Mastocytosis: The puzzling clinical spectrum and challenging diagnostic aspects of an enigmatic disease

Diagnostic criteria and classification of mastocytosis: a consensus proposal

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Mast cell secretory granules: armed for battle

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Mast cell-orchestrated immunity to pathogens

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Identification of a point mutation in the catalytic domain of the protooncogene c-kit in peripheral blood mononuclear cells of patients who have mastocytosis with an associated hematologic disorder.

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Identification of mutations in the coding sequence of the proto-oncogene c-kit in a human mast cell leukemia cell line causing ligand-independent activation of c-kit product.

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Tryptase levels as an indicator of mast-cell activation in systemic anaphylaxis and mastocytosis

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Standards and standardization in mastocytosis: consensus statements on diagnostics, treatment recommendations and response criteria

Valent, P., Akin, C., Escribano, L., Födinger, M., Hartmann, K., Brockow, K., Castells, M., Sperr, W. R., Kluin‐Nelemans, H. C., Hamdy, N. A. T., et al. (2007) · European Journal of Clinical Investigation · doi:10.1111/j.1365-2362.2007.01807.x · Cited by 750 · see citing works

Definitions, criteria and global classification of mast cell disorders with special reference to mast cell activation syndromes: a consensus proposal

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Structural Basis for the Autoinhibition and STI-571 Inhibition of c-Kit Tyrosine Kinase

Mol, C. D., Dougan, D. R., Schneider, T. R., Skene, R. J., Kraus, M. L., Scheibe, D. N., Snell, G., Zou, H., Sang, B., & Wilson, K. P. (2004) · Journal of Biological Chemistry · doi:10.1074/jbc.m403319200 · Cited by 634 · see citing works

Systemic mastocytosis in 342 consecutive adults: survival studies and prognostic factors

Lim, K., Tefferi, A., Lasho, T. L., Finke, C. M., Patnaik, M. M., Butterfield, J. H., McClure, R. F., Li, C., & Pardanani, A. D. (2009) · Blood · doi:10.1182/blood-2009-02-205237 · Cited by 585 · see citing works

Mast cells and mastocytosis

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Anaphylaxis in patients with mastocytosis: a study on history, clinical features and risk factors in 120 patients

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Systemic Mast Cell Disease

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Epidemiology of anaphylaxis: findings of the American College of Allergy, Asthma and Immunology Epidemiology of Anaphylaxis Working Group

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Increased production of prostaglandin D2 in patients with systemic mastocytosis

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Pediatric mastocytosis is a clonal disease associated with D816V and other activating c-KIT mutations

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Clonal mast cell disorders in patients with systemic reactions to Hymenoptera stings and increased serum tryptase levels

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A novel form of mastocytosis associated with a transmembrane c-kit mutation and response to imatinib

Akin, C., Fumo, G., Yavuz, A. S., Lipsky, P. E., Neckers, L., & Metcalfe, D. D. (2003) · Blood · doi:10.1182/blood-2003-11-3816 · Cited by 359 · see citing works

Classification and Diagnosis of Mastocytosis: Current Status

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Mast cell activation syndrome: Proposed diagnostic criteria

Akin, C., Valent, P., & Metcalfe, D. D. (2010) · Journal of Allergy and Clinical Immunology · doi:10.1016/j.jaci.2010.08.035 · Cited by 327 · see citing works

Prevalence and Functional Role of Anti-IgE Autoantibodies in Urticarial Syndromes

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Clinical, biological, and molecular characteristics of clonal mast cell disorders presenting with systemic mast cell activation symptoms

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Prognosis in adult indolent systemic mastocytosis: A long-term study of the Spanish Network on Mastocytosis in a series of 145 patients

Escribano, L., Álvarez‐Twöse, I., Sánchez‐Muñoz, L., García‐Montero, A. C., Núñez, R., Almeida, J., Jara‐Acevedo, M., Teodósio, C., García‐Cosío, M., Bellas, C., et al. (2009) · Journal of Allergy and Clinical Immunology · doi:10.1016/j.jaci.2009.05.003 · Cited by 290 · see citing works

The mast cell and allergic diseases: role in pathogenesis and implications for therapy

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Mast cells and mast cell neoplasia: a review*

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Comprehensive mutational profiling in advanced systemic mastocytosis

Schwaab, J., Schnittger, S., Sotlar, K., Walz, C., Fabarius, A. C., Pfirrmann, M., Kohlmann, A., Großmann, V., Meggendorfer, M., Horny, H., et al. (2013) · Blood · doi:10.1182/blood-2013-04-496448 · Cited by 262 · see citing works

Frequent TET2 mutations in systemic mastocytosis: clinical, KITD816V and FIP1L1-PDGFRA correlates

Tefferi, A., Levine, R., Lim, K., Abdel-Wahab, O., Lasho, T., Patel, J., Finke, C., Mullally, A., Li, C.-Y., Pardanani, A., et al. (2009) · Leukemia · doi:10.1038/leu.2009.37 · Cited by 251 · see citing works

Indolent Systemic Mast Cell Disease in Adults: Immunophenotypic Characterization of Bone Marrow Mast Cells and Its Diagnostic Implications

Escribano, L., Órfão, A., Dı́az-Agustı́n, B., Villarrubia, J., Cerveró, C. J., López, A., Marcos, M. A. G., Bellas, C., FERNANDEZCANADAS, S., Cuevas, M., et al. (1998) · Blood · doi:10.1182/blood.v91.8.2731.2731_2731_2736 · Cited by 250 · see citing works

Prevalence of allergy and anaphylactic symptoms in 210 adult and pediatric patients with mastocytosis in Spain: a study of the Spanish network on mastocytosis (REMA)

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Activity of the tyrosine kinase inhibitor PKC412 in a patient with mast cell leukemia with the D816V KIT mutation

Gotlib, J. R. (2005) · Blood · doi:10.1182/blood-2005-04-1568 · Cited by 242 · see citing works

Demonstration of an aberrant mast-cell population with clonal markers in a subset of patients with “idiopathic” anaphylaxis

Akin, C., Scott, L. M., Kocabas, C. N., Kushnir-Sukhov, N., Brittain, E., Noel, P., & Metcalfe, D. D. (2007) · Blood · doi:10.1182/blood-2006-06-028100 · Cited by 240 · see citing works

Epidemiology of systemic mastocytosis in Denmark

Cohen, S. S., Skovbo, S., Vestergaard, H., Kristensen, T. K., Møller, M. B., Bindslev‐Jensen, C., Fryzek, J. P., & Broesby‐Olsen, S. (2014) · British Journal of Haematology · doi:10.1111/bjh.12916 · Cited by 235 · see citing works

Aggressive systemic mastocytosis and related mast cell disorders: current treatment options and proposed response criteria

Valent, P. (2003) · Leukemia Research · doi:10.1016/s0145-2126(02)00168-6 · Cited by 233 · see citing works

Diagnosis of mastocytosis: general histopathological aspects, morphological criteria, and immunohistochemical findings

Horny, H., & Valent, P. (2001) · Leukemia Research · doi:10.1016/s0145-2126(01)00021-2 · Cited by 228 · see citing works

Diagnostic Value of Immunostaining for Tryptase in Patients With Mastocytosis

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Oral Disodium Cromoglycate in the Treatment of Systemic Mastocytosis

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Effects of tyrosine kinase inhibitor STI571 on human mast cells bearing wild-type or mutated c-kit

Akin, C., Brockow, K., D’Ambrosio, C., Kirshenbaum, A. S., Ma, Y., Longley, B. J., & Metcalfe, D. D. (2003) · Experimental Hematology · doi:10.1016/s0301-472x(03)00112-7 · Cited by 225 · see citing works

Systemic Mastocytosis

Akin, C., & Metcalfe, D. D. (2004) · Annual Review of Medicine · doi:10.1146/annurev.med.55.091902.103822 · Cited by 215 · see citing works

Recent advances in the understanding of mastocytosis: the role of KIT mutations*

Órfão, A., García‐Montero, A. C., Sánchez‐Muñoz, L., & Escribano, L. (2007) · British Journal of Haematology · doi:10.1111/j.1365-2141.2007.06619.x · Cited by 211 · see citing works

One-Step Detection of c-kit Point Mutations Using Peptide Nucleic Acid-Mediated Polymerase Chain Reaction Clamping and Hybridization Probes

Sotlar, K., Escribano, L., Landt, O., Möhrle, S., Herrero, S., Torrelo, A., Laß, U., Horny, H., & Bültmann, B. D. (2003) · American Journal Of Pathology · doi:10.1016/s0002-9440(10)63870-9 · Cited by 207 · see citing works

Fatal anaphylaxis after a yellow jacket sting, despite venom immunotherapy, in two patients with mastocytosis

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Mastocytosis: Pathology, genetics, and current options for therapy

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Systemic mast cell disease: A clinical and hematopathologic study of 26 cases

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Hematopoietic Stem-Cell Transplantation for Advanced Systemic Mastocytosis

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Mast cell leukemia

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CD25 Indicates the Neoplastic Phenotype of Mast Cells

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Omalizumab for the treatment of unprovoked anaphylaxis in patients with systemic mastocytosis

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Cromolyn sodium in the management of systemic mastocytosis

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Systemic mastocytosis with associated clonal haematological non-mast cell lineage diseases: a histopathological challenge

Horny, H. ‐., Sotlar, K., Sperr, W. R., & Valent, P. (2004) · Journal of Clinical Pathology · doi:10.1136/jcp.2003.014860 · Cited by 163 · see citing works

The Mastocytosis Syndrome: Clinical and Biological Studies

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Systemic mastocytosis and bone involvement in a cohort of 75 patients

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Treatment of Systemic Mast-Cell Disease with Cladribine

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Pathogenesis, classification and treatment of mastocytosis: state of the art in 2010 and future perspectives

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Pediatric Mastocytosis

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High prevalence of anaphylaxis in patients with systemic mastocytosis - a single-centre experience

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A new c‐kit mutation in a case of aggressive mast cell disease

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Urticaria pigmentosa; a report of a case with autopsy.

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Immunophenotypic analysis of mast cells in mastocytosis: When and how to do it. Proposals of the Spanish Network on Mastocytosis (REMA)

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Urticaria Pigmentosa: A Review of 67 Pediatric Cases

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Molecular targets on mast cells and basophils for novel therapies

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TREATMENT OF SYSTEMIC MAST CELL DISORDERS

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Mast cell activation syndrome: A newly recognized disorder with systemic clinical manifestations

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The biology of Kit in disease and the application of pharmacogenetics

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Mastocytosis (Mast Cell Disease)

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NTAL phosphorylation is a pivotal link between the signaling cascades leading to human mast cell degranulation following Kit activation and Fc RI aggregation

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Safety and effectiveness of immunotherapy in patients with indolent systemic mastocytosis presenting with Hymenoptera venom anaphylaxis

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Diagnostic and subdiagnostic accumulation of mast cells in the bone marrow of patients with anaphylaxis: monoclonal mast cell activation syndrome

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Refined diagnostic criteria and classification of mast cell leukemia (MCL) and myelomastocytic leukemia (MML): a consensus proposal

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Diagnostic Criteria and Classification of Mastocytosis in 2014

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Mast cell activation syndromes: definition and classification

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Bone mineral density, bone turnover markers and fractures in patients with indolent systemic mastocytosis

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Single Nucleotide Polymorphism Array Lesions, TET2, DNMT3A, ASXL1 and CBL Mutations Are Present in Systemic Mastocytosis

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Immunohistochemical properties of bone marrow mast cells in systemic mastocytosis: Evidence for expression of CD2, CD117/Kit, and bcl-xL

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Comparison of the therapeutic efficacy of cromolyn sodium with that of combined chlorpheniramine and cimetidine in systemic mastocytosis. Results of a double-blind clinical trial

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ASPIRIN AND SYSTEMIC MASTOCYTOSIS

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Rare forms of urticaria

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Systemic Mast Cell Disease

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Pediatric‐onset mastocytosis: A long term clinical follow‐up and correlation with bone marrow histopathology

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How I treat patients with indolent and smoldering mastocytosis (rare conditions but difficult to manage)

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Serum Interleukin-6 Reflects Disease Severity and Osteoporosis in Mastocytosis Patients

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Response of severe systemic mastocytosis to interferon alpha

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ALLERGY Net: High omalizumab dose controls recurrent reactions to venom immunotherapy in indolent systemic mastocytosis

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Photochemotherapy (PUVA) in the treatment of urticaria pigmentosa

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Clonal analysis of NRAS activating mutations in KIT-D816V systemic mastocytosis

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Mastocytosis: molecular mechanisms and clinical disease heterogeneity

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Anaphylaxis and Mast Cell Disorders

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Efficacy and safety of avapritinib in previously treated patients with advanced systemic mastocytosis

Reiter, A., Schwaab, J., DeAngelo, D. J., Gotlib, J. R., Deininger, M. W., Pettit, K. M., Álvarez‐Twöse, I., Vannucchi, A. M., Panse, J., Platzbecker, U., et al. (2022) · Blood Advances · doi:10.1182/bloodadvances.2022007539 · Cited by 44 · see citing works

Low frequency of IgE-mediated food hypersensitivity in mastocytosis

Jarkvist, J., Brockow, K., & Gülen, T. (2020) · The Journal of Allergy and Clinical Immunology In Practice · doi:10.1016/j.jaip.2020.05.044 · Cited by 41 · see citing works

Clinical Outcomes of Adults with Systemic Mastocytosis: A 15-Year Multidisciplinary Experience

Ungerstedt, J. S., Ljung, C., Klimkowska, M., & Gülen, T. (2022) · Cancers · doi:10.3390/cancers14163942 · Cited by 36 · see citing works

Idiopathic Anaphylaxis: a Perplexing Diagnostic Challenge for Allergists

Gülen, T., & Akin, C. (2021) · Current Allergy and Asthma Reports · doi:10.1007/s11882-021-00988-y · Cited by 35 · see citing works

Review and updates on systemic mastocytosis and related entities

Li, J. Y., Ryder, C. B., Zhang, H., Cockey, S. G., Hyjek, E., Moscinski, L. C., Sagatys, E., & Song, J. (2023) · Cancers · doi:10.3390/cancers15235626 · Cited by 31 · see citing works

Safety and efficacy of lirentelimab in patients with refractory indolent systemic mastocytosis: a first-in-human clinical trial

Siebenhaar, F., Altrichter, S., Bonnekoh, H., Hawro, T., Hawro, M., Michaelis, E. G., Kantor, A., Chang, A. T., Youngblood, B. A., Singh, B., et al. (2023) · British Journal of Dermatology · doi:10.1093/bjd/ljad191 · Cited by 30 · see citing works

Non-steroidal anti-inflammatory drug-induced anaphylaxis infrequent in 388 patients with mastocytosis: A two-center retrospective cohort study

Bonadonna, P., Olivieri, F., Jarkvist, J., Nalin, F., Zanotti, R., Maclachlan, L., & Gülen, T. (2022) · Frontiers in Allergy · doi:10.3389/falgy.2022.1071807 · Cited by 25 · see citing works

Everyday life and mastocytosis from a patient perspective—a qualitative study

Jensen, B., Broesby‐Olsen, S., Bindslev‐Jensen, C., & Nielsen, D. S. (2018) · Journal of Clinical Nursing · doi:10.1111/jocn.14676 · Cited by 25 · see citing works

Mastocytosis

Abid, A., Malone, M. A., & Curci, K. M. (2016) · Primary Care Clinics in Office Practice · doi:10.1016/j.pop.2016.04.007 · Cited by 24 · see citing works

Low Prevalence of Idiopathic Mast Cell Activation Syndrome Among 703 Patients With Suspected Mast Cell Disorders

Zaghmout, T., Maclachlan, L., Bedi, N., & Gülen, T. (2024) · The Journal of Allergy and Clinical Immunology: In Practice · doi:10.1016/j.jaip.2023.11.041 · Cited by 23 · see citing works

Diagnostic Significance of Tryptase for Suspected Mast Cell Disorders

Beyens, M., Toscano, A., Ebo, D., Gülen, T., & Sabato, V. (2023) · Diagnostics · doi:10.3390/diagnostics13243662 · Cited by 22 · see citing works

COVID-19 vaccination in the setting of mastocytosis—Pfizer-BioNTech mRNA vaccine is safe and well tolerated

Lazarinis, N., Bossios, A., & Gülen, T. (2022) · The Journal of Allergy and Clinical Immunology In Practice · doi:10.1016/j.jaip.2022.01.037 · Cited by 22 · see citing works

Distinct plasma biomarkers confirm the diagnosis of mastocytosis and identify increased risk of anaphylaxis

Gülen, T., Teufelberger, A. R., Ekoff, M., Westerberg, C. M., Lyberg, K., Dahlén, S., Dahlén, B., & Nilsson, G. P. (2021) · Journal of Allergy and Clinical Immunology · doi:10.1016/j.jaci.2021.02.023 · Cited by 21 · see citing works

A Puzzling Mast Cell Trilogy: Anaphylaxis, MCAS, and Mastocytosis

Gülen, T. (2023) · Diagnostics · doi:10.3390/diagnostics13213307 · Cited by 21 · see citing works

Pharmacotherapy of mast cell disorders

Gülen, T., & Akin, C. (2017) · Current Opinion in Allergy and Clinical Immunology · doi:10.1097/aci.0000000000000377 · Cited by 21 · see citing works

Using the Right Criteria for MCAS

Gülen, T. (2024) · Current Allergy and Asthma Reports · doi:10.1007/s11882-024-01126-0 · Cited by 20 · see citing works

Review of various molecular targets on mast cells and its relation to obesity: A future perspective

Bais, S., Kumari, R., Prashar, Y., & Gill, N. S. (2017) · Diabetes & Metabolic Syndrome Clinical Research & Reviews · doi:10.1016/j.dsx.2017.07.029 · Cited by 20 · see citing works

Systemic Mastocytosis, Kounis Syndrome and Coronary Intervention: Case Report and Systematic Review

Paratz, E. D., Khav, N., & Burns, A. (2017) · Heart Lung and Circulation · doi:10.1016/j.hlc.2016.12.009 · Cited by 18 · see citing works

Non-hematologic diagnosis of systemic mastocytosis: Collaboration of radiology and pathology

Öztürk, K., Caycı, Z., Gotlib, J. R., Akin, C., George, T. I., & Üstün, C. (2020) · Blood Reviews · doi:10.1016/j.blre.2020.100693 · Cited by 16 · see citing works

Drug-Induced Anaphylaxis Uncommon in Mastocytosis: Findings From Two Large Cohorts

Beyens, M. M. J., Sabato, V., Ebo, D. G., Zaghmout, T., & Gülen, T. (2024) · The Journal of Allergy and Clinical Immunology In Practice · doi:10.1016/j.jaip.2024.03.040 · Cited by 15 · see citing works

Management of Mediator Symptoms, Allergy, and Anaphylaxis in Mastocytosis

Gülen, T. (2023) · Immunology and Allergy Clinics of North America · doi:10.1016/j.iac.2023.04.010 · Cited by 14 · see citing works

Mastocytosis and related entities: A practical roadmap

Beyens, M., Elst, J., van der Poorten, M.-L., Van Gasse, A., Toscano, A., Verlinden, A., Vermeulen, K., Maes, M.-B., Oude Elberink, J. N. G. H., Ebo, D., et al. (2023) · Acta Clinica Belgica · doi:10.1080/17843286.2022.2137631 · Cited by 13 · see citing works

Perioperative anaphylaxis to fibrin sealants in children with Noonan Syndrome

Janas‐Naze, A., & Zhang, W. (2022) · Annals of Allergy Asthma & Immunology · doi:10.1016/j.anai.2022.03.014 · Cited by 13 · see citing works

Modeling myeloproliferative neoplasms: From mutations to mouse models and back again

Morotti, A., Rocca, S., Carrà, G., Saglio, G. N., & Brancaccio, M. (2016) · Blood Reviews · doi:10.1016/j.blre.2016.11.004 · Cited by 13 · see citing works

Bone fragility in patients affected by congenital diseases non skeletal in origin

Masi, L., Ferrari, S., Javaid, M. K., Papapoulos, S. E., Pierroz, D. D., Brandi, M. L., & IOF Skeletal Rare Diseases Working Group (2021) · Orphanet Journal of Rare Diseases · doi:10.1186/s13023-020-01611-5 · Cited by 12 · see citing works

Diagnostic Evaluation of Hypersensitivity Reactions to Antibiotics in a Large Cohort of Mastocytosis Patients

Jarkvist, J., & Gülen, T. (2023) · Diagnostics · doi:10.3390/diagnostics13132241 · Cited by 11 · see citing works

The Diagnostic Workup, Screening, and Treatment Approaches for Patients with Delusional Infestation

Coetzee, S., Mahajan, C., & França, K. (2023) · Dermatology and Therapy · doi:10.1007/s13555-023-01053-4 · Cited by 10 · see citing works

SYSTEMIC MASTOCYTOSIS: RADIOLOGICAL POINT OF VIEW

Leone, A., Macagnino, S., D’Ambra, G., & Perla, D. (2021) · Mediterranean Journal of Hematology and Infectious Diseases · doi:10.4084/mjhid.2021.056 · Cited by 10 · see citing works

Histamine Iontophoresis as in vivo Model to Study Human Skin Inflammation with Minimal Barrier Impairment: Pilot Study Results of Application of the Model to a Sensitive Skin Panel

Falcone, D., Uzunbajakava, N. E., Richters, R. J. H., van de Kerkhof, P. C. M., & van Erp, P. E. J. (2017) · Skin Pharmacology and Physiology · doi:10.1159/000477416 · Cited by 8 · see citing works

Multiple vertebral fractures as the first manifestation of systemic mastocytosis

Acosta-Mérida, Á., & Ojeda-Bruno, S. (2019) · Osteoporosis International · doi:10.1007/s00198-019-04897-9 · Cited by 8 · see citing works

The Mastocytosis Control Test: A Patient-Reported Outcome Measure Assessing Disease Control

Siebenhaar, F., Sofi, S., Neisinger, S., Akin, C., Pyatilova, P., Grekowitz, E. M., Haendel, A., Hawro, T., Kiefer, L. A., Magerl, M. A. K., et al. (2024) · The Journal of Allergy and Clinical Immunology In Practice · doi:10.1016/j.jaip.2024.11.021 · Cited by 6 · see citing works

Living with systemic mastocytosis: Balancing between vulnerability and resilience: A qualitative study

Levedahl, K. H., Nilsson, A. K., Ungerstedt, J. S., & Hedström, M. (2022) · European Journal of Oncology Nursing · doi:10.1016/j.ejon.2022.102172 · Cited by 5 · see citing works

How persons with systemic mastocytosis describe the time between symptom onset and receiving diagnosis

Levedahl, K. H., Nilsson, A. K., Johansson, B., & Hedström, M. (2022) · Primary Health Care Research & Development · doi:10.1017/s146342362200024x · Cited by 4 · see citing works

Exploration biologique des mastocytoses et des syndromes d’activation mastocytaire

Brun, M., Sarrat, A., & Vitte, J. (2017) · Revue française d'allergologie · doi:10.1016/j.reval.2017.08.008 · Cited by 4 · see citing works

In reply: Kounis syndrome: A review article on epidemiology, diagnostic findings, management and complications of allergic acute coronary syndrome: Mastocytosis and post-mortem diagnosis

Abdelghany, M., Shah, S., Subedi, R., & Kozman, H. (2017) · International Journal of Cardiology · doi:10.1016/j.ijcard.2017.04.008 · Cited by 4 · see citing works

Pre-emptive Evaluation of Venom Allergy in a Patient with Systemic Mastocytosis

Gülen, T., & Akin, C. (2017) · Acta Dermato Venereologica · doi:10.2340/00015555-2793 · Cited by 3 · see citing works

Mastocytosis in practice of a family doctors

Frolova, T. I., Tereshchenkova, I. I., & Стенкова, Н. Ф. (2018) · Shidnoevropejskij zurnal vnutrisnoi ta simejnoi medicini · doi:10.15407/internalmed2018.01.022 · Cited by 3 · see citing works

Anaphylaxis in Mastocytosis

Gülen, T., Elberink, J. N. G. O., & Brockow, K. (2019) · Springer eBooks · doi:10.1007/978-3-030-27820-5_9 · Cited by 2 · see citing works

Clinical characteristics of mastocytoma in dogs

Ivashkiv, B. B., Mysak, A. R., & Прицак, В. В. (2020) · Науковий вісник Львівського національного університету ветеринарної медицини та біотехнологій імені С.З. Ґжицького · doi:10.32718/nvlvet9825 · Cited by 2 · see citing works

Delayed diagnosis of adult-onset mastocytosis

Cavazos, A., Subrt, P., & Tschen, J. A. (2022) · Baylor University Medical Center Proceedings · doi:10.1080/08998280.2022.2081914 · Cited by 2 · see citing works

Hereditary Alpha-Tryptasemia and Mastocytosis: What We Know and What We Need To Learn

Rama, T. A., & Gülen, T. (2026) · Current Allergy and Asthma Reports · doi:10.1007/s11882-026-01262-9 · Cited by 1 · see citing works

Cardiac complications in a patient affected by systemic mastocytosis and primitive myelofibrosis: A case report

Suppa, M., Marino, L., Piccari, P., Masselli, G., & Gradini, R. (2021) · Clinical Case Reports · doi:10.1002/ccr3.4972 · Cited by 1 · see citing works

Case Report: Multidisciplinary management of a patient with indolent systemic mastocytosis and refractory symptoms

Hamilton, M. J., Greene, L. W., Madigan, L. M., Wang, S. A., Yi, C. A., Kuykendall, A. T., George, T. I., & Castells, M. (2024) · Frontiers in Allergy · doi:10.3389/falgy.2024.1401187 · Cited by 1 · see citing works

Gastrointestinal symptoms in children with mastocytosis

Kasikhina, E. I., Nada, A. Y., Жукова, О. В., & Ostretsova, M. N. (2024) · Meditsinskiy sovet = Medical Council · doi:10.21518/ms2024-415 · Cited by 1 · see citing works

Cutaneous mastocytosis: diagnostic challenges and dietary influences

Al‐Soufi, L., Marashli, A., HajBakri, R. C., & Alshehabi, Z. (2024) · Dermatology Reports · doi:10.4081/dr.2024.10143 · Cited by 1 · see citing works

Management of a Lumbar Burst Fracture Occurring After a Sneeze in a Patient Affected by Systemic Mastocytosis

Iure, F. D., Amendola, L., Fabbri, D., Chehrassan, M., Corghi, A., & Cappuccio, M. (2021) · JBJS Case Connector · doi:10.2106/jbjs.cc.20.00259 · Cited by 1 · see citing works

Mastocytosis

Birn, C. S. (2018) · Gastroenterology Nursing · doi:10.1097/sga.0000000000000344 · Cited by 1 · see citing works

Fracturas vertebrales múltiples en varón joven como primera manifestación de una mastocitosis sistémica

Cubero, C. C., & Carmona, E. C. (2016) · Reumatología Clínica · doi:10.1016/j.reuma.2016.02.006

Regulation of mast cell function and survival in health and disease

Lyberg, K. (2016) · Figshare

Multiple Vertebral Fractures in Young Man as First Manifestation of Systemic Mastocytosis

Cubero, C. C., & Carmona, E. C. (2017) · Reumatología Clínica (English Edition) · doi:10.1016/j.reumae.2016.02.008

Mast Cell Disorders and Anaphylaxis

Alagheband, S., Cranford, C., & Stewart, P. H. (2019) · Springer eBooks · doi:10.1007/978-3-319-58726-4_30-1

A Diffuse Papular Rash in an Adult

Swali, R., Wiggins, C. J., & Tyring, S. K. (2020) · The American Journal of Medicine · doi:10.1016/j.amjmed.2019.12.036

Síndrome de activación mastocitaria. A propósito de un caso clínico

Cardona, R., Muñoz, M., Gómez-Henao, C., Díez-Zuluaga, L. S., & Gálvez, K. (2019) · Revista Alergia México · doi:10.29262/ram.v66i4.587

Mast Cell Disorders and Anaphylaxis

Alagheband, S., Cranford, C., & Stewart, P. H. (2019) · Springer eBooks · doi:10.1007/978-3-030-05147-1_30

Systemic mastocytosis in Croatia

Krečak, I., Rončević, P., Kursar, M., Lucijanić, M., Galušić, D., Mrđenović, S., Perić, M. M., Ivanko, I., Matijaca, H., Budimir, J., et al. (2022) · Liječnički vjesnik · doi:10.26800/lv-144-9-10-3

Comprehensive Review of Mastocytosis From Pathophysiology to Management Strategies

Marchaj, M., Basiaga, B., Żądecka-Kobiałka, K., Putra, A., Bednarz, K., Nowicka-Jasińska, M., Frączyk, P., Bieniek-Zając, S., Baczkowski, S., & Krawiec, K. (2024) · Journal of Education Health and Sport · doi:10.12775/jehs.2024.66.015

Systemic mastocytosis: A rare differential diagnosis to be considered in pediatric patients presenting with cutaneous mastocytosis and seizures

Rajan, S., Shaji, E., & Zachariah, A. A. (2024) · Indian Journal of Case Reports · doi:10.32677/ijcr.v10i5.4517

Plasma Protein Profiling to Discern Indolent from Advanced Systemic Mastocytosis

Iribarren, C., Levedahl, K. H., Atanasoai, I., Mattsson, M., Höglund, M., Söderlund, S., Hägglund, H., Eriksson, N., Carlson, M., & Nilsson, G. P. (2024) · Journal of Molecular Diagnostics · doi:10.1016/j.jmoldx.2024.05.010

Beyond the Usual Suspects: Unraveling Spleen Mastocytosis in Hypersplenism Differential Diagnosis

Silva, I. F., Monteiro-Brás, T., Araújo, I., Caldeira, B., Coelho, R. R., Rodrigues, A. E. O., Fernandes, I. C., Pires, S. X., & Cabral, R. (2024) · Cureus · doi:10.7759/cureus.67124

Systemic Mastocytosis: Diagnosis and Management in 2024

Lee, S. (2024) · Canadian Hematology Today · doi:10.58931/cht.2024.3149

Skin manifestations in perioperative hypersensitivity: state of the art

Lim, X. R., & Thong, B. Y. (2025) · Current Opinion in Allergy and Clinical Immunology · doi:10.1097/aci.0000000000001094

A Conundrum in Coexistence

Sondhi, M., & Hayat, S. (2025) · Arthritis Care & Research · doi:10.1002/acr.25624

Features of the treatment of cutaneous mastocytosis in children

Kasikhina, E. I., Ostretsova, M. N., & Potekaev, N. N. (2025) · Meditsinskiy sovet = Medical Council · doi:10.21518/ms2025-265

Aggressive Systemic Mastocytosis Presenting as Pyrexia of Unknown Origin and Sclerotic Bone Lesions: An Uncommon Presentation of a Rare Haematological Disorder

Ismail, U., & Fatima, S. A. (2025) · Cureus · doi:10.7759/cureus.92162

Hereditary alpha-tryptasemia demonstrates relative basophil enrichment without signs of cellular hyperreactivity

Johnsson, A., Atanasoai, I., Nilsson, G. P., & Gülen, T. (2026) · Journal of Allergy and Clinical Immunology Global · doi:10.1016/j.jacig.2026.100699

Clinical Spectrum of Drug Hypersensitivity Reactions in Systemic Mastocytosis: Drug-Induced Anaphylaxis as a Unique Clinical Presentation

Aslan, E., Okan, K., Kural, R. F., İnan, S., Özeke, Y., Ateş, Ü., Yıldırım, O., Galata, Z., Kırdok, K., Ay, E., et al. (2026) · Medicina · doi:10.3390/medicina62040711

Advances in the Management of Mediator-Related Symptoms in Non-Advanced Systemic Mastocytosis

Gülen, T., & Sabato, V. (2026) · ImmunoTargets and Therapy · doi:10.2147/itt.s609692

Epigenetic alterations in Myeloid Malignancies

Cardoso, B. A. (2026) · Advances in experimental medicine and biology · doi:10.1007/978-3-032-12166-0_12

Barzolvolimab blocks stem cell factor–enhanced IgE activation without inducing apoptosis in KITD816V mast cells

Hu, M., He, J., Luo, Y., Alvarado, D., Miller, D. C., Scheffel, J., Frischbutter, S., Siebenhaar, F., & Pyatilova, P. (2026) · Journal of Allergy and Clinical Immunology · doi:10.1016/j.jaci.2026.08.019

How to Recognise Mastocytosis?

Grattan, C. E. H., Broesby‐Olsen, S., & Brockow, K. (2025) · Clinical & Experimental Allergy · doi:10.1111/cea.14608 · Cited by 3 · see citing works

Diagnosis and classification of mast cell proliferative disorders: delineation from immunologic diseases and non–mast cell hematopoietic neoplasms

Valent, P., Sperr, W. R., Schwartz, L. B., & Horny, H. (2004) · Journal of Allergy and Clinical Immunology · doi:10.1016/j.jaci.2004.02.045 · Cited by 160 · see citing works

Mastocytosis: State of the Art

Horny, H.-P., Sotlar, K., & Valent, P. (2007) · Pathobiology · doi:10.1159/000101711 · Cited by 225 · see citing works

Mastocytosis: a comprehensive insight.

Gysel, D. V., Maeseneer, H. D., & Oranje, A. P. (2016) · PubMed · Cited by 4 · see citing works

Diagnose und Klassifikation der Mastozytose

Brockow, K., Behrendt, H., & Ring, J. (2009) · Allergologie · doi:10.5414/alp32224 · Cited by 3 · see citing works