Idiopathic Pulmonary Fibrosis

An Official ATS/ERS/JRS/ALAT Statement: Idiopathic Pulmonary Fibrosis: Evidence-based Guidelines for Diagnosis and Management

Raghu, G., Collard, H. R., Egan, J. J., Martinez, F. J., Behr, J., Brown, K. K., Colby, T. V., Cordier, J.-F., Flaherty, K. R., Lasky, J. A., et al. (2011) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.2009-040gl · Cited by 7,186

Efficacy and Safety of Nintedanib in Idiopathic Pulmonary Fibrosis

Richeldi, L., du Bois, R. M., Raghu, G., Azuma, A., Brown, K. K., Costabel, U., Cottin, V., Flaherty, K. R., Hansell, D. M., Inoue, Y., et al. (2014) · New England Journal of Medicine · doi:10.1056/nejmoa1402584 · Cited by 4,654

A phase 3 trial of pirfenidone in patients with idiopathic pulmonary fibrosis.

King, T. E., Bradford, W. Z., Castro-Bernardini, S., Fagan, E. A., Glaspole, I., Glassberg, M. K., Gorina, E., Hopkins, P. M., Kardatzke, D., Lancaster, L., et al. (2014) · New England Journal of Medicine · doi:10.1056/nejmoa1402582 · Cited by 3,975

Screening for Lung Cancer: U.S. Preventive Services Task Force Recommendation Statement

Moyer, V. A., & on behalf of the U.S. Preventive Services Task Force* (2013) · Annals of Internal Medicine · doi:10.7326/m13-2771 · Cited by 2,642

Guidelines for Management of Incidental Pulmonary Nodules Detected on CT Images: From the Fleischner Society 2017.

MacMahon, H., Naidich, D. P., Goo, J. M., Lee, K. S., Leung, A. N. C., Mayo, J. R., Mehta, A. C., Ohno, Y., Powell, C. A., Prokop, M., et al. (2017) · Radiology · doi:10.1148/radiol.2017161659 · Cited by 2,491

An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline: Treatment of Idiopathic Pulmonary Fibrosis: An Update of the 2011 Clinical Practice Guideline

Raghu, G., Rochwerg, B., Zhang, Y., Garcia, C. A. C., Azuma, A., Behr, J., Brozek, J. L., Collard, H. R., Cunningham, W., Homma, S., et al. (2015) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.201506-1063st · Cited by 1,916

Prednisone, Azathioprine, and N -Acetylcysteine for Pulmonary Fibrosis

The Idiopathic Pulmonary Fibrosis Clinical Research Network (2012) · New England Journal of Medicine · doi:10.1056/nejmoa1113354 · Cited by 1,654

Acute Exacerbation of Idiopathic Pulmonary Fibrosis. An International Working Group Report

Collard, H. R., Ryerson, C. J., Corte, T. J., Jenkins, G., Kondoh, Y., Lederer, D. J., Lee, J. S., Maher, T. M., Wells, A. U., Antoniou, K. M., et al. (2016) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.201604-0801ci · Cited by 1,444

Telomerase Mutations in Families with Idiopathic Pulmonary Fibrosis

Armanios, M. Y., Chen, J. J.-L., Cogan, J. D., Alder, J. K., Ingersoll, R. G., Markin, C., Lawson, W. E., Xie, M., Vulto, I., Phillips, J. A., et al. (2007) · New England Journal of Medicine · doi:10.1056/nejmoa066157 · Cited by 1,357

A consensus document for the selection of lung transplant candidates: 2014–an update from the Pulmonary Transplantation Council of the International Society for Heart and Lung Transplantation

Weill, D., Benden, C., Corris, P. A., Dark, J. H., Davis, R. D., Keshavjee, S., Lederer, D. J., Mulligan, M. J., Patterson, G. A., Singer, L. G., et al. (2015) · The Journal of Heart and Lung Transplantation · doi:10.1016/j.healun.2014.06.014 · Cited by 1,329

Guidelines of the Polish Respiratory Society for Diagnosis and Treatment of Idiopathic Pulmonary Fibrosis

Piotrowski, W. J., Bestry, I., Białas, A. J., Boros, P. W., Grzanka, P., Jassem, E., Jastrzębski, D., Klimczak, D., Langfort, R., Lewandowska, K. B., et al. (2020) · Advances in respiratory medicine · doi:10.5603/arm.2020.0081 · Cited by 30

Pulmonary Daoyin as a traditional Chinese medicine rehabilitation programme for patients with IPF : A randomized controlled trial

Zhou, M., Zhang, H., Li, F., Yu, Z., Yuan, C., Oliver, B. G. G., & Li, J. (2020) · Respirology · doi:10.1111/resp.13972 · Cited by 28

An 8-ferroptosis-related genes signature from Bronchoalveolar Lavage Fluid for prognosis in patients with idiopathic pulmonary fibrosis

He, Y., Shang, Y., Li, Y., Wang, M., Yu, D., Yang, Y., Ning, S., & Chen, H. (2022) · BMC Pulmonary Medicine · doi:10.1186/s12890-021-01799-7 · Cited by 28

p62-Nrf2 Regulatory Loop Mediates the Anti-Pulmonary Fibrosis Effect of Bergenin

Zeng, Q., Zhou, T., Zhao, F., Xiong, D., He, B., Hua, Q., Lin, M., Deng, L., Sang, X., Xie, W., et al. (2022) · Antioxidants · doi:10.3390/antiox11020307 · Cited by 29

Prognostic Role of NLR, PLR and MHR in Patients With Idiopathic Pulmonary Fibrosis

Chen, Y., Cai, J., Zhang, M., & Yan, X. (2022) · Frontiers in Immunology · doi:10.3389/fimmu.2022.882217 · Cited by 28

Enriched collagen solution as a pulp dressing in pulpotomized teeth in monkeys.

Fuks, A. B., Michaeli, Y., Sofer-Saks, B., & Shoshan, S. (1984) · PubMed · Cited by 28

Interstitial Lung Fibrosis Imaging Reporting and Data System: What Radiologist Wants to Know?

Razek, A. A. K. A., Khairy, M., & Alnaghy, E. (2020) · Journal of Computer Assisted Tomography · doi:10.1097/rct.0000000000001075 · Cited by 27

PGF2α signaling drives fibrotic remodeling and fibroblast population dynamics in mice

Rodríguez, L. R., Tang, S. Y., Barboza, W. R., Murthy, A., Tomer, Y., Cai, T., Iyer, S., Chavez, K., Das, U. S., Ghosh, S., et al. (2023) · JCI Insight · doi:10.1172/jci.insight.172977 · Cited by 28

Three dimensional fibrotic extracellular matrix directs microenvironment fiber remodeling by fibroblasts

Nizamoglu, M., Alleblas, F., Koster, T., Borghuis, T., Vonk, J. M., Thomas, M. J., White, E. S., Watson, C. K., Timens, W., Kasmi, K. C. E., et al. (2024) · Acta Biomaterialia · doi:10.1016/j.actbio.2024.02.008 · Cited by 33

Incidence, prevalence and mortality of idiopathic pulmonary fibrosis in England from 2008 to 2018: a cohort study

Gupta, R. S., Morgan, A. D., George, P. M., & Quint, J. K. (2024) · Thorax · doi:10.1136/thorax-2023-220887 · Cited by 28

Immune cells crosstalk Pathways, and metabolic alterations in Idiopathic pulmonary fibrosis

Tiwari, P., Verma, S., Washimkar, K. R., & Mugale, M. N. (2024) · International Immunopharmacology · doi:10.1016/j.intimp.2024.112269 · Cited by 29

Role of epigenetic mechanisms in the pathogenesis of chronic respiratory diseases and response to inhaled exposures: From basic concepts to clinical applications

Jurkowska, R. Z. (2024) · Pharmacology & Therapeutics · doi:10.1016/j.pharmthera.2024.108732 · Cited by 29

Cytological changes in radiation-induced lung injury

Wang, Y., Zhang, J., & Shao, C. (2024) · Life Sciences · doi:10.1016/j.lfs.2024.123188 · Cited by 27

A Unique Protein Self-Assembling Nanoparticle with Significant Advantages in Vaccine Development and Production

Carter, D. C., Wright, B., Jerome, W. G., Rose, J. P., & Wilson, E. J. (2020) · Journal of Nanomaterials · doi:10.1155/2020/4297937 · Cited by 27

Genetic Variation in CCL18 Gene Influences CCL18 Expression and Correlates with Survival in Idiopathic Pulmonary Fibrosis—Part B

Caliskan, C., Seeliger, B., Jäger, B., Fuge, J., Welte, T., Terwolbeck, O., Freise, J., van Moorsel, C. H. M., Zhang, Y., & Prasse, A. (2020) · Journal of Clinical Medicine · doi:10.3390/jcm9061993 · Cited by 28

IL10 trains macrophage profibrotic function after lung injury

Bhattacharyya, A., Boostanpour, K., Bouzidi, M. S., Magee, L., Chen, T. Y., Wolters, R. M., Torre, P., Pillai, S. K., & Bhattacharya, M. (2022) · American Journal of Physiology-Lung Cellular and Molecular Physiology · doi:10.1152/ajplung.00458.2021 · Cited by 28

Celastrol Targets Cullin-Associated and Neddylation-Dissociated 1 to Prevent Fibroblast–Myofibroblast Transformation against Pulmonary Fibrosis

Zhou, Y., Li, M., Shen, T., Yang, T., Shi, G., Wei, Y., Chen, C., Wang, D., Wang, Y., & Zhang, T. (2022) · ACS Chemical Biology · doi:10.1021/acschembio.2c00099 · Cited by 28

Plasticity towards Rigidity: A Macrophage Conundrum in Pulmonary Fibrosis

Sari, E., He, C., & Margaroli, C. (2022) · International Journal of Molecular Sciences · doi:10.3390/ijms231911443 · Cited by 28

The Emerging Role of Extracellular Vesicles from Mesenchymal Stem Cells and Macrophages in Pulmonary Fibrosis: Insights into miRNA Delivery

Li, S., Zhang, G., Feng, G., Jiang, L., Chen, Z., Xin, W., & Zhang, X. (2022) · Pharmaceuticals · doi:10.3390/ph15101276 · Cited by 27

Blockade of the pentraxin 3/CD44 interaction attenuates lung injury‐induced fibrosis

Chi, J.-Y., Hsiao, Y., Liang, H., Huang, T., Chen, F., Chen, C., Ko, C., Cheng, C., & Wang, J. (2022) · Clinical and Translational Medicine · doi:10.1002/ctm2.1099 · Cited by 27

Ophiocordyceps lanpingensis polysaccharides attenuate pulmonary fibrosis in mice

Zhou, S., Zhou, Y., Yu, J., Du, Y., Tan, Y., Ying-Mei, K. E., Wang, J., Han, B., & Ge, F. (2020) · Biomedicine & Pharmacotherapy · doi:10.1016/j.biopha.2020.110058 · Cited by 28

The molecular mechanisms of extracellular matrix-derived hydrogel therapy in idiopathic pulmonary fibrosis models

Evangelista-Leite, D., Carreira, A. C. O., Nishiyama, M. Y., Gilpin, S. E., & Miglino, M. A. (2023) · Biomaterials · doi:10.1016/j.biomaterials.2023.122338 · Cited by 27

TWEAK-Fn14 signaling protects mice from pulmonary fibrosis by inhibiting fibroblast activation and recruiting pro-regenerative macrophages

Li, L., Wu, P., Wei, Y., Lü, M., Ge, H., Wang, P., Sun, J., Horng, T., Liu, X., Shen, X., et al. (2025) · Cell Reports · doi:10.1016/j.celrep.2024.115220 · Cited by 32

Alveolar epithelial cell dysfunction and epithelial-mesenchymal transition in pulmonary fibrosis pathogenesis

Zheng, C., Zhang, L., Sun, Y., Ma, Y., & Zhang, Y. (2025) · Frontiers in Molecular Biosciences · doi:10.3389/fmolb.2025.1564176 · Cited by 29

Aberrant intermediate alveolar epithelial cells promote pathogenic activation of lung fibroblasts in preclinical fibrosis models

Hoffman, E. T., Shah, A., Barboza, W. R., Rodríguez, L. R., Dherwani, R., Dooley, P. E., Minakin, K., Tomer, Y., Ayers, L. J., Jones, D. L., et al. (2025) · Nature Communications · doi:10.1038/s41467-025-63735-1 · Cited by 32

Gene Expression Changes Associated with Nintedanib Treatment in Idiopathic Pulmonary Fibrosis Fibroblasts: A Next-Generation Sequencing and Bioinformatics Study

Sheu, C., Chang, W., Tsai, M., Liao, S., Chong, I., & Kuo, P. (2019) · Journal of Clinical Medicine · doi:10.3390/jcm8030308 · Cited by 26

Oral administration of curcumin ameliorates pulmonary fibrosis in mice through 15d-PGJ2-mediated induction of hepatocyte growth factor in the colon

Miao, Y., Zhang, Y., Qiao, S., Xia, Y., Wei, Z., & Dai, Y. (2020) · Acta Pharmacologica Sinica · doi:10.1038/s41401-020-0469-4 · Cited by 26

Aberrant B Cell Receptor Signaling in Naïve B Cells from Patients with Idiopathic Pulmonary Fibrosis

Neys, S. F. H., Heukels, P., van Hulst, J. A. C., Rip, J., Wijsenbeek, M. S., Hendriks, R. W., & Corneth, O. B. J. (2021) · Cells · doi:10.3390/cells10061321 · Cited by 28

Sensitization of the UPR by loss of PPP1R15A promotes fibrosis and senescence in IPF

Monkley, S. J., Overed-Sayer, C. L., Parfrey, H., Rassl, D. M., Crowther, D. C., Escudero‐Ibarz, L., Davis, N., Carruthers, A. M., Berks, R., Coetzee, M., et al. (2021) · Scientific Reports · doi:10.1038/s41598-021-00769-7 · Cited by 25

Evaluation of Regional Lung Function in Pulmonary Fibrosis with Xenon-129 MRI

Mata, J. F., Guan, S., Qing, K., Tustison, N. J., Shim, Y. M., Mugler, J. P., Altes, T. A., Huaromo, J., & Mehrad, B. (2021) · Tomography · doi:10.3390/tomography7030039 · Cited by 26

Management of Progressive Fibrosing Interstitial Lung Diseases (PF-ILD)

Copeland, C. R., & LANCASTER, L. H. (2021) · Frontiers in Medicine · doi:10.3389/fmed.2021.743977 · Cited by 28

Mesenchymal stromal cells attenuate alveolar type 2 cells senescence through regulating NAMPT-mediated NAD metabolism

Lai, X., Huang, S., Lin, S., Pu, L., Wang, Y., Lin, Y., Huang, W., & Wang, Z. (2022) · Stem Cell Research & Therapy · doi:10.1186/s13287-021-02688-w · Cited by 26

Pulmonary Protein Oxidation and Oxidative Stress Modulation by Lemna minor L. in Progressive Bleomycin-Induced Idiopathic Pulmonary Fibrosis

Karamalakova, Y. D., Stefanov, I., Georgieva, E., & Nikolova, G. (2022) · Antioxidants · doi:10.3390/antiox11030523 · Cited by 28

Chronic Expression of a Clinical SFTPC Mutation Causes Murine Lung Fibrosis with Idiopathic Pulmonary Fibrosis Features

Rodríguez, L. R., Tomer, Y., Carson, P., Dimopoulos, T. T., Zhao, M., Chavez, K., Iyer, S., Huang, L., Ebert, C., Sereda, L., et al. (2022) · American Journal of Respiratory Cell and Molecular Biology · doi:10.1165/rcmb.2022-0203ma · Cited by 26

Lifestyle, Genetic Susceptibility, and the Risk of Idiopathic Pulmonary Fibrosis

Ma, Y., Cui, F., Li, D., Wang, J., Tang, L., Xie, J., Hu, Y., & Tian, Y. (2023) · CHEST Journal · doi:10.1016/j.chest.2023.04.008 · Cited by 26

Bleomycin Induces Drug Efflux in Lungs. A Pitfall for Pharmacological Studies of Pulmonary Fibrosis

Park, J. K., Coffey, N. J., Bodine, S. P., Zawatsky, C. N., Jay, L., Gahl, W. A., Kunos, G., Gochuico, B. R., Malicdan, M. C. V., & Çınar, R. (2019) · American Journal of Respiratory Cell and Molecular Biology · doi:10.1165/rcmb.2018-0147oc · Cited by 26

Real-world experiences: Efficacy and tolerability of pirfenidone in clinical practice

Fang, C., Huang, H. F., Guo, J., Ferianc, M., & Xu, Z. (2020) · PLoS ONE · doi:10.1371/journal.pone.0228390 · Cited by 27

Lung Transplantation

Ahya, V. N., & Diamond, J. M. (2019) · Medical Clinics of North America · doi:10.1016/j.mcna.2018.12.003 · Cited by 26

A comprehensive review of Siraitia grosvenorii (Swingle) C. Jeffrey: chemical composition, pharmacology, toxicology, status of resources development, and applications

Huang, H., Peng, Z., Zhan, S., Li, W., Liu, D., Huang, S., Zhu, Y., & Wang, W. (2024) · Frontiers in Pharmacology · doi:10.3389/fphar.2024.1388747 · Cited by 25

TGFβ1-RCN3-TGFBR1 loop facilitates pulmonary fibrosis by orchestrating fibroblast activation

Wu, M., Wang, Z., Shi, X., Zan, D., Chen, H., Yang, S., Ding, F., Liu, Y., Tan, P., Ma, R. Z., et al. (2023) · Respiratory Research · doi:10.1186/s12931-023-02533-z · Cited by 25

Integrating network pharmacology, experimental validation and molecular docking to reveal the alleviation of Yinhuang granule on idiopathic pulmonary fibrosis

Wu, Z., Shi, R., Yan, S., Zhang, S., Lü, B., Huang, Z., & Ji, L. (2024) · Phytomedicine · doi:10.1016/j.phymed.2024.155368 · Cited by 25

Multiomic analysis of monocyte-derived alveolar macrophages in idiopathic pulmonary fibrosis

Zhang, M., Zhang, J., Hu, H., Zhou, Y., Lin, Z., Jing, H., & Sun, B. (2024) · Journal of Translational Medicine · doi:10.1186/s12967-024-05398-y · Cited by 30

Single-Cell RNA Sequencing Reveals Monocyte-Derived Interstitial Macrophages with a Pro-Fibrotic Phenotype in Bleomycin-Induced Pulmonary Fibrosis

Wang, S. F., Li, J., Wu, C., Lei, Z., Wang, T., Huang, X., Zhang, S., Liu, Y., Bi, X., Zheng, F., et al. (2024) · International Journal of Molecular Sciences · doi:10.3390/ijms252111669 · Cited by 25

The Anti-Fibrotic Effects of CG-745, an HDAC Inhibitor, in Bleomycin and PHMG-Induced Mouse Models

Kim, Y.-S., Cha, H., Kim, H.-J., Cho, J.-M., & Kim, H.-R. (2019) · Molecules · doi:10.3390/molecules24152792 · Cited by 25

High-Resolution CT Change over Time in Patients with Idiopathic Pulmonary Fibrosis on Antifibrotic Treatment

Balestro, E., Cocconcelli, E., Giraudo, C., Polverosi, R., Biondini, D., Lacedonia, D., Bazzan, E., Mazzai, L., Rizzon, G., Lococo, S., et al. (2019) · Journal of Clinical Medicine · doi:10.3390/jcm8091469 · Cited by 25

Astragalus polysaccharides attenuate pulmonary�fibrosis by inhibiting the epithelial-mesenchymal�transition and NF-κB pathway activation

Zhang, R., Xu, L., An, X., Sui, X., & Lin, S. (2020) · International Journal of Molecular Medicine · doi:10.3892/ijmm.2020.4574 · Cited by 27

Appendicular Skeletal Muscle Mass Correlates with Patient-Reported Outcomes and Physical Performance in Patients with Idiopathic Pulmonary Fibrosis

Ebihara, K., Iwanami, Y., Yamasaki, K., あやめ, 竹., Sato, N., Usui, Y., Nakamura, Y., Kishi, K., Homma, S. A., & Ebihara, S. (2021) · The Tohoku Journal of Experimental Medicine · doi:10.1620/tjem.253.61 · Cited by 25

Fatty acid nitroalkene reversal of established lung fibrosis

Koudelka, A., Cechova, V., Rojas, M. M., Mitash, N., Bondonese, A., Croix, C. M. S., Ross, M. A., & Freeman, B. Α. (2021) · Redox Biology · doi:10.1016/j.redox.2021.102226 · Cited by 28

Protective effect of dapsone against bleomycin-induced lung fibrosis in rat

Yousefi‐Manesh, H., Noori, T., Asgardoon, M. H., Derakhshan, M. H., Tavangar, S. M., Sheibani, M., Shirooie, S., & Dehpour, A. R. (2021) · Experimental and Molecular Pathology · doi:10.1016/j.yexmp.2021.104737 · Cited by 27

Autologous Skin Fibroblast‐Based PLGA Nanoparticles for Treating Multiorgan Fibrosis

Long, Q., Liu, Z., Shao, Q., Shi, H., Huang, S., Jiang, C., Qian, B., Zhong, Y., He, X., Xiang, X., et al. (2022) · Advanced Science · doi:10.1002/advs.202200856 · Cited by 29

Discovery of Aryloxyphenyl–Heptapeptide Hybrids as Potent and Selective Matrix Metalloproteinase-2 Inhibitors for the Treatment of Idiopathic Pulmonary Fibrosis

Takeuchi, T., Hayashi, M., Tamita, T., Nomura, Y., Kojima, N., Mitani, A., Takeda, T., Hitaka, K., Kato, Y., Kamitani, M., et al. (2022) · Journal of Medicinal Chemistry · doi:10.1021/acs.jmedchem.2c00613 · Cited by 26

Quantitative Interstitial Abnormality Progression and Outcomes in the Genetic Epidemiology of COPD and Pittsburgh Lung Screening Study Cohorts

Choi, B., Adan, N. M., Doyle, T. J., Estépar, R. S. J., Harmouche, R., Humphries, S. M., Moll, M. R., Cho, M. H., Putman, R. K., Hunninghake, G. M., et al. (2022) · CHEST Journal · doi:10.1016/j.chest.2022.06.030 · Cited by 25

Urine-derived exosomes from individuals with IPF carry pro-fibrotic cargo

Elliot, S. J., Catanuto, P., Pereira‐Simon, S., Xia, X., Shahzeidi, S., Roberts, E. R., Ludlow, J. W., Hamdan, S., Daunert, S., Parra, J., et al. (2022) · eLife · doi:10.7554/elife.79543 · Cited by 26

Myofibroblast-specific inhibition of the Rho kinase-MRTF-SRF pathway using nanotechnology for the prevention of pulmonary fibrosis

Knipe, R. S., Nurunnabi, M., Probst, C. K., Spinney, J. J., Abe, E. A., Bose, R. J., Ha, K., Logue, A., Nguyen, T. H., Servis, R. L., et al. (2023) · American Journal of Physiology-Lung Cellular and Molecular Physiology · doi:10.1152/ajplung.00086.2022 · Cited by 29

Interstitial Macrophages Lead Early Stages of Bleomycin-Induced Lung Fibrosis and Induce Fibroblasts Activation

Libório‐Ramos, S., Barbosa-Matos, C., Fernandes, R., Borges-Pereira, C., & Costa, S. (2023) · Cells · doi:10.3390/cells12030402 · Cited by 28

Biomimetic lipid Nanocomplexes incorporating STAT3-inhibiting peptides effectively infiltrate the lung barrier and ameliorate pulmonary fibrosis

Keum, H., Kim, J., Yoo, D., Kim, T. W., Seo, C., Kim, D., & Jon, S. (2021) · Journal of Controlled Release · doi:10.1016/j.jconrel.2021.02.022 · Cited by 27

Thromboxane–Prostanoid Receptor Signaling Drives Persistent Fibroblast Activation in Pulmonary Fibrosis

Suzuki, T., Kropski, J. A., Chen, J., Carrier, E. J., Chen, X., Sherrill, T. P., Winters, N. I., Camarata, J. E., Polosukhin, V. V., Han, W., et al. (2022) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.202106-1503oc · Cited by 24

Rev-erbα agonists suppresses TGFβ1-induced fibroblast-to-myofibroblast transition and pro-fibrotic phenotype in human lung fibroblasts

Prasad, C., Hahn, K., Duraisamy, S. K., Salathe, M. A., Huang, S. K., Burris, T. P., & Sundar, I. K. (2023) · Biochemical and Biophysical Research Communications · doi:10.1016/j.bbrc.2023.05.092 · Cited by 23

Meta-Analysis of Interobserver Agreement in Assessment of Interstitial Lung Disease Using High-Resolution CT

Delaney, L., Alabed, S., Maiter, A., Salehi, M., Goodlad, M., Shah, H. Y., Checkley, E. W., Matthews, S., Kamil, M., Evans, O., et al. (2024) · Radiology · doi:10.1148/radiol.240016 · Cited by 26

Predicting the risk of subsequent progression in patients with systemic sclerosis-associated interstitial lung disease with progression: a multicentre observational cohort study

Hoffmann‐Vold, A., Petelytska, L., Fretheim, H., Aaløkken, T. M., Becker, M. O., Bjørkekjær, H. J., Brunborg, C., Bruni, C., Clarenbach, C. F., Diep, P. P., et al. (2025) · The Lancet Rheumatology · doi:10.1016/s2665-9913(25)00026-8 · Cited by 29

Megakaryocytes participate in the occurrence of bleomycin-induced pulmonary fibrosis

Zhou, Y., Zhang, B., Li, C., Huang, X., Cheng, H., Bao, X., Zhao, F., Cheng, Q., Yue, S., Han, J., et al. (2019) · Cell Death and Disease · doi:10.1038/s41419-019-1903-8 · Cited by 24

Assessment of viral RNA in idiopathic pulmonary fibrosis using RNA-seq

Yin, Q., Strong, M. J., Zhuang, Y., Flemington, E. K., Kaminski, N., de Andrade, J. A., & Lasky, J. A. (2020) · BMC Pulmonary Medicine · doi:10.1186/s12890-020-1114-1 · Cited by 24

Interstitial Lung Disease in Patients With Systemic Sclerosis: Toward Personalized-Medicine-Based Prediction and Drug Screening Models of Systemic Sclerosis-Related Interstitial Lung Disease (SSc-ILD)

Khedoe, P. P. S. J., Marges, E. R., Hiemstra, P. S., Ninaber, M. K., & Geelhoed, M. (2020) · Frontiers in Immunology · doi:10.3389/fimmu.2020.01990 · Cited by 24

Safety and tolerability of combination therapy with pirfenidone and nintedanib for idiopathic pulmonary fibrosis: A multicenter retrospective observational study in Japan

Hisata, S., Bando, M., Homma, S. A., Kataoka, K., Ogura, T., Izumi, S., Sakamoto, S., Watanabe, K., Saito, Y., Shimizu, Y., et al. (2021) · Respiratory Investigation · doi:10.1016/j.resinv.2021.04.005 · Cited by 25

Dynamic contrast enhanced MRI for the evaluation of lung perfusion in idiopathic pulmonary fibrosis

Torres, L. A., Lee, K. E., Barton, G. P., Hahn, A. D., Sandbo, N. K., Schiebler, M. L., & Fain, S. B. (2022) · European Respiratory Journal · doi:10.1183/13993003.02058-2021 · Cited by 24

C/EBP homologous protein promotes Sonic Hedgehog secretion from type II alveolar epithelial cells and activates Hedgehog signaling pathway of fibroblast in pulmonary fibrosis

Yang, X., Sun, W., Jing, X., Zhang, Q., Huang, H. F., & Xu, Z. (2022) · Respiratory Research · doi:10.1186/s12931-022-02012-x · Cited by 24

Analysis of necroptosis-related prognostic genes and immune infiltration in idiopathic pulmonary fibrosis

Chen, H., Xia, Z., Qing, B., Wang, W., Gu, L., Chen, Y., Wang, J., & Yuan, Y. (2023) · Frontiers in Immunology · doi:10.3389/fimmu.2023.1119139 · Cited by 27

Assessing the genetic relationship between gastroesophageal reflux disease and chronic respiratory diseases: a mendelian randomization study

Cheng, X., Shi, J., Zhang, D., Li, C., Xu, H., He, J., & Liang, W. (2023) · BMC Pulmonary Medicine · doi:10.1186/s12890-023-02502-8 · Cited by 28

Proinflammatory chemokine CXCL14 activates MAS-related G protein-coupled receptor MRGPRX2 and its putative mouse ortholog MRGPRB2

Hamwi, G. A., Namasivayam, V., Bueschbell, B., Gedschold, R., Gölz, S., & Müller, C. E. (2024) · Communications Biology · doi:10.1038/s42003-023-05739-5 · Cited by 24

MUC4 is overexpressed in idiopathic pulmonary fibrosis and collaborates with transforming growth factor β inducing fibrotic responses

Milara, J., Ballester, B., Safont, M. J., Artigues, E., Escrivá, J., Morcillo, E. J., & Cortijo, J. (2020) · Mucosal Immunology · doi:10.1038/s41385-020-00343-w · Cited by 22

Preparation, optimization, and in vivo evaluation of an inhaled solution of total saponins of Panax notoginseng and its protective effect against idiopathic pulmonary fibrosis

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