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Platelet mitochondria function in Parkinson's disease

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Age‐Dependent Striatal Excitotoxic Lesions Produced by the Endogenous Mitochondrial Inhibitor Malonate

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Regional Mitochondrial Respiratory Activity in Huntington's Disease Brain

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Evidence for a defect in NADH

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Inhibition of Succinate Dehydrogenase by Malonic Acid Produces an “Excitotoxic” Lesion in Rat Striatum

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Genetics and molecular biology of Huntington's disease

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Mitochondrial function and parental sex effect in Huntington's disease

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Neurochemistry and toxin models in Huntingtonʼs disease

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Mitochondrial Impairment Reduces the Threshold for in Vivo NMDA-Mediated Neuronal Death in the Striatum

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Cortical glucose metabolism in Huntington's disease

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Striatal glucose consumption in chorea-free subjects at risk of Huntington's disease

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Mitochondria. A practical approach

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Evidence for glutamate excitotoxicity in Huntington's disease with proton magnetic resonance spectroscopy

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Descending Telencephalic Information Reaches Longitudinal Torus and Cerebellum via the Dorsal Preglomerular Nucleus in the Teleost Fish, Pantodon buchholzi: A Case of Neural Preaptation?

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Mitochondrial Dysfunction and Oxidative Stress in Neurodegenerative Diseases

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Mice deficient in cellular glutathione peroxidase show increased vulnerability to malonate, 3-nitropropionic acid, and 1-methyl-4-phenyl-1,2,5,6-tetrahydropyridine

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Oxidative damage and metabolic dysfunction in Huntington's disease: Selective vulnerability of the basal ganglia

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Mitochondrial Dysfunction in Neurodegenerative Diseases

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Thermoregulatory and metabolic defects in Huntington's disease transgenic mice implicate PGC-1α in Huntington's disease neurodegeneration

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Oxidative stress in the brain: Novel cellular targets that govern survival during neurodegenerative disease

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Neuroprotective Effects of Creatine in a Transgenic Mouse Model of Huntington's Disease

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Oxidative stress in Huntington’s disease

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Dietary restriction normalizes glucose metabolism and BDNF levels, slows disease progression, and increases survival in huntingtin mutant mice

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Energy metabolism defects in Huntington's disease and effects of coenzyme Q₁₀

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Therapeutic Effects of Coenzyme Q₁₀and Remacemide in Transgenic Mouse Models of Huntington's Disease

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Mitochondrial Approaches for Neuroprotection

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Creatine Increases Survival and Delays Motor Symptoms in a Transgenic Animal Model of Huntington's Disease

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Protection from mitochondrial complex II inhibition <i>in vitro</i> and <i>in vivo</i> by Nrf2-mediated transcription

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Brain region‐specific deficit in mitochondrial electron transport chain complexes in children with autism

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The Energetics of Huntington's Disease

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Oxidative Stress and Huntington’s Disease: The Good, the Bad, and the Ugly

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Cannabinoid CB₂receptor agonists protect the striatum against malonate toxicity: Relevance for Huntington's disease

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Generalized brain and skin proteasome inhibition in Huntington’s disease

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Increased basal ganglia iron levels in Huntington disease

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Mitochondria and Huntington's Disease Pathogenesis: Insight from Genetic and Chemical Models

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Creatine therapy provides neuroprotection after onset of clinical symptoms in Huntington's disease transgenic mice

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Huntingtin-deficient zebrafish exhibit defects in iron utilization and development

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Coenzyme Q10 and remacemide hydrochloride ameliorate motor deficits in a Huntington's disease transgenic mouse model

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Nuclear and cytoplasmic huntingtin inclusions exhibit distinct biochemical composition, interactome and ultrastructural properties

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IRS2 increases mitochondrial dysfunction and oxidative stress in a mouse model of Huntington disease

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Dietary plant polyphenols as the potential drugs in neurodegenerative diseases: current evidence, advances, and opportunities

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Clinical correlates of mitochondrial function in Huntington's disease muscle

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Cytopathies involving mitochondrial complex II

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Poly (ADP-ribose) polymerase 1 and neurodegenerative diseases: past, present, and future

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Platelet-derived extracellular vesicles in Huntington’s disease

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3‐Nitropropionic Acid Inhibition of Succinate Dehydrogenase (Complex II) Activity in Cultured Chinese Hamster Ovary Cells: Antagonism by l‐Carnitine

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Mitochondrial Function and Neurodegenerative Diseases

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Altered cholesterol homeostasis contributes to enhanced excitotoxicity in Huntington’s disease

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Effects of striatal excitotoxicity on Huntingtin-like immunoreactivity

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Mutant huntingtin can paradoxically protect neurons from death

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Mitochondrial Respiratory Chain Dysfunction Caused by Coenzyme Q Deficiency

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