Cited by 47Circadian rhythm and melatoninAttention Deficit Hyperactivity DisorderSleep and related disorders

Human CRY1 variants associate with attention deficit/hyperactivity disorder

Open access
Onat, O. Emre, Kars, M. Ece, Gül, Şeref, Bilguvar, Kaya, Wu, Yiming, Özhan, Ayşe, Aydın, Cihan, Başak, A. Nazlı +10 more·2020·Journal of Clinical Investigation

Abstract

Attention deficit/hyperactivity disorder (ADHD) is a common and heritable phenotype frequently accompanied by insomnia, anxiety, and depression. Here, using a reverse phenotyping approach, we report heterozygous coding variations in the core circadian clock gene cryptochrome 1 in 15 unrelated multigenerational families with combined ADHD and insomnia. The variants led to functional alterations in the circadian molecular rhythms, providing a mechanistic link to the behavioral symptoms. One variant, CRY1Δ11 c.1657+3A>C, is present in approximately 1% of Europeans, therefore standing out as a diagnostic and therapeutic marker. We showed by exome sequencing in an independent cohort of patients with combined ADHD and insomnia that 8 of 62 patients and 0 of 369 controls carried CRY1Δ11. Also, we identified a variant, CRY1Δ6 c.825+1G>A, that shows reduced affinity for BMAL1/CLOCK and causes an arrhythmic phenotype. Genotype-phenotype correlation analysis revealed that this variant segregated with ADHD and delayed sleep phase disorder (DSPD) in the affected family. Finally, we found in a phenome-wide association study involving 9438 unrelated adult Europeans that CRY1Δ11 was associated with major depressive disorder, insomnia, and anxiety. These results defined a distinctive group of circadian psychiatric phenotypes that we propose to designate as "circiatric" disorders.

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  • CRY1 and CRY2, implicated in the ADHD-associated dysregulation of the circadian system, are modelled through AMPK activity by MPH improving the impairment of this system.

    “These CLOCK components CRY1 and CRY2, implicated in the ADHD-associated dysregulation of the circadian system [213], are modelled through AMPK activity by MPH improving the impairment of this system [214].”

    From Molecular Characterisation of the Mechanism of Action of Stimulant Drugs Lisdexamfetamine and Methylphenidate on ADHD Neurobiology: A Review (2022) · cites this paper as [214]

    The Introduction reports a strong association between a CRY1 variant, circadian dysfunction, and combined ADHD and delayed sleep phase disorder; the Discussion links pathogenic CRY1 mutations to disruption of the core molecular clock. The cited paper does not establish the same ADHD association for CRY2. The MPH–AMPK statement is attached to citation [214], not this source. (LLM, conf=0.87)

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Authors
Onat, O. E., Kars, M. E., Gül, Ş., Bilguvar, K., Wu, Y., Özhan, A., Aydın, C., Başak, A. N., Trusso, M. A., Goracci, A., Fallerini, C., Renieri, A., Casanova, J.-L., Itan, Y., Atbaşoğlu, C. E., Saka, M. C., Kavaklı, İ. H., & Özçelik, T.
Affiliations
  • Bilkent University (TR)
  • Koç University (TR)
  • Icahn School of Medicine at Mount Sinai (US)
  • Azienda Ospedaliera Universitaria Senese (IT)
  • University of Siena (IT)
  • Hôpital Necker-Enfants Malades (FR)
  • Ankara University (TR)
Venue
Journal of Clinical Investigation
Published
2020-06-15
Volume
130
Issue
7
Pages
3885-3900
ISSN
  • 0021-9738 (ISSN-L)
  • 1558-8238
OpenAlex
W3034207482
Cited by
47
References
10
Citations by year
2026: 7 · 2025: 4 · 2024: 5 · 2023: 9 · 2022: 12 · 2021: 9 · 2020: 1
FWCI
3.98
Type
journal article
Language
en
Open access
Locations
  • Journal of Clinical Investigation (publishedVersion)
  • PubMed (publishedVersion)
  • Bilkent University Institutional Repository (Bilkent University) (submittedVersion)
  • Digital Collections portal (Koç University) (submittedVersion)
  • Use Siena air (University of Siena) (submittedVersion)
Funders
Turkish Academy of Sciences, NIH, INSERM, Rockefeller University, HHMI, French National Research Agency (NIH M#UM1HG006504,U24 HG008956,UL1TR001866,R01AI088364,R01AI127564,R37AI095983,P01AI61093,ANR-10-IAHU-01,ANR-10-LABX-62-IBEID,ANR-14-CE14-0008-01,ANR 14-CE15-0009-01,2013-1-PL BIO-11-INSERM 5-1))
Topics
  • Life Sciences › Neuroscience › Endocrine and Autonomic Systems › Circadian rhythm and melatonin
  • Health Sciences › Medicine › Psychiatry and Mental health › Attention Deficit Hyperactivity Disorder
  • Social Sciences › Psychology › Experimental and Cognitive Psychology › Sleep and related disorders
Keywords
attention deficit hyperactivity disorder, CRY1, clock genes, insomnia, delayed sleep phase syndrome, major depressive disorder, anxiety, genotype-phenotype correlation, phenome-wide association study
MeSH terms
Adult, Attention Deficit Disorder with Hyperactivity, Female, Humans, Male, Mutation, Sleep Disorders, Circadian Rhythm, Genetic Association Studies, CLOCK Proteins, ARNTL Transcription Factors, Cryptochromes, HEK293 Cells

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