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The Catalysis of the 1,1-Proton Transfer by α-Methyl-acyl-CoA Racemase Is Coupled to a Movement of the Fatty Acyl Moiety Over a Hydrophobic, Methionine-rich Surface

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β-Oxidation in hepatocyte cultures from mice with peroxisomal gene knockouts

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Cerebellar and hepatic alterations in ACBD5-deficient mice are associated with unexpected, distinct alterations in cellular lipid homeostasis.

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Dietary bile acids promote sterol metabolism, bile acids enterohepatic circulation, and apoptosis in juvenile Pacific white shrimp (Litopenaeus vannamei)

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Current Knowledge on the Function of α-Methyl Acyl-CoA Racemase in Human Diseases

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Inhibition of Human α‐Methylacyl CoA Racemase (AMACR): a Target for Prostate Cancer

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Loss of Enzymes in the Bile Acid Synthesis Pathway Explains Differences in Bile Composition among Mammals

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Phytanic Acid, Amacr and Prostate Cancer Risk

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Peroxisomal membrane channel Pxmp2 in the mammary fat pad is essential for stromal lipid homeostasis and for development of mammary gland epithelium in mice

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Crystal Structure of Liganded Rat Peroxisomal Multifunctional Enzyme Type 1

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The isomerase and hydratase reaction mechanism of the crotonase active site of the multifunctional enzyme (type‐1), as deduced from structures of complexes with 3 S ‐hydroxy‐acyl‐ C o A

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Slc25a17 Gene Trapped Mice: PMP34 Plays a Role in the Peroxisomal Degradation of Phytanic and Pristanic Acid

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Peroxisomal Disorders and Their Mouse Models Point to Essential Roles of Peroxisomes for Retinal Integrity

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The Enolization Chemistry of a Thioester-Dependent Racemase: The 1.4 Å Crystal Structure of a Reaction Intermediate Complex Characterized by Detailed QM/MM Calculations

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Comparing Transcriptomes Reveals Key Metabolic Mechanisms in Superior Growth Performance Nile Tilapia (Oreochromis niloticus)

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Role of AMACR (α-methylacyl-CoA racemase) and MFE-1 (peroxisomal multifunctional enzyme-1) in bile acid synthesis in mice

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Hepatic symptoms and histology in 13 patients with a Zellweger spectrum disorder

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Disorders of Bile Acid Synthesis and Metabolism: A Metabolic Basis for Liver Disease

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Alpha-methylacyl coenzyme A racemase overexpression in gallbladder carcinoma confers an independent prognostic indicator

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FUNDUS FINDINGS IN A PATIENT WITH α-METHLYACYL-COA RACEMASE DEFICIENCY

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Mice with a deficiency in Peroxisomal Membrane Protein 4 (PXMP4) display mild changes in hepatic lipid metabolism

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Metabolic adaptation allows Amacr-deficient mice to remain symptom-free despite low levels of mature bile acids

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Phytol is lethal for Amacr-deficient mice

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Oncogenic Activity of Solute Carrier Family 45 Member 2 and Alpha‐Methylacyl‐Coenzyme A Racemase Gene Fusion Is Mediated by Mitogen‐Activated Protein Kinase

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Phytol Promotes the Formation of Slow-Twitch Muscle Fibers through PGC-1α/miRNA but Not Mitochondria Oxidation

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Structural Studies of MFE-1: the 1.9Å Crystal Structure of the Dehydrogenase Part of Rat Peroxisomal MFE-1

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Alpha-Methylacyl-CoA Racemase (AMACR) Protein is Upregulated in Early Proliferative Lesions of the Breast Irrespective of Apocrine Differentiation

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AMACR overexpression as a poor prognostic factor in patients with nasopharyngeal carcinoma

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Alpha‐methylacyl‐CoA racemase deletion has mutually counteracting effects on T‐cell responses, associated with unchanged course of EAE

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Organic Stereochemistry. Part 7

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Mouse Models to Study Peroxisomal Functions and Disorders: Overview, Caveats, and Recommendations

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Peroxisomal Disorders in Children

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Identification of Key Biomarkers Related to Lipid Metabolism in Acute Pancreatitis and Their Regulatory Mechanisms Based on Bioinformatics and Machine Learning

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Perturbed Mitochondrial Metabolism in Islets from Donors with Type-2 DiabetesPreprint

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Single Peroxisomal Enzyme and Transporter Deficiencies in Human Diseases and Mouse Models

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Phytol is lethal for Amacr-deficient mice

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Metabolic adaptation allows Amacr-deficient mice to remain symptom-free despite low levels of mature bile acids

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Role of AMACR (α-methylacyl-CoA racemase) and MFE-1 (peroxisomal multifunctional enzyme-1) in bile acid synthesis in mice

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Alpha-methylacyl-CoA racemase (AMACR) deficiency: report on novel patient and literature review

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