European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis Centre

The Prognostic Value of Exercise Testing in Patients with Cystic Fibrosis

Nixon, P. A., Orenstein, D. M., Kelsey, S. F., & Doershuk, C. F. (1992) · New England Journal of Medicine · doi:10.1056/nejm199212173272504 · Cited by 629 · see citing works

Cystic fibrosis mortality and survival in the UK: 1947–2003

DODGE, J. A., Lewis, P. A., Stanton, M., & Wilsher, J. (2006) · European Respiratory Journal · doi:10.1183/09031936.00099506 · Cited by 627 · see citing works

Standards of care for patients with cystic fibrosis: a European consensus

Kerem, E., Conway, S., Elborn, J. S., & Heijerman, H. G. M. (2005) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2004.12.002 · Cited by 477 · see citing works

Aerosol Deposition in Health and Disease

Darquenne, C. (2012) · Journal of Aerosol Medicine and Pulmonary Drug Delivery · doi:10.1089/jamp.2011.0916 · Cited by 453 · see citing works

Guidelines for the physiotherapy management of the adult, medical, spontaneously breathing patient

Bott, J., Blumenthal, S., Buxton, M., Ellum, S., Falconer, C., Garrod, R., Harvey, A., Hughes, T., Lincoln, M., Mikelsons, C., et al. (2009) · Thorax · doi:10.1136/thx.2008.110726 · Cited by 451 · see citing works

Infection control recommendations for patients with cystic fibrosis: Microbiology, important pathogens, and infection control practices to prevent patient-to-patient transmission

Saiman, L. M. (2003) · American Journal of Infection Control · doi:10.1067/mic.2003.78 · Cited by 307 · see citing works

Better nutritional status in early childhood is associated with improved clinical outcomes and survival in patients with cystic fibrosis

Yen, E. H., Quinton, H., & Borowitz, D. (2013) · The Journal of Pediatrics · doi:10.1016/j.jpeds.2012.08.040 · Cited by 306 · see citing works

BTS guidelines for home oxygen in children

Balfour-Lynn, I. M., Field, D. J., Gringras, P., Hicks, B., Jardine, E., Jones, R. C., Magee, A. G., Primhak, R. A., Samuels, M. P., Shaw, N. J., et al. (2009) · Thorax · doi:10.1136/thx.2009.116020 · Cited by 250 · see citing works

Clinical outcome in relation to care in centres specialising in cystic fibrosis: cross sectional studyCommentary: Management in paediatric and adult cystic fibrosis centres improves clinical outcome

Mahadeva, R., DODGE, J. A., Webb, A. K., Westerbeek, R. C., Carroll, N. R., Dodd, M. E., Bilton, D., & Lomas, D. A. (1998) · BMJ · doi:10.1136/bmj.316.7147.1771 · Cited by 248 · see citing works

Guidelines for the management of pregnancy in women with cystic fibrosis

Edenborough, F. P., Borgo, G., Knoop, C., Lannefors, L., Mackenzie, W. E., Madge, S. L., Morton, A. M., Oxley, H., Touw, D. J., Benham, M., et al. (2007) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2007.10.001 · Cited by 246 · see citing works

Infection Control Recommendations for Patients With Cystic Fibrosis: Microbiology, Important Pathogens, and Infection Control Practices to Prevent Patient-to-Patient Transmission

Saiman, L. M., & Siegel, J. D. (2003) · Infection Control and Hospital Epidemiology · doi:10.1086/503485 · Cited by 235 · see citing works

Factors Influencing Outcomes in Cystic Fibrosis

Johnson, C. A., Butler, S. M., Konstan, M. W., Morgan, W. J., & Wohl, M. E. B. (2003) · CHEST Journal · doi:10.1378/chest.123.1.20 · Cited by 226 · see citing works

Massive hemoptysis in cystic fibrosis

Flume, P. A., Yankaskas, J. R., Ebeling, M., Hulsey, T., & Clark, L. L. (2005) · Chest · doi:10.1378/chest.128.2.729 · Cited by 215 · see citing works

Cystic Fibrosis and Transition to Adult Medical Care

Tuchman, L. K., Schwartz, L. A., Sawicki, G. S., & Britto, M. T. (2010) · PEDIATRICS · doi:10.1542/peds.2009-2791 · Cited by 213 · see citing works

Chest physiotherapy compared to no chest physiotherapy for cystic fibrosis

Warnock, L., & Gates, A. (2015) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd001401.pub3 · Cited by 189 · see citing works

Conventional chest physiotherapy compared to other airway clearance techniques for cystic fibrosis

Main, E., Prasad, A., & van der Schans, C. P. (2005) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd002011.pub2 · Cited by 185 · see citing works

Treatment compliance in children and adults with Cystic Fibrosis

Llorente, R. P. A., García, C. B., & Díaz, J. J. (2008) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2008.01.003 · Cited by 169 · see citing works

Non-invasive ventilation for cystic fibrosis

Moran, F. M., Bradley, J. M., & Piper, A. J. (2017) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd002769.pub5 · Cited by 167 · see citing works

Pneumothorax in cystic fibrosis

Flume, P. A., Strange, C., Ye, X., Ebeling, M., Hulsey, T., & Clark, L. L. (2005) · Chest · doi:10.1378/chest.128.2.720 · Cited by 164 · see citing works

Physical training for cystic fibrosis

Bradley, J. M., & Moran, F. M. (2008) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd002768.pub2 · Cited by 148 · see citing works

Oscillating devices for airway clearance in people with cystic fibrosis

Morrison, L., & Agnew, J. L. (2009) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd006842.pub2 · Cited by 141 · see citing works

Structure and Function of the Mucus Clearance System of the LungPreprint

Button, B. M., & Button, B. (2013) · Cold Spring Harbor Perspectives in Medicine · doi:10.1101/cshperspect.a009720 · Cited by 131 · see citing works

Positive expiratory pressure physiotherapy for airway clearance in people with cystic fibrosis

Elkins, M. R., JONES, A. Y. M., & van der Schans, C. P. (2006) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd003147.pub3 · Cited by 121 · see citing works

Non-invasive ventilation assists chest physiotherapy in adults with acute exacerbations of cystic fibrosis

Holland, A. E. (2003) · Thorax · doi:10.1136/thorax.58.10.880 · Cited by 119 · see citing works

Methicillin-resistantStaphylococcus aureus(MRSA)

Goyal, N., Miller, A., Tripathi, M. S., & Parvizi, J. (2013) · The Bone & Joint Journal · doi:10.1302/0301-620x.95b1.27973 · Cited by 117 · see citing works

Cystic fibrosis across Europe: EuroCareCF analysis of demographic data from 35 countries

Mehta, G., Maçek, M., & Mehta, A. (2010) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2010.08.002 · Cited by 105 · see citing works

Cystic fibrosis‐related diabetes

Mackie, A. D. R., Thornton, S. J., & Edenborough, F. P. (2003) · Diabetic Medicine · doi:10.1046/j.1464-5491.2003.00924.x · Cited by 102 · see citing works

Association of body composition and lung function in children with cystic fibrosis

Pedreira, C. C., Robert, R., Dalton, V., Oliver, M. R., Carlin, J. B., Robinson, P. J., & Cameron, F. J. (2005) · Pediatric Pulmonology · doi:10.1002/ppul.20162 · Cited by 95 · see citing works

From registry to quality management: the German Cystic Fibrosis Quality Assessment project 1995–2006

Stern, M., Wiedemann, B., & WENZLAFF, P. (2007) · European Respiratory Journal · doi:10.1183/09031936.00056507 · Cited by 94 · see citing works

Chest physiotherapy compared to no chest physiotherapy for cystic fibrosis

van der Schans, C. P., Prasad, A., & Main, E. (2000) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd001401 · Cited by 94 · see citing works

Parents' Recollection of the Initial Communication of the Diagnosis of Cystic Fibrosis

Jedlicka-Köhler, I., Götz, M., & Eichler, I. (1996) · PEDIATRICS · doi:10.1542/peds.97.2.204 · Cited by 91 · see citing works

A spoonful of sugar

Blow, N. S. (2009) · Nature · doi:10.1038/457617a · Cited by 89 · see citing works

Cystic Fibrosis in the 21st Century

Bush, A., Alton, E. W. F. W., Davies, J. C., Uta Griesenbach, D., & Jaffé, A. (2005) · Progress in respiratory research/Progress in research in emphysema and chronic bronchitis/Progress in respiration research · doi:10.1159/isbn.978-3-318-01240-8 · Cited by 86 · see citing works

Active cycle of breathing technique for cystic fibrosis

Mckoy, N. A., Wilson, L. M., Saldanha, I. J., Odelola, O. A., & Robinson, K. A. (2016) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd007862.pub4 · Cited by 86 · see citing works

Transition programs in cystic fibrosis centers: Perceptions of patients

Anderson, D. L., Flume, P. A., Hardy, K. K., & Gray, S. (2002) · Pediatric Pulmonology · doi:10.1002/ppul.10083 · Cited by 84 · see citing works

Physiotherapy in infants and young children with cystic fibrosis: current practice and future developments.

Lannefors, L., Button, B., & McIlwaine, M. P. (2004) · PubMed · Cited by 82 · see citing works

Methicillin Resistant Staphylococcus aureus (MRSA)

Cabrera, E. C. (2012) · Cited by 79 · see citing works

Developmental and Psychosocial Issues in Cystic Fibrosis

Ernst, M. M., Johnson, M. C., & Stark, L. J. (2010) · Child and Adolescent Psychiatric Clinics of North America · doi:10.1016/j.chc.2010.01.004 · Cited by 75 · see citing works

Transition programs in cystic fibrosis centers: Perceptions of team members

Flume, P. A., Taylor, L. A., Anderson, D. L., Gray, S., & Turner, D. A. (2003) · Pediatric Pulmonology · doi:10.1002/ppul.10391 · Cited by 75 · see citing works

Motivational interviewing for adherence problems in cystic fibrosis

Duff, A. J. A., & Latchford, G. J. (2010) · Pediatric Pulmonology · doi:10.1002/ppul.21103 · Cited by 69 · see citing works

Antibiotic treatment of cystic fibrosis

Marino, J. T. (1981) · The Journal of Pediatrics · doi:10.1016/s0022-3476(81)80748-2 · Cited by 66 · see citing works

Posture and cystic fibrosis.

Tattersall, R. B., & Walshaw, M. J. (2003) · PubMed · Cited by 65 · see citing works

Transition of young people with respiratory diseases to adult health care

Rosen, D. S. (2004) · Paediatric Respiratory Reviews · doi:10.1016/j.prrv.2004.01.008 · Cited by 65 · see citing works

A model for transition from pediatric to adult care in cystic fibrosis

Madge, S. L., & Bryon, M. (2002) · Journal of Pediatric Nursing · doi:10.1053/jpdn.2002.126711 · Cited by 60 · see citing works

Lactate in cystic fibrosis sputum

Bensel, T., Stotz, M., Borneff-Lipp, M., Wollschläger, B., Wienke, A., Taccetti, G., Campana, S., Meyer, K. C., Jensen, P. Ø., Lechner, U., et al. (2010) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2010.09.004 · Cited by 59 · see citing works

Transition of adolescents with cystic fibrosis from paediatric to adult care

Towns, S. J., & Bell, S. C. (2010) · The Clinical Respiratory Journal · doi:10.1111/j.1752-699x.2010.00226.x · Cited by 58 · see citing works

Physical training for cystic fibrosis

Bradley, J. M., & Moran, F. M. (2002) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd002768 · Cited by 57 · see citing works

End of life care for patients with cystic fibrosis

Sands, D., Repetto, T., Dupont, L., Korzeniewska, A., Catastini, P., & Madge, S. L. (2011) · Journal of Cystic Fibrosis · doi:10.1016/s1569-1993(11)60007-6 · Cited by 57 · see citing works

Conventional chest physiotherapy compared to other forms of chest physiotherapy for cystic fibrosis

Main, E., Prasad, A., & van der Schans, C. (2003) · doi:10.1002/14651858.cd002011 · Cited by 56 · see citing works

The implementation of standards of care in Europe: State of the art

Colombo, C., & Littlewood, J. M. (2011) · Journal of Cystic Fibrosis · doi:10.1016/s1569-1993(11)60003-9 · Cited by 55 · see citing works

Stunting is an independent predictor of mortality in patients with cystic fibrosis

Vieni, G., Faraci, S., Collura, M., Lombardo, M., Traverso, G., Cristadoro, S., Termini, L., Lucanto, M. C., Furnari, M. L., Trimarchi, G. R., et al. (2012) · Clinical Nutrition · doi:10.1016/j.clnu.2012.08.017 · Cited by 53 · see citing works

Exercise improves lung function and habitual activity in children with cystic fibrosis

Paranjape, S. M., Barnes, L. A., Carson, K. A., von Berg, K., Loosen, H., & Mogayzel, P. J. (2011) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2011.08.003 · Cited by 51 · see citing works

Psychological interventions for people with cystic fibrosis and their families

Glasscoe, C. A., & Quittner, A. L. (2008) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd003148.pub2 · Cited by 49 · cited 1× · see citing works

Advance Care Planning in Adults with Cystic Fibrosis

Sawicki, G. S., Dill, E. J., Asher, D. I., Sellers, D. E., & Robinson, W. M. (2008) · Journal of Palliative Medicine · doi:10.1089/jpm.2008.0051 · Cited by 48 · see citing works

Compliance of Clinical Microbiology Laboratories in the United States with Current Recommendations for Processing Respiratory Tract Specimens from Patients with Cystic Fibrosis

Zhou, J. J., Garber, E., Desai, M., & Saiman, L. M. (2006) · Journal of Clinical Microbiology · doi:10.1128/jcm.44.4.1547-1549.2006 · Cited by 44 · see citing works

Benefits of Continuous Positive Airway Pressure during Exercise in Cystic Fibrosis and Relationship to Disease Severity

Henke, K. G., Regnis, J. A., & Bye, P. T. P. (1993) · American Review of Respiratory Disease · doi:10.1164/ajrccm/148.5.1272 · Cited by 42 · see citing works

EAHP survey 2010 on hospital pharmacy in Europe: parts 4 and 5. Clinical services and patient safety

Frontini, R., Miharija-Gala, T., & Sýkora, J. (2013) · European Journal of Hospital Pharmacy · doi:10.1136/ejhpharm-2013-000285 · Cited by 42 · see citing works

INCONTINENCE IN ADULT FEMALES WITH CYSTIC FIBROSIS: A NORTHERN IRELAND SURVEY

Moran, F., Bradley, J., Boyle, L. R., & Elborn, J. S. (2003) · International Journal of Clinical Practice · doi:10.1111/j.1742-1241.2003.tb10460.x · Cited by 41 · see citing works

Transition from Paediatric to Adult Care: Psychological Principles

Bryon, M., & Madge, S. L. (2001) · Journal of the Royal Society of Medicine · doi:10.1177/014107680109440s03 · Cited by 41 · see citing works

Technological and behavioral strategies to reduce treatment burden and improve adherence to inhaled antibiotics in cystic fibrosis

Geller, D. E., & Madge, S. L. (2011) · Respiratory Medicine · doi:10.1016/s0954-6111(11)70024-5 · Cited by 39 · see citing works

Palliative and end-of-life care in cystic fibrosis: what we know and what we need to know

Robinson, W. M. (2009) · Current Opinion in Pulmonary Medicine · doi:10.1097/mcp.0b013e3283304c29 · Cited by 38 · see citing works

Non-invasive ventilation for cystic fibrosis

Moran, F. M., Bradley, J. M., & Piper, A. J. (2013) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd002769.pub4 · Cited by 38 · see citing works

Cystic fibrosis in adolescents and young adults.

Nasr, S. Z. (2000) · PubMed · Cited by 35 · see citing works

Active cycle of breathing technique for cystic fibrosis

Mckoy, N. A., Saldanha, I. J., Odelola, O. A., & Robinson, K. A. (2012) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd007862.pub3 · Cited by 34 · see citing works

European Curriculum Recommendations for Training in Adult Respiratory Medicine

Loddenkemper, R., Haslam, P. L., Séverin, T., Annesi‐Maesano, I., Чучалин, А. Г., COLES, C. R., Maria, G. D., Leroyer, C., Magyar, P., Noël, J.-L., et al. (2008) · Breathe · doi:10.1183/18106838/breathe.5.1.80 · Cited by 32 · see citing works

‘A bed in the middle of nowhere’: Parents' meanings of place of death for adults with cystic fibrosis

Lowton, K. (2009) · Social Science & Medicine · doi:10.1016/j.socscimed.2009.07.007 · Cited by 29 · see citing works

Musculoskeletal involvement in cystic fibrosis.

Parasa, R. B., & Maffulli, N. (1999) · PubMed · Cited by 28 · see citing works

Oxygen-assisted exercise training in adult cystic fibrosis patients with pulmonary limitation to exercise

Heijerman, H. G. M., BARKER, W., Sterk, P. J., & JOOP, H. D. (1991) · International Journal of Rehabilitation Research · doi:10.1097/00004356-199106000-00002 · Cited by 27 · see citing works

The sexual health of adolescents with cystic fibrosis.

Roberts, S. A., & Green, P. (2005) · PubMed Central · Cited by 26 · see citing works

Multidisciplinary teams in the United Kingdom: Problems and solutions

Madge, S. L., & Khair, K. (2000) · Journal of Pediatric Nursing · doi:10.1053/jn.2000.5516 · Cited by 26 · see citing works

A comparison of the prevalence of urinary incontinence in girls with cystic fibrosis, asthma, and healthy controls

Prasad, S. A., Balfour-Lynn, I. M., Carr, S. B., & Madge, S. L. (2006) · Pediatric Pulmonology · doi:10.1002/ppul.20493 · Cited by 25 · see citing works

Airway clearance research in CF: the ‘perfect storm’ of strong preference and effortful participation in long-term, non-blinded studies

Main, E. (2013) · Thorax · doi:10.1136/thoraxjnl-2012-203054 · Cited by 20 · see citing works

Benefits of a dedicated cystic fibrosis pharmacist.

Redfern, J., & Webb, A. K. (2004) · Europe PMC (PubMed Central) · Cited by 20 · see citing works

How a clinical psychologist manages the problems of adults with cystic fibrosis.

Oxley, H., & Webb, A. K. (2005) · PubMed Central · Cited by 19 · see citing works

Using behavioral interventions to assist with routine procedures in children with cystic fibrosis

Ward, C. M., Brinkman, T. M., Slifer, K. J., & Paranjape, S. M. (2009) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2009.11.008 · Cited by 14 · see citing works

Phenotypic differences between asymptomatic airway hyperresponsiveness and remission of asthma

Yoshikawa, T., & Kanazawa, H. (2010) · Respiratory Medicine · doi:10.1016/j.rmed.2010.07.015 · Cited by 12 · see citing works

Physiotherapy for cystic fibrosis in A ustralia: Knowledge and acceptance of the C onsensus S tatement recommendations

Holland, A. E., Button, B., & International Physiotherapy Group for Cystic Fibrosis, A. C. (2012) · Respirology · doi:10.1111/resp.12032 · Cited by 11 · see citing works

Survey of professionals' expectations of developmental task achievement of cystic fibrosis self‐care in children

Patton, S. R., Graham, J. L., Holsclaw, D. S., & Varlotta, L. (2005) · Pediatric Pulmonology · doi:10.1002/ppul.20262 · Cited by 10 · see citing works

Environmental allergies and respiratory morbidities in cystic fibrosis

Collaco, J. M., Morrow, C. B., Green, D., Cutting, G. R., & Mogayzel, P. J. (2012) · Pediatric Pulmonology · doi:10.1002/ppul.22700 · Cited by 9 · see citing works

Growing up and growing older with cystic fibrosis.

Madge, S. L. (2006) · PubMed · Cited by 9 · see citing works

Cystic fibrosis in the 21st Century

Kollberg, H. (2006) · Acta Paediatrica · doi:10.1080/08035250600909108 · Cited by 7 · see citing works

376* The role of electronic patient records (EPR) in improving service efficiency and clinical performance in a regional adult UK centre

Etherington, C., Conway, S., & Peckham, D. G. (2011) · Journal of Cystic Fibrosis · doi:10.1016/s1569-1993(11)60388-3 · Cited by 6 · see citing works

Challenges for Nurses

Madge, S. L. (2005) · KARGER eBooks · doi:10.1159/000088610 · Cited by 5 · see citing works

Sexuality & Cystic Fibrosis

Bolyard, D. (2001) · MCN The American Journal of Maternal/Child Nursing · doi:10.1097/00005721-200101000-00010 · Cited by 5 · see citing works

National consensus standards for nursing children and young people with cystic fibrosis

Madge, S. L. (2002) · Nursing Children and Young People · doi:10.7748/paed.14.1.32.s25 · Cited by 4 · see citing works

Financial savings following the introduction of a cystic fibrosis electronic patient record system

Shaw, N. J., Conway, S. P., Etherington, C., Denton, M., & Peckham, D. G. (2010) · Journal of Cystic Fibrosis · doi:10.1016/s1569-1993(10)60446-8 · Cited by 2 · see citing works

Cystic fibrosis

Elborn, J. S. (2016) · The Lancet · doi:10.1016/s0140-6736(16)00576-6 · Cited by 1,710 · see citing works

The future of cystic fibrosis care: a global perspective

Bell, S. C., Mall, M. A., Gutierrez, H., Macek, M., Madge, S. L., Davies, J. C., Burgel, P., Tullis, E., Castaños, C., Castellani, C., et al. (2019) · The Lancet Respiratory Medicine · doi:10.1016/s2213-2600(19)30337-6 · Cited by 1,042 · see citing works

ECFS best practice guidelines: the 2018 revision

Castellani, C., Duff, A. J. A., Bell, S. C., Heijerman, H. G. M., Munck, A., Ratjen, F., Sermet-Gaudelus, I., Southern, K. W., Barben, J., Flume, P. A., et al. (2018) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2018.02.006 · Cited by 765 · see citing works

Emergence and spread of a human-transmissible multidrug-resistant nontuberculous mycobacterium

Bryant, J. M., Grogono, D., Rodriguez-Rincon, D., Everall, I., Brown, K., Moreno, P. A., Verma, D., Hill, E. M., Drijkoningen, J., Gilligan, P. H., et al. (2016) · Science · doi:10.1126/science.aaf8156 · Cited by 588 · see citing works

Cystic fibrosis

Ratjen, F. A., Bell, S. C., Rowe, S. M., Goss, C. H., Quittner, A. L., & Bush, A. (2015) · Nature Reviews Disease Primers · doi:10.1038/nrdp.2015.10 · Cited by 553 · see citing works

Cystic Fibrosis

Ong, T., & Ramsey, B. W. (2023) · JAMA · doi:10.1001/jama.2023.8120 · Cited by 327 · see citing works

Cystic fibrosis: a clinical view

Castellani, C., & Assael, B. M. (2016) · Cellular and Molecular Life Sciences · doi:10.1007/s00018-016-2393-9 · Cited by 255 · see citing works

Newborn screening for cystic fibrosis

Castellani, C., Massie, J., Sontag, M. K., & Southern, K. W. (2016) · The Lancet Respiratory Medicine · doi:10.1016/s2213-2600(16)00053-9 · Cited by 163 · see citing works

Brazilian guidelines for the diagnosis and treatment of cystic fibrosis

Athanazio, R. A., Filho, L. V. R. F. D. S., Vergara, A. A., Ribeiro, A. F., Riedi, C. A., Procianoy, E. D. F. A., Adde, F. V., Reis, F. J. C., Ribeiro, J. D., Torres, L. A. G. M. M., et al. (2017) · Jornal Brasileiro de Pneumologia · doi:10.1590/s1806-37562017000000065 · Cited by 151 · see citing works

Real-World Safety of CFTR Modulators in the Treatment of Cystic Fibrosis: A Systematic Review

Dagenais, R., Su, V., & Quon, B. S. (2020) · Journal of Clinical Medicine · doi:10.3390/jcm10010023 · Cited by 126 · see citing works

Gut microbiota signatures in cystic fibrosis: Loss of host CFTR function drives the microbiota enterophenotype

Vernocchi, P., CHIERICO, F. D., Russo, A., Majo, F., Rossitto, M., Valerio, M., Casadei, L., Storia, A. L., Filippis, F. D., Rizzo, C., et al. (2018) · PLoS ONE · doi:10.1371/journal.pone.0208171 · Cited by 122 · see citing works

Report of the European Respiratory Society/European Cystic Fibrosis Society task force on the care of adults with cystic fibrosis

Elborn, J. S., Bell, S. C., Madge, S. L., Burgel, P., Castellani, C., Conway, S., Rijcke, K. D., Dembski, B., Dřevı́nek, P., Heijerman, H. G. M., et al. (2015) · European Respiratory Journal · doi:10.1183/13993003.00592-2015 · Cited by 120 · see citing works

Current and future therapies for Pseudomonas aeruginosa infection in patients with cystic fibrosis

Smith, W. D., Bardin, E., Cameron, L. P., Edmondson, C. L., Farrant, K. V., Martin, I., Murphy, R. A., Soren, O., Turnbull, A. R., Wierre-Gore, N., et al. (2017) · FEMS Microbiology Letters · doi:10.1093/femsle/fnx121 · Cited by 103 · see citing works

Standards for the care of people with cystic fibrosis; establishing and maintaining health

Southern, K. W., Addy, C., Bell, S. C., Bevan, A., Borawska-Kowalczyk, U., Brown, C., Burgel, P., Button, B., Castellani, C., Chansard, A., et al. (2023) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2023.12.002 · Cited by 105 · see citing works

Epidemiology of CF: How registries can be used to advance our understanding of the CF population

Jackson, A. D., & Goss, C. H. (2017) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2017.11.013 · Cited by 92 · see citing works

Standards for the care of people with cystic fibrosis (CF); recognising and addressing CF health issues

Burgel, P., Southern, K. W., Addy, C., Battezzati, A., Berry, C. A., Bouchara, J., Brokaar, E. J., Brown, A. W., Azevedo, P., Durieu, I., et al. (2024) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2024.01.005 · Cited by 94 · see citing works

Improving transition to adult healthcare for young people with cystic fibrosis: A systematic review

Coyne, I., Sheehan, A., Heery, E., & While, A. (2017) · Journal of Child Health Care · doi:10.1177/1367493517712479 · Cited by 81 · see citing works

Cystic Fibrosis

Naehrig, S., Chao, C., & Naehrlich, L. (2017) · Deutsches Ärzteblatt international · doi:10.3238/arztebl.2017.0564 · Cited by 82 · see citing works

European Cystic Fibrosis Society Standards of Care: Quality Management in cystic fibrosis

Stern, M., Pougheon-Bertrand, D., Bignamini, E., Corey, M. L., Dembski, B., Goss, C. H., Pressler, T., Rault, G., Viviani, L., Elborn, J. S., et al. (2014) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2014.03.011 · Cited by 69 · see citing works

Rehabilitation in Patients with Chronic Respiratory Disease Other than Chronic Obstructive Pulmonary Disease: Exercise and Physical Activity Interventions in Cystic Fibrosis and Non-Cystic Fibrosis Bronchiectasis

Burtin, C., & Hebestreit, H. U. (2015) · Respiration · doi:10.1159/000375170 · Cited by 65 · see citing works

New horizons for cystic fibrosis treatment

Fajac, I., & Boeck, K. D. (2016) · Pharmacology & Therapeutics · doi:10.1016/j.pharmthera.2016.11.009 · Cited by 58 · see citing works

Prevalence, geographic risk factor, and development of a standardized protocol for fungal isolation in cystic fibrosis: Results from the international prospective study “MFIP”

Delhaès, L., Touati, K., Faure-Cognet, O., Cornet, M., Botterel, F., Dannaoui, É., Morio, F., Pape, P. L., Grenouillet, F., Favennec, L., et al. (2018) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2018.10.001 · Cited by 52 · see citing works

User Needs in the Development of a Health App Ecosystem for Self-Management of Cystic Fibrosis: User-Centered Development Approach

Floch, J., Zettl, A., Fricke, L., Weisser, T., Grut, L., Vilarinho, T., Stav, E., Ascolese, A., & Schauber, C. (2018) · JMIR mhealth and uhealth · doi:10.2196/mhealth.8236 · Cited by 51 · see citing works

State-of-the-art review of lung imaging in cystic fibrosis with recommendations for pulmonologists and radiologists from the “iMAging managEment of cySTic fibROsis” (MAESTRO) consortium

Ciet, P., Bertolo, S., Ros, M., Casciaro, R., Cipolli, M., Colagrande, S., Costa, S., Galici, V., Gramegna, A., Lanza, C., et al. (2022) · European Respiratory Review · doi:10.1183/16000617.0173-2021 · Cited by 52 · see citing works

A web-based psychological support program for caregivers of children with cystic fibrosis: a pilot study

Fidika, A., Herle, M., Lehmann, C., Weiss, C., Knaevelsrud, C., & Goldbeck, L. (2015) · Health and Quality of Life Outcomes · doi:10.1186/s12955-015-0211-y · Cited by 50 · see citing works

Cystic fibrosis foundation position paper: Redefining the cystic fibrosis care team

Brown, R. F., Close, C. T., Mailes, M. G., Gonzalez, L. J., Goetz, D., Filigno, S. S., Preslar, R., Tran, Q. T., Hempstead, S. E., Lomas, P., et al. (2024) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2024.09.011 · Cited by 49 · see citing works

Standards for the care of people with cystic fibrosis (CF); Planning for a longer life

Gramegna, A., Addy, C., Allen, L. J., Bakkeheim, E., Brown, C., Daniels, T. W. V., Davies, G., Davies, J. C., Marie, K. D., Downey, D. G., et al. (2024) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2024.05.007 · Cited by 44 · see citing works

A randomised, double-blind, placebo-controlled trial of repeated nebulisation of non-viral cystic fibrosis transmembrane conductance regulator (CFTR) gene therapy in patients with cystic fibrosis

Alton, E. W. F. W., Armstrong, D. K., Ashby, D., Bayfield, K. J., Bilton, D., Bloomfield, E. V., Boyd, A., Brand, J., Buchan, R., Calcedo, R., et al. (2016) · Efficacy and Mechanism Evaluation · doi:10.3310/eme03050 · Cited by 44 · see citing works

Chemoattractants and cytokines in primary ciliary dyskinesia and cystic fibrosis: key players in chronic respiratory diseases

Cockx, M., Gouwy, M., Damme, J. V., & Struyf, S. (2017) · Cellular and Molecular Immunology · doi:10.1038/cmi.2017.118 · Cited by 42 · see citing works

Organization of Patient Management and Fungal Epidemiology in Cystic Fibrosis

Schwarz, C., Bouchara, J.-P., Buzina, W., Chrenková, V., Dmeńska, H., de la Pedrosa, E. G. G., Cantón, R., Fiscarelli, E. V., Govic, Y. L., Kondori, N., et al. (2017) · Mycopathologia · doi:10.1007/s11046-017-0205-x · Cited by 41 · see citing works

Medical consensus, guidelines, and position papers: A policy for the ECFS

Boeck, K. D., Castellani, C., & Elborn, J. S. (2014) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2014.06.012 · Cited by 40 · see citing works

Interventions for promoting participation in shared decision-making for children and adolescents with cystic fibrosis

Malone, H., Biggar, S., Javadpour, S., Edworthy, Z., Sheaf, G., & Coyne, I. (2019) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd012578.pub2 · Cited by 39 · see citing works

Treatment of Pulmonary Disease of Cystic Fibrosis: A Comprehensive Review

Moreno, R. M. G., Clemente, M. M. G., Diab-Cáceres, L., Martínez-Vergara, A., Martínez‐García, M. Á., & Gómez-Punter, R. M. (2021) · Antibiotics · doi:10.3390/antibiotics10050486 · Cited by 35 · see citing works

Pain and its clinical associations in individuals with cystic fibrosis

Lee, A. L., Rawlings, S. L., Bennett, K. A., & Armstrong, D. (2016) · Chronic Respiratory Disease · doi:10.1177/1479972316631135 · Cited by 35 · see citing works

Newborn screening for cystic fibrosis

Mérelle, M. E., Dankert-Roelse, J., Dezateux, C. A., Lees, C., Nagelkerke, A. F., & Southern, K. W. (2001) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd001402 · Cited by 33 · see citing works

Users’ Experiences of a Mobile Health Self-Management Approach for the Treatment of Cystic Fibrosis: Mixed Methods Study

Floch, J., Vilarinho, T., Zettl, A., Ibáñez-Sánchez, G., Calvo‐Lerma, J., Stav, E., Haro, P. H., Aalberg, A. L., Fides-Valero, Á., & Bayo-Montón, J.-L. (2020) · JMIR mhealth and uhealth · doi:10.2196/15896 · Cited by 31 · see citing works

Bronchopulmonary infection–colonization patterns in Spanish cystic fibrosis patients: Results from a national multicenter study

Caballero, J. D. D., del Campo, R., Royuela, A., Solé, A., Máiz, L., Olveira, C., Quintana‐Gallego, E., de Gracia, J., Cobo, M., de la Pedrosa, E. G. G., et al. (2015) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2015.09.004 · Cited by 28 · see citing works

Perception of first respiratory infection with Pseudomonas aeruginosa by people with cystic fibrosis and those close to them: an online qualitative study

Palser, S. C., Rayner, O., Leighton, P. A., & Smyth, A. R. (2016) · BMJ Open · doi:10.1136/bmjopen-2016-012303 · Cited by 26 · see citing works

Insights into the cystic fibrosis care in Eastern Europe: Results of survey

Walicka‐Serzysko, K., Pecková, M., Noordhoek, J. J., Sands, D., & Dřevı́nek, P. (2018) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2018.04.003 · Cited by 26 · see citing works

Real life practice of sweat testing in Europe

Cirilli, N., Southern, K. W., Buzzetti, R., Barben, J., Naehrlich, L., Munck, À., Wilschanski, M. A., Boeck, K. D., & Derichs, N. (2017) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2017.09.002 · Cited by 25 · see citing works

Chest radiography and computed tomography imaging in cystic fibrosis: current challenges and new perspectives

Ciet, P., Booij, R., Dijkshoorn, M. L., van Straten, M., & Tiddens, H. A. W. M. (2022) · Pediatric Radiology · doi:10.1007/s00247-022-05522-4 · Cited by 25 · see citing works

Limitations to providing adult cystic fibrosis care in Europe: Results of a care centre survey

Madge, S. L., Bell, S. C., Burgel, P., Rijcke, K. D., Blasi, F., & Elborn, J. S. (2016) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2016.07.001 · Cited by 25 · see citing works

Cystic Fibrosis Diagnosis in Newborns, Children, and Adults

Castellani, C., Linnane, B. M., Pranke, I. M., Cresta, F., Sermet‐Gaudelus, I., & Peckham, D. G. (2019) · Seminars in Respiratory and Critical Care Medicine · doi:10.1055/s-0039-1697961 · Cited by 25 · see citing works

Videogames in the Treatment of Obstructive Respiratory Diseases: A Systematic Review

Torres‐Sánchez, I., Salmerón, Y. M., López, L. L., Ortíz‐Rubio, A., Rodríguez‐Torres, J., & Valenza, M. C. (2019) · Games for Health Journal · doi:10.1089/g4h.2018.0062 · Cited by 24 · see citing works

Standards of care guidance for sweat testing; phase two of the ECFS quality improvement programme

Cirilli, N., Southern, K. W., Barben, J., Vermeulen, F. L., Munck, À., Wilschanski, M. A., Nguyen‐Khoa, T., Aralica, M., Simmonds, N. J., & Wachter, E. D. (2022) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2022.01.004 · Cited by 23 · see citing works

Clinical outcomes of adults and children with cystic fibrosis during the COVID-19 pandemic

Doumit, M., Chuang, S., Middleton, P. G., Selvadurai, H. C., Sivam, S., Ruseckaite, R., Ahern, S., Mallitt, K., Pacey, V., Gray, K., et al. (2022) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2022.09.006 · Cited by 22 · see citing works

Hypertonic saline in patients with primary ciliary dyskinesia: on the road to evidence-based treatment for a rare lung disease

Kuehni, C. E., Goutaki, M., & Kobbernagel, H. E. (2017) · European Respiratory Journal · doi:10.1183/13993003.02514-2016 · Cited by 22 · see citing works

Interventions for promoting participation in shared decision-making for children and adolescents with cystic fibrosis

Malone, H., Biggar, S., Javadpour, S., Edworthy, Z., Sheaf, G., & Coyne, I. (2017) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd012578 · Cited by 21 · see citing works

Economic Burden And Health-Related Quality Of Life Of Patients With Cystic Fibrosis In Bulgaria

Iskrov, G. G., Stefanov, R. S., López‐Bastida, J., Linertová, R., Oliva, J., & Serrano-Aguilar, P. G. (2015) · Folia Medica · doi:10.1515/folmed-2015-0020 · Cited by 20 · see citing works

The Potential of Self-Management mHealth for Pediatric Cystic Fibrosis: Mixed-Methods Study for Health Care and App Assessment

Martínez-Millana, A., Zettl, A., Floch, J., Calvo‐Lerma, J., Sevillano, J. L., Ribes‐Koninckx, C., & Traver, V. (2019) · JMIR mhealth and uhealth · doi:10.2196/13362 · Cited by 19 · see citing works

OUP accepted manuscript

Jackson, A. D., Kirwan, L., Gibney, S., Jeleniewska, P., Fletcher, G., & Doyle, G. (2019) · European Journal of Public Health · doi:10.1093/eurpub/ckz148 · Cited by 19 · see citing works

Systematic Review of Postural Assessment in Individuals With Obstructive Respiratory Conditions

Lee, A. L., Zabjek, K., Goldstein, R. S., & Brooks, D. (2016) · Journal of Cardiopulmonary Rehabilitation and Prevention · doi:10.1097/hcr.0000000000000207 · Cited by 17 · see citing works

Diffusion weighted imaging in cystic fibrosis disease: beyond morphological imaging

Ciet, P., Serra, G., Andrinopoulou, E. R., Bertolo, S., Ros, M., Catalano, C., Colagrande, S., Tiddens, H. A. W. M., & Morana, G. (2016) · European Radiology · doi:10.1007/s00330-016-4248-z · Cited by 17 · see citing works

Standard (head-down tilt) versus modified (without head-down tilt) postural drainage in infants and young children with cystic fibrosis

de Freitas, D. A., Dias, F. A., Chaves, G. S., Ferreira, G. M., Ribeiro, C. T., Guerra, R. O., & de Mendonça, K. M. P. P. (2015) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd010297.pub2 · Cited by 16 · see citing works

Adult Care in Cystic Fibrosis

Elborn, J. S. (2019) · Seminars in Respiratory and Critical Care Medicine · doi:10.1055/s-0039-3400289 · Cited by 16 · see citing works

Tobramycin and Beta-Lactam Antibiotic Use in Cystic Fibrosis Exacerbations: A Pharmacist Approach

Zobell, J. T., Epps, K. L., Kittell, F., Sema, C. M., McDade, E. J., Peters, S. J., Duval, M. A., & Pettit, R. S. (2016) · The Journal of Pediatric Pharmacology and Therapeutics · doi:10.5863/1551-6776-21.3.239 · Cited by 15 · see citing works

Vancomycin Dosing and Monitoring in the Treatment of Cystic Fibrosis: Results of a National Practice Survey

Pettit, R. S., Peters, S. J., McDade, E. J., Kreilein, K., Patel, R., Epps, K. L., Kittell, F., Duval, M. A., & Zobell, J. T. (2017) · The Journal of Pediatric Pharmacology and Therapeutics · doi:10.5863/1551-6776-22.6.406 · Cited by 15 · see citing works

Ventilatory limitation and dynamic hyperinflation during exercise testing in Cystic Fibrosis

Karapanagiotis, S., Gambazza, S., Brivio, A., D’Abrosca, F., & Colombo, C. (2016) · Pediatric Pulmonology · doi:10.1002/ppul.23572 · Cited by 14 · see citing works

Cystic fibrosis – Ten promising therapeutic approaches in the current era of care

Somayaji, R., Nichols, D. P., & Bell, S. C. (2020) · Expert Opinion on Investigational Drugs · doi:10.1080/13543784.2020.1805733 · Cited by 14 · see citing works

Psychosocial needs and interventions for young children with cystic fibrosis and their families

Li, S., Douglas, T. A., & Fitzgerald, D. A. (2023) · Paediatric Respiratory Reviews · doi:10.1016/j.prrv.2023.04.002 · Cited by 13 · see citing works

Strategies used to access CFTR modulators in countries without reimbursement agreements

Guo, J., Hennessy, G., Young, B., & Hill, A. M. (2025) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2025.02.010 · Cited by 13 · see citing works

Telemedicine in the management of patients with chronic respiratory failure

Shah, N. M., & Kaltsakas, G. (2021) · Breathe · doi:10.1183/20734735.0008-2021 · Cited by 13 · see citing works

Physiological markers of exercise capacity and lung disease severity in cystic fibrosis

Smith, L., Reilly, C. C., MacBean, V., Jolley, C. J., Elston, C. M., Moxham, J., & Rafferty, G. F. (2016) · Respirology · doi:10.1111/resp.12954 · Cited by 13 · see citing works

“Thrust out of normality”—How adults living with cystic fibrosis experience pulmonary exacerbations: A qualitative study

Schmid‐Mohler, G., Caress, A., Spirig, R., Benden, C., & Yorke, J. (2018) · Journal of Clinical Nursing · doi:10.1111/jocn.14646 · Cited by 13 · see citing works

Management of Cystic Fibrosis during COVID-19: Patient Reported Outcomes based remote follow-up among CF patients in Denmark – A feasibility study

Rodkjær, L. Ø., Jeppesen, M., & Schougaard, L. M. V. (2021) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2021.10.010 · Cited by 13 · see citing works

Comparison of health-related quality of life among children with cystic fibrosis and their parents in two Eastern European countries

Borawska-Kowalczyk, U., Bodnár, R., Mészáros, Á., & Sands, D. (2015) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2015.03.008 · Cited by 13 · see citing works

Standards for the care of people with cystic fibrosis (CF)

Southern, K. W., Burgel, P., Castellani, C., Boeck, K. D., Davies, J. C., Dunlevy, F., Fajac, I., Gramegna, A., Lammertyn, E. J., Middleton, P. G., et al. (2023) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2023.09.009 · Cited by 13 · see citing works

Perceived burden of respiratory physiotherapy in people with cystic fibrosis taking elexacaftor–tezacaftor–ivacaftor combination: a 1-year observational study

Blardone, C., Gambazza, S., Mariani, A., Galgani, R., Brivio, A., Nobili, R., Rizza, C., Tutino, A. L., Gramegna, A., Daccò, V., et al. (2024) · Therapeutic Advances in Respiratory Disease · doi:10.1177/17534666241235054 · Cited by 14 · see citing works

Burkholderia cepacia complex in Serbian patients with cystic fibrosis: prevalence and molecular epidemiology

Vasiljevic, Z. V., Novović, K., Kojić, M., Minic, P. B., Sovtić, A., Djukić, S., & Jovčić, B. (2016) · European Journal of Clinical Microbiology & Infectious Diseases · doi:10.1007/s10096-016-2662-4 · Cited by 12 · see citing works

The effectiveness of exercise interventions to increase physical activity in Cystic Fibrosis: A systematic review

Curran, M., Tierney, A. C., Button, B., Collins, L., Kennedy, L., McDonnell, C., Casserly, B. P., & Cahalan, R. (2021) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2021.10.008 · Cited by 12 · see citing works

Current Practices and Potential Nanotechnology Perspectives for Pain Related to Cystic Fibrosis

Trandafir, L. M., Leon, M. M., Frăsinariu, O. E., Baciu, G., Dodi, G., & Cojocaru, E. (2019) · Journal of Clinical Medicine · doi:10.3390/jcm8071023 · Cited by 12 · see citing works

Standard (head-down tilt) versus modified (without head-down tilt) postural drainage in infants and young children with cystic fibrosis

de Freitas, D. A., Chaves, G. S., Santino, T. A., Ribeiro, C. T., Dias, F. A., Guerra, R. O., & de Mendonça, K. M. P. P. (2018) · Cochrane Database of Systematic Reviews · doi:10.1002/14651858.cd010297.pub3 · Cited by 12 · see citing works

Electronic home monitoring of children with cystic fibrosis to detect and treat acute pulmonary exacerbations and its effect on 1-year FEV1

Yanaz, M., Yeğit, C. Y., Gulieva, A., Kalyoncu, M., Selçuk, M., Uzunoğlu, B., Taştan, G., Ergenekon, P., Gökdemi̇r, Y., Eralp, E. E., et al. (2023) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2023.09.007 · Cited by 11 · see citing works

Exploring the Potential for Technology to Improve Cystic Fibrosis Care Provision

Rodger, S., & O'Hara, K. P. (2019) · Proceedings of the ACM on Human-Computer Interaction · doi:10.1145/3359223 · Cited by 12 · see citing works

Best practice standards for the delivery of NHS infection services in the United Kingdom

Ratnaraja, N., Davies, A. P., Atkins, B. L., Dhillon, R., Mahida, N., Moses, S. E., Herman, J., Checkley, A. M., Partridge, D. G., & Llewelyn, M. (2021) · Clinical Infection in Practice · doi:10.1016/j.clinpr.2021.100095 · Cited by 11 · see citing works

The prevalence of CFTR mutations in patients with chronic rhinosinusitis: A systematic review and meta‐analysis

Yong, M., Hernaiz‐Leonardo, J. C., Alqunaee, M., Quon, B. S., & Javer, A. R. (2021) · Clinical Otolaryngology · doi:10.1111/coa.13875 · Cited by 10 · see citing works

Microbiological diagnostic procedures for respiratory cystic fibrosis samples in Spain: towards standard of care practices

Caballero, J. D. D., del Campo, R., Tato, M., de la Pedrosa, E. G. G., Cobo, M., López-Causapé, C., Gómez-Mampaso, E., Oliver, A., Cantón, R., & Spanish Network for Cystic Fibrosis Microbiology Laboratories (2014) · BMC Microbiology · doi:10.1186/s12866-014-0335-y · Cited by 10 · see citing works

Evaluation of Home Medication Reconciliation by Clinical Pharmacists for Adult and Pediatric Cystic Fibrosis Patients

Louie, J. M., Hong, L. T., Garavaglia, L. R., Pinal, D. I., & O’Brien, C. E. (2018) · Pharmacy · doi:10.3390/pharmacy6030091 · Cited by 10 · see citing works

Adults with cystic fibrosis and pulmonologists: new training needed to recruit future specialists

Blasi, F., Elborn, J. S., & Palange, P. (2019) · European Respiratory Journal · doi:10.1183/13993003.02209-2018 · Cited by 10 · see citing works

Patient care in cystic fibrosis centers: a real-world analysis in Brazil

Procianoy, E. D. F. A., Neto, N. L., & Ribeiro, A. F. (2023) · Jornal Brasileiro de Pneumologia · doi:10.36416/1806-3756/e20220306 · Cited by 9 · see citing works

The Airway Colonization by Opportunistic Filamentous Fungi in Patients with Cystic Fibrosis: Recent Updates

Touati, K., Nguyen, D. N. L., & Delhaès, L. (2014) · Current Fungal Infection Reports · doi:10.1007/s12281-014-0197-7 · Cited by 9 · see citing works

Associations between genetics, medical status, physical exercise and psychological well-being in adults with cystic fibrosis

Backström-Eriksson, L., Brucefors, A. B., Hjelte, L., Melin, B., & Sorjonen, K. (2016) · BMJ Open Respiratory Research · doi:10.1136/bmjresp-2016-000141 · Cited by 9 · see citing works

A Cross-Sectional Study of the Psychological Needs of Adults Living with Cystic Fibrosis

Pakhale, S. S., Baron, J., Armstrong, M. B., Tasca, G. A., Gaudet, E., Aaron, S. D., Cameron, D. W., & Balfour, L. (2015) · PLoS ONE · doi:10.1371/journal.pone.0127944 · Cited by 9 · see citing works

Implementation of standardized cystic fibrosis care algorithm to improve the center data-quality improvement project international collaboration

Gökdemi̇r, Y., Eralp, E. E., Ergenekon, P., Yeğit, C. Y., Yanaz, M., Mursaloglu, H. H., Uzunoğlu, B., Kocamaz, D., Taştan, G., Keniş-Coşkun, Ö., et al. (2023) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2023.03.016 · Cited by 8 · see citing works

Was ist gesichert in der Therapie der Mukoviszidose?

Ringshausen, F. C., Hellmuth, T., & Dittrich, A.-M. (2020) · Der Internist · doi:10.1007/s00108-020-00896-9 · Cited by 8 · see citing works

Exploring the need for Transition Readiness Scales within cystic fibrosis services: A qualitative descriptive study

Bourke, M., & Houghton, C. (2018) · Journal of Clinical Nursing · doi:10.1111/jocn.14344 · Cited by 8 · see citing works

The International Depression Epidemiological Study (TIDES): unfinished business?

Webb, A. K., & Bryon, M. (2014) · Thorax · doi:10.1136/thoraxjnl-2014-206200 · Cited by 8 · see citing works

European cystic fibrosis society standards of care: A road map to improve CF outcome

Kerem, E., & Webb, A. K. (2014) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2014.05.003 · Cited by 8 · see citing works

Evaluation of ChatGPT-4 responses on physical activity guidance in children with cystic fibrosis: reliability, quality, and readability

Çelik, Z., & Sarı, F. (2025) · European Journal of Pediatrics · doi:10.1007/s00431-025-06488-9 · Cited by 7 · see citing works

Adherence to chest physiotherapy, airway clearance techniques and physical exercise by children and adolescents with cystic fibrosis

Modolo, L., Uliana, L. B., Liberato, F. M. G., Arpini, L. D. S. B., Santuzzi, C. H., Melotti, R. D. C. N. C., & Paro, F. M. (2024) · Journal of Human Growth and Development · doi:10.36311/jhgd.v34.15779 · Cited by 7 · see citing works

A model for active and healthy ageing with a rare genetic disease: cystic fibrosis

Chiron, R., Caimmi, D. P., Valiulis, A., Durieu, I., Tejedor, P., Cam, Y. L., Boudes, M., Jonquet, O., Strandberg, T. E., Michel, J., et al. (2016) · European Respiratory Journal · doi:10.1183/13993003.01237-2015 · Cited by 7 · see citing works

Adherence to infection prevention and control guidelines: A vignette-based study of decision-making and risk-taking in young adults with cystic fibrosis

Bowmer, G., Latchford, G. J., Duff, A. J. A., Denton, M., Dye, L., Lawton, C. L., & Lee, T. (2016) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2016.09.001 · Cited by 7 · see citing works

EnVisioning the future: Endocrinology in cystic fibrosis

Brennan, A. L., & Blackman, S. M. (2019) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2019.09.012 · Cited by 7 · see citing works

Availability of CFTR modulators in countries of Eastern Europe: The reality in 2022

Dřevı́nek, P., Stepankova, K., Woźniacki, Ł., Halász, A., Petrova, G., Makukh, H., Belinska, A., & Sands, D. (2022) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2022.08.014 · Cited by 6 · see citing works

Automated tube voltage selection in pediatric non-contrast chest CT

Hojreh, A., Homolka, P., Gamper, J., Unterhumer, S., Kienzl, D., Balássy, C., Wrba, T., & Prosch, H. (2018) · PLoS ONE · doi:10.1371/journal.pone.0204794 · Cited by 6 · see citing works

Microbiological evaluation of UV disinfection effectiveness in a specialist cystic fibrosis clinic

Allen, O., Jadkauskaite, L., Shafi, N., Jackson, A., Athithan, V., Chiu, Y., Evans, I., Floto, R. A., & HAWORTH, C. S. (2019) · Journal of Cystic Fibrosis · doi:10.1016/j.jcf.2019.04.019 · Cited by 6 · see citing works

Primary ciliary dyskinesia: the patients grow up

Kuehni, C. E., Goutaki, M., Carroll, M., & Lucas, J. S. (2016) · European Respiratory Journal · doi:10.1183/13993003.01098-2016 · Cited by 6 · see citing works

Role of pharmacists in the context of rare diseases: a scoping review protocol

Cunico, C., & Leite, S. N. (2023) · BMJ Open · doi:10.1136/bmjopen-2023-072001 · Cited by 5 · see citing works

Parent's report on oral health‐related quality of life of children with cystic fibrosis

Sisman, H. I., Peker, S., Gökdemi̇r, Y., Eralp, E. E., Karadag, B. T., & Kargül, B. (2022) · Pediatric Pulmonology · doi:10.1002/ppul.26191 · Cited by 5 · see citing works

Aerosol delivery practice in Italian Cystic Fibrosis centres: a national survey

Gambazza, S., Carta, F., Brivio, A., & Colombo, C. (2016) · Archives of Physiotherapy · doi:10.1186/s40945-016-0015-3 · Cited by 5 · see citing works

- Cystic fibrosis center care

Madge, S. L., Francis, J., & Bilton, D. (2015) · CRC Press eBooks · doi:10.1201/b18629-50

Adults with Cystic Fibrosis Should be Treated at a Specialist Centre

Jones, A. M. (2013) · Paediatric Respiratory Reviews · doi:10.1016/j.prrv.2013.01.009 · Cited by 5 · see citing works

Standardy opieki Europejskiego Towarzystwa Mukowiscydozy: zarys kształtu centrum mukowiscydozy

Conway, S., Balfour-Lynn, I. M., Rijcke, K. D., Dřevı́nek, P., Foweraker, J. E., Havermans, T., Heijerman, H. G. M., Lannefors, L., Lindblad, A., Maçek, M., et al. (2016) · Pediatria Polska · doi:10.1016/j.pepo.2016.08.018

Centre care of cystic fibrosis improves clinical outcome

(1998) · BMJ · doi:10.1136/bmj.316.7147.0a

The cystic fibrosis team

Thomson, A. H., & Harris, A. (2008) · doi:10.1093/oso/9780199295807.003.0006