Mutations in the mitochondrial GTPase mitofusin 2 cause Charcot-Marie-Tooth neuropathy type 2A

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Mitofusin-2 Determines Mitochondrial Network Architecture and Mitochondrial Metabolism

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Charcot-Marie-Tooth Disease Type 2A Caused by Mutation in a Microtubule Motor KIF1Bβ

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Developmentally Regulated Mitochondrial Fusion Mediated by a Conserved, Novel, Predicted GTPase

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Membrane topology and mitochondrial targeting of mitofusins, ubiquitous mammalian homologs of the transmembrane GTPase Fzo

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Mitochondrial transmission during mating in Saccharomyces cerevisiae is determined by mitochondrial fusion and fission and the intramitochondrial segregation of mitochondrial DNA.

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Mitochondrial filaments and clusters as intracellular power-transmitting cables

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Human cells are protected from mitochondrial dysfunction by complementation of DNA products in fused mitochondria

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Impaired Function is a Common Feature of Neuropathy-Associated Glycyl-tRNA Synthetase Mutations

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Mechanisms of HIV-1 Tat Neurotoxicity via CDK5 Translocation and Hyper-Activation: Role in HIV-Associated Neurocognitive Disorders

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Pharmacotherapeutic options for treating adverse effects of Cisplatin chemotherapy

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Fusion, fission, and transport control asymmetric inheritance of mitochondria and protein aggregates

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Disruption of mitochondrial dynamics increases stress resistance through activation of multiple stress response pathways

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Mitochondrial dynamics define muscle fiber type by modulating cellular metabolic pathways

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Organelle communication: Signaling crossroads between homeostasis and disease

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Sodium Channels, Mitochondria, and Axonal Degeneration in Peripheral Neuropathy

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The Rice Dynamin-Related Protein OsDRP1E Negatively Regulates Programmed Cell Death by Controlling the Release of Cytochrome c from Mitochondria

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Increased association between rough endoplasmic reticulum membranes and mitochondria in transgenic mice that express P301L tau

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Skeletal muscle mitochondrial network dynamics in metabolic disorders and aging

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Proximal nerve magnetization transfer MRI relates to disability in Charcot-Marie-Tooth diseases

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Deficiencies in mitochondrial dynamics sensitize Caenorhabditis elegans to arsenite and other mitochondrial toxicants by reducing mitochondrial adaptability

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SCO2 mutations cause early-onset axonal Charcot-Marie-Tooth disease associated with cellular copper deficiency

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Strategies for fighting mitochondrial diseases

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The influence of aerobic exercise on mitochondrial quality control in skeletal muscle

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Interorganelle communication, aging, and neurodegenerationPreprint

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Mitophagy receptors sense stress signals and couple mitochondrial dynamic machinery for mitochondrial quality control

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Clinical electrophysiology of the optic nerve and retinal ganglion cells

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New insights into mitochondrial fusion

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Estrogen and the regulation of mitochondrial structure and function in the brain

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Mitofusins and the mitochondrial permeability transition: the potential downside of mitochondrial fusion

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Neuropathology of Charcot-Marie-Tooth and Related Disorders

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Crystal structure and functional analysis of MiD49, a receptor for the mitochondrial fission protein Drp1

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Ascorbic acid for the treatment of Charcot-Marie-Tooth disease

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The Fine Tuning of Drp1-Dependent Mitochondrial Remodeling and Autophagy Controls Neuronal Differentiation

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Animal models of inherited neuropathies

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Mitochondrial dynamics and neuronal fate in Parkinson's disease

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Mitochondrial Mutations

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The Phosphorylation-Dependent Regulation of Mitochondrial Proteins in Stress Responses

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Molecular Genetics of Charcot-Marie-Tooth Disease: From Genes to Genomes

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Oligomerization of Dynamin Superfamily Proteins in Health and Disease

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Depletion of Mitofusin-2 Causes Mitochondrial Damage in Cisplatin-Induced Neuropathy

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Loss of Yme1L perturbates mitochondrial dynamics

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Get the balance right: Mitofusins roles in health and disease

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What comes first, misshape or dysfunction? The view from metabolic excess

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Approaches to Finding the Molecular Basis of Mitochondrial Oxidative Phosphorylation Disorders

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Analyzing Neuronal Mitochondria in vivo Using Fluorescent Reporters in Zebrafish

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Mitochondria in the Pulmonary Vasculature in Health and Disease: Oxygen‐Sensing, Metabolism, and Dynamics

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The role of mitochondrial dynamics in mtDNA maintenance

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Bile acids target mitofusin 2 to differentially regulate innate immunity in physiological versus cholestatic conditions

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Curcumin, a potential therapeutic candidate for retinal diseases

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Improved Locus-Specific Database forOPA1Mutations Allows Inclusion of Advanced Clinical Data

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Junctophilin-1 is a modifier gene of GDAP1-related Charcot–Marie–Tooth disease

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Characterization of the mitofusin 2 R94W mutation in a knock‐in mouse model

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Mitofusin-2 over-expresses and leads to dysregulation of cell cycle and cell invasion in lung adenocarcinoma

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Mitochondrial and Axonal Abnormalities Precede Disruption of the Neurofilament Network in a Model of Charcot-Marie-Tooth Disease Type 2E and Are Prevented by Heat Shock Proteins in a Mutant-Specific Fashion

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Possible Role of Mitochondrial Remodelling on Cellular Triacylglycerol Accumulation

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A patient-derived stem cell model of hereditary spastic paraplegia with SPAST mutations

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MFN2point mutations occur in 3.4% of Charcot-Marie-Tooth families. An investigation of 232 Norwegian CMT families

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Microtubule Defects and Neurodegeneration

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Moderate aerobic exercise training ameliorates impairment of mitochondrial function and dynamics in skeletal muscle of high‐fat diet‐induced obese mice

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Noncanonical PDK4 action alters mitochondrial dynamics to affect the cellular respiratory status

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Mitofusins: from mitochondria to fertility

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Energetic and Dynamic: How Mitochondria Meet Neuronal Energy Demands

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Mitophagy and neurodegeneration

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Glucose Stimulation Induces Dynamic Change of Mitochondrial Morphology to Promote Insulin Secretion in the Insulinoma Cell Line INS-1E

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Mitofusin 2 Dysfunction and Disease in Mice and Men

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Molecular Machinery and Pathophysiology of Mitochondrial Dynamics

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Mitochondrial dynamism and the pathogenesis of Amyotrophic Lateral Sclerosis

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Bax Interacting Factor-1 Promotes Survival and Mitochondrial Elongation in Neurons

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Novel insights into SLC25A46-related pathologies in a genetic mouse model

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The tethering function of mitofusin2 controls osteoclast differentiation by modulating the Ca2+–NFATc1 axis

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MFN2 mutations cause compensatory mitochondrial DNA proliferation

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Mitochondrial Dynamics and Liver Cancer

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Mitofusin 2 (MFN2) �쑀�쟾�옄 �룎�뿰蹂��씠媛� �엳�뒗 Charcot-Marie-Tooth 2A �솚�옄�뱾�쓽 �엫�긽 諛� �쑀�쟾�븰�쟻 �듅�꽦

源��꽭�썕, 源��듅誘�, & �꽑�슦�씪�궓 (2006) · YUHSpace (Yonsei University Medical Library)

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