalk between ion channels and organs

Sims‐Lucas, S., Goetzman, E. S., & Kleyman, T. R. (2024) · Journal of Clinical Investigation · doi:10.1172/jci182329 · Cited by 4

Evaluating the effects of ivacaftor exposure on Staphylococcus aureus small colony variant development and antibiotic tolerance

Bollar, G. E., Shaffer, K. M., Keith, J. D., Oden, A. M., Dowell, A. E., Ryan, K. J., Acosta, E. P., Guimbellot, J. S., Kiedrowski, M. R., & Birket, S. E. (2024) · JAC-Antimicrobial Resistance · doi:10.1093/jacamr/dlae185 · Cited by 4

Identification of a vimentin-expressing α-cell phenotype in CF and normal pancreas

Kattner, N., Hang, Y., Krentz, N. A. J., Russell, L. A., Palmer, M., Flaxman, C. S., Plett, N., Coulthard, R., Al-Selwi, Y., Dyson, N. J., et al. (2025) · Journal of Endocrinology · doi:10.1530/joe-24-0190 · Cited by 4

AI-facilitated home monitoring for cystic fibrosis exacerbations across pediatric and adult populations

Mazurek, H., Emeryk, A., Janeczek, K., Derom, E., Kuźnar-Kamińska, B., Grzywalski, T., Biniakowski, A., Szarzyński, K., Pastusiak, A., Kaminiarczyk‐Pyzałka, D., et al. (2025) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2025.02.011 · Cited by 4

Wound repair and immune function in the Pseudomonas infected CF lung: before and after highly effective modulator therapy

Matthews, E. L., Hirsch, M. J., Prokopczuk, F. I., Jones, L., Martínez, E., Barnes, J. W., & Krick, S. (2025) · Frontiers in Cellular and Infection Microbiology · doi:10.3389/fcimb.2025.1566495 · Cited by 4

Height Velocity in Pediatric Cystic Fibrosis Under Triple CFTR Modulator Therapy: A Real-Life Monocentric Experience

Boni, A., d’Aniello, F., Ubertini, G., Cappa, M., Ciciriello, F., Majo, F., Cristiani, L., Alghisi, F., Montemitro, E., Bella, S., et al. (2025) · Journal of Clinical Medicine · doi:10.3390/jcm14155259 · Cited by 4

Utility of Continuous Glucose Monitors for Improved Detection of Cystic Fibrosis‐Related Diabetes

Moore, C. E., Chen, W., Bichl, S., Wong, A., Heyman, C., Ratnam, S., & Bianco, M. E. (2025) · Pediatric Pulmonology · doi:10.1002/ppul.71267 · Cited by 4

Modulators of anion channels and transporters as alternative therapeutic agents to normalize airway surface liquid in cystic fibrosis

Lipani, A., Mascolo, F. L., Giuffrida, S., Barreca, M., Bivacqua, R., Spanò, V., Raimondi, M. V., Borrelli, A., Venturini, A., Guidone, D., et al. (2025) · European Journal of Medicinal Chemistry · doi:10.1016/j.ejmech.2025.118325 · Cited by 4

Quantification of chloride in sweat by using ion chromatography instead of chloridometer

Bertges, M., & Weiskirchen, R. (2022) · SN Applied Sciences · doi:10.1007/s42452-022-05162-1 · Cited by 4

CFTR pharmacological modulators: A great advance in cystic fibrosis management

Foucaud, P., & Mercier, J. (2022) · Archives de Pédiatrie · doi:10.1016/j.arcped.2022.11.019 · Cited by 4

Seroprevalence and clinical characteristics of SARS‐CoV‐2 infection in children with cystic fibrosis

Hergenroeder, G. E., Faino, A., Cogen, J. D., Genatossio, A., McNamara, S., Pascual, M., & Hernandez, R. E. (2023) · Pediatric Pulmonology · doi:10.1002/ppul.26528 · Cited by 4

Lung function decline is mitigated following liver transplantation in people with cystic fibrosis: A retrospective cohort study

Albaiz, F. A., Ramos, K. J., Sykes, J. R., Stanojevic, S., Ma, X., Quon, B. S., Marshall, B. C., Cromwell, E. A., Ostrenga, J. S., Faro, A., et al. (2023) · Liver Transplantation · doi:10.1097/lvt.0000000000000232 · Cited by 4

Improving health literacy of antibiotic use in people with cystic fibrosis (CF)—comparison of the readability of patient information leaflets (PILs) from the EU, USA and UK of 23 CF-related antibiotics used in the treatment of CF respiratory infections

Tang, K. W. K., Millar, B. C., & Moore, J. E. (2023) · JAC-Antimicrobial Resistance · doi:10.1093/jacamr/dlad129 · Cited by 5

Galectin-3 levels in children with cystic fibrosis

Tural, D. A., Emiralioğlu, N., Akın, Ş., Alboğa, D., Özsezen, B., Büyükşahin, H. N., Güzelkaş, İ., Kaşıkçı, M., Sunman, B., Gungor, I., et al. (2024) · European Journal of Pediatrics · doi:10.1007/s00431-024-05479-6 · Cited by 4

Longitudinal improvements in clinical and functional outcomes following initiation of elexacaftor/tezacaftor/ivacaftor in patients with cystic fibrosis

Vijaykumar, K., Leung, H. M., Barrios, A., Wade, J., Hathorne, H. Y., Nichols, D. P., Tearney, G. J., Rowe, S. M., & Solomon, G. M. (2024) · Heliyon · doi:10.1016/j.heliyon.2024.e29188 · Cited by 4

Elexacaftor/tezacaftor/ivacaftor, a game-changer in cystic fibrosis: The Portuguese experience

FRAGOSO, E. C., Boaventura, R. D. P., Almeida, L., Amorim, A. A., Gamboa, F., Santos, A. S., Gonçalves, F., Cruz, C. M., Carreiro, A., Gonçalves, A. S., et al. (2024) · Pulmonary Pharmacology & Therapeutics · doi:10.1016/j.pupt.2024.102328 · Cited by 4

Improvement of intestinal inflammation after treatment with CFTR modulators in cystic fibrosis patients

Romero, R. G., Cárdenes, C. M. L., Crehuá‐Gaudiza, E., Beltrán, M. Á., Hurtado, M. M., Gómez, C. T., Eseverri, I. L., Rubio, E. T., García‐Volpe, C., Lobato, E. S., et al. (2025) · Anales de Pediatría (English Edition) · doi:10.1016/j.anpede.2025.503836 · Cited by 4

Viruses to the rescue—Use of bacteriophage to treat resistant pulmonary infections

Toporek, A. H., & Lechtzin, N. (2022) · Cell · doi:10.1016/j.cell.2022.04.037 · Cited by 4

Deciphering the interplay between autophagy and polarity in epithelial tubulogenesis

Alfonso‐Pérez, T., Baonza, G., Herranz, G., & Martín‐Belmonte, F. (2022) · Seminars in Cell and Developmental Biology · doi:10.1016/j.semcdb.2022.05.015 · Cited by 4

Acute soluble fibre supplementation has no impact on reducing post-prandial glucose excursions in adults with cystic fibrosis and glucose intolerance

Dubois, C. L., Boudreau, V., Potter, K. J., Colomba, J., Lavoie, A., Mailhot, M., Desjardins, K., & RABASA-LHORET, R. P. R. (2023) · Annales d Endocrinologie · doi:10.1016/j.ando.2023.02.001 · Cited by 4

A foetus with cystic fibrosis – To treat or not to treat?

Padmakumar, N., & Khan, H. S. (2023) · Respiratory Medicine and Research · doi:10.1016/j.resmer.2023.101006 · Cited by 4

Characteristics associated with cystic fibrosis-related pulmonary exacerbation treatment location

Gold, L. S., Hansen, R. N., Heltshe, S. L., Flume, P. A., Goss, C. H., West, N. E., Sanders, D. B., & Kessler, L. G. (2023) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2023.10.004 · Cited by 4

Prevalence of Scoliosis in Children and Adolescents with Cystic Fibrosis

Fainardi, V., Nora, M., Salghetti, A., Petraglia, F., Fanzaghi, P., Anelli, G., Cattabiani, M., Scopelliti, G., Deolmi, M., Ferrari, I., et al. (2024) · Children · doi:10.3390/children11030321 · Cited by 4

Emerging Approaches to Monitor and Modify Care in the era of CFTR Modulators

Britto, C. J., Ratjen, F. A., & Clancy, J. P. (2022) · Clinics in Chest Medicine · doi:10.1016/j.ccm.2022.06.006 · Cited by 4

Yardstick for managing cough, part 2: In children

Chang, A. B., Oppenheimer, J. J., Dunlap, W., Lieberman, P., & Irwin, R. S. (2023) · Annals of Allergy Asthma & Immunology · doi:10.1016/j.anai.2023.01.026 · Cited by 4

Drug Hypersensitivity Reactions in Patients with Cystic Fibrosis: Potential Value of the Lymphocyte Toxicity Assay to Assess Risk

Abuzgaia, A. M., Elzagallaai, A. A., Mullowney, T., & Rieder, M. J. (2023) · Molecular Diagnosis & Therapy · doi:10.1007/s40291-023-00644-3 · Cited by 4

Validation of the ACMG/AMP guidelines-based seven-category variant classification systemPreprint

Chen, J., Masson, E., Zou, W., Liao, Z., Génin, E., Cooper, D. N., & Férec, C. (2023) · medRxiv · doi:10.1101/2023.01.23.23284909 · Cited by 4

Flow cytometric measurement of CFTR-mediated chloride transport in human neutrophils

Montanez-Barragan, A., Robledo-Avila, F. H., Rascón, R., McCoy, K., Kopp, B. T., & Partida‐Sánchez, S. (2025) · Journal of Leukocyte Biology · doi:10.1093/jleuko/qiaf006 · Cited by 3

Prevalence and characteristics of gastrointestinal disorders, medication use, and diagnostic interventions in pediatric patients with cystic fibrosis: a nested case–control analysis from the TriNetX EMR-derived global research network real-world dataset

Trocchia, C., Mosha, M. H., Hamner, B., Goldenberg, N. A., & Khalaf, R. T. (2025) · Frontiers in Gastroenterology · doi:10.3389/fgstr.2024.1489876 · Cited by 3

Esc peptides and derivatives potentiate the activity of CFTR with gating defects and display antipseudomonal activity in cystic fibrosis-like lung disease

Ferrera, L., Cappiello, F., Venturini, A., Lu, H., Casciaro, B., Cappella, G., Bontempi, G., Corrente, A., Strippoli, R., Zara, F., et al. (2025) · Cellular and Molecular Life Sciences · doi:10.1007/s00018-025-05633-9 · Cited by 3

Mejoría de la inflamación intestinal tras tratamiento con moduladores de la proteína CFTR en pacientes con fibrosis quística

Romero, R. G., Cárdenes, C. M. L., Crehuá‐Gaudiza, E., Beltrán, M. Á., Hurtado, M. M., Gómez, C. T., Eseverri, I. L., Rubio, E. T., García‐Volpe, C., Lobato, E. S., et al. (2025) · Anales de Pediatría · doi:10.1016/j.anpedi.2025.503836 · Cited by 3

The Spectrum and Carrier Frequencies of Common Pathogenic Cystic Fibrosis Transmembrane Conductance Regulator Gene Mutations in Men from the General Population: The Role of Ethnicity

Осадчук, Л. В., Ivanov, M., Komova, E. G., & Осадчук, А. В. (2025) · International Journal of Molecular Sciences · doi:10.3390/ijms26146625 · Cited by 3

Mycobacteriophages in the Treatment of Mycobacterial Infections: From Compassionate Use to Targeted Therapy

Druszczyńska, M., Sadowska, B., Zabłotni, A., Zhuravska, L., Kulesza, J., & Fol, M. (2025) · Applied Sciences · doi:10.3390/app15158543 · Cited by 3

Contrast-enhanced multispectral optoacoustic tomography for the assessment of the gastrointestinal transit in patients with cystic fibrosis

Fuchte, J., Wachter, F., Claßen, M., Vogt-Wolz, H., Paulus, L., Mandelbaum, H., Büehler, A., Siebenlist, G., Jüngert, J., Wölfle, J., et al. (2025) · Photoacoustics · doi:10.1016/j.pacs.2025.100766 · Cited by 3

CFTR High Expresser BEST4 + cells are pH-sensing neuropod cells: new implications for intestinal physiology and cystic fibrosis disease

dos Reis, D. C., Jin, J. G., Santos, A. K., Dastoor, P. K., Muiler, C., Zagoren, E., Donnelley, M., Parsons, D., Cmielewski, P., Reyne, N., et al. (2025) · American Journal of Physiology-Cell Physiology · doi:10.1152/ajpcell.00082.2025 · Cited by 3

Isolation and Characterization of Four New Coliphages against Extra Intestinal Pathogenic Escherichia coli Isolates Recovered from Cystic Fibrosis Patients

García‐González, G., García-Pérez, J. M., Flores, P. D. M., Ríos, R. R., Espinoza-Mellado, M. D. R., Velázquez‐Guadarrama, N., Encinas-Basurto, D., Juárez, J., López‐Mata, M. A., Eslava-Campos, C. A., et al. (2025) · ACS Omega · doi:10.1021/acsomega.5c04140 · Cited by 3

Activating the Osteoblastic USP26 Pathway Alleviates Multi‐Organ Fibrosis by Decreasing Insulin Resistance

Tang, J., Ye, W., He, L., Zhou, D., Chang, L., You, Z., Jiang, Y., Tang, G., Deng, L., & Li, C. (2025) · Advanced Science · doi:10.1002/advs.202512424 · Cited by 3

Prenatal Elexacaftor/Tezacaftor/Ivacaftor for Fetal Meconium Ileus: First Italian Case and Narrative Overview of the Emerging Evidence

Boni, A., Vassallo, C., Ciciriello, F., Cristiani, L., Mancini, A., Zucaro, L., Graziano, S., Goffredo, B. M., Alghisi, F., Raponi, M., et al. (2026) · Journal of Clinical Medicine · doi:10.3390/jcm15072625 · Cited by 3

Hypoxia: a critical pathophysiological driver in respiratory inflammatory diseases

Zhong, B., Yang, L., Sun, S.-L., Chen, H., & Wang, D. Y. (2026) · Military Medical Research · doi:10.1016/j.mmr.2026.100023 · Cited by 3

Re-balancing immunity with CRISPR-Cas9: Novel strategies for cancer and autoimmune disorders

Ren, X., Zhou, Z., Kong, L., Guo, Y., Liu, Y., Li, J., Gu, X., Jiang, C., & Wu, J. (2026) · Biotechnology Advances · doi:10.1016/j.biotechadv.2026.108921 · Cited by 3

KDM2A and KDM3B as Potential Targets for the Rescue of F508del-CFTR

D’Amore, C., Borgo, C., Bosello-Travain, V., & Salvi, M. (2022) · International Journal of Molecular Sciences · doi:10.3390/ijms23179612 · Cited by 3

What is the Perceived Role of the Dietitian Amongst People with Cystic Fibrosis? Results of an International survey

Anderson, H. L., Lynch, V., Moore, J. E., & Millar, B. C. (2023) · Canadian Journal of Dietetic Practice and Research · doi:10.3148/cjdpr-2022-044 · Cited by 3

Antimicrobial resistance of Pseudomonas aeruginosa in a cystic fibrosis population after introduction of a novel cephalosporin/β‐lactamase inhibitor combination

Katzenstein, T. L., Faurholt‐Jepsen, D., Qvist, T., Jensen, P. Ø., Pressler, T., Johansen, H. K., & Kolpen, M. (2023) · Apmis · doi:10.1111/apm.13331 · Cited by 3

Treatment of intestinal and liver features in cystic fibrosis mice by the osmotic laxative polyethylene glycol

Bertolini, A., Bloks, V. W., Wilmink, M., Bos, E., van de Peppel, I. P., Eilers, R. E., Prins, S. D., Thomas, R., de Bruin, A., Verkade, H. J., et al. (2023) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2023.09.015 · Cited by 3

Health care resource utilization preceding death or lung transplantation in people with cystic fibrosis

Guyot, E., Reynaud, Q., Belhassen, M., Bérard, M., Dehillotte, C., Lemonnier, L., Viprey, M., Ganse, E. H. V., Burgel, P., & Durieu, I. (2024) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2024.03.001 · Cited by 3

Restored Cytokine-Producing Capacities of Mucosal-associated Invariant T Cells in Pediatric Cystic Fibrosis Patients Treated with Elexacaftor/Tezacaftor/Ivacaftor

Bardin, E., Dietrich, C., Attailia, M., Ferroni, A., Jamet, A., Lezmi, G., Sermet‐Gaudelus, I., & Leite‐de‐Moraes, M. (2024) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.202401-0201le · Cited by 3

Cystic Fibrosis

Blevings, P. J., Moore, J. E., & Millar, B. C. (2022) · Journal of Preventive Diagnostic and Treatment Strategies in Medicine · doi:10.4103/jpdtsm.jpdtsm_10_22 · Cited by 3

Endocrine pathology in young rabbits with cystic fibrosis

Liang, X., Hou, X., Chen, Y. E., Jin, J., Zhang, K., & Xu, J. (2024) · eGastroenterology · doi:10.1136/egastro-2024-100102 · Cited by 3

Airway Remodeling in Cystic Fibrosis Is Heterogeneous

Vermaut, A., Geudens, V., Willems, L., Aerts, G., Kerckhof, P., Hooft, C., Beeckmans, H., Kaes, J., Jin, X., Fays, C. D., et al. (2024) · Annals of the American Thoracic Society · doi:10.1513/annalsats.202404-446oc · Cited by 3

Mesenchymal stromal cells reduce inflammation and improve lung function in a mouse model of cystic fibrosis lung disease

Doherty, D. F., Roets, L. E., Dougan, C. M., Brown, R. R., Hawthorne, I. J., O’Kane, C. M., Krasnodembskaya, A. D., Mall, M. A., Taggart, C. C., & Weldon, S. (2024) · Scientific Reports · doi:10.1038/s41598-024-81276-3 · Cited by 3

Evaluating the Diagnostic Potential of the FIB-4 Index for Cystic Fibrosis-Associated Liver Disease in Adults: A Comparison with Transient Elastography

Armstrong, S., Rajiah, K., Courtenay, A. J., Ali, N., & Abuelhana, A. (2025) · Journal of Clinical Medicine · doi:10.3390/jcm14155404 · Cited by 3

Non-viral mRNA cystic fibrosis therapies and their ongoing clinical trials

Gill, N. A., Fung, V., VanKeulen‐Miller, R., Narasipura, E. A., & Fenton, O. S. (2025) · Expert Opinion on Drug Delivery · doi:10.1080/17425247.2025.2586172 · Cited by 3

Advances in Cystic Fibrosis Research in Qatar: A Commentary

Hammoudeh, S., & Janahi, I. A. (2023) · Journal of Personalized Medicine · doi:10.3390/jpm13030448 · Cited by 3

Hope in Every Breath: Navigating the Therapeutic Landscape of Cystic Fibrosis

Sreenivasulu, H., Muppalla, S. K., Vuppalapati, S., Shokrolahi, M., & Pulliahgaru, A. R. (2023) · Cureus · doi:10.7759/cureus.43603 · Cited by 3

Morbidity and treatment costs of cystic fibrosis in a middle-income country

Hng, S. Y., Thinakaran, A. S., Ooi, C. J., Eg, K. P., Thong, M., Tae, S. K., Goh, S. H., Chew, K. S., Tan, L. T., Koh, M. T., et al. (2023) · Singapore Medical Journal · doi:10.4103/singaporemedj.smj-2022-093 · Cited by 3

The Role of Cystic Fibrosis Transmembrane Conductance Regulator Modulators After Liver Transplantation in Persons With Cystic Fibrosis

Maradiaga, R., Ramsey, M. L., Kirkby, S. E., & Sobotka, L. A. (2024) · ACG Case Reports Journal · doi:10.14309/crj.0000000000001261 · Cited by 3

Recommended Tool Compounds for Modifying the Cystic Fibrosis Transmembrane Conductance Regulator Channel Variants

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