Idiopathic Pulmonary Fibrosis

An Official ATS/ERS/JRS/ALAT Statement: Idiopathic Pulmonary Fibrosis: Evidence-based Guidelines for Diagnosis and Management

Raghu, G., Collard, H. R., Egan, J. J., Martinez, F. J., Behr, J., Brown, K. K., Colby, T. V., Cordier, J.-F., Flaherty, K. R., Lasky, J. A., et al. (2011) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.2009-040gl · Cited by 7,186

Efficacy and Safety of Nintedanib in Idiopathic Pulmonary Fibrosis

Richeldi, L., du Bois, R. M., Raghu, G., Azuma, A., Brown, K. K., Costabel, U., Cottin, V., Flaherty, K. R., Hansell, D. M., Inoue, Y., et al. (2014) · New England Journal of Medicine · doi:10.1056/nejmoa1402584 · Cited by 4,654

A phase 3 trial of pirfenidone in patients with idiopathic pulmonary fibrosis.

King, T. E., Bradford, W. Z., Castro-Bernardini, S., Fagan, E. A., Glaspole, I., Glassberg, M. K., Gorina, E., Hopkins, P. M., Kardatzke, D., Lancaster, L., et al. (2014) · New England Journal of Medicine · doi:10.1056/nejmoa1402582 · Cited by 3,975

Screening for Lung Cancer: U.S. Preventive Services Task Force Recommendation Statement

Moyer, V. A., & on behalf of the U.S. Preventive Services Task Force* (2013) · Annals of Internal Medicine · doi:10.7326/m13-2771 · Cited by 2,642

Guidelines for Management of Incidental Pulmonary Nodules Detected on CT Images: From the Fleischner Society 2017.

MacMahon, H., Naidich, D. P., Goo, J. M., Lee, K. S., Leung, A. N. C., Mayo, J. R., Mehta, A. C., Ohno, Y., Powell, C. A., Prokop, M., et al. (2017) · Radiology · doi:10.1148/radiol.2017161659 · Cited by 2,491

An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline: Treatment of Idiopathic Pulmonary Fibrosis: An Update of the 2011 Clinical Practice Guideline

Raghu, G., Rochwerg, B., Zhang, Y., Garcia, C. A. C., Azuma, A., Behr, J., Brozek, J. L., Collard, H. R., Cunningham, W., Homma, S., et al. (2015) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.201506-1063st · Cited by 1,916

Prednisone, Azathioprine, and N -Acetylcysteine for Pulmonary Fibrosis

The Idiopathic Pulmonary Fibrosis Clinical Research Network (2012) · New England Journal of Medicine · doi:10.1056/nejmoa1113354 · Cited by 1,654

Acute Exacerbation of Idiopathic Pulmonary Fibrosis. An International Working Group Report

Collard, H. R., Ryerson, C. J., Corte, T. J., Jenkins, G., Kondoh, Y., Lederer, D. J., Lee, J. S., Maher, T. M., Wells, A. U., Antoniou, K. M., et al. (2016) · American Journal of Respiratory and Critical Care Medicine · doi:10.1164/rccm.201604-0801ci · Cited by 1,444

Telomerase Mutations in Families with Idiopathic Pulmonary Fibrosis

Armanios, M. Y., Chen, J. J.-L., Cogan, J. D., Alder, J. K., Ingersoll, R. G., Markin, C., Lawson, W. E., Xie, M., Vulto, I., Phillips, J. A., et al. (2007) · New England Journal of Medicine · doi:10.1056/nejmoa066157 · Cited by 1,357

A consensus document for the selection of lung transplant candidates: 2014–an update from the Pulmonary Transplantation Council of the International Society for Heart and Lung Transplantation

Weill, D., Benden, C., Corris, P. A., Dark, J. H., Davis, R. D., Keshavjee, S., Lederer, D. J., Mulligan, M. J., Patterson, G. A., Singer, L. G., et al. (2015) · The Journal of Heart and Lung Transplantation · doi:10.1016/j.healun.2014.06.014 · Cited by 1,329

Endocannabinoid signalling/cannabinoid receptor 2 is involved in icariin-mediated protective effects against bleomycin-induced pulmonary fibrosis

Du, W., Zhang, T., Yang, F., Gul, A., Tang, Z., Zhang, H., Jiang, S., Wang, S., & Dong, J. (2022) · Phytomedicine · doi:10.1016/j.phymed.2022.154187 · Cited by 18

Novel mediators of idiopathic pulmonary fibrosis

Saito, S., Deskin, B., Rehan, M., Yadav, S., Matsunaga, Y., Lasky, J. A., & Thannickal, V. J. (2022) · Clinical Science · doi:10.1042/cs20210878 · Cited by 19

Fenbendazole Attenuates Bleomycin-Induced Pulmonary Fibrosis in Mice via Suppression of Fibroblast-to-Myofibroblast Differentiation

Wang, L., Xu, K., Wang, N., Ding, L., Zhao, W., Wan, R., Zhao, W., Guo, X., Pan, X., Yang, J., et al. (2022) · International Journal of Molecular Sciences · doi:10.3390/ijms232214088 · Cited by 18

Disparities in Antifibrotic Medication Utilization Among Veterans With Idiopathic Pulmonary Fibrosis

Kaul, B., Lee, J. S., Petersen, L. A., McCulloch, C. E., Rosas, I. O., Bandi, V., Zhang, N., DeDent, A. M., Collard, H. R., & Whooley, M. A. (2023) · CHEST Journal · doi:10.1016/j.chest.2023.02.027 · Cited by 18

TrxR/Trx inhibitor butaselen ameliorates pulmonary fibrosis by suppressing NF-κB/TGF-β1/Smads signaling

Chen, Y., Yin, H., Sun, J., Zhang, G., Zhang, Y., & Zeng, H. (2023) · Biomedicine & Pharmacotherapy · doi:10.1016/j.biopha.2023.115822 · Cited by 18

The usual Interstitial pneumonia pattern in autoimmune rheumatic diseases

Luppi, F., Manfredi, A., Faverio, P., Andersen, M. B., Bono, F., Pagni, F., Salvarani, C., Bendstrup, E. M., & Sebastiani, M. (2023) · BMC Pulmonary Medicine · doi:10.1186/s12890-023-02783-z · Cited by 18

A WNT mimetic with broad spectrum FZD-specificity decreases fibrosis and improves function in a pulmonary damage model

Patel, M., Post, Y., Hill, N., Sura, A., Ye, J., Fisher, T., Suen, N., Zhang, M., Cheng, L., Pribluda, A., et al. (2024) · Respiratory Research · doi:10.1186/s12931-024-02786-2 · Cited by 18

IL20Rb aggravates pulmonary fibrosis through enhancing bone marrow derived profibrotic macrophage activation

Zhu, J., Jiang, Q., Gao, S., Xia, Q., Zhang, H., Liu, B., Zhao, R., Jiang, H., Li, X., Xu, A., et al. (2024) · Pharmacological Research · doi:10.1016/j.phrs.2024.107178 · Cited by 18

Exploring ABHD5 as a Lipid-Related Biomarker in Idiopathic Pulmonary Fibrosis: Integrating Machine Learning, Bioinformatics, and In Vitro Experiments

Liao, Y., Peng, X., Yang, Y., Zhou, G., Chen, L., Yang, Y., Li, H., Chen, X., Guo, S., Zuo, Q., et al. (2024) · Inflammation · doi:10.1007/s10753-024-02107-1 · Cited by 18

IL-25/IL-33/TSLP contributes to idiopathic pulmonary fibrosis: Do alveolar epithelial cells and (myo)fibroblasts matter?

Xu, X., Zhang, J., & Dai, H. (2020) · Experimental Biology and Medicine · doi:10.1177/1535370220915428 · Cited by 19

A multicentre retrospective observational study on Polish experience of pirfenidone therapy in patients with idiopathic pulmonary fibrosis: the PolExPIR study

Majewski, S., Białas, A. J., Buchczyk, M., Gomółka, P., Górska, K., Jagielska-Len, H., Jarzemska, A., Jassem, E., Jastrzębski, D., Kania, A., et al. (2020) · BMC Pulmonary Medicine · doi:10.1186/s12890-020-1162-6 · Cited by 19

Periostin secreted by activated fibroblasts in idiopathic pulmonary fibrosis promotes tumorigenesis of non-small cell lung cancer

Yamato, H., Kimura, K., Fukui, E., Kanou, T., Ose, N., Funaki, S., Minami, M., & Shintani, Y. (2021) · Scientific Reports · doi:10.1038/s41598-021-00717-5 · Cited by 18

Network Pharmacology and Experimental Assessment to Explore the Pharmacological Mechanism of Qimai Feiluoping Decoction Against Pulmonary Fibrosis

Yang, Y., Ding, L., Bao, T., Li, Y., Ma, J., Li, Q., Gao, Z., Song, S., Wang, J., Zhao, J., et al. (2021) · Frontiers in Pharmacology · doi:10.3389/fphar.2021.770197 · Cited by 18

Non-linear archetypal analysis of single-cell RNA-seq data by deep autoencoders

Wang, Y., & Zhao, H. (2022) · PLoS Computational Biology · doi:10.1371/journal.pcbi.1010025 · Cited by 17

Derivation and Validation of a Diagnostic Prediction Tool for Interstitial Lung Disease

Pugashetti, J. V., Kitich, A., Alqalyoobi, S., Maynard-Paquette, A.-C., Pritchard, D., Graham, J., Boctor, N., Kulinich, A. G., LaFond, E., Foster, E. E., et al. (2020) · CHEST Journal · doi:10.1016/j.chest.2020.02.044 · Cited by 17

The Future of Clinical Trials in Idiopathic Pulmonary Fibrosis

Podolanczuk, A. J., Richeldi, L., & Martínez, F. J. (2023) · JAMA · doi:10.1001/jama.2022.23955 · Cited by 17

The future of clinical trials in idiopathic pulmonary fibrosis

Spagnolo, P., & Maher, T. M. (2024) · Current Opinion in Pulmonary Medicine · doi:10.1097/mcp.0000000000001099 · Cited by 18

Bexotegrast Shows Dose-Dependent Integrin αvβ6 Receptor Occupancy in Lungs of Participants with Idiopathic Pulmonary Fibrosis: A Phase 2, Open-Label Clinical Trial

Mooney, J. J., Jacobs, S. S., Lefebvre, E. A., Cosgrove, G. P., Clark, A., Turner, S., Decaris, M. L., Barnes, C. N., Jurek, M., Williams, B., et al. (2024) · Annals of the American Thoracic Society · doi:10.1513/annalsats.202409-969oc · Cited by 18

Research Progress of Fibroblasts in Human Diseases

Li, X., Li, N., Wang, Y., Han, Q., & Sun, B. (2024) · Biomolecules · doi:10.3390/biom14111478 · Cited by 20

PPARG/SPP1/CD44 signaling pathway in alveolar macrophages: Mechanisms of lipid dysregulation and therapeutic targets in idiopathic pulmonary fibrosis

Li, G., Zhang, Y., Jiang, H., Wu, X., Hao, Y., Su, Y., Zou, Y., Xian, W., Wang, F., & Du, Q. (2025) · Heliyon · doi:10.1016/j.heliyon.2025.e41628 · Cited by 17

Rare variants and survival of patients with idiopathic pulmonary fibrosis: analysis of a multicentre, observational cohort study with independent validation

Alonso-González, A., Jáspez, D., Lorenzo-Salazar, J. M., Ma, S., Strickland, E., Mychaleckyj, J. C., Kim, J. S., Huang, Y., Adegunsoye, A., Oldham, J. M., et al. (2025) · The Lancet Respiratory Medicine · doi:10.1016/s2213-2600(25)00045-1 · Cited by 21

GPRC5A reduction contributes to pollutant benzo[a]pyrene injury via aggravating murine fibrosis, leading to poor prognosis of IIP patients

Huang, Z., Wang, S., Liu, Y., Fan, L., Zeng, Y., Han, H., Zhang, H., Yu, X., Zhang, Y., Huang, D., et al. (2020) · The Science of The Total Environment · doi:10.1016/j.scitotenv.2020.139923 · Cited by 17

Factor analysis identifies three separate symptom clusters in idiopathic pulmonary fibrosis

Seppälä, S., Rajala, K., Lehto, J. T., Sutinen, E., Mäkitalo, L., Kautiainen, H., Kankaanranta, H., Ainola, M., Saarto, T., & Myllärniemi, M. (2020) · ERJ Open Research · doi:10.1183/23120541.00347-2020 · Cited by 19

Silencing Heat Shock Protein 47 (HSP47) in Fibrogenic Precision-Cut Lung Slices: A Surprising Lack of Effects on Fibrogenesis?

Ruigrok, M. J. R., Amasi, K. E., Leeming, D. J., Sand, J. M. B., Frijlink, H. W., Hinrichs, W. L. J., & Olinga, P. (2021) · Frontiers in Medicine · doi:10.3389/fmed.2021.607962 · Cited by 17

Sine oculis homeobox homolog 1 plays a critical role in pulmonary fibrosis

Wilson, C., Mertens, T. C. J., Shivshankar, P., Bi, W., Collum, S. D., Wareing, N. E., Ko, J., Weng, T., Naikawadi, R. P., Wolters, P. J., et al. (2022) · JCI Insight · doi:10.1172/jci.insight.142984 · Cited by 18

Extrapulmonary manifestations of a telomere syndrome in patients with idiopathic pulmonary fibrosis are associated with decreased survival

Hoffman, T. W., van der Vis, J. J., Biesma, D. H., Grutters, J. C., & van Moorsel, C. H. M. (2022) · Respirology · doi:10.1111/resp.14264 · Cited by 17

Screening for Inhibitors of YAP Nuclear Localization Identifies Aurora Kinase A as a Modulator of Lung Fibrosis

Yang, Y., dos Santos, D. M., Pantano, L., Knipe, R. S., Abe, E. A., Logue, A., Pronzati, G., Black, K. E., Spinney, J. J., Giacona, F. L., et al. (2022) · American Journal of Respiratory Cell and Molecular Biology · doi:10.1165/rcmb.2021-0428oc · Cited by 20

S-Glutathionylation-Controlled Apoptosis of Lung Epithelial Cells; Potential Implications for Lung Fibrosis

Corteselli, E., Aboushousha, R., & Janssen-Heininger, Y. M. W. (2022) · Antioxidants · doi:10.3390/antiox11091789 · Cited by 17

Idiopathic Pulmonary Fibrosis and Telomeres

Mulet, A., & Signes‐Costa, J. (2022) · Journal of Clinical Medicine · doi:10.3390/jcm11236893 · Cited by 20

Silencing FHL2 inhibits bleomycin-induced pulmonary fibrosis through the TGF-β1/Smad signaling pathway

Shi, M., Cui, H., Shi, J., & Mei, Y. (2023) · Experimental Cell Research · doi:10.1016/j.yexcr.2023.113470 · Cited by 17

Imaging of Pulmonary Fibrosis: An Update, From the AJR Special Series on Imaging of Fibrosis

Lee, K. S., Han, J., Wada, N., Hata, A., Lee, H. Y., Yi, C.-A., Hino, T., Doyle, T. J., Franquet, T., & Hatabu, H. (2023) · American Journal of Roentgenology · doi:10.2214/ajr.23.29119 · Cited by 17

Idiopathic pulmonary fibrosis therapy development: a clinical pharmacology perspective

Tu, H., Han, L. W., Hsu, J. C., Kamath, N., & Pan, L. (2023) · Therapeutic Advances in Respiratory Disease · doi:10.1177/17534666231181537 · Cited by 16

Asarinin attenuates bleomycin-induced pulmonary fibrosis by activating PPARγ

Zeng, Q., Zhou, T., Huang, W., Huang, X., Huang, L., Zhang, X., Sang, X., Luo, Y.-Y., Tian, Y., Wu, B., et al. (2023) · Scientific Reports · doi:10.1038/s41598-023-41933-5 · Cited by 18

Overexpression of KLF4 Suppresses Pulmonary Fibrosis through the HIF-1α/Endoplasmic Reticulum Stress Signaling Pathway

Wei, S., Qi, F., Wu, Y., & Liu, X. (2023) · International Journal of Molecular Sciences · doi:10.3390/ijms241814008 · Cited by 18

The Role of Lung Microbiome in Fibrotic Interstitial Lung Disease—A Systematic Review

Puiu, R., Motoc, N. Ş., Lucaciu, S.-R., Ruta, M. V., Râjnoveanu, R., Todea, D. A., & Man, M. A. (2024) · Biomolecules · doi:10.3390/biom14030247 · Cited by 18

A real-world study of antifibrotic drugs-related adverse events based on the United States food and drug administration adverse event reporting system and VigiAccess databases

He, M., Zhou, J., Yang, T., Li, X., & Wang, R. (2024) · Frontiers in Pharmacology · doi:10.3389/fphar.2024.1310286 · Cited by 17

Mesenchymal stromal cell-based therapy in lung diseases; from research to clinic

Yuan, D. (2024) · American Journal of Stem Cells · doi:10.62347/jawm2040 · Cited by 17

Drug discovery and development in idiopathic pulmonary fibrosis: the changing landscape

Cruwys, S., Hein, P., Humphries, B., & Black, D. (2024) · Drug Discovery Today · doi:10.1016/j.drudis.2024.104207 · Cited by 18

Endogenous Long Pentraxin 3 Exerts a Protective Role in a Murine Model of Pulmonary Fibrosis

Maccarinelli, F., Bugatti, M., Schuind, A. C., Ganzerla, S., Vermi, W., Presta, M., & Ronca, R. (2021) · Frontiers in Immunology · doi:10.3389/fimmu.2021.617671 · Cited by 16

Mortality Associated with Idiopathic Pulmonary Fibrosis in Northeastern Italy, 2008–2020: A Multiple Cause of Death Analysis

Marcon, A., Schievano, E., & Fedeli, U. (2021) · International Journal of Environmental Research and Public Health · doi:10.3390/ijerph18147249 · Cited by 17

Interstitial lung abnormalities – current knowledge and future directions

Axelsson, G. T., & Guðmundsson, G. (2021) · European Clinical Respiratory Journal · doi:10.1080/20018525.2021.1994178 · Cited by 17

Use of peripheral neutrophil to lymphocyte ratio and peripheral monocyte levels to predict survival in fibrotic hypersensitivity pneumonitis (fHP): a multicentre retrospective cohort study

Barratt, S. L., Creamer, A. W., Adamali, H. I., Duckworth, A., Fallon, J., Fidan, S., Nancarrow, T., Wollerton, R. L., Steward, M., Gooptu, B., et al. (2021) · BMJ Open Respiratory Research · doi:10.1136/bmjresp-2021-001063 · Cited by 17

CCAAT/enhancer-binding protein (C/EBP) homologous protein promotes alveolar epithelial cell senescence via the nuclear factor-kappa B pathway in pulmonary fibrosis

Jing, X., Sun, W., Yang, X., Huang, H. F., Wang, P., Luo, Q., Xia, S., Fang, C., Zhang, Q., Guo, J., et al. (2021) · The International Journal of Biochemistry & Cell Biology · doi:10.1016/j.biocel.2021.106142 · Cited by 17

CDKN2B antisense RNA 1 expression alleviates idiopathic pulmonary fibrosis by functioning as a competing endogenouse RNA through the miR-199a-5p/Sestrin-2 axis

Yang, M. X., Yin, E. G., Xu, Y., Liu, Y.-J., Li, T., Dong, Z., & Tai, W. (2022) · Bioengineered · doi:10.1080/21655979.2022.2044252 · Cited by 17

Ginkgolic acid improves bleomycin‐induced pulmonary fibrosis by inhibiting SMAD4 SUMOylation

Yu, L., Bian, X., Zhang, C., Wu, Z., Huang, N., Yang, J., Jin, W., Feng, Z., Li, D., Huo, X., et al. (2022) · Oxidative Medicine and Cellular Longevity · doi:10.1155/2022/8002566 · Cited by 17

Human pluripotent stem cell-derived macrophages and macrophage-derived exosomes: therapeutic potential in pulmonary fibrosis

Rasaei, R., Tyagi, A., Rasaei, S., Lee, S., Yang, S., Kim, K.-S., Ramakrishna, S., & Hong, S. (2022) · Stem Cell Research & Therapy · doi:10.1186/s13287-022-03136-z · Cited by 18

Calpain-1 Up-Regulation Promotes Bleomycin-Induced Pulmonary Fibrosis by Activating Ferroptosis

wei, S., Liu, Y., Ran, C., Li, Y., Tang, B., Lu, M., & Wang, H. (2024) · American Journal Of Pathology · doi:10.1016/j.ajpath.2024.09.004 · Cited by 17

Single-cell transcriptome analysis revealing mechanotransduction via the Hippo/YAP pathway in promoting fibroblast-to-myofibroblast transition and idiopathic pulmonary fibrosis development

Lu, J., Wang, Z., & Zhang, L. (2025) · Gene · doi:10.1016/j.gene.2025.149271 · Cited by 16

Air pollution and alveolar health

Sofia, C., Parkin, J., Bell, J. A., Dean, L. S. N., Edgeway, L. J., Sayer, L. N., Easton, N. H. C., Davies, D. E., Marshall, B. G., Holgate, S. T., et al. (2025) · European Respiratory Review · doi:10.1183/16000617.0280-2024 · Cited by 20

Hermansky-Pudlak syndrome-2 alters mitochondrial homeostasis in the alveolar epithelium of the lung

Cuevas-Mora, K., Roque, W., Shaghaghi, H., Gochuico, B. R., Rosas, I. O., Summer, R. S., & Romero, F. (2021) · Respiratory Research · doi:10.1186/s12931-021-01640-z · Cited by 16

Multi-Pharmaceutical Activities of Chinese Herbal Polysaccharides in the Treatment of Pulmonary Fibrosis: Concept and Future Prospects

Wu, X., Huang, J., Wang, J., Xu, Y., Yang, X., Sun, M., & Shi, J. (2021) · Frontiers in Pharmacology · doi:10.3389/fphar.2021.707491 · Cited by 16

SHP2 : The protein tyrosine phosphatase involved in chronic pulmonary inflammation and fibrosis

Chang, C., Lin, C., Chen, B.-C., Lin, P., & Chen, C. (2021) · IUBMB Life · doi:10.1002/iub.2559 · Cited by 17

The effects and safety of pirfenidone in the treatment of idiopathic pulmonary fibrosis: a meta-analysis and systematic review

Zang, C., Zheng, Y., Wang, Y., & Li, L. (2021) · European journal of medical research · doi:10.1186/s40001-021-00601-y · Cited by 19

Treating Pulmonary Fibrosis with Non-Viral Gene Therapy: From Bench to Bedside

Huang, T., Gao, J. L., Cai, L., Xie, H., Wang, Y., Wang, Y., & Zhou, Q. (2022) · Pharmaceutics · doi:10.3390/pharmaceutics14040813 · Cited by 15

Verbascoside and isoverbascoside ameliorate transforming growth factor β1-induced collagen expression by lung fibroblasts through Smad/non-Smad signaling pathways

Chen, C., Tung, H.-Y., Tseng, Y., Huang, J., Shi, L.-S., & Ye, Y. (2022) · Life Sciences · doi:10.1016/j.lfs.2022.120950 · Cited by 17

Enhanced secretion of hepatocyte growth factor in human umbilical cord mesenchymal stem cells ameliorates pulmonary fibrosis induced by bleomycin in rats

Chen, H., Luo, Y., Zhu, Y., Ye, Y., Chen, D., Song, X., Xiao, Z., Liu, M., & Li, S. (2023) · Frontiers in Pharmacology · doi:10.3389/fphar.2022.1070736 · Cited by 15

Krebs von den Lungen-6 (KL-6) as a diagnostic marker for pulmonary fibrosis: A systematic review and meta-analysis

Wang, C., Wang, Q., Liu, T., Zhu, J., & Zhang, B. (2023) · Clinical Biochemistry · doi:10.1016/j.clinbiochem.2023.01.010 · Cited by 16

Is pulmonary fibrosis a precancerous disease?

Hosseini, M., & Salvatore, M. M. (2023) · European Journal of Radiology · doi:10.1016/j.ejrad.2023.110723 · Cited by 16

The role of interleukin -1 family in fibrotic diseases

Wang, H., Wu, J., Li, M., Bai, Y., & Liu, J. (2023) · Cytokine · doi:10.1016/j.cyto.2023.156161 · Cited by 16

Pharmacotherapy and pulmonary fibrosis risk after SARS-CoV-2 infection: a prospective nationwide cohort study in the United States

Adegunsoye, A., Baccile, R., Best, T. J., Zaksas, V., Hui, Z., Karnik, R., Patel, B. K., Solomonides, A. E., Parker, W. F., & Solway, J. (2023) · The Lancet Regional Health - Americas · doi:10.1016/j.lana.2023.100566 · Cited by 16

N-(2-Aminophenyl)-benzamide Inhibitors of Class I HDAC Enzymes with Antiproliferative and Antifibrotic Activity

Gerokonstantis, D. T., Mantzourani, C., Gkikas, D., Wu, K., Hoang, H. N., Triandafillidi, I., Barbayianni, I., Kanellopoulou, P., Kokotos, A. C., Moutevelis‐Minakakis, P., et al. (2023) · Journal of Medicinal Chemistry · doi:10.1021/acs.jmedchem.3c01422 · Cited by 16

PTK2-associated gene signature could predict the prognosis of IPF

Feng, A., Caro, Y. M., Gardner, C., Grischo, G., Liang, Y., Wickremasinghe, P. D., Polmann, M. B., Kala, M., Marlowe, T. A., Black, S. M., et al. (2023) · Respiratory Research · doi:10.1186/s12931-023-02582-4 · Cited by 17

A Step towards understanding coronary artery disease: a complication in idiopathic pulmonary fibrosis

Sinha, R., Nanavaty, D., AZHAR, A., Devarakonda, P. K., Singh, S., Garikipati, R., Sanghvi, A., Manoharan, S., Parhar, G., Zaman, K., et al. (2024) · BMJ Open Respiratory Research · doi:10.1136/bmjresp-2023-001834 · Cited by 16

Combination of losartan with pirfenidone: a protective anti-fibrotic against pulmonary fibrosis induced by bleomycin in rats

Amirkhosravi, A., Goki, M. M., Heidari, M. R., Karami‐Mohajeri, S., Iranpour, M., Torshabi, M., Mehrabani, M., Mandegary, A., & Mehrabani, M. (2024) · Scientific Reports · doi:10.1038/s41598-024-59395-8 · Cited by 16

Antifibrotic treatment adherence, efficacy and outcomes for patients with idiopathic pulmonary fibrosis in Spain: a real-world evidence study

Ortíz, A. D. R., Jiménez-Rodríguez, B. M., Ramírez, C. L., López-Bauzá, Á., Perez-Morales, M. D., Delgado-Torralbo, J. A., Moral, C. V., & Navarrete, B. A. (2024) · BMJ Open Respiratory Research · doi:10.1136/bmjresp-2023-001687 · Cited by 18

Pulmonary fibroblast-specific delivery of siRNA exploiting exosomes-based nanoscaffolds for IPF treatment

Lu, H., Liu, X., Zhang, M., Bera, H., Xu, W., Jiang, H., Zhao, X., Wu, L., Cun, D., & Yang, M. (2024) · Asian Journal of Pharmaceutical Sciences · doi:10.1016/j.ajps.2024.100929 · Cited by 17

Pathological mechanisms and novel drug targets in fibrotic interstitial lung disease

Nishioka, Y., Araya, J., Tanaka, Y., & Kumanogoh, A. (2024) · Inflammation and Regeneration · doi:10.1186/s41232-024-00345-2 · Cited by 18

Cardiovascular implications of idiopathic pulmonary fibrosis: A way forward together?

Mosher, C. L., & Mentz, R. J. (2020) · American Heart Journal · doi:10.1016/j.ahj.2020.04.027 · Cited by 15

Identification of a unique temporal signature in blood and BAL associated with IPF progression

Norman, K. C., O’Dwyer, D. N., Salisbury, M. L., DiLillo, K. M., Lama, V. N., Xia, M., Gurczynski, S. J., White, E. S., Flaherty, K. R., Martínez, F. J., et al. (2020) · Scientific Reports · doi:10.1038/s41598-020-67956-w · Cited by 16

Inhibitory effects of alkaline extract from the pericarp of Citrus reticulata Blanco on collagen behavior in bleomycin-induced pulmonary fibrosis

Li, R., Chen, X., Xu, Y., Feng, F., He, H., & Zhou, X. (2020) · Journal of Ethnopharmacology · doi:10.1016/j.jep.2020.113761 · Cited by 16

Pulmonary Fibrosis After COVID-19 Pneumonia

Malik, B. H., Abdelazeem, B., & GHATOL, A. G. (2021) · Cureus · doi:10.7759/cureus.13923 · Cited by 15

Antifibrotic therapies reduce mortality and hospitalization among Medicare beneficiaries with idiopathic pulmonary fibrosis

Mooney, J. J., Reddy, S. R., Chang, E. Y., Broder, M. S., Gokhale, S., & Corral, M. (2021) · Journal of Managed Care & Specialty Pharmacy · doi:10.18553/jmcp.2021.27.12.1724 · Cited by 17

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Caffeic Acid Acts as a Potent Senomorphic and Alleviates Inflammation and Lung Fibrosis by Covalently Targeting Annexin A5 Protein in Mice

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Spatially Resolved Identification of Transglutaminase Substrates by Proteomics in Pulmonary Fibrosis

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BMP3b is a Novel Antifibrotic Molecule Regulated by Meflin in Lung Fibroblasts

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Emodin inhibiting epithelial‐mesenchymal transition in pulmonary fibrosis through the c‐MYC / miR ‐182‐5p/ ZEB2 axis

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Sparganii Rhizoma alleviates pulmonary fibrosis by inhibiting fibroblasts differentiation and epithelial-mesenchymal transition mediated by TGF-β1/ Smad2/3 pathway

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Deciphering the molecular mechanisms of Maxing Huoqiao Decoction in treating pulmonary fibrosis via transcriptional profiling and circRNA-miRNA-mRNA network analysis

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Impact of aging on immune function in the pathogenesis of pulmonary diseases: potential for therapeutic targets

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Idiopathic pulmonary fibrosis: current diagnosis and treatment

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Exploration of the shared genes and signaling pathways between lung adenocarcinoma and idiopathic pulmonary fibrosis

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Mesenchymal stem cells and pulmonary fibrosis: a bibliometric and visualization analysis of literature published between 2002 and 2021

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Substrate-specific binding of 8-oxoguanine DNA glycosylase 1 (OGG1) reprograms mucosal adaptations to chronic airway injury

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A role for the terminal C5-C9 complement pathway in idiopathic pulmonary fibrosis

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Idiopathic pulmonary fibrosis: Addressing the current and future therapeutic advances along with the role of Sotatercept in the management of pulmonary hypertension

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Interaction between long noncoding RNA and microRNA in lung inflammatory diseases

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Qingfei xieding prescription ameliorates mitochondrial DNA-initiated inflammation in bleomycin-induced pulmonary fibrosis through activating autophagy

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Diabetes mellitus and idiopathic pulmonary fibrosis: a Mendelian randomization study

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Perlin noise generation of physiologically realistic cardiac fibrosis

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Molecular Endotypes of Idiopathic Pulmonary Fibrosis: A Latent Class Analysis of Two Multicenter Observational Cohorts

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Selective imaging, gene, and therapeutic delivery using PEGylated and pH-Sensitive nanoparticles for enhanced lung disorder treatment

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Human respiratory airway progenitors derived from pluripotent cells generate alveolar epithelial cells and model pulmonary fibrosis

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Idiopathic pulmonary fibrosis: an Australian perspective

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