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Mitochondrial dynamics in degenerative disease and disease models

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Neuroprotective effects of farnesol on motor and cognitive impairment against 3- nitropropionic acid-induced Huntington’s disease

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Therapeutic advances in Huntington’s disease

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Therapeutic strategies in Huntington?s disease

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ROLE OF REDOX AND CERULOPLASMIN IN IRON DEPOSITION IN GLIAL CELLS: IMPLICATION IN NEURODEGENERATIVE DAMAGES

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Intrinsically Disordered Chaperones and Neurodegeneration

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HUNTINGTON'S DISEASE AND OTHER CHOREAS

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Mitochondrial Degradation, Autophagy and Neurodegenerative Disease

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Brain Bio-Energetic State Does Not Correlate to Muscle Mitochondrial Function in Huntington’s Disease

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What Is the Role of Adenosine Tone and Adenosine Receptors in Huntington’s Disease?

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Herbal remedies against Huntington's disease: Preclinical evidences and future directions

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Huntington’s Disease

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Energy Metabolism in Huntington’s Disease

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Dopamine Neurotoxicity and Neurodegeneration

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THE EFFECT OF NORMOBARIC HYPEROXIA ON SUPEROXIDE DISMUTASE ACTIVITY AND NEUROLOGICAL DEFICITS IN AN ANIMAL MODEL OF HUNTINGTON DISEASE

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Therapeutic Prospects for Polyglutamine Disease

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Huntington's Disease-like 2

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Phytotherapeutic targeting of the mitochondria in neurodegenerative disorders

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BDNF Mitigates Early Oxidative Stress and Promotes Release of Neuroprotective Mitochondria From Striatal Astrocytes of zQ175 Huntington's Disease Mice

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ROS-HIF1α-driven glycolytic reprogramming sustains ATP production in Huntington's disease

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Chief Role of Neuroinflammation and Oxidative Stress in Brain Disorders

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Methylene Blue Attenuates 3-Nitropropionic Acid-Induced Oxidative Stress and Mitochondrial Dysfunction in Striatal Cells: Therapeutic Implications in Huntington’s Disease Neuropathology

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Huntington disease

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Mechanistic Insights into the Polyglutamine Ataxias

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Therapeutics in Huntington’s Disease

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Systemic Administration of 3-Nitropropionic Acid

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Animal Models of Huntington’s Disease

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Caudate Nucleus

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Huntingtin preserves mitochondrial genome integrity in neurons, which is impaired in Huntington’s diseasePreprint

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Molecular mechanisms, clinical phenotypes, and advances in Huntington’s disease therapeutics

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REVIEW ARTICLE Mechanisms of neurodegeneration in Huntington's disease

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Mitochondrial Dynamics and Huntington’s Disease: A Dance of Fate

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Huntington disease

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Huntington Disease and Other Choreas

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Extrachromosomal DNA: Molecular perspectives in aging and neurodegenerative diseases

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Oxidative Stress, Redox Homeostasis and NF-κB Signaling in Neurodegeneration

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Cellular and Molecular Mechanisms of Neuronal Dysfunction in Huntington's Disease

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Assessment of Mitochondrial Complex II and III Activity in Brain Sections: A Histoenzymological Technique

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Protein Oxidation in Some Age‐Related Diseases

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Huntington Disease and Other Genetic Choreas

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Mitochondrial trafficking in healthy and injured neurons

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A Gain of Function of the Huntington’s Disease and Amyotrophic Lateral Sclerosis-Associated Genetic Mutations May Be a Loss of Bioenergetics

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Impairment of neuronal mitophagy by mutant huntingtinPreprint

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Ribosome Profiling Reveals a Dichotomy Between Ribosome Occupancy of Nuclear-Encoded and Mitochondrial-Encoded OXPHOS mRNA Transcripts in a Striatal Cell Model of Huntington DiseasePreprint

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Evidence for glutamate excitotoxicity that occurs before the onset of striatal cell loss and motor symptoms in an ovine Huntington’s Disease modelPreprint

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PEX11β-mediated improvement of mitochondrial dysfunction restores behavioral defect and cellular viability in neuropathological conditionsPreprint

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The molecular pathogenesis of Huntington’s disease

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THE ROLE OF DOPAMINE OXIDATION IN DOPAMINE-INDUCED TOXICITY, INITIATION OF ENDOPLASMIC RETICULUM STRESS, AND POTENTIATION OF ROTENONE-INDUCED TOXICITY IN DIFFERENTIATED PC12 CELLS

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STUDIES OF FACTORS AFFECTING INTRACELLULAR TOXICITY OF THE SCA7 DISEASE PROTEIN ATAXIN - 7 : FOCUS ON ATAXIN-7 DEGRADATION AND OXIDATIVE STRESS

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Chapter 10 Hyperkinetic Movement Disorders

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THE ROLE OF P53 IN OXIDATIVE STRESS AND POLYGLUTAMINE NEUROTOXICITY

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Mechanisms of dopaminergic neurotoxin-induced blood-brain barrier disruption

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Huntington's Disease

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3-AMINOBENZAMIDE, A POLY (ADP-RIBOSE) POLYMERASE INHIBITOR, RESTORES BIOENERGETICS BUT FAILS TO ALLEVIATE EXCITOTOXICITY AND MOTOR FUNCTIONS IN 3-NITROPROPIONIC ACID INTOXICATED MICE

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