ALS/FTD mutations in UBQLN2 impede autophagy by reducing autophagosome acidification through loss of function

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UBQLN2 Mediates Autophagy-Independent Protein Aggregate Clearance by the Proteasome

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Ubiquilins Chaperone and Triage Mitochondrial Membrane Proteins for Degradation

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Ubiquilin 2 modulates ALS/FTD-linked FUS–RNA complex dynamics and stress granule formation

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Ubiquilin-1 Is a Molecular Chaperone for the Amyloid Precursor Protein*

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Dendritic spinopathy in transgenic mice expressing ALS/dementia-linked mutant UBQLN2

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Pathogenic Ubqln2 gains toxic properties to induce neuron death

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A novel ALS-associated variant in UBQLN4 regulates motor axon morphogenesis

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Structure of hRpn10 Bound to UBQLN2 UBL Illustrates Basis for Complementarity between Shuttle Factors and Substrates at the Proteasome

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Striking phenotypic variation in a family with the P506S UBQLN2 mutation including amyotrophic lateral sclerosis, spastic paraplegia, and frontotemporal dementia

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