Early mitochondrial calcium defects in Huntington's disease are a direct effect of polyglutamines

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Items 301–400 of 1,000

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  9. Creatine therapy for Huntington’s disease: Clinical and MRS findings in a 1-year pilot study
    Sarah J. Tabrizi, Andrew Matthew Blamire, David Neil Manners, B Rajagopalan, Peter Styles, Anthony H.V. Schapira, Thomas T. Warner · 2003 · Neurology
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  16. Effects of CAG repeat length, HTT protein length and protein context on cerebral metabolism measured using magnetic resonance spectroscopy in transgenic mouse models of Huntington's disease
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  19. Treating neurodegeneration by modifying mitochondria: potential solutions to a “complex” problem
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  41. Protective effects of ginseng saponins on 3-nitropropionic acid-induced striatal degeneration in rats
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  44. Dopamine determines the vulnerability of striatal neurons to the N-terminal fragment of mutant huntingtin through the regulation of mitochondrial complex II
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  47. Abnormal morphology of peripheral cell tissues from patients with Huntington disease
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  48. Impaired mitochondrial trafficking in Huntington's disease
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  49. Bi-phasic dose response in the preclinical and clinical developments of sigma-1 receptor ligands for the treatment of neurodegenerative disorders
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  56. From Pathways to Targets: Understanding the Mechanisms behind Polyglutamine Disease
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  58. Adenosine and glutamate extracellular concentrations and mitogen-activated protein kinases in the striatum of Huntington transgenic mice. Selective antagonism of adenosine A2A receptors reduces transmitter outflow
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  65. Magnetic resonance imaging and spectroscopy in assessing 3-nitropropionic acid-induced brain lesions: an animal model of Huntington’s disease
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  100. HAP1 facilitates effects of mutant huntingtin on inositol 1,4,5‐trisphosphate‐induced Ca2+ release in primary culture of striatal medium spiny neurons
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