Iron–sulfur cluster biogenesis and trafficking in mitochondria

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The Nfs1 interacting protein Isd11 has an essential role in Fe/S cluster biogenesis in mitochondria

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H2S and its role in redox signaling

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The human mitochondrial ISCA1, ISCA2, and IBA57 proteins are required for [4Fe-4S] protein maturation

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Human Ind1, an Iron-Sulfur Cluster Assembly Factor for Respiratory Complex I

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Biogenesis of iron–sulfur proteins in eukaryotes: a novel task of mitochondria that is inherited from bacteria

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Both human ferredoxins 1 and 2 and ferredoxin reductase are important for iron-sulfur cluster biogenesis

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Sulfur Transfer from IscS to IscU: The First Step in Iron−Sulfur Cluster Biosynthesis

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Subcellular compartmentalization of human Nfu, an iron-sulfur cluster scaffold protein, and its ability to assemble a [4Fe-4S] cluster

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Frataxin: a protein in search for a function

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Molecular Chaperones HscA/Ssq1 and HscB/Jac1 and Their Roles in Iron-Sulfur Protein Maturation

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Structural bases for the interaction of frataxin with the central components of iron–sulphur cluster assembly

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Functional reconstitution of mitochondrial Fe/S cluster synthesis on Isu1 reveals the involvement of ferredoxin

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Mammalian frataxin directly enhances sulfur transfer of NFS1 persulfide to both ISCU and free thiols

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The iron–sulphur protein Ind1 is required for effective complex I assembly

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The mitochondrial acyl carrier protein (ACP) coordinates mitochondrial fatty acid synthesis with iron sulfur cluster biogenesis

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Mitochondrial Iba57p Is Required for Fe/S Cluster Formation on Aconitase and Activation of Radical SAM Enzymes

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Human Frataxin Activates Fe–S Cluster Biosynthesis by Facilitating Sulfur Transfer Chemistry

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Monothiol CGFS Glutaredoxins and BolA-like Proteins: [2Fe-2S] Binding Partners in Iron Homeostasis

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Highly divergent mitochondrion-related organelles in anaerobic parasitic protozoa

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(IscS‐IscU)2 Complex Structures Provide Insights into Fe2S2 Biogenesis and Transfer

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Role of Nfu1 and Bol3 in iron-sulfur cluster transfer to mitochondrial clients

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Mitochondrial Bol1 and Bol3 function as assembly factors for specific iron-sulfur proteins

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Mitochondrial fatty acid synthesis and respiration

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The mitochondrial Hsp70 chaperone Ssq1 facilitates Fe/S cluster transfer from Isu1 to Grx5 by complex formation

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Jac1, a mitochondrial J-type chaperone, is involved in the biogenesis of Fe/S clusters in Saccharomyces cerevisiae

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The crystal structure of human GLRX5: iron–sulfur cluster co-ordination, tetrameric assembly and monomer activity

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Formation of [4Fe-4S] Clusters in the Mitochondrial Iron–Sulfur Cluster Assembly Machinery

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The roles of glutaredoxins ligating Fe–S clusters: Sensing, transfer or repair functions?

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Assembly of Fe/S proteins in bacterial systems

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Viperin is an iron-sulfur protein that inhibits genome synthesis of tick-borne encephalitis virus via radical SAM domain activity

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Disease-Causing SDHAF1 Mutations Impair Transfer of Fe-S Clusters to SDHB

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Mammalian Fe–S cluster biogenesis and its implication in disease

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A Proposed Role for the Azotobacter vinelandii NfuA Protein as an Intermediate Iron-Sulfur Cluster Carrier

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Monothiol glutaredoxins and A-type proteins: partners in Fe–S cluster trafficking

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The LYR protein subunit NB4M/NDUFA6 of mitochondrial complex I anchors an acyl carrier protein and is essential for catalytic activity

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Molecular organization, biochemical function, cellular role and evolution of NfuA, an atypical Fe‐S carrier

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Evolutionary conservation and in vitro reconstitution of microsporidian iron–sulfur cluster biosynthesis

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Monothiol Glutaredoxins Function in Storing and Transporting [Fe2S2] Clusters Assembled on IscU Scaffold Proteins

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Frataxin Directly Stimulates Mitochondrial Cysteine Desulfurase by Exposing Substrate-binding Sites, and a Mutant Fe-S Cluster Scaffold Protein with Frataxin-bypassing Ability Acts Similarly

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Ferredoxin Competes with Bacterial Frataxin in Binding to the Desulfurase IscS*

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How Is Fe-S Cluster Formation Regulated?

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Spectroscopic and Functional Characterization of Iron–Sulfur Cluster-Bound Forms of Azotobacter vinelandii Nif IscA

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Facilitated Transfer of IscU–[2Fe2S] Clusters by Chaperone-Mediated Ligand Exchange

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The E. coli Monothiol Glutaredoxin GrxD Forms Homodimeric and Heterodimeric FeS Cluster Containing Complexes

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Arabidopsis thaliana Nfu2 Accommodates [2Fe-2S] or [4Fe-4S] Clusters and Is Competent for in Vitro Maturation of Chloroplast [2Fe-2S] and [4Fe-4S] Cluster-Containing Proteins

Gao, H., Sowmya, S., Couturier, J., Naik, S., Kim, S., Leustek, T., Knaff, D. B., Wu, H.-C., Vignols, F., Huynh, B. H., et al. (2013) · Biochemistry · doi:10.1021/bi4007622 · Cited by 84

Eukaryotic LYR Proteins Interact with Mitochondrial Protein Complexes

Angerer, H. (2015) · Biology · doi:10.3390/biology4010133 · Cited by 81

Fe/S protein assembly gene IBA57 mutation causes hereditary spastic paraplegia

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The Relationship between Environmental Dioxygen and Iron-Sulfur Proteins Explored at the Genome Level

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Monothiol glutaredoxin Grx5 interacts with Fe–S scaffold proteins Isa1 and Isa2 and supports Fe–S assembly and DNA integrity in mitochondria of fission yeast

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Ferredoxin, in conjunction with NADPH and ferredoxin-NADP reductase, transfers electrons to the IscS/IscU complex to promote iron–sulfur cluster assembly

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Persulfide formation on mitochondrial cysteine desulfurase: enzyme activation by a eukaryote-specific interacting protein and Fe–S cluster synthesis

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Binding of the Chaperone Jac1 Protein and Cysteine Desulfurase Nfs1 to the Iron-Sulfur Cluster Scaffold Isu Protein Is Mutually Exclusive

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Mutation of the iron‐sulfur cluster assembly gene IBA57 causes fatal infantile leukodystrophy

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Mitochondrial Cysteine Desulfurase and ISD11 Coexpressed in Escherichia coli Yield Complex Containing Acyl Carrier Protein

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Structural and Spectroscopic Insights into BolA-Glutaredoxin Complexes

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Structural/Functional Properties of Human NFU1, an Intermediate [4Fe-4S] Carrier in Human Mitochondrial Iron-Sulfur Cluster Biogenesis

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