The challenges of primary biliary cholangitis: What is new and what needs to be done

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Biochemical response to ursodeoxycholic acid and long-term prognosis in primary biliary cirrhosis

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A Placebo-Controlled Trial of Bezafibrate in Primary Biliary Cholangitis

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Primary Biliary Cirrhosis Associated with <i>HLA, IL12A,</i> and <i>IL12RB2</i> Variants

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New paradigms in the treatment of hepatic cholestasis: from UDCA to FXR, PXR and beyond

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SEROLOGICAL TESTS IN DIAGNOSIS OF PRIMARY BILIARY CIRRHOSIS

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Levels of alkaline phosphatase and bilirubin are surrogate end points of outcomes of patients with primary biliary cirrhosis: an international follow-up study

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Budesonide combined with UDCA to improve liver histology in primary biliary cirrhosis: A three‐year randomized trial†

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Bile Salts Control the Antimicrobial Peptide Cathelicidin Through Nuclear Receptors in the Human Biliary Epithelium

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IL-12/Th1 and IL-23/Th17 Biliary Microenvironment in Primary Biliary Cirrhosis: Implications for Therapy

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Primary biliary cirrhosis is associated with altered hepatic microRNA expression

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Decreased Anion Exchanger 2 Immunoreactivity in the Liver of Patients With Primary Biliary Cirrhosis

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A controlled trial of prednisolone treatment in primary biliary cirrhosis. Three-year results.

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Ae2-Deficient Mice Develop Antimitochondrial Antibodies and Other Features Resembling Primary Biliary Cirrhosis

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Stromal Fibroblasts in Tertiary Lymphoid Structures: A Novel Target in Chronic Inflammation

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Role of nuclear bile acid receptor, FXR, in adaptive ABC transporter regulation by cholic and ursodeoxycholic acid in mouse liver, kidney and intestine

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Development of the bile ducts: Essentials for the clinical hepatologist

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Altered Monocyte Responses to Defined TLR Ligands in Patients With Primary Biliary Cirrhosis *

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Macrophages contribute to the pathogenesis of sclerosing cholangitis in mice

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Loss of tolerance in C57BL/6 mice to the autoantigen E2 subunit of pyruvate dehydrogenase by a xenobiotic with ensuing biliary ductular disease†

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Long-term efficacy and safety of obeticholic acid for patients with primary biliary cholangitis: 3-year results of an international open-label extension study

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NOD.c3c4 congenic mice develop autoimmune biliary disease that serologically and pathogenetically models human primary biliary cirrhosis

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The Nuclear Receptor PPARs as Important Regulators of T-Cell Functions and Autoimmune Diseases

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The FXR agonist PX20606 ameliorates portal hypertension by targeting vascular remodelling and sinusoidal dysfunction

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Incidence and prevalence of primary biliary cirrhosis in the city of Newcastle upon Tyne, England

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Pemphigus autoantibodies generated through somatic mutations target the desmoglein-3 cis-interface

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The Surface-Associated Exopolysaccharide of Bifidobacterium longum 35624 Plays an Essential Role in Dampening Host Proinflammatory Responses and Repressing Local T H 17 Responses

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Comprehensive Analysis of Serum and Fecal Bile Acid Profiles and Interaction with Gut Microbiota in Primary Biliary Cholangitis

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Overlap of Autoimmune Hepatitis and Primary Biliary Cirrhosis: Long-Term Outcomes

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Pharmacokinetics and Pharmacodynamic Action of Budesonide in Early– and Late–Stage Primary Biliary Cirrhosis

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Changes in microbial ecology after fecal microbiota transplantation for recurrent C. difficile infection affected by underlying inflammatory bowel disease

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Hepatic Expression of Secondary Lymphoid Chemokine (CCL21) Promotes the Development of Portal-Associated Lymphoid Tissue in Chronic Inflammatory Liver Disease

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Fractalkine and CX3CR1 are involved in the recruitment of intraepithelial lymphocytes of intrahepatic bile ducts†

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Cognitive impairment in primary biliary cirrhosis: Symptom impact and potential etiology†

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Pretreatment prediction of response to ursodeoxycholic acid in primary biliary cholangitis: development and validation of the UDCA Response Score

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Biochemical and Immunologic Effects of Rituximab in Patients With Primary Biliary Cirrhosis and an Incomplete Response to Ursodeoxycholic Acid

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Immunochip analyses identify a novel risk locus for primary biliary cirrhosis at 13q14, multiple independent associations at four established risk loci and epistasis between 1p31 and 7q32 risk variants

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Primary Biliary Cirrhosis Showing a High Titer of Autoantibody

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Transplantation trends in primary biliary cirrhosis

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Effects of angiogenic factor overexpression by human and rodent cholangiocytes in polycystic liver diseases

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Autoimmune hepatitis overlap syndromes: an evaluation of treatment response, long‐term outcome and survival

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Nuclear receptors as therapeutic targets in cholestatic liver diseases

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Development of autoantibodies precedes clinical manifestations of autoimmune diseases: A comprehensive review

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Bacterial CpG induces hyper-IgM production in CD27+ memory B cells in primary biliary cirrhosis

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A genome-wide association study identifies six novel risk loci for primary biliary cholangitis

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Increasing Prevalence of Primary Biliary Cholangitis and Reduced Mortality With Treatment

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Large-scale characterization study of patients with antimitochondrial antibodies but nonestablished primary biliary cholangitis

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Loss of CFTR Affects Biliary Epithelium Innate Immunity and Causes TLR4–NF-κB—Mediated Inflammatory Response in Mice

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THE RELATIONSHIP BETWEEN SERUM LIPIDS AND SKIN XANTHOMATA IN EIGHTEEN PATIENTS WITH PRIMARY BILIARY CIRRHOSIS

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Factors Associated With Recurrence of Primary Biliary Cholangitis After Liver Transplantation and Effects on Graft and Patient Survival

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Interaction between Toll-like receptors and natural killer cells in the destruction of bile ducts in primary biliary cirrhosis

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B-Cell Depletion With Rituximab in Patients With Primary Biliary Cirrhosis Refractory to Ursodeoxycholic Acid

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Chronic expression of interferon‐gamma leads to murine autoimmune cholangitis with a female predominance

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Deletion of interleukin-12p40 suppresses autoimmune cholangitis in dominant negative transforming growth factor β receptor type II mice #

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IL-10-producing regulatory B cells restrain the T follicular helper cell response in primary Sjögren’s syndrome

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Autoimmune hepatitis-PBC overlap syndrome: a simplified scoring system may assist in the diagnosis

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Combination of ursodeoxycholic acid and glucocorticoids upregulates the AE2 alternate promoter in human liver cells

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Preventive administration of UDCA after liver transplantation for primary biliary cirrhosis is associated with a lower risk of disease recurrence

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Ursodeoxycholic Acid at 18–22 mg/kg/d Showed a Promising Capacity for Treating Refractory Primary Biliary Cholangitis

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