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Polyglutamine Disorders Including Huntington's Disease

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Inborn and Induced Defects of Mitochondria

Schapira, A. H. V. (1998) · Archives of Neurology · doi:10.1001/archneur.55.10.1293 · Cited by 19

Analysis of brain region-specific co-expression networks reveals clustering of established and novel genes associated with Alzheimer disease

Lancour, D., Dupuis, J., Mayeux, R. P., Haines, J. L., Pericak‐Vance, M. A., Schellenberg, G. D., Crovella, M. E., Farrer, L. A., & Kasif, S. (2020) · Alzheimer s Research & Therapy · doi:10.1186/s13195-020-00674-7 · Cited by 17

Compromised respiratory adaptation and thermoregulation in aging and age-related diseases

Chan, S. L., Wei, Z., Chigurupati, S., & Tu, W. (2009) · Ageing Research Reviews · doi:10.1016/j.arr.2009.09.006 · Cited by 18

Huntington’s Disease: Pathogenic Mechanisms and Therapeutic Targets

Wright, D. J., Renoir, T., Gray, L. J., & Hannan, A. J. (2017) · Advances in neurobiology · doi:10.1007/978-3-319-57193-5_4 · Cited by 17

Imaging in cell-based therapy for neurodegenerative diseases

Kirik, D., Breysse, N., Björklund, T., Besret, L., & Hantraye, P. (2005) · European Journal of Nuclear Medicine and Molecular Imaging · doi:10.1007/s00259-005-1909-6 · Cited by 18

Oxidative DNA Damage: A Role in Altering Neuronal Function

Behrouzi, A., Kelley, M. R., & Fehrenbacher, J. C. (2022) · Journal of Cellular Signaling · doi:10.33696/signaling.3.079 · Cited by 17

Neurodegenerative disorders: Dysregulation of a carefully maintained balance?

Swart, C., Haylett, W. L., Kinnear, C. J., Johnson, G., Bardien, S., & Loos, B. (2014) · Experimental Gerontology · doi:10.1016/j.exger.2014.09.003 · Cited by 19

Complex I Controls Mitochondrial and Plasma Membrane Potentials in Nerve Terminals

Kilbride, S. M., Telford, J. E., & Davey, G. P. (2020) · Neurochemical Research · doi:10.1007/s11064-020-02990-8 · Cited by 17

Age-related mitochondrial alterations in brain and skeletal muscle of the YAC128 model of Huntington disease

Bečanović, K., Asghar, M., Gadawska, I., Sachdeva, S., Walker, D., Lazarowski, E. R., Franciosi, S., Park, K. H. J., Côté, H. C. F., & Leavitt, B. R. (2021) · npj Aging and Mechanisms of Disease · doi:10.1038/s41514-021-00079-2 · Cited by 18

Toxin-induced mitochondrial dysfunction

Browne, S. E., & Beal, M. F. (2002) · International review of neurobiology · doi:10.1016/s0074-7742(02)53010-5 · Cited by 17

Preventing polyglutamine-induced activation of c-Jun delays neuronal dysfunction in a mouse model of SCA7 retinopathy

Mérienne, K., Friedman, J. S., Akimoto, M., Sleymane, G. A., Weber, C., Swaroop, A., & Trottier, Y. (2007) · Neurobiology of Disease · doi:10.1016/j.nbd.2006.11.002 · Cited by 18

HSF1 and Its Role in Huntington’s Disease Pathology

Kim, H., & Gómez‐Pastor, R. (2022) · Advances in experimental medicine and biology · doi:10.1007/5584_2022_742 · Cited by 21

Neonatal Iron Supplementation Induces Striatal Atrophy in Female YAC128 Huntington’s Disease Mice

Berggren, K. L., Lu, Z., Fox, J. A., Dudenhoeffer, M., Agrawal, S., & Fox, J. H. (2016) · Journal of Huntington s Disease · doi:10.3233/jhd-150182 · Cited by 16

Identification of cyclin D1 as a major modulator of 3-nitropropionic acid-induced striatal neurodegeneration

Dietrich, P., Alli, S., Mulligan, M. K., Cox, R., Ashbrook, D. G., Williams, R. W., & Dragatsis, I. (2021) · Neurobiology of Disease · doi:10.1016/j.nbd.2021.105581 · Cited by 16

Huntington's disease

Bonelli, R. M., & Beal, M. F. (2012) · Handbook of clinical neurology · doi:10.1016/b978-0-444-52002-9.00030-9 · Cited by 16

Gastrodia elata alleviates mutant huntingtin aggregation through mitochondrial function and biogenesis mediation

Huang, C., Wang, K.-C., Yang, Y.-C., Chiou, C., Tan, C.-H., Lin, Y., & Huang, N. (2017) · Phytomedicine · doi:10.1016/j.phymed.2017.12.017 · Cited by 16

No Evidence for Increased Oxidative Damage to Lipids, Proteins, or DNA in Huntington's Disease

Alam, Z. I., Halliwell, B. B., & Jenner, P. G. (2000) · Journal of Neurochemistry · doi:10.1046/j.1471-4159.2000.0750840.x · Cited by 50

Oxidative damage to mitochondrial DNA in Huntington's disease parietal cortex

Polidori, M. C., Mecocci, P., Browne, S. E., Senin, U., & Beal, M. F. (1999) · Neuroscience Letters · doi:10.1016/s0304-3940(99)00578-9 · Cited by 211

Oxidative Damage in Huntington's Disease Pathogenesis

Browne, S. E., & Beal, M. F. (2006) · Antioxidants and Redox Signaling · doi:10.1089/ars.2006.8.2061 · Cited by 313

Oxidative stress in Huntington’s disease

Browne, S. E., Ferrante, R. J., & Beal, M. F. (1999) · Brain Pathology · doi:10.1111/j.1750-3639.1999.tb00216.x · Cited by 508

Neurochemistry and toxin models in Huntingtonʼs disease

Beal, M. F. (1994) · Current Opinion in Neurology · doi:10.1097/00019052-199412000-00012 · Cited by 120